VARIANT: 3284v1
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Entry
3284v1 Variant
Name
HSD3B2 deficiency
Type
Loss of function
Gene
HSD3B2
hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2 [KO:
K00070
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
613890
Network
nt06019
Steroid hormone biosynthesis
Disease
H00216
Congenital adrenal hyperplasia
Reference
PMID:
1363812
Authors
Rheaume E, Simard J, Morel Y, Mebarki F, Zachmann M, Forest MG, New MI, Labrie F
Title
Congenital adrenal hyperplasia due to point mutations in the type II 3 beta-hydroxysteroid dehydrogenase gene.
Journal
Nat Genet 1:239-45 (1992)
DOI:
10.1038/ng0792-239
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