Homo sapiens (human): 33
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Entry
33 CDS
T01001
Symbol
ACADL, ACAD4, LCAD
Name
(RefSeq) acyl-CoA dehydrogenase long chain
KO
K00255
long-chain-acyl-CoA dehydrogenase [EC:
1.3.8.8
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00071
Fatty acid degradation
hsa01100
Metabolic pathways
hsa01212
Fatty acid metabolism
hsa03320
PPAR signaling pathway
Module
hsa_M00087
beta-Oxidation
Network
nt06020
beta-Oxidation in mitochondria
Element
N00804
beta-Oxidation
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09103 Lipid metabolism
00071 Fatty acid degradation
33 (ACADL)
09150 Organismal Systems
09152 Endocrine system
03320 PPAR signaling pathway
33 (ACADL)
Enzymes [BR:
hsa01000
]
1. Oxidoreductases
1.3 Acting on the CH-CH group of donors
1.3.8 With a flavin as acceptor
1.3.8.8 long-chain acyl-CoA dehydrogenase
33 (ACADL)
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GFIT
Motif
Pfam:
Acyl-CoA_dh_1
Acyl-CoA_dh_N
Acyl-CoA_dh_M
Acyl-CoA_dh_2
ACOX_C_alpha1
Acyl-CoA_ox_N
Motif
Other DBs
NCBI-GeneID:
33
NCBI-ProteinID:
NP_001599
OMIM:
609576
HGNC:
88
Ensembl:
ENSG00000115361
UniProt:
P28330
Structure
PDB
PDBj
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All DBs
Position
2:complement(210187923..210225447)
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AA seq
430 aa
AA seq
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MAARLLRGSLRVLGGHRAPRQLPAARCSHSGGEERLETPSAKKLTDIGIRRIFSPEHDIF
RKSVRKFFQEEVIPHHSEWEKAGEVSREVWEKAGKQGLLGVNIAEHLGGIGGDLYSAAIV
WEEQAYSNCSGPGFSIHSGIVMSYITNHGSEEQIKHFIPQMTAGKCIGAIAMTEPGAGSD
LQGIKTNAKKDGSDWILNGSKVFISNGSLSDVVIVVAVTNHEAPSPAHGISLFLVENGMK
GFIKGRKLHKMGLKAQDTAELFFEDIRLPASALLGEENKGFYYIMKELPQERLLIADVAI
SASEFMFEETRNYVKQRKAFGKTVAHLQTVQHKLAELKTHICVTRAFVDNCLQLHEAKRL
DSATACMAKYWASELQNSVAYDCVQLHGGWGYMWEYPIAKAYVDARVQPIYGGTNEIMKE
LIAREIVFDK
NT seq
1293 nt
NT seq
+upstream
nt +downstream
nt
atggccgcacgccttctccgagggtccctacgcgtcctgggcggccaccgtgcgccgcgc
cagctgcccgccgcgcgatgttctcattccggaggggaagaacgtctagaaactccttct
gctaaaaaattaacagatataggaattcgaagaatcttttctccagagcatgacattttc
cggaaaagtgtaaggaagtttttccaagaagaagtgattcctcatcactcagaatgggag
aaagctggagaagtaagtagggaggtttgggaaaaagctggaaaacaaggactgcttggt
gtcaatattgcagagcatcttggtggaattggaggggatctgtactccgcagctattgtc
tgggaggagcaagcttattcaaattgttcaggcccaggttttagtattcattcaggtatt
gtcatgtcctatattacaaaccatggctcagaagaacagattaagcactttattccccag
atgactgcaggcaaatgtattggtgcaatagcaatgacagagcctggagctggaagtgac
ttacagggaataaaaacaaatgctaaaaaggatggaagtgactggattctcaatggaagc
aaggtgttcatcagtaatgggtcattaagtgatgttgtgattgtagttgcggtcacaaat
catgaagctccctcccctgcccatggtattagcctttttctggtggaaaatggaatgaaa
ggatttatcaagggacgaaagctacataaaatgggattaaaagcccaggataccgcagaa
ctattctttgaagatatacggttgccagctagtgccctacttggagaagagaataaaggc
ttctattacatcatgaaagagcttccacaggaaaggctgttaattgctgatgtggcaatt
tcagctagtgaattcatgtttgaagaaaccaggaactatgttaaacaaagaaaagctttt
ggcaaaacagttgctcacctacagacagtgcaacataaattagcagaattaaaaacacat
atatgtgtaacccgagcatttgtggacaactgtctccagctgcatgaagcgaaacgtttg
gactccgccactgcttgcatggcgaaatattgggcatctgagttacaaaatagtgtagct
tacgactgtgtacagctccatggaggttggggatacatgtgggagtacccaattgcaaaa
gcttatgtggatgccagagttcagccaatctatggtggtacaaatgaaataatgaaggag
ctgattgcaagagagattgtctttgacaagtag
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