REACTION: R01701
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Entry
R01701 Reaction
Name
3-methyl-2-oxobutanoate:[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] lipoyllysine 2-oxidoreductase (decarboxylating, acceptor-2-methylpropanoylating)
Definition
3-Methyl-2-oxobutanoic acid + Enzyme N6-(lipoyl)lysine <=> [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine + CO2
Equation
C00141
+
C15972
<=>
C15977
+
C00011
Comment
3-methyl-2-oxobutanoate dehydrogenase complexes:3-methyl-2-oxobutanoate dehydrogenase
a part of multi-step reaction (see
R01701+R02662+R07618
, possibly identical to
R01210
)
subsequently
R02662
TPP-dependent enzyme (see
R07599+R07600
)
Reaction class
RC00627
C15972_C15977
RC02856
C00141_C15977
Enzyme
1.2.4.4
Pathway
rn01100
Metabolic pathways
Orthology
K00166
2-oxoisovalerate dehydrogenase E1 component alpha subunit [EC:
1.2.4.4
]
K00167
2-oxoisovalerate dehydrogenase E1 component beta subunit [EC:
1.2.4.4
]
K11381
2-oxoisovalerate dehydrogenase E1 component [EC:
1.2.4.4
]
Other DBs
RHEA:
13460
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