Danio rerio (zebrafish): 569980
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Entry
569980 CDS
T01004
Symbol
bckdhb
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
KO
K00167
2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:
1.2.4.4
]
Organism
dre
Danio rerio (zebrafish)
Pathway
dre00280
Valine, leucine and isoleucine degradation
dre00640
Propanoate metabolism
dre00785
Lipoic acid metabolism
dre01100
Metabolic pathways
dre01210
2-Oxocarboxylic acid metabolism
Module
dre_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
dre00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
569980 (bckdhb)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
569980 (bckdhb)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
569980 (bckdhb)
Enzymes [BR:
dre01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
569980 (bckdhb)
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GFIT
Motif
Pfam:
Transket_pyr
Transketolase_C
Motif
Other DBs
NCBI-GeneID:
569980
NCBI-ProteinID:
NP_001074122
ZFIN:
ZDB-GENE-030124-2
Ensembl:
ENSDARG00000014676
UniProt:
A1L2C0
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Position
16:complement(5014287..5105295)
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AA seq
391 aa
AA seq
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MAATRLFLRSSCVKSRLTGFTGGVHGSLSLTLLKRSPDCAAQPRAQRRHAAHFTYQPDPV
PTQYGPTQKMNLFQSVTSALDNTLSIDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVFN
TPLCEQGIVGFGIGAAAAGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGNMYDCGKLT
IRSPWGCVGHGSLYHSQSPEAFFAHCPGLKVVVPRGPVQAKGLLLSCIEDKNPCIFFEPK
ILYRAAVEQVPTEAYYIPLSQAEVLQEGSDLTLVAWGTQIHVMREVAAMAQEKLGVSCEL
IDLQTILPWDKETVCKSVMKTGRLLISHEAPVTGGFAAEISSAVQEECFLNLEAPISWVC
GYDTPFPHIFEPFYIPDKWKCFEAVKRMINY
NT seq
1176 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgacgcggctcttcttaagaagttcgtgtgtgaagtctcgtttaacggggttc
actggcggagtgcacggtagtttgagcttaacactgctcaaacggtcgccggactgcgca
gcccagccgcgggcgcagaggagacatgcagcgcacttcacataccagcccgacccggtg
cccactcagtacggcccaacacagaagatgaatttgttccagtctgtgaccagcgccttg
gacaacactctgtccattgacccgaccgcagtcatctttggggaggacgtggcctttggt
ggagtgtttcgatgcacggtcggactccgagataaatacggtaaggaccgtgtgtttaac
actccactgtgtgagcaaggcattgtgggatttgggatcggagcggctgctgccggagcc
accgctattgcagagattcagtttgccgactacattttcccagcatttgatcagattgta
aacgaagcggcgaagtaccgctaccgctcagggaacatgtacgactgtgggaagctgacc
atcagatctccatggggctgcgtgggtcacggatcgctctatcactcccaaagcccagag
gccttcttcgctcactgtcctggattaaaggttgtagtgccgaggggtccagtccaggcc
aagggtctcctattgtcctgcatcgaagataaaaacccctgcatcttctttgagcccaaa
atcctgtacagagcagcagtggagcaggtgccgacagaagcctattacattcccttgtct
caggcagaggtgctgcaggagggcagtgatctgacgctggtggcctgggggactcagatt
catgtgatgcgggaggttgcagccatggctcaggaaaagctgggtgtctcctgtgagctc
atcgaccttcagaccatcctaccctgggacaaagagaccgtctgcaagtcggtgatgaag
acgggtcgtctgctcatcagtcacgaggctccagtgaccggaggtttcgcagcggagatc
agctctgcggttcaggaggagtgtttcctcaacctggaggctcccatcagctgggtttgt
ggatatgatacacctttccctcacatctttgagcctttctacatcccggataagtggaag
tgctttgaggccgtcaagagaatgatcaactactga
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