Homo sapiens (human): 9973
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Entry
9973 CDS
T01001
Symbol
CCS
Name
(RefSeq) copper chaperone for superoxide dismutase
KO
K04569
copper chaperone for superoxide dismutase
Organism
hsa
Homo sapiens (human)
Pathway
hsa05014
Amyotrophic lateral sclerosis
hsa05022
Pathways of neurodegeneration - multiple diseases
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09160 Human Diseases
09164 Neurodegenerative disease
05014 Amyotrophic lateral sclerosis
9973 (CCS)
05022 Pathways of neurodegeneration - multiple diseases
9973 (CCS)
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Gene cluster
GFIT
Motif
Pfam:
Sod_Cu
HMA
DUF6286
Motif
Other DBs
NCBI-GeneID:
9973
NCBI-ProteinID:
NP_005116
OMIM:
603864
HGNC:
1613
Ensembl:
ENSG00000173992
UniProt:
O14618
Structure
PDB
PDBj
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All DBs
Position
11:66593185..66606019
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AA seq
274 aa
AA seq
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MASDSGNQGTLCTLEFAVQMTCQSCVDAVRKSLQGVAGVQDVEVHLEDQMVLVHTTLPSQ
EVQALLEGTGRQAVLKGMGSGQLQNLGAAVAILGGPGTVQGVVRFLQLTPERCLIEGTID
GLEPGLHGLHVHQYGDLTNNCNSCGNHFNPDGASHGGPQDSDRHRGDLGNVRADADGRAI
FRMEDEQLKVWDVIGRSLIIDEGEDDLGRGGHPLSKITGNSGERLACGIIARSAGLFQNP
KQICSCDGLTIWEERGRPIAGKGRKESAQPPAHL
NT seq
825 nt
NT seq
+upstream
nt +downstream
nt
atggcttcggattcggggaaccaggggaccctctgcacgttggagttcgcggtgcagatg
acctgtcagagctgtgtggacgcggtgcgcaaatccctgcaaggggtggcaggtgtccag
gatgtggaggtgcacttggaggaccagatggtcttggtacacaccactctacccagccag
gaggtgcaggctctcctggaaggcacggggcggcaggcggtactcaagggcatgggcagc
ggccagttgcagaatctgggggcagcagtggccatcctgggggggcctggcaccgtgcag
ggggtggtgcgcttcctacagctgacccctgagcgctgcctcatcgagggaactattgac
ggcctggagcctgggctgcatggactccacgtccatcagtacggggaccttacaaacaac
tgcaacagctgtgggaatcactttaaccctgatggagcatctcatgggggcccccaggac
tctgaccggcaccgcggagacctgggcaatgtccgtgctgatgctgacggccgcgccatc
ttcagaatggaggatgagcagctgaaggtgtgggatgtgattggccgcagcctgattatt
gatgagggagaagatgacctgggccggggaggccatcccttatccaagatcacagggaac
tccggggagaggttggcctgtggcatcattgcacgctccgctggccttttccagaacccc
aagcagatctgctcttgcgatggcctcaccatctgggaggagcgaggccggcccatcgct
ggcaagggccgaaaggagtcagcgcagccccctgcccacctttga
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integrated database retrieval system