KEGG   Danio rerio (zebrafish): 777632
Entry
777632            CDS       T01004                                 
Symbol
mccc1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
dre  Danio rerio (zebrafish)
Pathway
dre00280  Valine, leucine and isoleucine degradation
dre01100  Metabolic pathways
Module
dre_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:dre00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    777632 (mccc1)
Enzymes [BR:dre01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     777632 (mccc1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 RimK ATP-grasp_3 ATPgrasp_ST HlyD_3 GARS_A HlyD_D23 ATP-grasp_4 MCC_alpha_BT RnfC_N
Other DBs
NCBI-GeneID: 777632
NCBI-ProteinID: NP_001038380
ZFIN: ZDB-GENE-050208-450
Ensembl: ENSDARG00000102538
UniProt: A0A0R4IH35
LinkDB
Position
22:36875400..36899777
AA seq 711 aa
MAAVFLKTHINGTINKHLLTLIWTKGSVRHGSVGRIEKVVIANRGEIACRVMRTARKMGV
RSVAVYSDADRHSMHVAMADEAYHIGPAASQQSYLCMDKILDVAKKSSAQAVHPGYGFLS
ENTEFAEQCKQEGIIFIGPPSSAIRDMGIKSTSKHIMSAAGVPIIEGYHGDDQSDARLQS
EAARIGYPVMIKAVRGGGGKGMRIAQSEAEFHEQLESARREARKSFNDDVMLIEKFVENP
RHVEVQVFGDQYGDAVYLFERDCSVQRRHQKIIEEAPGPGISPEVRRKLGEAAVRAAKAV
NYVGAGTVEFIMDAQHNFYFMEMNTRLQVEHPVSEMITGTDLVEWQLRVAAGEKLPLSQE
QIELRGHSFEARIYAEDPNNNFLPGAGPLLHLSTPPGDHNTRIETGVREGDEVSAHYDPM
IAKLVVWGEDRSAALKKLRYCLRQYNIVGLNTNIDFLLSLSGHPEFEAGNVHTSFIPQHY
DHLFPPAQSPSGEVICQAALGLLLREKQQTQKYREQTSDVFSPFASSNGRRLNVLQCRNM
SLQLGDNKVAVSITYNPDGTYSMETGGRVFAVSGELQLEGDVTYLCCSVNGVLSRPKLVI
LDNTVHLFSMEGSAQVDVPVPMFLAGVSGSSAQGGAVAPMTGTIEKVLVKAGDSVQKGDP
LMVMIAMKMEHTIRAPKAGVIKKVFFKEGSQASRHAALVEMQEEEEAAGEE
NT seq 2136 nt   +upstreamnt  +downstreamnt
atggctgccgtgtttttgaaaactcacatcaacggaactataaacaaacatctgctgacg
ctgatttggaccaaaggatccgtcagacatggctctgtgggccggatcgagaaggtggtc
atcgctaacagaggagagatcgcctgtcgggtgatgcggacggcgaggaagatgggggtt
cgttcggtcgcggtttacagcgacgcagacagacattccatgcatgtggccatggcggac
gaggcgtatcacatcggtccagcagcgtctcagcagagttacctgtgcatggacaagatc
ctggatgtggccaagaagtcatctgcacaggcggttcaccctggatatggtttcctctct
gaaaacactgagtttgctgaacagtgcaaacaggaaggcatcatcttcattgggcctcca
tcatcagccattcgggacatgggcatcaaaagtacatccaaacacatcatgtcagctgcc
ggcgtgccaatcatcgagggctaccatggggacgaccaatcagatgcgagacttcagagc
gaggcagcgaggattggttaccctgtgatgattaaagcggttcgaggaggcggcggaaag
ggaatgcgaatcgcgcagtctgaagcagagtttcatgaacagctggagtccgcaagaaga
gaagctcgcaaatcctttaatgatgacgtgatgctgattgagaagtttgttgaaaacccc
agacatgtggaggtgcaggtgtttggagatcagtatggggacgctgtgtatctgtttgag
agggactgcagtgttcagagacgacaccagaagatcatcgaggaggctccggggccaggc
atcagtcctgaggtcaggaggaaactcggagaggccgcggttcgagcagctaaggcagtc
aactatgtcggagcaggaactgtggagttcatcatggacgcgcagcacaatttctacttc
atggagatgaacacacgtctgcaggtggagcatccggtctcagagatgatcacaggaact
gacctagtggagtggcagctgcgggtggccgcaggagagaagcttcctctctctcaggag
cagatcgagctgcgaggtcattcgtttgaggccagaatctatgcagaagaccccaataac
aactttcttcccggagcaggacctctgctacacctgtccacaccaccgggagaccacaac
actcgcatcgagacgggggtccgagaaggtgatgaagtgtccgctcattatgacccgatg
atcgctaaactggtggtttggggtgaagatcgttcagccgctctgaagaagctcagatac
tgcctgcgacaatacaacattgtgggtctcaacaccaacatcgacttcctgctgagtctg
tcgggacacccagagtttgaggcggggaacgttcacaccagcttcatcccgcagcactac
gatcatctgtttccacccgctcagagtccgtcaggagaggtgatctgtcaggcggcgctc
ggcctgctgctccgagaaaaacagcagacgcagaaatacagagagcagaccagcgatgtg
ttttctccgtttgcctccagtaacgggagacgtttgaatgtcctgcagtgcagaaacatg
agcctgcagctcggagacaacaaagtggcggtatcaattacctacaaccctgatggcaca
tacagtatggagactggcggtcgggtgtttgctgtatcaggagagctgcagctggagggc
gacgtgacgtacctgtgctgctccgtcaatggagttctgtcccgacccaaactggtcatc
ctggacaacaccgtacacctcttttctatggaaggaagtgctcaagtggacgtcccagtg
cccatgtttctggcaggtgtcagtggctccagtgcacagggtggcgctgttgcacccatg
actggcactattgaaaaggtgttagtcaaggctggagactcggtccagaaaggagatccg
ttaatggtgatgattgccatgaaaatggagcacaccatccgcgcacccaaagccggcgtc
atcaagaaggtgttcttcaaggagggctcgcaggccagcagacatgcagctttggtggag
atgcaggaggaagaggaggccgctggagaagagtaa

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