Homo sapiens (human): 5105
Help
Entry
5105 CDS
T01001
Symbol
PCK1, PCKDC, PEPCK-C, PEPCK1, PEPCKC
Name
(RefSeq) phosphoenolpyruvate carboxykinase 1
KO
K01596
phosphoenolpyruvate carboxykinase (GTP) [EC:
4.1.1.32
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00010
Glycolysis / Gluconeogenesis
hsa00020
Citrate cycle (TCA cycle)
hsa00620
Pyruvate metabolism
hsa01100
Metabolic pathways
hsa03320
PPAR signaling pathway
hsa04068
FoxO signaling pathway
hsa04151
PI3K-Akt signaling pathway
hsa04152
AMPK signaling pathway
hsa04910
Insulin signaling pathway
hsa04920
Adipocytokine signaling pathway
hsa04922
Glucagon signaling pathway
hsa04931
Insulin resistance
hsa04964
Proximal tubule bicarbonate reclamation
Module
hsa_M00003
Gluconeogenesis, oxaloacetate => fructose-6P
Network
nt06031
Citrate cycle and pyruvate metabolism
Element
N01605
Gluconeogenesis
Disease
H02520
Phosphoenolpyruvate carboxykinase deficiency
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00010 Glycolysis / Gluconeogenesis
5105 (PCK1)
00020 Citrate cycle (TCA cycle)
5105 (PCK1)
00620 Pyruvate metabolism
5105 (PCK1)
09130 Environmental Information Processing
09132 Signal transduction
04068 FoxO signaling pathway
5105 (PCK1)
04151 PI3K-Akt signaling pathway
5105 (PCK1)
04152 AMPK signaling pathway
5105 (PCK1)
09150 Organismal Systems
09152 Endocrine system
04910 Insulin signaling pathway
5105 (PCK1)
04922 Glucagon signaling pathway
5105 (PCK1)
04920 Adipocytokine signaling pathway
5105 (PCK1)
03320 PPAR signaling pathway
5105 (PCK1)
09155 Excretory system
04964 Proximal tubule bicarbonate reclamation
5105 (PCK1)
09160 Human Diseases
09167 Endocrine and metabolic disease
04931 Insulin resistance
5105 (PCK1)
Enzymes [BR:
hsa01000
]
4. Lyases
4.1 Carbon-carbon lyases
4.1.1 Carboxy-lyases
4.1.1.32 phosphoenolpyruvate carboxykinase (GTP)
5105 (PCK1)
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
PEPCK_GTP
PEPCK_N
Motif
Other DBs
NCBI-GeneID:
5105
NCBI-ProteinID:
NP_002582
OMIM:
614168
HGNC:
8724
Ensembl:
ENSG00000124253
UniProt:
P35558
Structure
PDB
LinkDB
All DBs
Position
20:57561110..57568121
Genome browser
AA seq
622 aa
AA seq
DB search
MPPQLQNGLNLSAKVVQGSLDSLPQAVREFLENNAELCQPDHIHICDGSEEENGRLLGQM
EEEGILRRLKKYDNCWLALTDPRDVARIESKTVIVTQEQRDTVPIPKTGLSQLGRWMSEE
DFEKAFNARFPGCMKGRTMYVIPFSMGPLGSPLSKIGIELTDSPYVVASMRIMTRMGTPV
LEAVGDGEFVKCLHSVGCPLPLQKPLVNNWPCNPELTLIAHLPDRREIISFGSGYGGNSL
LGKKCFALRMASRLAKEEGWLAEHMLILGITNPEGEKKYLAAAFPSACGKTNLAMMNPSL
PGWKVECVGDDIAWMKFDAQGHLRAINPENGFFGVAPGTSVKTNPNAIKTIQKNTIFTNV
AETSDGGVYWEGIDEPLASGVTITSWKNKEWSSEDGEPCAHPNSRFCTPASQCPIIDAAW
ESPEGVPIEGIIFGGRRPAGVPLVYEALSWQHGVFVGAAMRSEATAAAEHKGKIIMHDPF
AMRPFFGYNFGKYLAHWLSMAQHPAAKLPKIFHVNWFRKDKEGKFLWPGFGENSRVLEWM
FNRIDGKASTKLTPIGYIPKEDALNLKGLGHINMMELFSISKEFWEKEVEDIEKYLEDQV
NADLPCEIEREILALKQRISQM
NT seq
1869 nt
NT seq
+upstream
nt +downstream
nt
atgcctcctcagctgcaaaacggcctgaacctctcggccaaagttgtccagggaagcctg
gacagcctaccccaggcagtgagggagtttctcgagaataacgctgagctgtgtcagcct
gatcacatccacatctgtgacggctctgaggaggagaatgggcggcttctgggccagatg
gaggaagagggcatcctcaggcggctgaagaagtatgacaactgctggttggctctcact
gaccccagggatgtggccaggatcgaaagcaagacggttatcgtcacccaagagcaaaga
gacacagtgcccatccccaaaacaggcctcagccagctcggtcgctggatgtcagaggag
gattttgagaaagcgttcaatgccaggttcccagggtgcatgaaaggtcgcaccatgtac
gtcatcccattcagcatggggccgctgggctcgcctctgtcaaagatcggcatcgagctg
acggattcaccctacgtggtggccagcatgcggatcatgacgcggatgggcacgcccgtc
ctggaagcagtgggcgatggggagtttgtcaaatgcctccattctgtggggtgccctctg
cctttacaaaagcctttggtcaacaactggccctgcaacccggagctgacgctcatcgcc
cacctgcctgaccgcagagagatcatctcctttggcagtgggtacggcgggaactcgctg
ctcgggaagaagtgctttgctctcaggatggccagccggctggccaaggaggaagggtgg
ctggcagagcacatgctgattctgggtataaccaaccctgagggtgagaagaagtacctg
gcggccgcatttcccagcgcctgcgggaagaccaacctggccatgatgaaccccagcctc
cccgggtggaaggttgagtgcgtcggggatgacattgcctggatgaagtttgacgcacaa
ggtcatttaagggccatcaacccagaaaatggctttttcggtgtcgctcctgggacttca
gtgaagaccaaccccaatgccatcaagaccatccagaagaacacaatctttaccaatgtg
gccgagaccagcgacgggggcgtttactgggaaggcattgatgagccgctagcttcaggt
gtcaccatcacgtcctggaagaataaggagtggagctcagaggatggggaaccttgtgcc
caccccaactcgaggttctgcacccctgccagccagtgccccatcattgatgctgcctgg
gagtctccggaaggtgttcccattgaaggcattatctttggaggccgtagacctgctggt
gtccctctagtctatgaagctctcagctggcaacatggagtctttgtgggggcggccatg
agatcagaggccacagcggctgcagaacataaaggcaaaatcatcatgcatgaccccttt
gccatgcggcccttctttggctacaacttcggcaaatacctggcccactggcttagcatg
gcccagcacccagcagccaaactgcccaagatcttccatgtcaactggttccggaaggac
aaggaaggcaaattcctctggccaggctttggagagaactccagggtgctggagtggatg
ttcaaccggatcgatggaaaagccagcaccaagctcacgcccataggctacatccccaag
gaggatgccctgaacctgaaaggcctggggcacatcaacatgatggagcttttcagcatc
tccaaggaattctgggagaaggaggtggaagacatcgagaagtatctggaggatcaagtc
aatgccgacctcccctgtgaaatcgagagagagatccttgccttgaagcaaagaataagc
cagatgtaa
Homo sapiens (human): 5106
Help
Entry
5106 CDS
T01001
Symbol
PCK2, PEPCK, PEPCK-M, PEPCK2, mtPCK2
Name
(RefSeq) phosphoenolpyruvate carboxykinase 2, mitochondrial
KO
K01596
phosphoenolpyruvate carboxykinase (GTP) [EC:
4.1.1.32
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00010
Glycolysis / Gluconeogenesis
hsa00020
Citrate cycle (TCA cycle)
hsa00620
Pyruvate metabolism
hsa01100
Metabolic pathways
hsa03320
PPAR signaling pathway
hsa04068
FoxO signaling pathway
hsa04151
PI3K-Akt signaling pathway
hsa04152
AMPK signaling pathway
hsa04910
Insulin signaling pathway
hsa04920
Adipocytokine signaling pathway
hsa04922
Glucagon signaling pathway
hsa04931
Insulin resistance
hsa04964
Proximal tubule bicarbonate reclamation
Module
hsa_M00003
Gluconeogenesis, oxaloacetate => fructose-6P
Network
nt06031
Citrate cycle and pyruvate metabolism
Element
N01605
Gluconeogenesis
Disease
H02520
Phosphoenolpyruvate carboxykinase deficiency
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00010 Glycolysis / Gluconeogenesis
5106 (PCK2)
00020 Citrate cycle (TCA cycle)
5106 (PCK2)
00620 Pyruvate metabolism
5106 (PCK2)
09130 Environmental Information Processing
09132 Signal transduction
04068 FoxO signaling pathway
5106 (PCK2)
04151 PI3K-Akt signaling pathway
5106 (PCK2)
04152 AMPK signaling pathway
5106 (PCK2)
09150 Organismal Systems
09152 Endocrine system
04910 Insulin signaling pathway
5106 (PCK2)
04922 Glucagon signaling pathway
5106 (PCK2)
04920 Adipocytokine signaling pathway
5106 (PCK2)
03320 PPAR signaling pathway
5106 (PCK2)
09155 Excretory system
04964 Proximal tubule bicarbonate reclamation
5106 (PCK2)
09160 Human Diseases
09167 Endocrine and metabolic disease
04931 Insulin resistance
5106 (PCK2)
Enzymes [BR:
hsa01000
]
4. Lyases
4.1 Carbon-carbon lyases
4.1.1 Carboxy-lyases
4.1.1.32 phosphoenolpyruvate carboxykinase (GTP)
5106 (PCK2)
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
PEPCK_GTP
PEPCK_N
Motif
Other DBs
NCBI-GeneID:
5106
NCBI-ProteinID:
NP_004554
OMIM:
614095
HGNC:
8725
Ensembl:
ENSG00000100889
UniProt:
Q16822
A0A384MTT2
LinkDB
All DBs
Position
14:24094171..24104125
Genome browser
AA seq
640 aa
AA seq
DB search
MAALYRPGLRLNWHGLSPLGWPSCRSIQTLRVLSGDLGQLPTGIRDFVEHSARLCQPEGI
HICDGTEAENTATLTLLEQQGLIRKLPKYNNCWLARTDPKDVARVESKTVIVTPSQRDTV
PLPPGGARGQLGNWMSPADFQRAVDERFPGCMQGRTMYVLPFSMGPVGSPLSRIGVQLTD
SAYVVASMRIMTRLGTPVLQALGDGDFVKCLHSVGQPLTGQGEPVSQWPCNPEKTLIGHV
PDQREIISFGSGYGGNSLLGKKCFALRIASRLARDEGWLAEHMLILGITSPAGKKRYVAA
AFPSACGKTNLAMMRPALPGWKVECVGDDIAWMRFDSEGRLRAINPENGFFGVAPGTSAT
TNPNAMATIQSNTIFTNVAETSDGGVYWEGIDQPLPPGVTVTSWLGKPWKPGDKEPCAHP
NSRFCAPARQCPIMDPAWEAPEGVPIDAIIFGGRRPKGVPLVYEAFNWRHGVFVGSAMRS
ESTAAAEHKGKIIMHDPFAMRPFFGYNFGHYLEHWLSMEGRKGAQLPRIFHVNWFRRDEA
GHFLWPGFGENARVLDWICRRLEGEDSARETPIGLVPKEGALDLSGLRAIDTTQLFSLPK
DFWEQEVRDIRSYLTEQVNQDLPKEVLAELEALERRVHKM
NT seq
1923 nt
NT seq
+upstream
nt +downstream
nt
atggccgcattgtaccgccctggcctgcggcttaactggcatgggctgagccccttgggc
tggccatcatgccgtagcatccagaccctgcgagtgcttagtggagatctgggccagctt
cccactggcattcgagattttgtagagcacagtgcccgcctgtgccaaccagagggcatc
cacatctgtgatggaactgaggctgagaatactgccacactgaccctgctggagcagcag
ggcctcatccgaaagctccccaagtacaataactgctggctggcccgcacagaccccaag
gatgtggcacgagtagagagcaagacggtgattgtaactccttctcagcgggacacggta
ccactcccgcctggtggggcccgtgggcagctgggcaactggatgtccccagctgatttc
cagcgagctgtggatgagaggtttccaggctgcatgcagggccgcaccatgtatgtgctt
ccattcagcatgggtcctgtgggctccccgctgtcccgcatcggggtgcagctcactgac
tcagcctatgtggtggcaagcatgcgtattatgacccgactggggacacctgtgcttcag
gccctgggagatggtgactttgtcaagtgtctgcactccgtgggccagcccctgacagga
caaggggagccagtgagccagtggccgtgcaacccagagaaaaccctgattggccacgtg
cccgaccagcgggagatcatctccttcggcagcggctatggtggcaactccctgctgggc
aagaagtgctttgccctacgcatcgcctctcggctggcccgggatgagggctggctggca
gagcacatgctgatcctgggcatcaccagccctgcagggaagaagcgctatgtggcagcc
gccttccctagtgcctgtggcaagaccaacctggctatgatgcggcctgcactgccaggc
tggaaagtggagtgtgtgggggatgatattgcttggatgaggtttgacagtgaaggtcga
ctccgggccatcaaccctgagaacggcttctttggggttgcccctggtacctctgccacc
accaatcccaacgccatggctacaatccagagtaacactatttttaccaatgtggctgag
accagtgatggtggcgtgtactgggagggcattgaccagcctcttccacctggtgttact
gtgacctcctggctgggcaaaccctggaaacctggtgacaaggagccctgtgcacatccc
aactctcgattttgtgccccggctcgccagtgccccatcatggacccagcctgggaggcc
ccagagggtgtccccattgacgccatcatctttggtggccgcagacccaaaggggtaccc
ctggtatacgaggccttcaactggcgtcatggggtgtttgtgggcagcgccatgcgctct
gagtccactgctgcagcagaacacaaagggaagatcatcatgcacgacccatttgccatg
cggcccttttttggctacaacttcgggcactacctggaacactggctgagcatggaaggg
cgcaagggggcccagctgccccgtatcttccatgtcaactggttccggcgtgacgaggca
gggcacttcctgtggccaggctttggggagaatgctcgggtgctagactggatctgccgg
cggttagagggggaggacagtgcccgagagacacccattgggctggtgccaaaggaagga
gccttggatctcagcggcctcagagctatagacaccactcagctgttctccctccccaag
gacttctgggaacaggaggttcgtgacattcggagctacctgacagagcaggtcaaccag
gatctgcccaaagaggtgttggctgagcttgaggccctggagagacgtgtgcacaaaatg
tga
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integrated database retrieval system