Homo sapiens (human): 9361
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Entry
9361 CDS
T01001
Symbol
LONP1, CODASS, LON, LONP, LonHS, PIM1, PRSS15, hLON
Name
(RefSeq) lon peptidase 1, mitochondrial
KO
K08675
ATP-dependent Lon protease [EC:
3.4.21.53
]
Organism
hsa
Homo sapiens (human)
Disease
H01824
CODAS syndrome
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09180 Brite Hierarchies
09181 Protein families: metabolism
01002 Peptidases and inhibitors [BR:
hsa01002
]
9361 (LONP1)
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis [BR:
hsa03029
]
9361 (LONP1)
Enzymes [BR:
hsa01000
]
3. Hydrolases
3.4 Acting on peptide bonds (peptidases)
3.4.21 Serine endopeptidases
3.4.21.53 endopeptidase La
9361 (LONP1)
Peptidases and inhibitors [BR:
hsa01002
]
Serine peptidases
Family S16: lon protease family
9361 (LONP1)
Mitochondrial biogenesis [BR:
hsa03029
]
Mitochondrial quality control factors
Regulator of mitochondrial biogenesis
Other regulator of mitochondrial biogenesis
9361 (LONP1)
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
Lon_C
LON_substr_bdg
AAA
Lon_lid
AAA_5
AAA_2
RuvB_N
ChlI
AAA_PrkA
AAA_16
AAA_22
AAA_14
ATPase_2
NPHP3_N
bpMoxR
RNA_helicase
nSTAND3
LXG
NTPase_1
AAA_18
AAA_17
Parvo_NS1
NB-ARC
RsgA_GTPase
Viral_helicase1
AAA_28
TsaE
NACHT
AAA_7
IstB_IS21
AAA_24
AAA_19
ABC_tran
AAA_3
Motif
Other DBs
NCBI-GeneID:
9361
NCBI-ProteinID:
NP_004784
OMIM:
605490
HGNC:
9479
Ensembl:
ENSG00000196365
UniProt:
P36776
Structure
PDB
PDBj
LinkDB
All DBs
Position
19:complement(5691834..5720452)
Genome browser
AA seq
959 aa
AA seq
DB search
MAASTGYVRLWGAARCWVLRRPMLAAAGGRVPTAAGAWLLRGQRTCDASPPWALWGRGPA
IGGQWRGFWEASSRGGGAFSGGEDASEGGAEEGAGGAGGSAGAGEGPVITALTPMTIPDV
FPHLPLIAITRNPVFPRFIKIIEVKNKKLVELLRRKVRLAQPYVGVFLKRDDSNESDVVE
SLDEIYHTGTFAQIHEMQDLGDKLRMIVMGHRRVHISRQLEVEPEEPEAENKHKPRRKSK
RGKKEAEDELSARHPAELAMEPTPELPAEVLMVEVENVVHEDFQVTEEVKALTAEIVKTI
RDIIALNPLYRESVLQMMQAGQRVVDNPIYLSDMGAALTGAESHELQDVLEETNIPKRLY
KALSLLKKEFELSKLQQRLGREVEEKIKQTHRKYLLQEQLKIIKKELGLEKDDKDAIEEK
FRERLKELVVPKHVMDVVDEELSKLGLLDNHSSEFNVTRNYLDWLTSIPWGKYSNENLDL
ARAQAVLEEDHYGMEDVKKRILEFIAVSQLRGSTQGKILCFYGPPGVGKTSIARSIARAL
NREYFRFSVGGMTDVAEIKGHRRTYVGAMPGKIIQCLKKTKTENPLILIDEVDKIGRGYQ
GDPSSALLELLDPEQNANFLDHYLDVPVDLSKVLFICTANVTDTIPEPLRDRMEMINVSG
YVAQEKLAIAERYLVPQARALCGLDESKAKLSSDVLTLLIKQYCRESGVRNLQKQVEKVL
RKSAYKIVSGEAESVEVTPENLQDFVGKPVFTVERMYDVTPPGVVMGLAWTAMGGSTLFV
ETSLRRPQDKDAKGDKDGSLEVTGQLGEVMKESARIAYTFARAFLMQHAPANDYLVTSHI
HLHVPEGATPKDGPSAGCTIVTALLSLAMGRPVRQNLAMTGEVSLTGKILPVGGIKEKTI
AAKRAGVTCIVLPAENKKDFYDLAAFITEGLEVHFVEHYREIFDIAFPDEQAEALAVER
NT seq
2880 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgagcactggctacgtgcgactgtggggagcggcgcggtgctgggtgctgcgg
cggccgatgctggccgccgccggggggcgggttcccactgcagcaggagcgtggttgctc
cgaggccagcggacctgcgacgcctctcctccttgggcactgtggggccgaggcccggca
attgggggccaatggcgggggttttgggaagcgagcagccgcggcggaggcgcattctcg
gggggcgaggacgcctccgagggcggcgcggaggaaggagccggcggcgcggggggcagc
gcgggcgccggggaaggcccggtcataacggcgctcacgcccatgacgatccccgatgtg
tttccgcacctgccgctcatcgccatcacccgcaacccggtgttcccgcgctttatcaag
attatcgaggttaaaaataagaagttggttgagctgctgagaaggaaagttcgtctcgcc
cagccttatgtcggcgtctttctaaagagagatgacagcaatgagtcggatgtggtcgag
agcctggatgaaatctaccacacggggacgtttgcccagatccatgagatgcaggacctt
ggggacaagctgcgcatgatcgtcatgggacacagaagagtccatatcagcagacagctg
gaggtggagcccgaggagccggaggcggagaacaagcacaagccccgcaggaagtcaaag
cggggcaagaaggaggcggaggacgagctgagcgccaggcacccggcggagctggcgatg
gagcccacccctgagctcccggctgaggtgctcatggtggaggtagagaacgttgtccac
gaggacttccaggtcacggaggaggtgaaagccctgactgcagagatcgtgaagaccatc
cgggacatcattgccttgaaccctctctacagggagtcagtgctgcagatgatgcaggct
ggccagcgggtggtggacaaccccatctacctgagcgacatgggcgccgcgctcaccggg
gccgagtcccatgagctgcaggacgtcctggaagagaccaatattcctaagcggctgtac
aaggccctctccctgctgaagaaggaatttgaactgagcaagctgcagcagcgcctgggg
cgggaggtggaggagaagatcaagcagacccaccgtaagtacctgctgcaggagcagcta
aagatcatcaagaaggagctgggcctggagaaggacgacaaggatgccatcgaggagaag
ttccgggagcgcctgaaggagctcgtggtccccaagcacgtcatggatgttgtggacgag
gagctgagcaagctgggcctgctggacaaccactcctcggagttcaatgtcacccgcaac
tacctagactggctcacgtccatcccttggggcaagtacagcaacgagaacctggacctg
gcgcgggcacaggcagtgctggaggaagaccactacggcatggaggacgtcaagaaacgc
atcctggagttcattgccgttagccagctccgcggctccacccagggcaagatcctctgc
ttctatggcccccctggcgtgggtaagaccagcattgctcgctccatcgcccgcgccctg
aaccgagagtacttccgcttcagcgtcgggggcatgactgacgtggctgagatcaagggc
cacaggcggacctacgtgggcgccatgcccgggaagatcatccagtgtttgaagaagacc
aagacggagaaccccctgatcctcatcgacgaggtggacaagatcggccgaggctaccag
ggggacccgtcgtcggcactgctggagctgctggacccagagcagaatgccaacttcctg
gaccactacctggacgtgcccgtggacttgtccaaggtgctgttcatctgcacggccaac
gtcacggacaccatccccgagccgctgcgagaccgtatggagatgatcaacgtgtcgggc
tacgtggcccaggagaagctggccattgcggagcgctacctggtgccccaggctcgcgcc
ctgtgtggcttggatgagagcaaggccaagctgtcatcggacgtgctgacgctgctcatc
aagcagtactgccgcgagagcggtgtccgcaacctgcagaagcaagtggagaaggtgtta
cggaaatcggcctacaagattgtcagcggcgaggccgagtccgtggaggtgacgcccgag
aacctgcaggacttcgtggggaagcccgtgttcaccgtggagcgcatgtatgacgtgaca
ccgcccggcgtggtcatggggctggcctggaccgcaatgggaggctccacgctgtttgtg
gagacatccctgagacggccacaggacaaggatgccaagggtgacaaggatggcagcctg
gaggtgacaggccagctgggggaggtgatgaaggagagcgcccgcatagcctacaccttc
gccagagccttcctcatgcagcacgcccccgccaatgactacctggtgacctcacacatc
cacctgcatgtgcccgagggcgccacccccaaggacggcccaagcgcaggctgcaccatc
gtcacggccctgctgtccctggccatgggcaggcctgtccggcagaatctggccatgact
ggcgaagtctccctcacgggcaagatcctgcctgttggtggcatcaaggagaagaccatt
gcggccaagcgcgcaggggtgacgtgcatcgtcctgccagccgagaacaagaaggacttc
tacgacctggcagccttcatcaccgagggcctggaggtgcacttcgtggaacactaccgg
gagatcttcgacatcgccttcccggacgagcaggcagaggcgctggccgtggaacggtga
DBGET
integrated database retrieval system
