Entry |
|
Symbol |
ACADVL, ACAD6, LCACD, VLCAD
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Name |
(RefSeq) acyl-CoA dehydrogenase very long chain
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KO |
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Organism |
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Pathway |
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Module |
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Network |
nt06020 beta-Oxidation in mitochondria |
Element |
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Disease |
H00525 | Disorders of mitochondrial fatty-acid oxidation |
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Brite |
KEGG Orthology (KO) [BR:hsa00001]
09100 Metabolism
09103 Lipid metabolism
00071 Fatty acid degradation
37 (ACADVL)
09160 Human Diseases
09167 Endocrine and metabolic disease
04936 Alcoholic liver disease
37 (ACADVL)
Enzymes [BR:hsa01000]
1. Oxidoreductases
1.3 Acting on the CH-CH group of donors
1.3.8 With a flavin as acceptor
1.3.8.9 very-long-chain acyl-CoA dehydrogenase
37 (ACADVL)
|
SSDB |
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Motif |
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Other DBs |
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Structure |
|
LinkDB |
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Position |
17:7217125..7225266
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AA seq |
655 aa
MQAARMAASLGRQLLRLGGGSSRLTALLGQPRPGPARRPYAGGAAQLALDKSDSHPSDAL
TRKKPAKAESKSFAVGMFKGQLTTDQVFPYPSVLNEEQTQFLKELVEPVSRFFEEVNDPA
KNDALEMVEETTWQGLKELGAFGLQVPSELGGVGLCNTQYARLVEIVGMHDLGVGITLGA
HQSIGFKGILLFGTKAQKEKYLPKLASGETVAAFCLTEPSSGSDAASIRTSAVPSPCGKY
YTLNGSKLWISNGGLADIFTVFAKTPVTDPATGAVKEKITAFVVERGFGGITHGPPEKKM
GIKASNTAEVFFDGVRVPSENVLGEVGSGFKVAMHILNNGRFGMAAALAGTMRGIIAKAV
DHATNRTQFGEKIHNFGLIQEKLARMVMLQYVTESMAYMVSANMDQGATDFQIEAAISKI
FGSEAAWKVTDECIQIMGGMGFMKEPGVERVLRDLRIFRIFEGTNDILRLFVALQGCMDK
GKELSGLGSALKNPFGNAGLLLGEAGKQLRRRAGLGSGLSLSGLVHPELSRSGELAVRAL
EQFATVVEAKLIKHKKGIVNEQFLLQRLADGAIDLYAMVVVLSRASRSLSEGHPTAQHEK
MLCDTWCIEAAARIREGMAALQSDPWQQELYRNFKSISKALVERGGVVTSNPLGF |
NT seq |
1968 nt +upstreamnt +downstreamnt
atgcaggcggctcggatggccgcgagcttggggcggcagctgctgaggctcgggggcgga
agctcgcggctcacggcgctcctggggcagccccggcccggccctgcccggcggccctat
gccgggggtgccgctcagctggctctggacaagtcagattcccacccctctgacgctctg
accaggaaaaaaccggccaaggcggaatctaagtcctttgctgtgggaatgttcaaaggc
cagctcaccacagatcaggtgttcccatacccgtccgtgctcaacgaagagcagacacag
tttcttaaagagctggtggagcctgtgtcccgtttcttcgaggaagtgaacgatcccgcc
aagaatgacgctctggagatggtggaggagaccacttggcagggcctcaaggagctgggg
gcctttggtctgcaagtgcccagtgagctgggtggtgtgggcctttgcaacacccagtac
gcccgtttggtggagatcgtgggcatgcatgaccttggcgtgggcattaccctgggggcc
catcagagcatcggtttcaaaggcatcctgctctttggcacaaaggcccagaaagaaaaa
tacctccccaagctggcatctggggagactgtggccgctttctgtctaaccgagccctca
agcgggtcagatgcagcctccatccgaacctctgctgtgcccagcccctgtggaaaatac
tataccctcaatggaagcaagctttggatcagtaatgggggcctagcagacatcttcacg
gtctttgccaagacaccagttacagatccagccacaggagccgtgaaggagaagatcaca
gcttttgtggtggagaggggcttcgggggcattacccatgggccccctgagaagaagatg
ggcatcaaggcttcaaacacagcagaggtgttctttgatggagtacgggtgccatcggag
aacgtgctgggtgaggttgggagtggcttcaaggttgccatgcacatcctcaacaatgga
aggtttggcatggctgcggccctggcaggtaccatgagaggcatcattgctaaggcggta
gatcatgccactaatcgtacccagtttggggagaaaattcacaactttgggctgatccag
gagaagctggcacggatggttatgctgcagtatgtaactgagtccatggcttacatggtg
agtgctaacatggaccagggagccacggacttccagatagaggccgccatcagcaaaatc
tttggctcggaggcagcctggaaggtgacagatgaatgcatccaaatcatggggggtatg
ggcttcatgaaggaacctggagtagagcgtgtgctccgagatcttcgcatcttccggatc
tttgaggggacaaatgacattcttcggctgtttgtggctctgcagggctgtatggacaaa
ggaaaggagctctctgggcttggcagtgctctaaagaatccctttgggaatgctggcctc
ctgctaggagaggcaggcaaacagctgaggcggcgggcagggctgggcagcggcctgagt
ctcagcggacttgtccacccggagttgagtcggagtggcgagctggcagtacgggctctg
gagcagtttgccactgtggtggaggccaagctgataaaacacaagaaggggattgtcaat
gaacagtttctgctgcagcggctggcagacggggccatcgacctctatgccatggtggtg
gttctctcgagggcctcaagatccctgagtgagggccaccccacggcccagcatgagaaa
atgctctgtgacacctggtgtatcgaggctgcagctcggatccgagagggcatggccgcc
ctgcagtctgacccctggcagcaagagctctaccgcaacttcaaaagcatctccaaggcc
ttggtggagcggggtggtgtggtcaccagcaacccacttggcttctga |