ORTHOLOGY: K16816
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Entry
K16816 KO
Symbol
PNPLA2, ATGL
Name
patatin-like phospholipase domain-containing protein 2 [EC:
3.1.1.3
]
Pathway
map00561
Glycerolipid metabolism
map01100
Metabolic pathways
map04714
Thermogenesis
map04923
Regulation of lipolysis in adipocytes
Module
M00098
Acylglycerol degradation
Disease
H01297
Neutral lipid storage disease with myopathy
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09103 Lipid metabolism
00561 Glycerolipid metabolism
K16816 PNPLA2, ATGL; patatin-like phospholipase domain-containing protein 2
09150 Organismal Systems
09152 Endocrine system
04923 Regulation of lipolysis in adipocytes
K16816 PNPLA2, ATGL; patatin-like phospholipase domain-containing protein 2
09159 Environmental adaptation
04714 Thermogenesis
K16816 PNPLA2, ATGL; patatin-like phospholipase domain-containing protein 2
Enzymes [BR:
ko01000
]
3. Hydrolases
3.1 Acting on ester bonds
3.1.1 Carboxylic-ester hydrolases
3.1.1.3 triacylglycerol lipase
K16816 PNPLA2, ATGL; patatin-like phospholipase domain-containing protein 2
BRITE hierarchy
Other DBs
RN:
R02250
R02687
GO:
0004806
Genes
HSA:
57104
(PNPLA2)
PTR:
112207805
450937
(PNPLA2)
PPS:
100970121
(PNPLA2)
GGO:
101145251
(PNPLA2)
PON:
100438169
(PNPLA2)
NLE:
100607328
(PNPLA2)
MCC:
700824
(PNPLA2)
MCF:
102141858
(PNPLA2)
MTHB:
126935831
CSAB:
103233992
(PNPLA2)
CATY:
105577222
(PNPLA2)
PANU:
101013650
(PNPLA2)
TGE:
112607117
(PNPLA2)
RRO:
104681771
(PNPLA2)
RBB:
108513010
(PNPLA2)
TFN:
117079862
(PNPLA2)
PTEH:
111520551
(PNPLA2)
CANG:
105503281
(PNPLA2)
CJC:
100408814
(PNPLA2)
SBQ:
101033046
(PNPLA2)
MMUR:
105874051
(PNPLA2)
LCAT:
123642954
(PNPLA2)
PCOQ:
105816532
(PNPLA2)
OGA:
100947855
(PNPLA2)
MMU:
66853
(Pnpla2)
MCAL:
110298572
(Pnpla2)
MPAH:
110322307
(Pnpla2)
RNO:
361676
(Pnpla2)
MCOC:
116103223
(Pnpla2)
MUN:
110553920
(Pnpla2)
CGE:
100753746
(Pnpla2)
MAUA:
101835287
(Pnpla2)
PLEU:
114693780
(Pnpla2)
MORG:
121458007
(Pnpla2)
MFOT:
126498761
AAMP:
119816161
(Pnpla2)
NGI:
103751092
(Pnpla2)
HGL:
101701275
(Pnpla2)
CPOC:
100732516
(Pnpla2)
CCAN:
109698331
(Pnpla2)
DORD:
105998579
(Pnpla2)
DSP:
122102587
(Pnpla2)
NCAR:
124960604
OPI:
101521600
(PNPLA2)
TUP:
102481526
(PNPLA2)
GVR:
103604003
(PNPLA2)
CFA:
611403
(PNPLA2)
CLUD:
112663249
(PNPLA2)
VVP:
112924122
(PNPLA2)
VLG:
121471418
(PNPLA2)
AML:
100463707
(PNPLA2)
UMR:
103671100
(PNPLA2)
UAH:
113248812
(PNPLA2)
UAR:
123775516
(PNPLA2)
ELK:
111150106
LLV:
125078242
MPUF:
101692455
(PNPLA2)
ORO:
101376822
(PNPLA2)
EJU:
114201537
(PNPLA2)
ZCA:
113915050
(PNPLA2)
MLX:
118016211
(PNPLA2)
NSU:
110580667
(PNPLA2)
LWW:
102726814
(PNPLA2)
FCA:
101082263
(PNPLA2)
PYU:
121022827
(PNPLA2)
PBG:
122484151
(PNPLA2)
LRUF:
124527533
PTG:
102955281
(PNPLA2)
PPAD:
109259787
(PNPLA2)
AJU:
106988897
(PNPLA2)
HHV:
120223431
(PNPLA2)
BTA:
508493
(PNPLA2)
BOM:
102280861
(PNPLA2)
BBUB:
102409429
(PNPLA2)
BBIS:
104998825
(PNPLA2)
CHX:
100860889
(PNPLA2)
OAS:
101123166
(PNPLA2)
ODA:
120874195
(PNPLA2)
CCAD:
122430658
(PNPLA2)
SSC:
100049704
(PNPLA2)
CFR:
102522737
(PNPLA2)
CBAI:
105069757
(PNPLA2)
CDK:
105105445
(PNPLA2)
VPC:
102545377
(PNPLA2)
BACU:
102997570
(PNPLA2)
LVE:
103080064
(PNPLA2)
OOR:
101283683
(PNPLA2)
DLE:
111170300
(PNPLA2)
PCAD:
102980462
(PNPLA2)
PSIU:
116758204
(PNPLA2)
ECB:
100146758
(PNPLA2)
EPZ:
103544296
(PNPLA2)
EAI:
106824961
(PNPLA2)
MYB:
102242697
(PNPLA2)
MYD:
102764823
(PNPLA2)
MMYO:
118648996
(PNPLA2)
MNA:
107542321
(PNPLA2)
PKL:
118717946
(PNPLA2)
HAI:
109375650
(PNPLA2)
DRO:
112317241
(PNPLA2)
SHON:
118982231
(PNPLA2)
AJM:
119062187
(PNPLA2)
PDIC:
114499336
(PNPLA2)
PHAS:
123807331
(PNPLA2)
MMF:
118643197
(PNPLA2)
RFQ:
117029952
(PNPLA2)
PALE:
102878066
(PNPLA2)
PGIG:
120584680
(PNPLA2)
PVP:
105305945
(PNPLA2)
RAY:
107507296
(PNPLA2)
MJV:
108408640
(PNPLA2)
TOD:
119249833
(PNPLA2)
SARA:
101547288
(PNPLA2)
LAV:
100657987
(PNPLA2)
TMU:
101353614
ETF:
101649578
(PNPLA2)
DNM:
101411289
(PNPLA2)
MDO:
100031359
(PNPLA2)
SHR:
100925043
(PNPLA2)
PCW:
110202950
(PNPLA2)
OAA:
103168938
(PNPLA2)
GGA:
418233
(PNPLA3)
431066
(PNPLA2)
PCOC:
116231444
116239020
(PNPLA2)
MGP:
100294555
(PNPLA2)
CJO:
107314514
(PNPLA2)
107317383
NMEL:
110396835
110401530
(PNPLA2)
APLA:
101796497
(PNPLA2)
101802708
ACYG:
106031781
(PNPLA2)
106038244
AFUL:
116489179
116489933
(PNPLA2)
TGU:
100219060
(PNPLA2)
100231669
LSR:
110473186
110484489
(PNPLA2)
SCAN:
103819680
103824075
(PNPLA2)
PMOA:
120507696
120511422
(PNPLA2)
OTC:
121344884
(PNPLA2)
121347853
PRUF:
121351902
121360899
(PNPLA2)
GFR:
102044651
102044787
(PNPLA2)
FAB:
101805858
(PNPLA2)
101820592
PHI:
102100353
(PNPLA2)
102102532
PMAJ:
107205005
107205543
(PNPLA2)
CCAE:
111923366
111930735
(PNPLA2)
CCW:
104688026
(PNPLA2)
104696128
CBRC:
103619970
103620898
(PNPLA2)
ETL:
114064564
114068481
(PNPLA2)
ZAB:
102068522
(PNPLA2)
102072203
ACHL:
103801310
103808279
(PNPLA2)
FPG:
101917296
101922710
(PNPLA2)
FCH:
102055351
102059870
(PNPLA2)
CLV:
102085397
102093271
(PNPLA2)
EGZ:
104127095
(PNPLA2)
104135158
NNI:
104012676
(PNPLA5)
104017312
(PNPLA2)
PLET:
104614711
104626945
PCRI:
104024032
104024972
(PNPLA2)
PCAO:
104047097
104048124
(PNPLA1)
ACUN:
113480980
(PNPLA2)
113490465
TALA:
104363487
104366877
(PNPLA2)
PADL:
103916456
(PNPLA2)
103924466
AFOR:
103896228
(PNPLA2)
103898753
ACHC:
115351746
(PNPLA2)
115352620
HALD:
104315696
(PNPLA2)
104321468
HLE:
104828694
(PNPLA2)
104829392
(PNPLA5)
AGEN:
126046894
126047801
GCL:
127016675
127021437
CCRI:
104166270
(PNPLA2)
104169570
CSTI:
104556172
104563559
(PNPLA2)
EHS:
104506485
(PNPLA2)
104507978
CMAC:
104483937
(PNPLA2)
104486759
MUI:
104541793
104546955
FGA:
104074271
104076872
(PNPLA2)
GSTE:
104251186
104257470
(PNPLA2)
LDI:
104354916
(PNPLA2)
OHA:
104326726
(PNPLA2)
104326998
NNT:
104406957
(PNPLA2)
104410541
DPUB:
104296337
104299845
(PNPLA2)
PGUU:
104459071
(PNPLA2)
104462038
ACAR:
104518832
(PNPLA2)
104522273
CPEA:
104387655
(PNPLA2)
104395097
AVIT:
104276410
104278299
(PNPLA2)
CVF:
104281671
104290297
(PNPLA2)
CUCA:
104067327
(PNPLA5)
104068918
(PNPLA2)
TEO:
104379771
104381342
(PNPLA2)
BRHI:
104500532
104502313
(PNPLA2)
AAM:
106488311
106490004
(PNPLA2)
AROW:
112962696
(PNPLA2)
112967076
NPD:
112943580
(PNPLA2)
112956866
TGT:
104569230
104575011
(PNPLA2)
DNE:
112988036
(PNPLA2)
112991526
SCAM:
104143770
(PNPLA2)
104146640
ASN:
102381486
(PNPLA2)
AMJ:
102569620
(PNPLA2)
CPOO:
109316348
109321166
(PNPLA2)
GGN:
109296345
109299202
(PNPLA2)
PSS:
102443833
102450379
(PNPLA2)
CMY:
102931307
(PNPLA2)
102938324
CPIC:
101936184
101948343
(PNPLA2)
TST:
117871694
117877337
(PNPLA2)
CABI:
116825742
116838665
(PNPLA2)
MRV:
120392979
120403898
(PNPLA2)
ACS:
100551847
(pnpla2)
PVT:
110074181
(PNPLA2)
SUND:
121930050
(PNPLA2)
121931193
PBI:
103048393
(PNPLA2)
PMUR:
107283959
(PNPLA2)
CTIG:
120298306
(PNPLA2)
TSR:
106542070
(PNPLA2)
PGUT:
117665196
(PNPLA2)
VKO:
123021115
(PNPLA2)
123033938
PMUA:
114599534
(PNPLA2)
ZVI:
118088392
(PNPLA2)
GJA:
107116418
(PNPLA2)
STOW:
125426968
(PNPLA2)
125435637
(PNPLA3)
XLA:
108713865
(pnpla2.L)
108715180
(pnpla2.S)
XTR:
780152
(pnpla2)
NPR:
108794583
(PNPLA2)
RTEM:
120917311
(PNPLA2)
BBUF:
120981001
(PNPLA2)
BGAR:
122920167
(PNPLA2)
DRE:
101887155
(pnpla2)
SRX:
107716673
107726855
SANH:
107665735
107674849
107679605
SGH:
107551437
107577070
CCAR:
109051066
109065140
CAUA:
113041015
113042895
113043026
113094068
MAMB:
125246844
(pnpla2)
IPU:
108269288
108274701
(pnpla2)
PHYP:
113529505
(pnpla2)
113546554
SMEO:
124392162
(pnpla2)
TFD:
113654047
(pnpla2)
AMEX:
103023613
103029861
(pnpla2)
EEE:
113588195
TRU:
101061643
(pnpla2)
101066653
101066877
101077770
TNG:
GSTEN00004542G001
GSTEN00004543G001
GSTEN00029863G001
LCO:
104928846
(pnpla2)
104929551
104931885
104937568
NCC:
104941548
104956192
(pnpla2)
104967347
CGOB:
115009445
115009967
115010160
(pnpla2)
115010995
ELY:
117258923
117261910
117262194
117262738
(pnpla2)
EFO:
125886905
125887442
125887874
(pnpla2)
125891590
(pnpla1)
PLEP:
121947371
121950525
121950590
(pnpla2)
121950639
SLUC:
116046811
116046813
116058550
ECRA:
117947636
117948724
(pnpla2)
117948731
117948735
ESP:
116692440
116693591
116693596
116694270
PFLV:
114558527
114559722
114560038
114560097
GAT:
120808694
(pnpla2)
120809531
120829597
PPUG:
119195725
(pnpla2)
119196411
119223144
MSAM:
119893301
(pnpla2)
119905147
CUD:
121515003
(pnpla2)
121515174
121515211
121517178
ALAT:
119023544
119023958
119023963
119024376
(pnpla2)
MZE:
101470022
101482270
101483520
ONL:
100690902
100692445
100697369
100697903
OAU:
116313958
116314001
116326215
(pnpla2)
116330832
OLA:
101155345
101155596
101156893
101168619
OML:
112151928
112151964
112152880
(pnpla2)
112159858
XMA:
102226589
102228835
102237891
XCO:
114151724
114153411
(pnpla2)
114156880
114156892
XHE:
116721947
116730918
116730988
116732186
PRET:
103465704
103465705
103466503
(pnpla2)
103467428
PFOR:
103141311
(pnpla2)
103149658
103156562
103156563
PLAI:
106938997
106939005
106942002
(pnpla2)
106946660
PMEI:
106925505
106930769
(pnpla2)
106933962
106933968
GAF:
122828025
122831272
122835711
(pnpla2)
122835866
CVG:
107092186
107101198
CTUL:
119784346
119787400
(pnpla2)
119798185
GMU:
124855728
124856623
(pnpla2)
124865635
(pnpla1)
NFU:
107388365
107388367
107388678
107390959
KMR:
108229859
(pnpla2)
108235201
108245711
108245735
ALIM:
106521184
106522640
106522811
NWH:
119415787
(pnpla2)
119416090
119417263
AOCE:
111573854
111577265
111580511
MCEP:
125011729
(pnpla1)
125014442
125014443
125015534
(pnpla2)
CSEM:
103379814
103379815
103380279
(pnpla2)
POV:
109624276
109624498
109635035
109648188
(pnpla2)
SSEN:
122775535
122776372
122776514
(pnpla2)
122777289
(pnpla1)
HHIP:
117762912
(pnpla2)
117763670
117764010
HSP:
118109338
118109375
(pnpla2)
118110631
(pnpla1)
LCF:
108877866
108886921
(pnpla2)
108889297
108889299
SDU:
111229787
111229788
111229822
(pnpla2)
SLAL:
111650403
111650476
111667036
111669001
XGL:
120793349
120793552
(pnpla2)
120803292
HCQ:
109507635
(pnpla2)
109528676
109530843
BPEC:
110160334
110160347
110164878
110169305
(pnpla2)
MALB:
109951167
109956420
109968666
109972349
BSPL:
114857222
114857223
114857781
(pnpla2)
114858894
SASA:
106572965
106584779
106590753
106596546
106612943
STRU:
115165257
115192928
115197722
115206838
OTW:
112238871
112242251
(pnpla2)
OMY:
110503375
110512506
110522695
OGO:
124004937
124018191
124032000
124036978
(pnpla2)
ONE:
115122496
115125484
115141301
SALP:
111957907
112070263
SNH:
120052317
(pnpla2)
120066504
CCLU:
121531591
121540758
121587368
ELS:
105006487
105009990
105018061
SFM:
108939144
108941267
(pnpla2)
PKI:
111848020
(pnpla2)
AANG:
118207390
118227161
(pnpla2)
LOC:
102689456
102693732
PSPA:
121294827
(pnpla2)
121329755
ARUT:
117434920
PSEX:
120535878
(pnpla2)
LCM:
102349054
(PNPLA2)
102364578
(PNPLA1)
CMK:
103186006
(pnpla2)
RTP:
109926498
SPU:
582648
APLC:
110975490
SKO:
100374988
ACOZ:
120955150
CPII:
120428645
AME:
551055
ACER:
107993792
ALAB:
122719328
BIM:
100747930
BBIF:
117213842
BVK:
117234400
BVAN:
117163341
BTER:
100651324
BPYO:
122568718
CCAL:
108629084
OBB:
114878435
MGEN:
117217515
NMEA:
116430358
CGIG:
122399516
SOC:
105207573
MPHA:
105831282
AEC:
105144242
ACEP:
105619246
PBAR:
105432178
VEM:
105565342
HST:
105181728
DQU:
106746566
CFO:
105250235
FEX:
115236395
LHU:
105676997
PGC:
109852332
OBO:
105284717
PCF:
106786103
PFUC:
122514765
VPS:
122636730
NVI:
100118986
CSOL:
105365411
CCIN:
107268531
TCA:
659311
(bmm)
DPA:
109534185
ATD:
109598159
NVL:
108562167
API:
100162729
DNX:
107163238
AGS:
114131901
RMD:
113548305
BTAB:
109037409
109040591
CLEC:
106661470
106667235
NLU:
111053138
PHU:
Phum_PHUM457610
ZNE:
110829229
FCD:
110857045
DPX:
DAPPUDRAFT_199604
DAPPUDRAFT_40590
PCHN:
125045619
125045642
HAZT:
108671161
EAF:
111712249
ISC:
IscW_ISCW017608
VJA:
111269670
DPTE:
113795201
CSCU:
111623246
111638480
PTEP:
107455774
SDM:
118192788
LGI:
LOTGIDRAFT_104376
CRG:
105328357
MYI:
110445973
PMAX:
117335822
OSN:
115228520
LAK:
106181783
SMM:
Smp_124390
OVI:
T265_08820
ATEN:
116304047
ADF:
107346163
AMIL:
114958515
PDAM:
113669342
SPIS:
111325998
DGT:
114527358
XEN:
124455523
HMG:
100205181
TAD:
TRIADDRAFT_18195
AQU:
100642049
EHX:
EMIHUDRAFT_432975
» show all
Taxonomy
UniProt
Reference
PMID:
16239926
Authors
Smirnova E, Goldberg EB, Makarova KS, Lin L, Brown WJ, Jackson CL
Title
ATGL has a key role in lipid droplet/adiposome degradation in mammalian cells.
Journal
EMBO Rep 7:106-13 (2006)
DOI:
10.1038/sj.embor.7400559
Reference
PMID:
15550674
Authors
Zimmermann R, Strauss JG, Haemmerle G, Schoiswohl G, Birner-Gruenberger R, Riederer M, Lass A, Neuberger G, Eisenhaber F, Hermetter A, Zechner R
Title
Fat mobilization in adipose tissue is promoted by adipose triglyceride lipase.
Journal
Science 306:1383-6 (2004)
DOI:
10.1126/science.1100747
Sequence
[hsa:
57104
]
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