ORTHOLOGY: K12390
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Entry
K12390 KO
Symbol
CLN5
Name
ceroid-lipofuscinosis neuronal protein 5
Pathway
map04142
Lysosome
Disease
H00149
Neuronal ceroid lipofuscinosis
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
K12390 CLN5; ceroid-lipofuscinosis neuronal protein 5
BRITE hierarchy
Genes
HSA:
1203
(CLN5)
PTR:
452607
(CLN5)
PPS:
100983703
(CLN5)
GGO:
101142223
(CLN5)
PON:
100454233
(CLN5)
PPYG:
129011442
(CLN5)
NLE:
100581316
(CLN5)
HMH:
116467361
(CLN5)
SSYN:
129463538
(CLN5)
MCC:
696352
(CLN5)
MCF:
102126341
(CLN5)
MTHB:
126940508
MNI:
105481732
(CLN5)
CSAB:
103214596
(CLN5)
CATY:
105597927
(CLN5)
PANU:
101009061
(CLN5)
TGE:
112610669
(CLN5)
MLEU:
105554268
(CLN5)
RRO:
104671178
(CLN5)
RBB:
108516648
(CLN5)
TFN:
117063669
(CLN5)
PTEH:
111522239
(CLN5)
CANG:
105520241
(CLN5)
CJC:
100405405
(CLN5)
SBQ:
101037602
(CLN5)
CIMI:
108282829
(CLN5)
ANAN:
105730669
(CLN5)
CSYR:
103254967
(CLN5)
MMUR:
105855854
(CLN5)
LCAT:
123648967
(CLN5)
ERUF:
138382637
(CLN5)
PCOQ:
105804994
(CLN5)
OGA:
100948512
(CLN5)
MMU:
211286
(Cln5)
MCAL:
110309187
(Cln5)
MPAH:
110325480
(Cln5)
RNO:
306128
(Cln5)
310166
(Cln5l1)
MCOC:
116085308
(Cln5)
ANU:
117705024
(Cln5)
ASYL:
127691194
(Cln5)
MUN:
110550929
(Cln5)
CGE:
100763877
(Cln5)
MAUA:
101828006
(Cln5)
PROB:
127230125
(Cln5)
PLEU:
114690200
(Cln5)
MORG:
121463994
(Cln5)
MFOT:
126503157
AAMP:
119799789
(Cln5)
CNL:
130885290
(Cln5)
NGI:
103724870
(Cln5)
HGL:
101715781
(Cln5)
CPOC:
100726787
(Cln5)
CCAN:
109695359
109702168
DORD:
105980734
(Cln5)
DSP:
122112520
(Cln5)
DMER:
138811654
138814040
(Cln5)
PLOP:
125348193
(Cln5)
NCAR:
124984580
MMMA:
107153260
(Cln5)
ITI:
101964183
(Cln5)
OCU:
100344063
OPI:
101535162
(CLN5)
OCZ:
121163636
(CLN5)
TUP:
102483815
(CLN5)
GVR:
103588558
(CLN5)
CFA:
485498
(CLN5)
CLUD:
112656104
(CLN5)
VVP:
112934296
(CLN5)
VLG:
121477112
(CLN5)
NPO:
129516385
(CLN5)
AML:
100469545
(CLN5)
UMR:
103659206
(CLN5)
UAH:
113251434
(CLN5)
UAR:
123801089
(CLN5)
ELK:
111146993
LLV:
125094712
MPUF:
101691219
(CLN5)
MNP:
132002803
(CLN5)
MLK:
131814068
(CLN5)
NVS:
122907160
(CLN5)
ORO:
101376758
(CLN5)
EJU:
114211491
(CLN5)
ZCA:
113919337
(CLN5)
113938726
118355991
MLX:
118009323
(CLN5)
MANO:
123839819
(CLN5)
NSU:
110587616
(CLN5)
LWW:
102750921
(CLN5)
FCA:
101085427
(CLN5)
PYU:
121037831
(CLN5)
PCOO:
112860303
(CLN5)
PBG:
122483625
(CLN5)
PVIV:
125162521
(CLN5)
LRUF:
124513110
LGF:
123598940
(CLN5)
AJU:
106965756
PTG:
102971937
(CLN5)
PPAD:
109264204
(CLN5)
PUC:
125933882
PLEZ:
122213885
(CLN5)
HHV:
120245400
(CLN5)
CCRU:
144219970
(CLN5)
BTA:
529186
(CLN5)
BOM:
102267280
(CLN5)
BIU:
109567068
(CLN5)
BBUB:
102395624
(CLN5)
BKE:
129624583
(CLN5)
BBIS:
104999569
(CLN5)
CHX:
102184070
(CLN5)
OAS:
100034668
(CLN5)
BTAX:
128057643
(CLN5)
CSUM:
138089090
(CLN5)
ODA:
120883025
(CLN5)
CCAD:
122447149
(CLN5)
MREE:
136144413
(CLN5)
OVR:
110152933
(CLN5)
MBEZ:
129556431
(CLN5)
SSC:
100152208
(CLN5)
CFR:
102509906
(CLN5)
CBAI:
105083629
(CLN5)
CDK:
105103148
(CLN5)
VPC:
102526564
(CLN5)
BACU:
103003976
(CLN5)
BMUS:
118884034
(CLN5)
LVE:
103074099
(CLN5)
OOR:
101283929
(CLN5)
LALB:
132508964
(CLN5)
GMF:
115843041
(CLN5)
DDP:
132413579
(CLN5)
DLE:
111176479
(CLN5)
PCAD:
102974434
(CLN5)
PSIU:
116743052
(CLN5)
PPHC:
136137718
(CLN5)
NASI:
112405522
(CLN5)
ECB:
100052699
(CLN5)
EPZ:
103554778
(CLN5)
EAI:
106843086
(CLN5)
MYB:
102248244
(CLN5)
MYD:
102771882
(CLN5)
MMYO:
118650336
(CLN5)
MLF:
102421744
(CLN5)
MDT:
132228453
(CLN5)
MYUM:
139006569
(CLN5)
PKL:
118728832
(CLN5)
EFUS:
103288389
(CLN5)
MNA:
107539874
(CLN5)
DRO:
112312497
(CLN5)
SHON:
118996123
(CLN5)
AJM:
119047864
(CLN5)
PDIC:
114508542
(CLN5)
PHAS:
123818732
(CLN5)
MMF:
118622651
(CLN5)
PPAM:
129080921
(CLN5)
HAI:
109389064
(CLN5)
RFQ:
117021279
(CLN5)
PALE:
102891140
(CLN5)
PGIG:
120621521
(CLN5)
PVP:
105304175
(CLN5)
RAY:
107513077
(CLN5)
MJV:
108398687
(CLN5)
TOD:
119259910
(CLN5)
SARA:
101546268
(CLN5)
SFUM:
130019140
(CLN5)
SETR:
126016353
(CLN5)
LAV:
100664362
(CLN5)
TMU:
101356357
ETF:
101638816
(CLN5)
DNM:
101433919
(CLN5)
MDO:
100012768
(CLN5)
GAS:
123242661
(CLN5)
SHR:
100930872
(CLN5)
AFZ:
127553326
PCW:
110198791
(CLN5)
TVP:
118848887
(CLN5)
PBRV:
138145175
(CLN5)
MLAO:
141491182
(CLN5)
OAA:
100081850
(CLN5)
TACU:
119942308
(CLN5)
GGA:
101752092
(CLN5)
PCOC:
116239180
(CLN5)
MGP:
100547560
(CLN5)
CJO:
107308048
(CLN5)
TPAI:
128071576
(CLN5)
LMUT:
125703343
(CLN5)
NMEL:
110408452
(CLN5)
APLA:
101794974
(CLN5)
AACU:
137853777
(CLN5)
OJA:
118163571
(CLN5)
ACYG:
106043928
(CLN5)
CATA:
118255246
(CLN5)
AFUL:
116502017
(CLN5)
TGU:
100220546
(CLN5)
LSR:
110480233
(CLN5)
VMC:
128804377
(CLN5)
SCAN:
103812593
(CLN5)
PMOA:
120504764
(CLN5)
OTC:
121344173
(CLN5)
PRUF:
121355658
(CLN5)
ATRC:
139591861
(CLN5)
GFR:
102032500
(CLN5)
FAB:
101817375
(CLN5)
OMA:
130253163
(CLN5)
PHI:
102102477
(CLN5)
PMAJ:
107201942
(CLN5)
CCAE:
111928525
(CLN5)
CCW:
104695874
(CLN5)
CBRC:
103624433
(CLN5)
ACOE:
138107465
(CLN5)
ETL:
114062622
(CLN5)
ZAB:
102068629
(CLN5)
ZLE:
135447932
(CLN5)
ACHL:
103807354
(CLN5)
SVG:
106850005
(CLN5)
MMEA:
130573785
(CLN5)
HRT:
120748648
(CLN5)
SATI:
136357821
(CLN5)
CFAI:
136285300
(CLN5)
CCIC:
134057792
(CLN5)
FPG:
101918499
(CLN5)
FCH:
102047954
(CLN5)
CCRI:
104164361
(CLN5)
NNT:
104399125
(CLN5)
SHAB:
115603832
(CLN5)
ACUN:
113491190
(CLN5)
ANOC:
141972956
(CLN5)
SURA:
141939541
(CLN5)
TALA:
104364946
(CLN5)
ACHC:
115350551
(CLN5)
HALD:
104321489
(CLN5)
HLE:
104838552
(CLN5)
AGEN:
126045187
HHAR:
128141327
(CLN5)
BBUT:
142039492
(CLN5)
GCL:
127029388
CSTI:
104550427
(CLN5)
LDI:
104350158
(CLN5)
MNB:
103768347
(CLN5)
DPUB:
104310322
(CLN5)
PPUS:
135191478
(CLN5)
AVIT:
104280338
(CLN5)
BRHI:
104491796
(CLN5)
EGZ:
104127057
(CLN5)
NNI:
104018832
(CLN5)
PCRI:
104025893
(CLN5)
PCAO:
104039488
(CLN5)
PARX:
142055194
(CLN5)
PADL:
103923689
(CLN5)
AFOR:
103900952
(CLN5)
FGA:
104075569
(CLN5)
CBOR:
142076575
(CLN5)
CBOY:
140646318
(CLN5)
MAME:
142402672
(CLN5)
CLV:
102096239
(CLN5)
CNIC:
135999928
(CLN5)
MUI:
104548243
(CLN5)
PGUU:
104458960
(CLN5)
PLET:
104618719
(CLN5)
EHS:
104505861
(CLN5)
CMAC:
104473768
(CLN5)
CUCA:
104054969
(CLN5)
TEO:
104369811
(CLN5)
BREG:
104629139
(CLN5)
GAME:
129206595
(CLN5)
OHA:
104336657
(CLN5)
ACAR:
104522737
(CLN5)
CPEA:
104393985
(CLN5)
CVF:
104294426
(CLN5)
RTD:
128913334
(CLN5)
CRID:
134516040
(CLN5)
LMIC:
141733423
(CLN5)
NARQ:
141470577
(CLN5)
AAM:
106491625
(CLN5)
AROW:
112971753
(CLN5)
NPD:
112951761
(CLN5)
TGT:
104570871
(CLN5)
DNE:
112995733
(CLN5)
SCAM:
104147474
(CLN5)
ASN:
102370427
(CLN5)
AMJ:
102567515
(CLN5)
CPOO:
109306432
(CLN5)
GGN:
109303268
(CLN5)
PSS:
102456361
(CLN5)
CIZ:
142010606
(CLN5)
CMY:
102941707
(CLN5)
CCAY:
125637709
(CLN5)
LKP:
140912542
(CLN5)
NDS:
141982294
(CLN5)
DCC:
119849829
(CLN5)
CPIC:
101940237
(CLN5)
TST:
117870880
(CLN5)
CABI:
116836337
(CLN5)
MRV:
120395605
(CLN5)
ACS:
100561102
(cln5)
ASAO:
132771437
(CLN5)
PVT:
110073856
(CLN5)
SUND:
121926674
(CLN5)
PBI:
103060314
(CLN5)
PMUR:
107303130
(CLN5)
CTIG:
120318282
(CLN5)
PGUT:
117665316
(CLN5)
PCAE:
139316320
(CLN5)
APRI:
131200085
(CLN5)
PTEX:
113439431
(CLN5)
NSS:
113415880
(CLN5)
VKO:
123027205
(CLN5)
PMUA:
114596592
(CLN5)
PRAF:
128411967
(CLN5)
ZVI:
118085383
(CLN5)
HCG:
128346462
128351691
(CLN5)
GJA:
107113674
(CLN5)
STOW:
125431467
(CLN5)
EMC:
129325973
(CLN5)
XLA:
100158286
(cln5.L)
XTR:
733746
(cln5)
NPR:
108794351
(CLN5)
RTEM:
120929694
(CLN5)
ACAT:
141127636
(CLN5)
PADS:
140330567
(CLN5)
BBUF:
120995871
(CLN5)
BGAR:
122931258
(CLN5)
DTC:
141094534
(CLN5)
PWL:
138250403
(CLN5)
MUO:
115468689
(CLN5)
GSH:
117363026
(CLN5)
DRE:
569407
(cln5)
SRX:
107728242
107749021
SANH:
107664004
107670900
SGH:
107549738
107549926
CCAR:
109085633
(cln5)
CAUA:
113109038
(cln5)
CGIB:
127965017
PTET:
122351394
(cln5)
LROH:
127170857
(cln5)
GRF:
141340843
(cln5)
OMC:
131546986
(cln5)
PPRM:
120487154
(cln5)
RKG:
130086078
(cln5)
MAMB:
125269901
(cln5)
CIDE:
127518807
CERY:
137036059
(cln5)
MASI:
127446747
127447818
TDW:
130428046
(cln5)
MANU:
129452371
(cln5)
PDAB:
135782641
(cln5)
IPU:
108266343
IFU:
128608805
(cln5)
PHYP:
113525934
(cln5)
SMEO:
124382864
(cln5)
TFD:
113654350
(cln5)
TVC:
132850173
(cln5)
CGAR:
128524091
(cln5)
NGRA:
132891840
(cln5)
TRN:
134324750
(cln5)
AMEX:
103022676
(cln5)
CMAO:
118803600
(cln5)
EEE:
113579019
(cln5)
CHAR:
105893405
(cln5)
SPIL:
134078069
(cln5)
ASAD:
121688355
(cln5)
TRU:
101063269
(cln5)
TFS:
130536957
(cln5)
TNG:
GSTEN00027939G001
LCO:
104921478
(cln5)
NCC:
104958625
(cln5)
TBEN:
117481071
(cln5)
CGOB:
115026313
(cln5)
PGEO:
117466471
(cln5)
GACU:
117544507
(cln5)
EMAC:
134866879
(cln5)
ELY:
117250018
(cln5)
EFO:
125899396
(cln5)
PLEP:
121948873
121963312
SLUC:
116043399
(cln5)
ECRA:
117952397
(cln5)
ESP:
116697874
(cln5)
PFLV:
114564406
(cln5)
GAT:
120833797
(cln5)
PPUG:
119228514
(cln5)
AFB:
129104599
(cln5)
CLUM:
117750196
(cln5)
PSWI:
130203883
(cln5)
CANA:
137782611
(cln5)
CVE:
137866317
(cln5)
MSAM:
119884542
(cln5)
SCHU:
122885873
(cln5)
EARM:
139292154
(cln5)
CUD:
121522197
(cln5)
SPUL:
138592793
(cln5)
LMIX:
132986679
(cln5)
HTC:
141808888
(cln5)
ALAT:
119025713
(cln5)
ASTR:
137605092
(cln5)
PKLU:
139208174
(cln5)
MZE:
101483334
(cln5)
ONL:
100698606
(cln5)
OAU:
116316040
(cln5)
OLA:
101161927
(cln5)
OML:
112154752
(cln5)
CSAI:
133446220
(cln5)
XMA:
102237598
(cln5)
XCO:
114148937
(cln5)
XHE:
116723694
(cln5)
PRET:
103479326
(cln5)
PFOR:
103134733
(cln5)
PLAI:
106962426
(cln5)
PMEI:
106927815
(cln5)
GAF:
122840373
(cln5)
PPRL:
129361124
(cln5)
CVG:
107104579
(cln5)
CTUL:
119794719
(cln5)
GMU:
124871165
(cln5)
NFU:
107389735
(cln5)
KMR:
108232476
(cln5)
ALIM:
106527135
(cln5)
NWH:
119419375
AOCE:
111576529
(cln5)
EJA:
138201089
(cln5)
MCEP:
125017439
(cln5)
CSEM:
103391950
(cln5)
POV:
109637977
(cln5)
SSEN:
122762154
(cln5)
SSOE:
131449624
(cln5)
HHIP:
117755247
(cln5)
HSP:
118119805
(cln5)
PPLT:
128455615
(cln5)
SMAU:
118320550
(cln5)
LCF:
108901245
SDU:
111218128
(cln5)
SLAL:
111673034
(cln5)
XGL:
120801547
(cln5)
HCQ:
109531254
(cln5)
SSCV:
125973447
(cln5)
SBIA:
133511897
(cln5)
PEE:
133411061
(cln5)
PTAO:
133486402
(cln5)
BPEC:
110170639
(cln5)
ENY:
140359720
(cln5)
MALB:
109965427
(cln5)
BSPL:
114847391
(cln5)
SJO:
128367950
(cln5)
SSCO:
133992814
(cln5)
TTY:
137192935
(cln5)
GMH:
115532899
(cln5)
SASA:
106581620
(cln5)
STRU:
115156249
(cln5)
OTW:
112225046
(cln5)
OMY:
110501239
(cln5)
OGO:
124014459
(cln5)
ONE:
115133591
(cln5)
OKI:
109870974
(cln5)
OKE:
118385899
(cln5)
OMM:
135547046
(cln5)
OCLA:
139380406
SALP:
111959332
(cln5)
SNH:
120064475
(cln5)
SFON:
129816425
(cln5)
CCLU:
121546847
(cln5)
ELS:
105031337
(cln5)
OEP:
134017704
(cln5)
SFM:
108920565
(cln5)
PKI:
111852750
(cln5)
AANG:
118213734
(cln5)
AROT:
135241410
(cln5)
CCOG:
133116340
(cln5)
LOC:
102688678
(cln5)
PSPA:
121320930
(cln5)
ARUT:
117406857
(cln5)
PSEX:
120523766
(cln5)
LCM:
102360623
(CLN5)
CMK:
103176898
(cln5)
121852577
RTP:
109911800
(cln5)
CPLA:
122550531
(cln5)
CPUN:
140481557
(cln5)
HOC:
132816399
(cln5)
SCAU:
119977624
(cln5)
LERI:
129697969
(cln5)
HAKA:
140715511
(cln5)
PMRN:
116943473
(CLN5)
116943474
LRJ:
133349961
133349962
BFO:
118419850
BBEL:
109487801
LGI:
LOTGIDRAFT_125348
PVUL:
126831149
PCAN:
112560721
LSAX:
138969307
BARL:
143283998
143298733
BGT:
106051205
GAE:
121376374
HRF:
124115632
124115645
124115646
124115648
124132726
HRJ:
124281897
124285680
124289648
124290006
HASI:
137272048
137272928
137272931
137273077
137274419
HCRA:
139449967
139449970
139449971
139450871
139450873
CRG:
105338453
CANU:
128155357
CVN:
111125418
OED:
125678667
MYI:
110440413
PMAX:
117329276
AIRR:
138327710
YBA:
132544756
MCAF:
127714842
MMER:
123556533
RPHI:
132722867
DPOL:
127876356
127877784
MAEA:
128228691
LJP:
135472394
LAK:
106150521
CCLM:
134189919
134190050
DDI:
DDB_G0275299
(cln5)
DPP:
DICPUDRAFT_50132
DFA:
DFA_06195
(cln5)
EHX:
EMIHUDRAFT_436971
» show all
Taxonomy
UniProt
Reference
PMID:
23160995
Authors
Haddad SE, Khoury M, Daoud M, Kantar R, Harati H, Mousallem T, Alzate O, Meyer B, Boustany RM
Title
CLN5 and CLN8 protein association with ceramide synthase: Biochemical and proteomic approaches.
Journal
Electrophoresis 33:3798-809 (2012)
DOI:
10.1002/elps.201200472
Sequence
[hsa:
1203
]
LinkDB
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DBGET
integrated database retrieval system