Homo sapiens (human): 54344
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Entry
54344 CDS
T01001
Symbol
DPM3, CDG1O, MDDGB15, MDDGC15
Name
(RefSeq) dolichyl-phosphate mannosyltransferase subunit 3, regulatory
KO
K09659
dolichol-phosphate mannosyltransferase subunit 3
Organism
hsa
Homo sapiens (human)
Pathway
hsa00510
N-Glycan biosynthesis
hsa01100
Metabolic pathways
Network
nt06015
N-Glycan biosynthesis
Element
N00667
N-Glycan precursor biosynthesis, Glc-6P to Man-P-Dol
Disease
H00118
Congenital disorders of glycosylation type I
H01959
Muscular dystrophy-dystroglycanopathy type C
H01960
Muscular dystrophy-dystroglycanopathy type B
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00510 N-Glycan biosynthesis
54344 (DPM3)
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Gene cluster
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Motif
Pfam:
DPM3
DUF6478
Motif
Other DBs
NCBI-GeneID:
54344
NCBI-ProteinID:
NP_714963
OMIM:
605951
HGNC:
3007
Ensembl:
ENSG00000179085
UniProt:
Q9P2X0
Q86TM7
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All DBs
Position
1:complement(155139891..155140531)
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AA seq
92 aa
AA seq
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MTKLAQWLWGLAILGSTWVALTTGALGLELPLSCQEVLWPLPAYLLVSAGCYALGTVGYR
VATFHDCEDAARELQSQIQEARADLARRGLRF
NT seq
279 nt
NT seq
+upstream
nt +downstream
nt
atgacgaaattagcgcagtggctttggggactagcgatcctgggctccacctgggtggcc
ctgaccacgggagccttgggcctggagctgcccttgtcctgccaggaagtcctgtggcca
ctgcccgcctacttgctggtgtccgccggctgctatgccctgggcactgtgggctatcgt
gtggccacttttcatgactgcgaggacgccgcacgcgagctgcagagccagatacaggag
gcccgagccgacttagcccgcagggggctgcgcttctga
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