ORTHOLOGY: K23166
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Entry
K23166 KO
Symbol
OPA3
Name
optic atrophy 3 protein
Disease
H00754
3-Methylglutaconic aciduria
H01020
Optic atrophy
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K23166 OPA3; optic atrophy 3 protein
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial quality control factors
Mitochondrial dynamics
Fission and Fusion factors
K23166 OPA3; optic atrophy 3 protein
BRITE hierarchy
Genes
HSA:
80207
(OPA3)
PTR:
107969761
(OPA3)
PPS:
100987559
(OPA3)
GGO:
101129177
(OPA3)
PON:
100461332
(OPA3)
PPYG:
129019992
(OPA3)
NLE:
100604849
(OPA3)
HMH:
116483766
(OPA3)
SSYN:
129466264
(OPA3)
MCC:
714806
(OPA3)
MCF:
123566765
(OPA3)
MTHB:
126943506
MNI:
105478549
(OPA3)
CSAB:
103234867
(OPA3)
CATY:
105595152
(OPA3)
PANU:
101000953
(OPA3)
TGE:
112612370
(OPA3)
MLEU:
105535861
(OPA3)
RRO:
104673437
(OPA3)
RBB:
108531095
(OPA3)
TFN:
117091409
(OPA3)
PTEH:
111519984
(OPA3)
CANG:
105526880
(OPA3)
CJC:
100409355
(OPA3)
SBQ:
101049854
CIMI:
108285354
(OPA3)
ANAN:
105713072
(OPA3)
105713078
MMUR:
105869539
(OPA3)
LCAT:
123623951
(OPA3)
PCOQ:
105817569
(OPA3)
105817571
OGA:
100965245
(OPA3)
MMU:
102637572
(Gm38499)
403187
(Opa3)
MCAL:
110298879
(Opa3)
115029057
MPAH:
110336649
(Opa3)
110336899
RNO:
308409
(Opa3)
MCOC:
116101745
(Opa3)
ANU:
117712989
(Opa3)
ASYL:
127675717
(Opa3)
MUN:
110551484
110551509
CGE:
100762085
(Opa3)
113837291
113837304
MAUA:
101835118
(Opa3)
PROB:
127238693
(Opa3)
PLEU:
114709854
(Opa3)
PMAV:
102917605
(Opa3)
MORG:
121449573
121449743
MFOT:
126490950
AAMP:
119820688
(Opa3)
119821052
119821844
NGI:
103749197
HGL:
101707936
(Opa3)
101720060
CPOC:
100722414
100735530
CCAN:
109692388
(Opa3)
DORD:
105997996
(Opa3)
DSP:
122125828
DMER:
138811494
138812494
138812908
138814038
PLOP:
125338567
125338958
(Opa3)
NCAR:
124967236
124967458
MMMA:
107151346
ITI:
101974042
(Opa3)
OCU:
100349723
100349976
OPI:
101519897
101520142
OCZ:
121153560
121166915
(OPA3)
TUP:
102484384
(OPA3)
GVR:
103594529
103594534
CFA:
119863922
(OPA3)
CLUD:
112645296
(OPA3)
VVP:
112931310
(OPA3)
VLG:
121478962
121485675
(OPA3)
NPO:
129500116
129500680
AML:
100478264
(OPA3)
UMR:
103657055
103657190
UAH:
113243240
113243423
UAR:
123799488
(OPA3)
ELK:
111160554
LLV:
125090034
MPUF:
101688908
(OPA3)
MNP:
132005398
(OPA3)
MLK:
131818797
(OPA3)
NVS:
122911937
(OPA3)
122913365
ORO:
101370512
101378053
EJU:
114197058
114197177
ZCA:
113935733
(OPA3)
MLX:
117997957
117998148
NSU:
110572688
110572772
(OPA3)
LWW:
102735096
(OPA3)
102735400
FCA:
111556189
(OPA3)
PYU:
121018622
121018873
PBG:
122494941
(OPA3)
122495278
PVIV:
125152503
(OPA3)
LRUF:
124511016
124511717
LGF:
123578195
(OPA3)
AJU:
106973644
PTG:
102949269
(OPA3)
PPAD:
109253232
(OPA3)
PUC:
125915375
125916146
PLEZ:
122208895
122209165
(OPA3)
HHV:
120241844
(OPA3)
BTA:
523579
(OPA3)
BOM:
102264875
102281553
(OPA3)
BIU:
109572584
(OPA3)
BBUB:
102390691
(OPA3)
BBIS:
104997704
(OPA3)
CHX:
102171909
(OPA3)
OAS:
101114131
(OPA3)
BTAX:
128062940
(OPA3)
CSUM:
138096839
(OPA3)
138097078
ODA:
120872332
(OPA3)
CCAD:
122420262
122421256
MREE:
136161460
136161461
OVR:
110139934
(OPA3)
MBEZ:
129546666
(OPA3)
SSC:
106508274
(OPA3)
CFR:
102505094
(OPA3)
CBAI:
105062522
(OPA3)
CDK:
105095445
(OPA3)
VPC:
102539596
(OPA3)
BACU:
103013852
(OPA3)
BMUS:
118884677
118884678
LVE:
103068538
103091656
OOR:
101272441
101272684
LALB:
132509689
(OPA3)
132509690
GMF:
115862297
(OPA3)
DDP:
132416563
(OPA3)
DLE:
111180732
(OPA3)
PCAD:
102982836
(OPA3)
102996508
PSIU:
116743556
116743557
PPHC:
136140207
136140208
NASI:
112415275
112415656
ECB:
100070858
(OPA3)
EPZ:
103566347
(OPA3)
EAI:
106843759
(OPA3)
MYB:
102246614
(OPA3)
MYD:
102768632
(OPA3)
MMYO:
118652803
118674693
MLF:
102442534
(OPA3)
MDT:
132216733
(OPA3)
MYUM:
138999691
(OPA3)
PKL:
118706838
118706841
EFUS:
103301434
129147066
MNA:
107536782
(OPA3)
DRO:
112312851
112312946
(OPA3)
SHON:
118995567
(OPA3)
AJM:
119051333
(OPA3)
PDIC:
114511342
(OPA3)
PHAS:
123822984
(OPA3)
MMF:
118638392
(OPA3)
118638887
PPAM:
129082674
129082865
HAI:
109374707
109374745
RFQ:
117034540
117034541
PALE:
102893331
(OPA3)
PGIG:
120605303
(OPA3)
PVP:
105297339
(OPA3)
MJV:
108392095
TOD:
119248660
119248664
119249447
SARA:
101537454
101539848
SFUM:
130043848
(OPA3)
SETR:
126028262
(OPA3)
LAV:
100675353
111749541
(OPA3)
TMU:
101342180
101355882
ETF:
101649630
(OPA3)
DNM:
101411557
101442512
(OPA3)
MDO:
100011547
(OPA3)
GAS:
123239971
(OPA3)
SHR:
100931395
(OPA3)
AFZ:
127556311
PCW:
110203325
(OPA3)
TVP:
118836352
(OPA3)
PBRV:
138161947
(OPA3)
MLAO:
141509610
(OPA3)
OAA:
114812126
(OPA3)
TACU:
119945973
(OPA3)
GGA:
107057641
(OPA3)
PCOC:
116241805
(OPA3)
MGP:
104916412
(OPA3)
CJO:
107325056
(OPA3)
NMEL:
110391152
(OPA3)
ACYG:
136787472
(OPA3)
TGU:
115493191
(OPA3)
LSR:
110478780
(OPA3)
PMOA:
120508277
(OPA3)
OTC:
121346902
(OPA3)
PRUF:
121357344
(OPA3)
PHI:
102104976
(OPA3)
ACOE:
138100502
(OPA3)
ZLE:
135441995
(OPA3)
SVG:
106864044
(OPA3)
HRT:
120748136
(OPA3)
SATI:
136374865
(OPA3)
CCIC:
134056027
(OPA3)
SHAB:
115603338
(OPA3)
TALA:
122154702
(OPA3)
ACHC:
115338056
115338057
AGEN:
126036011
HHAR:
128137048
(OPA3)
CBOR:
142074088
(OPA3)
CBOY:
140645470
(OPA3)
MAME:
142403792
(OPA3)
CNIC:
136001156
(OPA3)
ASN:
102369584
(OPA3)
AMJ:
102567610
(OPA3)
CPOO:
109322674
(OPA3)
PSS:
102458484
(OPA3)
CIZ:
142024524
(OPA3)
CMY:
102930388
(OPA3)
CCAY:
125629105
(OPA3)
DCC:
119847321
(OPA3)
CPIC:
101935364
(OPA3)
CABI:
116835279
(OPA3)
MRV:
120388699
(OPA3)
ACS:
100554982
(opa3)
ASAO:
132780801
(OPA3)
PVT:
110075751
(OPA3)
SUND:
121915304
(OPA3)
PBI:
103049164
(OPA3)
PMUR:
107291655
(OPA3)
CTIG:
120316482
(OPA3)
TSR:
106546157
(OPA3)
PGUT:
117677809
(OPA3)
PCAE:
139321489
(OPA3)
APRI:
131204770
(OPA3)
PTEX:
113450274
(OPA3)
NSS:
113426477
(OPA3)
VKO:
123026229
(OPA3)
PMUA:
114603129
(OPA3)
PRAF:
128418218
(OPA3)
ZVI:
118086285
(OPA3)
HCG:
128333228
(OPA3)
GJA:
107125469
(OPA3)
STOW:
125434246
(OPA3)
EMC:
129343381
(OPA3)
XLA:
108698513
(opa3.L)
494632
(opa3.S)
XTR:
100485565
(opa3)
NPR:
108804130
(OPA3)
RTEM:
120914381
(OPA3)
120916068
ACAT:
141107383
(OPA3)
BBUF:
121009288
(OPA3)
BGAR:
122922929
122923106
DTC:
141073790
(OPA3)
MUO:
115480908
(OPA3)
GSH:
117365932
(OPA3)
DRE:
497278
(opa3)
SRX:
107705493
107758233
SANH:
107662143
107676748
SGH:
107554481
107560148
CCAR:
109082882
122134005
(opa3)
CAUA:
113061683
113118453
CGIB:
127934025
127977676
PTET:
122362972
(opa3)
LROH:
127180403
(opa3)
GRF:
141346022
(opa3)
OMC:
131524206
(opa3)
PPRM:
120487597
(opa3)
RKG:
130103870
(opa3)
MAMB:
125253794
(opa3)
CIDE:
127499802
CERY:
137022961
(opa3)
MASI:
127417344
127456422
TROS:
130562831
(opa3)
TDW:
130435636
(opa3)
MANU:
129419099
(opa3)
PDAB:
135773193
(opa3)
IPU:
108264292
IFU:
128606496
(opa3)
PHYP:
113526496
(opa3)
SMEO:
124395622
(opa3)
TFD:
113635642
(opa3)
TVC:
132850961
(opa3)
CGAR:
128527909
(opa3)
NGRA:
132887761
(opa3)
TRN:
134323051
(opa3)
AMEX:
103037513
(opa3)
CMAO:
118818342
(opa3)
EEE:
113589585
(opa3)
CHAR:
105897156
(opa3)
SPIL:
134099465
(opa3)
ASAD:
121683990
(opa3)
TRU:
101072560
(opa3)
TFS:
130534659
(opa3)
TNG:
GSTEN00035199G001
LCO:
104934299
(opa3)
NCC:
104960645
(opa3)
TBEN:
117471024
(opa3)
CGOB:
115017790
(opa3)
PGEO:
117457134
(opa3)
GACU:
117555588
(opa3)
EMAC:
134879739
(opa3)
ELY:
117259512
(opa3)
EFO:
125888771
(opa3)
PLEP:
121943619
(opa3)
SLUC:
116040144
(opa3)
ECRA:
117941959
(opa3)
ESP:
116678226
(opa3)
PFLV:
114552820
(opa3)
GAT:
120819262
(opa3)
PPUG:
119211958
(opa3)
AFB:
129095120
(opa3)
CLUM:
117741651
(opa3)
PSWI:
130210647
(opa3)
CANA:
137790860
(opa3)
CVE:
137874734
(opa3)
MSAM:
119882726
(opa3)
SCHU:
122879079
(opa3)
CUD:
121524692
(opa3)
SPUL:
138597324
(opa3)
LMIX:
132980783
(opa3)
HTC:
141798121
(opa3)
ALAT:
119034332
(opa3)
ASTR:
137596982
(opa3)
MZE:
101472855
(opa3)
ONL:
100705817
(opa3)
OAU:
116336487
(opa3)
OLA:
101156266
(opa3)
OML:
112149786
(opa3)
CSAI:
133442021
(opa3)
XMA:
102237899
(opa3)
XCO:
114161858
(opa3)
XHE:
116707607
(opa3)
PRET:
103475108
(opa3)
PFOR:
103138252
(opa3)
PLAI:
106963168
(opa3)
PMEI:
106918558
(opa3)
GAF:
122832127
(opa3)
PPRL:
129359119
(opa3)
CVG:
107091615
(opa3)
CTUL:
119785720
(opa3)
GMU:
124883917
(opa3)
NFU:
107379831
(opa3)
KMR:
108244665
(opa3)
ALIM:
106529667
(opa3)
NWH:
119411424
(opa3)
AOCE:
111579610
(opa3)
EJA:
138205457
(opa3)
BFRE:
138634224
(opa3)
MCEP:
125013485
(opa3)
CSEM:
103377854
(opa3)
POV:
109630104
(opa3)
SSEN:
122772989
(opa3)
SSOE:
131462720
(opa3)
HHIP:
117772400
(opa3)
HSP:
118106711
(opa3)
PPLT:
128440091
(opa3)
128440092
128440094
128440095
128440406
SMAU:
118299764
(opa3)
LCF:
108876154
SDU:
111216950
(opa3)
SLAL:
111662225
(opa3)
XGL:
120791563
(opa3)
HCQ:
109510682
109510695
SSCV:
125972075
(opa3)
SBIA:
133504808
(opa3)
PEE:
133405254
(opa3)
PTAO:
133482154
(opa3)
BPEC:
110163671
(opa3)
ENY:
140366198
(opa3)
MALB:
109963221
(opa3)
BSPL:
114868631
(opa3)
SJO:
128360531
(opa3)
SSCO:
133980502
(opa3)
TTY:
137186415
(opa3)
GMH:
115560716
(opa3)
SASA:
106613367
(opa3)
STRU:
115206701
(opa3)
OTW:
112255828
(opa3)
OMY:
110503273
(opa3)
OGO:
124006506
(opa3)
ONE:
115124783
(opa3)
OKI:
109909297
(opa3)
OKE:
118376680
(opa3)
127926655
OMM:
135546737
(opa3)
OCLA:
139382996
SALP:
112075176
(opa3)
SNH:
120028893
(opa3)
SFON:
129831757
(opa3)
CCLU:
121567841
(opa3)
ELS:
105027017
(opa3)
OEP:
134028701
(opa3)
SFM:
108941950
(opa3)
PKI:
111841460
(opa3)
AANG:
118209600
(opa3)
AROT:
135235553
(opa3)
CCOG:
133108483
(opa3)
LOC:
102685035
(opa3)
PSPA:
121303855
(opa3)
ARUT:
117395957
117415840
PSEX:
120538693
(opa3)
LCM:
102351300
(OPA3)
RTP:
109916827
(opa3)
CPLA:
122542781
(opa3)
CPUN:
140454585
(opa3)
HOC:
132836550
(opa3)
SCAU:
119957824
(opa3)
LERI:
129714111
(opa3)
HAKA:
140737408
(opa3)
PMRN:
116953860
(OPA3)
LRJ:
133356353
(OPA3)
BFO:
118419183
BBEL:
109477136
CIN:
100185809
SCLV:
120325405
SPU:
579385
LPIC:
129264928
LVG:
121419087
AJJ:
139971750
APLC:
110988087
ARUN:
117295289
AAMU:
139936358
AFIL:
140153104
AJC:
117124875
SKO:
100373269
PFLL:
139143210
DME:
Dmel_CG13601
(CG13601)
Dmel_CG43999
(CG43999)
DER:
6555209
6555305
6555306
DSE:
6607644
6607646
DSI:
Dsimw501_GD18338
(Dsim_GD18338)
Dsimw501_GD18339
(Dsim_GD18339)
Dsimw501_GD18341
(Dsim_GD18341)
DYA:
Dyak_GE23909
Dyak_GE23910
Dyak_GE23911
DAN:
6500759
DSR:
110191341
110191343
110191345
DPO:
117184915
4801687
4801688
DPE:
113564948
6587252
6587560
DMN:
108156750
108156751
108156752
DWI:
111519372
6649692
DGR:
116805856
6568120
DMO:
Dmoj_GI10378
Dmoj_GI16934
DAZ:
108613171
108613187
DNV:
108660016
DHE:
111603659
111603661
DVI:
6629938
CCAT:
101451506
101456028
BOD:
106621238
106621239
106625275
BDR:
105224507
105224508
RZE:
108362438
108370216
AOQ:
129236482
129252853
129253165
ALUD:
128855615
128855617
128859002
128871790
TDA:
119683512
MDE:
101897524
SCAC:
106089827
LCQ:
111676090
LSQ:
119604336
CVJ:
135958817
GFS:
119634976
119634988
ECOE:
129942489
CLON:
129611715
HIS:
119652846
AGA:
1281776
ACOZ:
120952162
AARA:
120897831
AMER:
121590524
ASTE:
118506486
AMAP:
126559867
AFUN:
125763112
AMOU:
128310076
AMRS:
128706754
AALI:
118461999
ACOS:
131272591
AAG:
5565063
AALB:
109412100
109430902
ASUA:
134207615
CQU:
CpipJ_CPIJ003331
CPII:
120428782
CBRI:
134834385
CNS:
116352662
BCOO:
119066860
119082717
LLL:
129788024
PPAP:
129798410
AME:
552659
ACER:
107994403
ALAB:
122714940
ADR:
102675191
AFLR:
100871901
BIM:
105680715
BBIF:
117213099
BVK:
117232534
BVAN:
117156296
BHUN:
126871844
BTER:
105665775
BAFF:
126922291
BPYO:
122567583
BPAS:
132912889
FVI:
122529652
CCAL:
108631363
OBB:
114872867
OLG:
117609940
MGEN:
117221357
NMEA:
116427351
CGIG:
122398707
SOC:
105193296
105200334
MPHA:
105831454
105835562
AEC:
105143374
105143960
ACEP:
105620500
ACOC:
108688102
MZT:
108726935
108727645
CCOA:
108773265
108780652
TCZ:
108763008
108767417
TSEP:
108750203
108757074
PBAR:
105433349
VEM:
105558576
105569067
COBS:
139104174
TLN:
139809541
139813827
HST:
105182256
112589842
DQU:
106747324
CFO:
105253789
105257060
FEX:
115232923
115237298
PMEC:
138936856
138941501
LHU:
105673842
105679789
PGC:
109859529
OBO:
105288023
PCF:
106788163
PFUC:
122526590
VPS:
122637312
VCRB:
124421802
VVE:
124954655
NVI:
100118653
103316126
CSOL:
105364649
105365623
TPRE:
106650450
106660306
LHT:
122511862
LBD:
127278464
127281429
MDL:
103576682
CGLO:
123273678
123275204
CTYP:
141531334
FAS:
105272503
DAM:
107046437
AGIF:
122854941
VCAN:
122408748
CCIN:
107269119
DSM:
124414048
NPT:
124223116
NFB:
124186415
NLO:
107223533
NVG:
124308829
AROA:
105683206
105685356
TCA:
103313710
TMOL:
138122610
138129627
DPA:
109537213
ESIM:
136410720
EFOR:
136349284
SOY:
115885115
RFG:
143201316
AGRG:
126743538
ATD:
109602829
CSET:
123306375
HAXR:
123676479
AGB:
108909238
LDC:
111507109
DVV:
126884046
NVL:
108562151
APLN:
112904110
112904113
PPYR:
116171102
116171110
116171118
OTU:
111413786
BMOR:
101745372
BMAN:
114245822
MSEX:
115451521
DPL:
KGM_201909
KGM_202316
BANY:
112044275
MJU:
123874724
NIQ:
126775870
VCD:
124530897
124538223
MCIX:
123662544
PMAC:
106721561
PPOT:
106100979
PXU:
106119982
BPHI:
137919892
PRAP:
110997468
PBX:
123716155
PNAP:
125052940
ZCE:
119828540
CCRC:
123699965
LSIN:
126972414
AAGE:
121725962
HAW:
110373438
HZE:
124640192
TNL:
113504761
SLIU:
111350472
111352562
OFU:
114364964
ONU:
135080587
135088200
ATRA:
106130306
GMW:
113519675
PXY:
105382371
PGW:
126374951
LGLY:
125232495
CSTB:
134748124
CFUM:
141428593
141432619
CFEL:
113364022
113381915
CCRN:
123293187
API:
100163297
DNX:
107173317
AGS:
114120696
RMD:
113548652
ACOO:
126837329
DVT:
126896835
BTAB:
109034673
DCI:
103516403
CLEC:
106668421
HHAL:
106684768
NLU:
111051121
111059300
LDA:
142325103
HVI:
124373882
124373925
MQU:
128983091
PHU:
Phum_PHUM515080
Phum_PHUM515090
FOC:
113218228
TPAL:
117643246
ZNE:
110836783
CSEC:
111862457
PAME:
138704561
SGRE:
126352475
BROR:
134536048
IEL:
124167970
HAMR:
139698933
FCD:
110848877
DPX:
DAPPUDRAFT_5603
DMK:
116921165
DPZ:
124336452
AFRA:
136030554
PVM:
138862687
PJA:
122261261
PCHN:
125029028
PMOO:
119573947
HAME:
121878352
PCLA:
123760412
CQD:
128690935
PTRU:
123517162
ESN:
126999684
MNZ:
135196085
135196399
MRJ:
136840780
PORN:
139756905
HAZT:
108668815
EAF:
111705846
111709096
LSM:
121114375
TCF:
131889528
PPOI:
119093505
119093507
119112369
DSV:
119431263
DALB:
135901401
RSAN:
119406855
RMP:
119163360
VDE:
111249631
VJA:
111271041
GOE:
100903473
TUT:
107365502
DPTE:
113795474
DFR:
124498508
CSCU:
111620623
111620637
111637455
CVS:
136972867
136985344
PTEP:
107450907
ABRU:
129963473
UDV:
129224028
SDM:
118187869
LPOL:
106460078
106461933
106466153
PMEO:
129598539
TSP:
Tsp_11892
HRO:
HELRODRAFT_70587
LGI:
LOTGIDRAFT_154920
LOTGIDRAFT_210779
PVUL:
126821126
PCAN:
112570777
LSAX:
138952162
BARL:
143281231
GAE:
121372087
HRF:
124132328
HRJ:
124255472
124280080
HASI:
137294019
HCRA:
139442927
CRG:
109620899
CANU:
128177175
CVN:
111130724
OED:
130054721
MYI:
110442580
PMAX:
117323768
AIRR:
138319448
YBA:
132559738
MMER:
123535451
RPHI:
132758614
DPOL:
127873813
MAEA:
128207587
128209380
OBI:
106875290
OSN:
115213280
115232495
LAK:
106166138
SMM:
Smp_004280
OVI:
T265_10178
EGL:
EGR_01537
LLON:
135484963
NVE:
5513030
EPA:
110233393
ATEN:
116297024
AMIL:
114954915
MCAZ:
138026136
MFOO:
137979995
PDAM:
113670422
DGT:
114522155
114532963
XEN:
124441710
124442819
HMG:
100213638
HSY:
130656704
RES:
135689209
TAD:
TRIADDRAFT_7238
AQU:
100637385
ATH:
AT1G28510
AT3G58150
ALY:
9314259
9329595
CRB:
17874320
17884918
17898922
CSAT:
104712506
104741461
104757198
104776913
104781732
104792112
EUS:
EUTSA_v10006401mg
EUTSA_v10008880mg
EUTSA_v10019778mg
BRP:
103829003
103835315
103862998
BNA:
106356343
106361681
106380136
106389636
106394784
106395006
BOE:
106304937
106331924
106340307
RSZ:
108834926
108836482
108852969
108860198
THJ:
104812621
104820576
CPAP:
110815124
110822082
CIT:
102619764
102629720
CIC:
CICLE_v10016976mg
CICLE_v10016978mg
PVY:
116106269
116132430
MINC:
123192178
123197061
123218447
TCC:
18596769
18608794
GRA:
105768681
105794839
GHI:
107896958
107909504
107941731
121217754
GAB:
108453602
108461773
HSYR:
120121866
120135583
120171278
120190608
120194866
120215201
DZI:
111275013
111278162
111308469
EGR:
104424966
104440974
RARG:
115739756
115754479
GMX:
100527103
100779734
100817281
GSJ:
114369809
114379519
114417156
PVU:
137832543
VRA:
106755131
106775354
VAR:
108339941
108340956
VUN:
114168887
114187232
VUM:
124833180
124840085
CCAJ:
109806085
109811542
APRC:
113852431
113858570
MTR:
11439259
11441277
TPRA:
123899495
CAM:
101495252
101515038
PSAT:
127081448
127106916
VVO:
131607236
131623209
131629470
LJA:
130726028
130742596
ADU:
107478077
AIP:
107629807
AHF:
112737732
112789858
LANG:
109345590
109351849
PCIN:
129304573
129315470
QSA:
O6P43_000778
O6P43_012701
O6P43_031895
FVE:
101294872
101308647
105350433
AANS:
126788343
126799055
RCN:
112166478
112189244
112203523
PPER:
18778271
18780706
18780971
PMUM:
103326042
103342971
103343488
PAVI:
110769144
110770397
110774468
PDUL:
117623622
117624999
117625341
MDM:
103427862
103446360
103448850
MSYL:
126584482
126590520
126622271
PXB:
103933304
103937017
103944148
PCOX:
137726844
137730014
137741928
ZJU:
107409106
107410400
MNT:
21393837
21398152
CSAV:
115698106
115698610
HLP:
133801572
133817412
CSV:
101205978
101219777
CMO:
103484486
103495636
BHJ:
120074575
120078458
MCHA:
111007808
111012461
CMAX:
111468327
111478633
111497311
CMOS:
111432953
111433530
111455053
CPEP:
111781165
111803180
111811819
RCU:
8281875
8283797
MEAN:
126666276
JCU:
105646867
105649602
HBR:
110633234
110643532
110643548
110643555
110650022
MESC:
110604505
110629683
POP:
18103088
18104552
PEU:
105108562
105134649
PALZ:
118031640
118050425
118050426
PNZ:
133669507
133702975
JRE:
108993650
109004402
CILL:
122275109
122278814
122304071
CAVE:
132168140
132171198
132180485
AGLU:
133861359
133867710
QSU:
112000536
112013414
112020131
QLO:
115956628
115992090
CSAA:
142633622
142637874
142638991
TWL:
119988285
120004375
120005620
VVI:
100265844
100267816
VRI:
117903936
117926398
SLY:
101251516
101256787
101266689
SPEN:
107011131
107024233
107032469
SOT:
102584488
102586765
102590653
SSTN:
125848826
125865388
125877037
SDUL:
129874411
129877756
129891303
CANN:
107844866
107859339
107877402
107878398
LBB:
132616689
132623447
132631216
NTA:
107759184
107769563
107771110
107772012
107794614
107810743
107823058
NSY:
104226261
104227682
104229285
NTO:
104086126
104086565
104093374
104099568
NAU:
109215668
109216043
109228718
109228959
109230566
109230568
INI:
109167808
109171104
ITR:
116021582
116025146
SIND:
105175585
105178461
OEU:
111370303
111372100
111381489
111384816
111392922
111407246
EGT:
105964645
105969171
SSPL:
121743084
121773419
121790616
121811082
SMIL:
130985451
131009183
131011146
SHIS:
125190241
125212719
125215919
APAN:
127249537
127265900
HPUM:
140864437
140883093
PHUA:
140976875
PEBU:
140805324
140813233
140820923
PTAB:
142527890
142548940
CARB:
113687637
113689940
113690235
113726087
113731002
113743469
HAN:
110917160
110921523
110921876
110935056
ECAD:
122593958
122596280
122596388
LSV:
111884656
111894981
111914672
CCAV:
112517845
112522836
112526990
DCR:
108206526
AGRV:
141668352
141698217
CSIN:
114259537
114286721
114289371
114319495
RVL:
131313269
131323138
131331560
AEW:
130773907
130783435
130791169
130795111
DLT:
127792647
127808448
BVG:
104900614
104903432
SOE:
110784029
110798885
CQI:
110689990
110700176
110730506
ATRI:
130805822
130815954
SLAF:
141592898
141596140
141616761
141657188
MOF:
131144205
131148922
NNU:
104599503
104613192
MING:
122066397
122078864
122092833
TSS:
122639319
122652580
PSOM:
113287527
113291192
113304166
113307774
113311624
113329149
113340538
OSA:
4327695
4329131
9268108
DOSA:
Os01g0242300
Os01g0753150
Os02g0312500
OBR:
102712856
102713597
102719248
OGL:
127759843
127763242
127779045
BDI:
100830003
100832874
100842447
ATS:
109760737
109777944
TDC:
119267814
119269021
119275640
119277013
119285629
119305400
TAES:
123060932
123062081
123069484
123070805
123077982
123079195
123115958
123125370
TUA:
125543518
125544824
125554670
125554671
HVG:
123443335
123444431
LPER:
127342164
127343759
127343898
LRD:
124665807
124666788
124667706
124668631
SBI:
8059072
8072084
8077542
ZMA:
100276616
100277999
MFLO:
136451287
136452990
136453245
136459025
136467013
136532742
SITA:
101774741
101781246
101781623
SVS:
117855383
117858745
117858795
PVIR:
120679308
120691277
120708067
PHAI:
112875542
112875864
112894085
PAUA:
133883176
133908760
133918836
TANG:
140768596
140770339
PDA:
103703389
103713157
EGU:
105032208
105040968
105043340
MUS:
103976461
135606840
135607690
ZOF:
122009727
122014517
122051488
DCT:
110091934
110106169
PEQ:
110020545
110036096
AOF:
109845595
MSIN:
131241111
131245299
ACAK:
137955015
137957837
137962946
NCOL:
116246499
ATR:
18442272
CJF:
131040261
SMO:
SELMODRAFT_102874
SELMODRAFT_107205
PPP:
112279219
112279550
112288969
MNG:
MNEG_1776
CVR:
CHLNCDRAFT_143552
OLU:
OSTLU_30344
OTA:
OT_ostta03g00260
BPG:
Bathy14g00220
MIS:
MICPUN_99389
AGO:
AGOS_ACL018W
ERC:
Ecym_3047
KLA:
KLLA0_C05896g
KMX:
KLMA_10258
LTH:
KLTH0C10626g
SLUD:
SCDLUD_000908
DHA:
DEHA2E05698g
PIC:
PICST_53659
PGU:
PGUG_05562
SPAA:
SPAPADRAFT_72332
LEL:
PVL30_001985
LBG:
92207599
(LODBEIA_P24030)
CAL:
CAALFM_C303270WA
(CaO19.326)
CTP:
CTRG_00448
COT:
CORT_0B04490
CDU:
CD36_83220
CTEN:
18247860
(PSN45_000675)
CLU:
CLUG_00614
CLUS:
A9F13_15g00220
CAUR:
CJI96_0002481
ASAU:
88172655
(PUMCH_001590)
PPA:
PAS_chr4_0155
PKZ:
C5L36_0D02860
BNN:
FOA43_003744
OPA:
HPODL_03576
YLI:
2907761
(YALI2_F00939g)
SLB:
AWJ20_1587
NCR:
NCU09257
NTE:
NEUTE1DRAFT143493
(NEUTE1DRAFT_143493)
SMP:
10804985
(SMAC4_04860)
PAN:
PODANSg09992
PBEL:
QC761_107230
PPSD:
QC762_107230
PPSP:
QC763_107230
PPSA:
QC764_107230
MTM:
MYCTH_2294872
CTHR:
CTHT_0054020
RTHE:
98126884
(VTJ83DRAFT_562)
MGR:
MGG_09959
PPEI:
PpBr36_07738
PGRI:
PgNI_06373
SSCK:
SPSK_10626
FGR:
FGSG_01270
FPU:
FPSE_00421
FPOA:
FPOAC1_001366
FVN:
FVRRES_01558
FVR:
FVEG_01401
FOX:
FOXG_00115
FFC:
NCS54_00058400
FKR:
NCS57_00056600
FMU:
J7337_000622
TRE:
TRIREDRAFT_2830
TRR:
M419DRAFT_99307
TATV:
25783571
(TrAtP1_003986)
TASP:
36609986
(TrAFT101_003470)
MAW:
19251822
(J3458_013462)
MAJ:
MAA_00135
MBRN:
26243357
(G6M90_00g108790)
PCHM:
VFPPC_13868
UVI:
66063754
(UV8b_02976)
CMT:
CCM_06971
AMUS:
LMH87_012139
PLJ:
28885457
(PLICBS_007013)
PTKZ:
JDV02_001721
DCON:
63720621
(DCS_07978)
VAL:
VDBG_05976
VDA:
VDAG_03136
CFJ:
CFIO01_10488
CLUP:
CLUP02_05970
CHIG:
CH63R_00988
CDET:
87939720
(CDEST_03217)
SAPO:
SAPIO_CDS3662
ELA:
UCREL1_11024
PFY:
PFICI_01449
SSL:
SS1G_04688
BFU:
BCIN_01g08660
MBE:
MBM_06180
PSCO:
LY89DRAFT_704331
GLZ:
GLAREA_07531
ANI:
ANIA_01559
AFM:
AFUA_8G05670
ACT:
ACLA_059100
NFI:
NFIA_098430
AOR:
AO090005000575
ANG:
An15g04510
AFV:
AFLA_003381
ALUC:
AKAW2_60296S
ACHE:
ACHE_31258A
APUU:
APUU_21641S
PCS:
N7525_002213
PDP:
PDIP_03290
POU:
POX_h09746
TMF:
EYB26_006552
TRG:
TRUGW13939_02295
CIM:
CIMG_08772
CPW:
9696080
(D8B26_004788)
URE:
UREG_02714
ABE:
ARB_05898
TVE:
TRV_06799
PBL:
PAAG_03140
AJE:
HCAG_06166
BGH:
BDBG_02381
PNO:
SNOG_04681
PTE:
PTT_17363
PTRR:
6345917
(PtrM4_140360)
BZE:
COCCADRAFT_87600
BSC:
COCSADRAFT_33863
BOR:
COCMIDRAFT_23528
AALT:
CC77DRAFT_816322
ADAC:
96086901
(ACET3X_006579)
ARAB:
EKO05_0002167
ZTR:
MYCGRDRAFT_72526
PFJ:
MYCFIDRAFT_23654
FFU:
CLAFUR5_07807
CBET:
CB0940_04266
BCOM:
BAUCODRAFT_35065
NPA:
UCRNP2_1311
TML:
GSTUM_00008437001
SPO:
2539959
(opa3)
SOM:
SOMG_01144
(opa3)
CNE:
CNC06580
CNB:
CNBC0620
CNG:
CNAG_01524
CGI:
CGB_C0640C
CDEU:
CNBG_3911
CDEC:
89988286
(IAS62_001511)
CTEG:
91988564
(I308_101706)
CBAS:
91981751
(I312_101703)
CDEP:
91090166
(L203_105958)
KMG:
30165263
(I203_101396)
KNE:
92179708
(IAR55_002450)
KDJ:
28966638
(I303_102919)
KBI:
30205261
(I302_102175)
KPIN:
30171234
(I206_102514)
KSH:
87954811
(IL334_002680)
KER:
91102542
(V865_003739)
KSN:
43591426
(CI109_100882)
KEP:
91093508
(L201_002837)
TMS:
TREMEDRAFT_73990
TASA:
A1Q1_05021
CCAC:
CcaHIS019_0504250
(CcaverHIS019_0504250)
TVS:
TRAVEDRAFT_146752
DSQ:
DICSQDRAFT_113250
PCO:
PHACADRAFT_145226
SHS:
STEHIDRAFT_64672
HIR:
HETIRDRAFT_379059
PSQ:
PUNSTDRAFT_39239
ADL:
AURDEDRAFT_87550
FME:
FOMMEDRAFT_104702
GTR:
GLOTRDRAFT_112759
RSX:
RhiXN_06561
LBC:
LACBIDRAFT_154085
CCI:
CC1G_05294
ABP:
AGABI1DRAFT62322
(AGABI1DRAFT_62322)
ABV:
AGABI2DRAFT188831
(AGABI2DRAFT_188831)
AGABI2DRAFT73503
(AGABI2DRAFT_73503)
MRR:
Moror_4675
MORE:
E1B28_006331
CPUT:
CONPUDRAFT_88085
SLA:
SERLADRAFT_372534
UMA:
UMAG_10141
PFP:
PFL1_01690
SGRA:
EX895_004862
MGL:
MGL_0779
MRT:
MRET_0036
PTRC:
PtA15_11A119
PtA15_7A395
PSTR:
Pst134EA_013314
Pst134EA_013346
MLR:
MELLADRAFT_101179
MELLADRAFT_106493
RIE:
OCT59_010824
MBR:
MONBRDRAFT_23251
SRE:
PTSG_01565
DDI:
DDB_G0284959
DPP:
DICPUDRAFT_11174
PFA:
PF3D7_1459300
PFH:
PFHG_00711
PREI:
PRSY57_1458600
PGAB:
PGSY75_1459300
PLAG:
39744530
(PADL01_1459300)
PYO:
PY17X_1326700
PCB:
PCHAS_1326200
PBE:
PBANKA_1322900
PVV:
PVVCY_1302440
PKN:
PKNH_1222500
PVX:
PVX_117495
PCY:
PCYB_125580
PMAL:
PMUG01_12057600
PBRS:
92372582
(MKS88_004495)
PREL:
PRELSG_1221600
PCOT:
PCOAH_00045220
TAN:
TA19850
TPV:
TP01_0053
TOT:
TOT_010001204
BEQ:
BEWA_034190
BBO:
BBOV_IV000380
BMIC:
BmR1_04g09231
BBIG:
BBBOND_0403640
TGO:
TGME49_254050
BBES:
BESB_012880
TET:
TTHERM_00191250
TTHERM_00348870
PTM:
GSPATT00005474001
GSPATT00010546001
GSPATT00019671001
GSPATT00024151001
GSPATT00036634001
FCY:
FRACYDRAFT_154143
TPS:
THAPSDRAFT_33019
PIF:
PITG_20061
PSOJ:
PHYSODRAFT_328250
SPAR:
SPRG_03850
SPRG_19833
EHX:
EMIHUDRAFT_104959
EMIHUDRAFT_206880
EMIHUDRAFT_233579
GTT:
GUITHDRAFT_46539
» show all
Taxonomy
UniProt
Reference
PMID:
11668429
Authors
Anikster Y, Kleta R, Shaag A, Gahl WA, Elpeleg O
Title
Type III 3-methylglutaconic aciduria (optic atrophy plus syndrome, or Costeff optic atrophy syndrome): identification of the OPA3 gene and its founder mutation in Iraqi Jews.
Journal
Am J Hum Genet 69:1218-24 (2001)
DOI:
10.1086/324651
Sequence
[hsa:
80207
]
LinkDB
All DBs
DBGET
integrated database retrieval system