Homo sapiens (human): 8802
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Entry
8802 CDS
T01001
Symbol
SUCLG1, GALPHA, MTDPS9, SUCLA1
Name
(RefSeq) succinate-CoA ligase GDP/ADP-forming subunit alpha
KO
K01899
succinyl-CoA synthetase alpha subunit [EC:
6.2.1.4
6.2.1.5
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00020
Citrate cycle (TCA cycle)
hsa00640
Propanoate metabolism
hsa01100
Metabolic pathways
hsa01200
Carbon metabolism
Module
hsa_M00009
Citrate cycle (TCA cycle, Krebs cycle)
hsa_M00011
Citrate cycle, second carbon oxidation, 2-oxoglutarate => oxaloacetate
Network
nt06031
Citrate cycle and pyruvate metabolism
Element
N01617
Citrate cycle, second carbon oxidation 2
Disease
H00469
Mitochondrial DNA depletion syndrome
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00020 Citrate cycle (TCA cycle)
8802 (SUCLG1)
00640 Propanoate metabolism
8802 (SUCLG1)
Enzymes [BR:
hsa01000
]
6. Ligases
6.2 Forming carbon-sulfur bonds
6.2.1 Acid-thiol ligases
6.2.1.4 succinate---CoA ligase (GDP-forming)
8802 (SUCLG1)
6.2.1.5 succinate---CoA ligase (ADP-forming)
8802 (SUCLG1)
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Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
CoA_binding
Ligase_CoA
Succ_CoA_lig
CoA_binding_2
Motif
Other DBs
NCBI-GeneID:
8802
NCBI-ProteinID:
NP_003840
OMIM:
611224
HGNC:
11449
Ensembl:
ENSG00000163541
UniProt:
P53597
Structure
PDB
PDBj
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All DBs
Position
2:complement(84423528..84459280)
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AA seq
346 aa
AA seq
DB search
MTATLAAAADIATMVSGSSGLAAARLLSRSFLLPQNGIRHCSYTASRQHLYVDKNTKIIC
QGFTGKQGTFHSQQALEYGTKLVGGTTPGKGGQTHLGLPVFNTVKEAKEQTGATASVIYV
PPPFAAAAINEAIEAEIPLVVCITEGIPQQDMVRVKHKLLRQEKTRLIGPNCPGVINPGE
CKIGIMPGHIHKKGRIGIVSRSGTLTYEAVHQTTQVGLGQSLCVGIGGDPFNGTDFIDCL
EIFLNDSATEGIILIGEIGGNAEENAAEFLKQHNSGPNSKPVVSFIAGLTAPPGRRMGHA
GAIIAGGKGGAKEKISALQSAGVVVSMSPAQLGTTIYKEFEKRKML
NT seq
1041 nt
NT seq
+upstream
nt +downstream
nt
atgaccgcaacccttgccgctgccgctgacatcgctaccatggtctccggcagcagcggc
ctcgccgccgcccgtctcctgtcgcgcagcttcctcctgccgcagaatggaattcggcat
tgttcctacacagcttctcggcaacatctctatgttgataaaaatacaaagattatttgc
cagggtttcactggcaaacagggcacctttcacagccagcaggcattggaatatggcacc
aaactcgttggaggaaccactccagggaaaggaggccagacacatctgggcttacctgtc
tttaatactgtgaaggaggccaaagaacagacaggagcaacggcttctgtcatttatgtt
cctccgccttttgctgctgctgccattaatgaagctattgaggcagaaattcccttggtt
gtgtgtatcactgaaggaattccccagcaggacatggtacgagtcaagcacaaactgctg
cgccaggaaaagacaaggctaattgggcccaactgccctggagtcatcaatcctggagaa
tgtaaaattggcatcatgcctggccatattcacaaaaaaggaaggattggcattgtgtcc
agatctggcaccctgacttatgaagcagttcaccaaacaacgcaagttggattggggcag
tctttgtgcgttggcattggaggtgatccttttaatggaacagattttattgactgcctc
gaaatctttttgaacgattctgccacagaaggcatcatattgattggtgaaattggtggt
aatgcagaagagaatgctgcagaatttttgaagcaacataattcaggtccaaattccaag
cctgtagtgtccttcattgctggtttaactgctcctcctgggagaagaatgggtcatgcc
ggggcaattattgctggaggaaaaggtggagctaaagagaagatctctgcccttcagagt
gcaggagttgtggtcagtatgtctcctgcacagctgggaaccacgatctacaaggaattt
gaaaagaggaagatgctatga
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