ORTHOLOGY: K08900
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Entry
K08900 KO
Symbol
BCS1
Name
mitochondrial chaperone BCS1
Disease
H00820
Bjornstad syndrome
H02007
GRACILE syndrome
H02086
Mitochondrial complex III deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K08900 BCS1; mitochondrial chaperone BCS1
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial quality control factors
Mitochondrial respiratory chain complex assembly factors
Complex-III assembly factors
K08900 BCS1; mitochondrial chaperone BCS1
BRITE hierarchy
Genes
HSA:
617
(BCS1L)
PTR:
459946
(BCS1L)
PPS:
100988698
GGO:
101129851
PON:
100437347
PPYG:
129031812
NLE:
100604478
HMH:
116810294
SSYN:
129488428
MCC:
699690
(BCS1L)
MCF:
102123539
(BCS1L)
MTHB:
126933002
MNI:
105481221
CSAB:
103217874
(BCS1L)
CATY:
105587061
PANU:
101026133
116272889
TGE:
112636274
MLEU:
105528044
RRO:
104660028
RBB:
108518458
TFN:
117094520
PTEH:
111548624
CANG:
105504721
CJC:
100390879
SBQ:
101030917
CIMI:
108309068
ANAN:
105712816
CSYR:
103261231
MMUR:
105857695
LCAT:
123644004
ERUF:
138382555
(BCS1L)
PCOQ:
105808818
OGA:
100949740
MMU:
66821
(Bcs1l)
MCAL:
110304618
MPAH:
110321210
RNO:
301514
(Bcs1l)
MCOC:
116088578
ANU:
117706140
ASYL:
127693018
MUN:
110566690
CGE:
100771607
MAUA:
101843673
PROB:
127226440
PLEU:
114709312
PMAV:
102911234
(Bcs1l)
MORG:
121447630
MFOT:
126492920
AAMP:
119820775
CNL:
130869428
NGI:
103727722
HGL:
101703804
CPOC:
100714176
CCAN:
109681369
DORD:
105994466
DSP:
122107371
DMER:
138823657
(Bcs1l)
PLOP:
125350300
NCAR:
124979008
MMMA:
107138700
ITI:
101961358
OCU:
100351828
OPI:
101519160
OCZ:
121160589
TUP:
102474109
GVR:
103588917
CFA:
478911
(BCS1L)
CLUD:
112656454
VVP:
112922551
VLG:
121480528
NPO:
129522857
AML:
100480908
UMR:
103662759
UAH:
113250450
UAR:
123779425
ELK:
111141577
LLV:
125095100
MPUF:
101686401
MNP:
132013549
MLK:
131827453
NVS:
122902309
ORO:
101372781
EJU:
114200147
ZCA:
113919560
MLX:
118012041
MANO:
123838855
NSU:
110591931
LWW:
102750114
FCA:
101090709
(BCS1L)
PYU:
121031075
PCOO:
112872073
PBG:
122481776
PVIV:
125173876
LRUF:
124515383
LGF:
123599474
AJU:
106970107
PTG:
102957048
PPAD:
109265064
PUC:
125911179
PLEZ:
122228248
HHV:
120232393
CCRU:
144218711
(BCS1L)
BTA:
539713
(BCS1L)
BOM:
102274064
(BCS1L)
BIU:
109570660
BBUB:
102395153
BKE:
129646766
BBIS:
105003770
CHX:
102169634
OAS:
101111607
BTAX:
128059852
CSUM:
138076471
(BCS1L)
ODA:
120854373
CCAD:
122426180
MREE:
136164913
(BCS1L)
OVR:
110144741
(BCS1L)
MBEZ:
129537814
SSC:
100626589
(BCS1L)
CFR:
102516038
CBAI:
105064018
CDK:
105096086
VPC:
102537226
BACU:
103019425
BMUS:
118897698
LVE:
103072648
103081436
OOR:
101289848
LALB:
132522098
GMF:
115847995
(BCS1L)
DDP:
132428366
(BCS1L)
DLE:
111171833
PCAD:
102975790
PSIU:
116756455
PPHC:
136125603
(BCS1L)
NASI:
112411814
ECB:
100055811
(BCS1L)
EPZ:
103561960
(BCS1L)
EAI:
106838454
MYB:
102254268
MYD:
102759665
MMYO:
118661226
MLF:
102420176
MDT:
132238239
MYUM:
139015549
(BCS1L)
PKL:
118717015
EFUS:
103289313
MNA:
107524850
DRO:
112307980
SHON:
118975278
AJM:
119039496
PDIC:
114495281
PHAS:
123828767
MMF:
118625343
PPAM:
129080637
HAI:
109380564
RFQ:
117025746
PALE:
102884217
PGIG:
120587662
PVP:
105291060
RAY:
107516724
MJV:
108390512
TOD:
119256212
SARA:
101542527
SFUM:
130021020
SETR:
126000868
LAV:
100663108
TMU:
101346481
ETF:
101660980
DNM:
101429430
MDO:
100011174
(BCS1L)
GAS:
123255192
SHR:
100919063
AFZ:
127553104
PCW:
110219454
TVP:
118846599
PBRV:
138151631
(BCS1L)
MLAO:
141490933
(BCS1L)
OAA:
100088885
TACU:
119926482
GGA:
424212
(BCS1L)
PCOC:
116227316
MGP:
100539820
CJO:
107316916
TPAI:
128077284
LMUT:
125697175
NMEL:
110400533
APLA:
101804030
AACU:
137858863
(BCS1L)
OJA:
118169722
ACYG:
106039323
(BCS1L)
CATA:
118252592
AFUL:
116490779
TGU:
100217866
LSR:
110468346
(BCS1L)
SCAN:
103814353
PMOA:
120496862
OTC:
121335723
PRUF:
121356454
ATRC:
139593791
(BCS1L)
GFR:
102035159
FAB:
101818392
OMA:
130255421
PHI:
102100470
PMAJ:
107207603
CCAE:
111932188
CCW:
104693969
CBRC:
103625551
ACOE:
138113076
(BCS1L)
ETL:
114055309
ZAB:
102064861
ZLE:
135450107
ACHL:
103806808
SVG:
106860297
MMEA:
130574376
HRT:
120755227
SATI:
136363603
(BCS1L)
CFAI:
136293410
(BCS1L)
CCIC:
134047260
FPG:
101920870
FCH:
102054232
CCRI:
104155733
NNT:
104400147
SHAB:
115607820
ACUN:
113482394
ANOC:
141962434
(BCS1L)
SURA:
141945377
(BCS1L)
TALA:
104365562
ACHC:
115342639
HALD:
104323451
HLE:
104832162
AGEN:
126044553
HHAR:
128143952
BBUT:
142031362
(BCS1L)
GCL:
127018496
CSTI:
104550580
LDI:
104353420
MNB:
103771147
DPUB:
104309746
PPUS:
135186964
AVIT:
104273110
BRHI:
104502183
EGZ:
104132407
NNI:
104010070
PCRI:
104037544
PCAO:
104053547
PARX:
142057349
(BCS1L)
PADL:
103917660
AFOR:
103895379
FGA:
104080820
CBOR:
142083507
(BCS1L)
GSTE:
104253763
CBOY:
140657298
(BCS1L)
MAME:
142414274
(BCS1L)
CLV:
102084072
CNIC:
135990295
MUI:
104541606
PGUU:
104470543
PLET:
104622474
EHS:
104511472
CMAC:
104479957
CUCA:
104056339
TEO:
104373542
BREG:
104630259
GAME:
129208132
OHA:
104339182
ACAR:
104529768
CPEA:
104387332
CVF:
104285326
RTD:
128913067
CRID:
134518421
LMIC:
141746102
(BCS1L)
NARQ:
141462942
(BCS1L)
AAM:
106499293
AROW:
112972044
NPD:
112959484
TGT:
104568439
DNE:
112980381
SCAM:
104153719
ASN:
102386059
AMJ:
102570697
(BCS1L)
CPOO:
109323069
GGN:
109301475
PSS:
102458646
CIZ:
142016970
(BCS1L)
CMY:
102934334
CCAY:
125644582
LKP:
140895383
(BCS1L)
NDS:
141995715
(BCS1L)
DCC:
119863265
CPIC:
101950145
TST:
117885011
EOB:
135885775
CABI:
116824545
MRV:
120375121
ACS:
100552242
ASAO:
132773869
PVT:
110078237
SUND:
121923391
PBI:
103059046
PMUR:
107291479
CTIG:
120310404
TSR:
106546238
PGUT:
117675250
PCAE:
139327334
(BCS1L)
PTEX:
113441187
NSS:
113410808
VKO:
123027448
PMUA:
114603205
PRAF:
128420486
ZVI:
118090985
HCG:
128339496
GJA:
107116965
STOW:
125425854
EMC:
129323826
XLA:
380366
(bcs1l.L)
XTR:
549619
(bcs1l)
NPR:
108783879
RTEM:
120944216
ACAT:
141147208
(BCS1L)
PADS:
140335414
(BCS1L)
BBUF:
121008621
BGAR:
122945675
DTC:
141049205
(BCS1L)
HSQ:
130330318
PCOB:
134944950
PWL:
138286649
(BCS1L)
MUO:
115474511
GSH:
117360276
DRE:
394157
(bcs1l)
SRX:
107714219
107741911
SANH:
107673730
SGH:
107555925
CCAR:
109064884
109088803
CAUA:
113108396
CGIB:
127964816
PTET:
122351849
LROH:
127170563
GRF:
141340362
(bcs1l)
OMC:
131546659
PPRM:
120461534
RKG:
130096619
MAMB:
125270560
CIDE:
127518364
CERY:
137035980
(bcs1l)
MASI:
127447173
127448509
TROS:
130556085
TDW:
130427059
MANU:
129452196
(bcs1l)
PDAB:
135733450
(bcs1l)
IPU:
108266488
IFU:
128609027
PHYP:
113525793
SMEO:
124380542
TFD:
113654494
TVC:
132850339
CGAR:
128524491
NGRA:
132891346
TRN:
134324317
134324321
AMEX:
103024599
CMAO:
118807254
EEE:
113577203
CHAR:
105907990
SPIL:
134078556
ASAD:
121703957
TRU:
101062889
TFS:
130534312
TNG:
GSTEN00029106G001
LCO:
104936008
NCC:
104955626
104955697
TBEN:
117485662
CGOB:
115026783
PGEO:
117466251
(bcs1l)
GACU:
117549480
EMAC:
134867201
ELY:
117251442
EFO:
125899965
PLEP:
121939096
121939097
SLUC:
116047636
ECRA:
117952977
ESP:
116698139
PFLV:
114563934
GAT:
120834104
PPUG:
119228517
AFB:
129104546
CLUM:
117750157
PSWI:
130205919
CANA:
137782989
(bcs1l)
CVE:
137868371
(bcs1l)
MSAM:
119903814
SCHU:
122886091
EARM:
139292484
(bcs1l)
CUD:
121522928
SPUL:
138592619
(bcs1l)
LMIX:
132987079
HTC:
141807946
(bcs1l)
ALAT:
119026141
ASTR:
137605086
(bcs1l)
PKLU:
139208483
(bcs1l)
MZE:
101465291
ONL:
100691587
OAU:
116334059
OLA:
101159054
OML:
112155081
CSAI:
133446095
XMA:
102234420
XCO:
114147795
XHE:
116723686
PRET:
103461861
PFOR:
103138136
PLAI:
106945402
PMEI:
106916313
GAF:
122839536
PPRL:
129355961
129374574
CVG:
107086200
CTUL:
119774006
GMU:
124870769
NFU:
107396454
KMR:
108244286
ALIM:
106524009
106532709
NWH:
119419002
AOCE:
111568523
EJA:
138201402
(bcs1l)
BFRE:
138621061
(bcs1l)
MCEP:
125017611
CSEM:
103380769
POV:
109637352
SSEN:
122783813
SSOE:
131443632
HHIP:
117755217
HSP:
118120563
PPLT:
128456475
SMAU:
118283047
LCF:
108897206
SDU:
111218464
SLAL:
111667464
XGL:
120801157
HCQ:
109517562
SSCV:
125974143
(bcs1l)
SBIA:
133512250
PEE:
133410998
PTAO:
133486534
BPEC:
110171371
ENY:
140372710
MALB:
109972625
BSPL:
114846973
SJO:
128367541
SSCO:
133992793
TTY:
137192382
(bcs1l)
GMH:
115533135
SASA:
106581856
(BCS1)
STRU:
115156160
OTW:
112225126
OMY:
110501572
OGO:
124041786
ONE:
115136607
OKI:
109871105
OKE:
118385932
OMM:
135547115
OCLA:
139380554
SALP:
111959728
SNH:
120064453
SFON:
129816390
CCLU:
121551365
ELS:
105016180
OEP:
134017581
SFM:
108924223
PKI:
111845386
AANG:
118214184
AROT:
135241275
CCOG:
133116665
LOC:
102689884
PSPA:
121323327
ARUT:
117408813
PSEX:
120531250
LCM:
102353356
CMK:
103189807
RTP:
109925086
CPLA:
122551838
CPUN:
140482486
(bcs1l)
HOC:
132817372
SCAU:
119962206
HAKA:
140728084
(bcs1l)
PMRN:
116938625
LRJ:
133346020
BFO:
118427781
BBEL:
109477776
CIN:
100181911
SCLV:
120329916
CLEP:
143462455
SPU:
579223
LPIC:
129279513
129279618
LVG:
121429974
AJJ:
139974716
APLC:
110983248
ARUN:
117298717
AAMU:
139945477
AFIL:
140154875
AJC:
117123263
SKO:
100373593
(Bcs1l)
PFLL:
139118907
DME:
Dmel_CG4908
(Bcs1)
DER:
6543296
DSE:
6611931
DSI:
Dsimw501_GD23665
(Dsim_GD23665)
DYA:
Dyak_GE18907
DAN:
6498557
DSR:
110183353
DPO:
4817725
DPE:
6589332
DMN:
108162510
DWI:
26528938
DGR:
6567051
DMO:
Dmoj_GI18626
DAZ:
108611976
DNV:
108650013
DHE:
111596641
DVI:
6636640
(Bcs1)
CCAT:
101457483
BOD:
106627159
BDR:
105233581
RZE:
108365657
AOQ:
129248116
ALUD:
128865047
TDA:
119688903
MDE:
101895172
131800603
131806963
131806965
SCAC:
106085701
LCQ:
111685091
LSQ:
119611246
119611248
CVJ:
135951336
(Bcs1)
GFS:
119642971
ECOE:
129951955
CLON:
129613019
HIS:
119660305
AGA:
1274111
ACOZ:
120948658
AARA:
120897450
AMER:
121588481
ASTE:
118508363
AMAP:
126558109
AFUN:
125766555
AMOU:
128309355
AMRS:
128709608
ANIL:
128720696
AALI:
118461355
ADAR:
125950612
ACOS:
131272245
AAG:
110680973
5574412
AALB:
109415992
ASUA:
134227792
CQU:
CpipJ_CPIJ013393
CPII:
120426830
CBRI:
134838056
CNS:
116352327
BCOO:
119072349
119074626
119080249
119080251
LLL:
129786098
PPAP:
129805305
AME:
552253
ACER:
108002999
ALAB:
122711947
ADR:
102678648
AFLR:
100869705
BIM:
100743520
BBIF:
117209381
BVK:
117234460
BVAN:
117158473
BHUN:
126866269
BTER:
100650655
BAFF:
126928812
BPYO:
122571884
BPAS:
132908888
FVI:
122536057
CCAL:
108632124
OBB:
114874519
OLG:
117606860
MGEN:
117223338
NMEA:
116433674
CGIG:
122403635
SOC:
105203992
MPHA:
105834075
AEC:
105149548
ACEP:
105622394
ACOC:
108694321
MZT:
108729267
(Bcs1)
CCOA:
108778215
TCZ:
108767534
TSEP:
108754493
PBAR:
105429900
VEM:
105562905
COBS:
139106186
(Bcs1)
TLN:
139821031
(Bcs1)
TAME:
143900488
(Bcs1)
HST:
105188058
DQU:
106743898
CFO:
105249499
FEX:
115233376
PMEC:
138933400
(Bcs1)
LHU:
105669594
(Bcs1)
PGC:
109863623
OBO:
105276498
PCF:
106787652
PFUC:
122515888
VPS:
122635473
VCRB:
124428751
VVE:
124955763
NVI:
116415701
CSOL:
105363191
TPRE:
106659837
LHT:
122511678
LBD:
127287939
MDL:
103579753
CGLO:
123264213
CTYP:
141524265
(Bcs1)
FAS:
105264170
DAM:
107042189
AGIF:
122860790
CINS:
118071924
VCAN:
122415868
CCIN:
107264008
DSM:
124409961
NPT:
124218040
(Bcs1)
NFB:
124180080
NLO:
107226780
NVG:
124303873
AROA:
105685917
TCA:
660477
TMOL:
138131125
(Bcs1)
DPA:
109534243
ESIM:
136417048
(Bcs1)
EFOR:
136342048
(Bcs1)
SOY:
115881604
RFG:
143192926
(Bcs1)
AGRG:
126745381
ATD:
109602088
CSET:
123311952
HAXR:
123678216
AGB:
108917604
LDC:
111507128
DVV:
114338424
NVL:
108569424
DCOR:
135795893
(Bcs1)
APLN:
108740721
PPYR:
116172211
OTU:
111427984
BMOR:
101736280
BMAN:
114249360
MSEX:
115445775
119191815
DPL:
KGM_204429
BANY:
112043319
MJU:
123864480
NIQ:
126775621
VCD:
124541534
MCIX:
123664979
PMAC:
106712330
PPOT:
106107858
PXU:
106117330
BPHI:
137929536
(Bcs1)
PRAP:
111003140
PBX:
123717858
PNAP:
125061886
ZCE:
119830176
119830273
CCRC:
123704089
LSIN:
126971409
AAGE:
121729870
HAW:
110371416
HZE:
124638224
TNL:
113492660
SLIU:
111357868
OFU:
114356658
ONU:
135081951
ATRA:
106138708
GMW:
113522670
ECLR:
140747485
(Bcs1)
PXY:
105398371
PGW:
126381832
LGLY:
125240714
CSTB:
134754633
CFUM:
141427855
(Bcs1)
CFEL:
113370470
113371263
CCRN:
123292229
API:
100162321
100169445
DNX:
107166059
107168560
AGS:
114120869
114128076
RMD:
113550892
113551515
ACOO:
126835010
126839728
126844263
DVT:
126895406
126905949
BTAB:
109037756
DCI:
103513085
CLEC:
106669641
NLU:
111054792
LDA:
142327631
(Bcs1)
HVI:
124359891
MQU:
128992030
PHU:
Phum_PHUM137330
FOC:
113207910
TPAL:
117643381
ZNE:
110834516
CSEC:
111875325
PAME:
138703574
(Bcs1)
SGRE:
126316774
126324046
126334571
BROR:
134536182
IEL:
124160872
HAMR:
139697353
(Bcs1)
FCD:
110844062
110849568
110854448
110854449
110854482
110862033
110863633
DPX:
DAPPUDRAFT_300604
DMK:
116932338
DPZ:
124348517
AFRA:
136033772
PVM:
113817728
(Bcs1)
PJA:
122262845
PCHN:
125047616
PMOO:
119596340
HAME:
121864178
PCLA:
123774232
(Bcs1)
CQD:
128702195
(Bcs1)
PTRU:
123507651
SPRM:
135112121
ESN:
126998096
MNZ:
135222826
MRJ:
136847690
(Bcs1)
PORN:
139762473
(Bcs1)
HAZT:
108673945
OOT:
143037575
(Bcs1)
EAF:
111698880
111702947
TCF:
131884679
131888818
PPOI:
119096782
119097252
ISC:
8030434
DSV:
119435136
119441360
DALB:
135920343
(Bcs1)
RSAN:
119386523
RMP:
119178182
OTI:
135366805
VDE:
111244414
VJA:
111269147
GOE:
100901228
TUT:
107359060
107371948
CSCU:
111613733
CVS:
136989004
(Bcs1)
PTEP:
107446447
ABRU:
129967046
UDV:
129222574
SDM:
118194532
LPOL:
106462422
PMEO:
129593535
129594417
129595659
129595667
129597390
129600290
129601334
CEL:
CELE_F54C9.6
(bcs-1)
CBR:
CBG_00560
CRQ:
GCK72_004937
NAI:
NECAME_15407
BMY:
BM_BM4351
(Bma-bcs-1)
LOA:
LOAG_07266
TSP:
Tsp_03371
Tsp_13180
HRO:
HELRODRAFT_75858
LGI:
LOTGIDRAFT_185574
PVUL:
126820446
PCAN:
112570803
LSAX:
138952469
BARL:
143280872
BGT:
106056922
GAE:
121372159
HRF:
124145405
HRJ:
124275597
HASI:
137293903
HCRA:
139442903
CRG:
105345623
CANU:
128175474
CVN:
111130467
OED:
130054724
MYI:
110442582
PMAX:
117323770
AIRR:
138319440
YBA:
132550519
MCAF:
127739145
MMER:
123534686
RPHI:
132720752
DPOL:
127870756
MAEA:
128209149
128209283
OBI:
106871007
OSN:
115225556
115231427
LJP:
135466883
LAK:
106166292
SMM:
Smp_083120
SHX:
MS3_00001389
(BCS1L_1)
OVI:
T265_10613
EGL:
EGR_04258
LLON:
135485105
NVE:
5507567
EPA:
110235005
ATEN:
116288917
ADF:
107335077
AMIL:
114953348
MCAZ:
138045187
MFOO:
137976186
PDAM:
113684820
SPIS:
111322625
DGT:
114528719
XEN:
124451306
HSY:
130662540
RES:
135688792
TAD:
TRIADDRAFT_25447
AQU:
100639781
MNG:
MNEG_0052
OLU:
OSTLU_32455
OTA:
OT_ostta07g00590
MIS:
MICPUN_99023
MPP:
MICPUCDRAFT_50635
CCP:
CHC_T00006054001
CHC_T00006134001
CHC_T00007058001
CHC_T00007066001
SCE:
YDR375C
(BCS1)
SEUB:
DI49_0552
SPAO:
SPAR_D05640
AGO:
AGOS_ACR200C
ERC:
Ecym_4643
KLA:
KLLA0_E02487g
KMX:
KLMA_20605
LTH:
KLTH0F15730g
VPO:
Kpol_1062p18
ZRO:
ZYRO0G01716g
CGR:
2886299
(GVI51_A02805)
NCS:
NCAS_0H02120
(NCAS0H02120)
NDI:
NDAI_0C01530
(NDAI0C01530)
TPF:
TPHA_0E01660
(TPHA0E01660)
TBL:
TBLA_0A02720
(TBLA0A02720)
TGB:
HG536_0F02670
TDL:
TDEL_0D02530
(TDEL0D02530)
KAF:
KAFR_0D05090
(KAFR0D05090)
KNG:
KNAG_0B04170
(KNAG0B04170)
ZMK:
HG535_0C04310
SLUD:
SCDLUD_003229
DHA:
DEHA2G10516g
PIC:
PICST_47614
PGU:
PGUG_04778
SPAA:
SPAPADRAFT_59502
LEL:
PVL30_002680
(BCS1)
LBG:
92206919
(LODBEIA_P17230)
CAL:
CAALFM_CR05970CA
(CaO19.458)
CTP:
CTRG_00657
COT:
CORT_0D05260
CDU:
CD36_31350
CTEN:
18246335
(BCS1)
CLU:
CLUG_03609
CLUS:
A9F13_01g05522
CAUR:
CJI96_0003437
ASAU:
88174502
(PUMCH_003438)
PPA:
PAS_chr3_0116
PKZ:
C5L36_0C11030
BBRX:
BRETT_000146
OPA:
HPODL_00956
YLI:
2910576
(YALI2_D01060g)
SLB:
AWJ20_5248
(BCS1)
NCR:
NCU03231
NCU03921
NTE:
NEUTE1DRAFT124799
(NEUTE1DRAFT_124799)
NEUTE1DRAFT72346
(NEUTE1DRAFT_72346)
SMP:
10803307
(SMAC4_06339)
10805910
(SMAC4_02951)
PAN:
PODANSg09459
PODANSg3026
PODANSg9009
PBEL:
QC761_102170
(BCS1)
QC761_211510
QC761_408300
PPSD:
QC762_102170
(BCS1)
QC762_211510
QC762_408300
PPSP:
QC763_102170
(BCS1)
QC763_211510
QC763_408300
PPSA:
QC764_102170
(BCS1)
QC764_211510
QC764_408300
TTT:
THITE_2108409
THITE_2109894
THITE_2120356
THITE_2120877
MTM:
MYCTH_2131445
MYCTH_2302213
MYCTH_2303320
MYCTH_2306553
CTHR:
CTHT_0043750
CTHT_0056430
CTHT_0061310
RTHE:
98122153
(VTJ83DRAFT_1359)
98123354
(VTJ83DRAFT_244)
98124477
(VTJ83DRAFT_3453)
98126846
(VTJ83DRAFT_5586)
MGR:
MGG_02058
MGG_04018
MGG_10383
MGG_14588
MGG_15496
PPEI:
PpBr36_00024
PpBr36_00115
PpBr36_04495
PpBr36_05765
PpBr36_05823
PpBr36_08114
PpBr36_10371
PpBr36_11036
PpBr36_11184
PpBr36_11264
PpBr36_11327
PGRI:
PgNI_01123
PgNI_05018
PgNI_05108
PgNI_06899
PgNI_08217
PgNI_12226
PgNI_12266
PgNI_12271
TMN:
UCRPA7_2017
UCRPA7_4687
UCRPA7_6887
SSCK:
SPSK_00784
SPSK_03063
FGR:
FGSG_02212
FGSG_02769
FGSG_05889
FGSG_07544
FGSG_09267
FPU:
FPSE_00225
FPSE_09659
FPSE_10319
FPSE_10591
FPSE_12249
FPOA:
FPOAC1_002358
FPOAC1_002908
FPOAC1_008852
FPOAC1_011338
FPOAC1_012430
FVN:
FVRRES_02601
FVRRES_03225
FVRRES_09466
FVRRES_12372
FVRRES_13513
FVR:
FVEG_01652
FVEG_03843
FVEG_04549
FVEG_07241
FVEG_08925
FVEG_12753
FOX:
FOXG_02822
FOXG_04127
FOXG_05975
FOXG_07622
FOXG_10276
FOXG_12511
FOXG_14028
FOXG_15422
NHE:
NECHADRAFT_1988
NECHADRAFT_49155
NECHADRAFT_56027
NECHADRAFT_62313
NECHADRAFT_63271
NECHADRAFT_91444
NECHADRAFT_94191
FFC:
NCS54_00304600
NCS54_00317200
NCS54_00790800
NCS54_00870000
NCS54_01099100
NCS54_01112000
NCS54_01175700
FKR:
NCS57_00300000
NCS57_00312800
NCS57_00336000
NCS57_00346800
NCS57_00670600
NCS57_00833400
NCS57_00910400
NCS57_01102500
NCS57_01166500
FMU:
J7337_003239
J7337_003852
J7337_005466
J7337_006590
J7337_008023
J7337_010745
TRE:
TRIREDRAFT_56396
TRIREDRAFT_60378
TRIREDRAFT_68571
TRR:
M419DRAFT_12213
M419DRAFT_127450
M419DRAFT_50927
TATV:
25777474
(TrAtP1_011582)
25777914
(TrAtP1_002950)
25779756
(TrAtP1_003864)
TASP:
36608222
(TrAFT101_008544)
36616842
(TrAFT101_006656)
36619214
(TrAFT101_003367)
MAW:
19250355
(J3458_001679)
19252578
(J3458_000386)
19253184
(BCS1_1)
MAJ:
MAA_00280
MAA_01276
MAA_02020
MAA_03253
MAA_06175
MAA_09964
MBRN:
26237984
(G6M90_00g020030)
26239612
(G6M90_00g036580)
26243216
(BCS1)
26244572
(G6M90_00g062560)
26247752
(G6M90_00g030610)
PCHM:
VFPPC_01684
VFPPC_05458
VFPPC_06174
UVI:
66060937
(UV8b_00159)
66066971
(UV8b_06194)
CMT:
CCM_00312
CCM_00737
CCM_04955
CCM_07856
CCM_09618
AMUS:
LMH87_000553
LMH87_001017
LMH87_003097
LMH87_007615
PLJ:
28885299
(PLICBS_006871)
28886224
(PLICBS_007711)
28888718
(PLICBS_009149)
PTKZ:
JDV02_001394
JDV02_004433
JDV02_005425
(BCS1)
JDV02_005841
DCON:
63716930
(DCS_04287)
63718360
(DCS_05717)
63719115
(DCS_06472)
63719496
(DCS_06853)
VAL:
VDBG_04049
VDBG_08199
VDBG_08974
VDBG_09104
VDA:
VDAG_01279
VDAG_02425
VDAG_05219
VDAG_07252
VDAG_07853
VDAG_10092
CFJ:
CFIO01_00929
CFIO01_02103
CFIO01_02317
CFIO01_06985
CFIO01_10139
CLUP:
CLUP02_07728
CLUP02_11704
CLUP02_12097
CLUP02_16493
CHIG:
CH63R_04054
CH63R_09751
CH63R_10605
CH63R_11211
CH63R_11525
CH63R_14149
CDET:
87937815
(CDEST_01312)
87938473
(CDEST_01970)
87941090
(CDEST_04587)
87945751
(CDEST_09248)
87945972
(CDEST_09469)
87946271
(CDEST_09769)
87947719
(CDEST_11219)
87950827
(CDEST_14327)
87952123
(CDEST_15624)
SAPO:
SAPIO_CDS5453
ELA:
UCREL1_4431
UCREL1_470
UCREL1_6784
UCREL1_8674
UCREL1_9169
UCREL1_9428
PFY:
PFICI_00502
PFICI_04801
PFICI_08057
PFICI_14167
PFICI_15067
SSL:
SS1G_01232
SS1G_07866
SS1G_09686
BFU:
BCIN_07g05710
BCIN_11g01350
(Bcbcs1)
BCIN_15g01200
MBE:
MBM_00289
MBM_04271
MBM_05269
MBM_06925
PSCO:
LY89DRAFT_678561
LY89DRAFT_683146
LY89DRAFT_691695
GLZ:
GLAREA_06003
GLAREA_08666
GLAREA_11432
ANI:
ANIA_03131
ANIA_06397
ANIA_07549
AFM:
AFUA_2G14760
AFUA_3G13000
AFUA_4G01260
ACT:
ACLA_040740
ACLA_072720
NFI:
NFIA_044060
NFIA_064320
NFIA_089990
AOR:
AO090012000830
AO090020000632
AO090026000803
ANG:
An02g08900
An15g03540
AFV:
AFLA_002545
AFLA_005485
AFLA_007616
AFLA_010014
ALUC:
AKAW2_10757A
AKAW2_20446S
AKAW2_60373A
ACHE:
ACHE_20243A
ACHE_31326S
APUU:
APUU_20491S
APUU_30381S
APUU_80408A
PCS:
N7525_002311
N7525_002638
N7525_008384
PDP:
PDIP_04100
PDIP_05600
PDIP_23210
PDIP_75210
POU:
POX_b02867
POX_c04563
POX_h09711
PPSF:
300786914
(PFLUO_LOCUS1414)
300787251
(PFLUO_LOCUS1718)
TMF:
EYB26_000759
EYB26_004931
EYB26_005072
EYB26_009737
TRG:
TRUGW13939_02344
TRUGW13939_08793
TRUGW13939_08803
TRUGW13939_10123
TRUGW13939_10157
TRUGW13939_10343
CIM:
CIMG_03460
CPW:
9694227
(D8B26_003010)
URE:
UREG_06573
UREG_07271
ABE:
ARB_02245
ARB_05203
ARB_06889
TVE:
TRV_03619
TRV_05949
TRV_07953
PBL:
PAAG_07167
PBN:
PADG_00929
AJE:
HCAG_00371
HCAG_00382
HCAG_01622
HCAG_01624
HCAG_01753
HCAG_01926
HCAG_02395
HCAG_02538
HCAG_02886
HCAG_03392
HCAG_04063
HCAG_04641
HCAG_05640
HCAG_06331
HCAG_06626
HCAG_07516
HCAG_07597
HCAG_07712
HCAG_08528
HCAG_08540
HCAG_08568
HCAG_08917
HCAG_09086
BGH:
BDBG_00758
BDBG_02928
BDBG_08151
BDBG_16825
PNO:
SNOG_03232
SNOG_05174
(SNOG_05173)
SNOG_08322
SNOG_15480
PTE:
PTT_15640
PTT_18203
PTT_18957
PTT_19104
PTRR:
6346609
(PtrM4_149070)
BZE:
COCCADRAFT_23237
COCCADRAFT_34683
COCCADRAFT_5582
BSC:
COCSADRAFT_163326
COCSADRAFT_182878
COCSADRAFT_94323
BOR:
COCMIDRAFT_3845
COCMIDRAFT_6825
COCMIDRAFT_91607
AALT:
CC77DRAFT_1098237
CC77DRAFT_555241
CC77DRAFT_931733
CC77DRAFT_982004
CC77DRAFT_993546
ADAC:
96080636
(ACET3X_000314)
96083462
(ACET3X_003140)
96084067
(ACET3X_003745)
96084230
(ACET3X_003908)
ARAB:
EKO05_0004698
EKO05_0010030
ZTR:
MYCGRDRAFT_110524
MYCGRDRAFT_30173
MYCGRDRAFT_67763
MYCGRDRAFT_77213
PFJ:
MYCFIDRAFT_125208
MYCFIDRAFT_138975
MYCFIDRAFT_146481
MYCFIDRAFT_39750
FFU:
CLAFUR5_05496
CLAFUR5_08611
CLAFUR5_10257
CBET:
CB0940_00527
CB0940_05938
CB0940_09888
BCOM:
BAUCODRAFT_112384
BAUCODRAFT_261705
BAUCODRAFT_56533
NPA:
UCRNP2_211
UCRNP2_6997
TML:
GSTUM_00002227001
GSTUM_00004552001
GSTUM_00009605001
SPO:
2543663
(bcs1)
SOM:
SOMG_03525
(bcs1)
CNE:
CNC04110
CNB:
CNBC3080
CNG:
CNAG_02792
CGI:
CGB_C6210W
CDEU:
CNBG_3447
CDEC:
89987897
(IAS62_001122)
CTEG:
91988952
(I308_102094)
CBAS:
91982145
(I312_102097)
CDEP:
91085224
(L203_101010)
KMG:
30159815
(I203_105052)
30159816
(I203_105050)
30159821
(I203_105045)
30159834
(I203_105032)
30162053
(I203_107488)
30167425
(I203_106335)
KNE:
92177508
(IAR55_000248)
92178246
(IAR55_000987)
KDJ:
28964627
(I303_100924)
28965800
(I303_101763)
28967319
(I303_103598)
28969960
(I303_106242)
28969961
(I303_106243)
28969995
(I303_106277)
28969996
(I303_106278)
KBI:
30207203
(I302_104097)
30208443
(I302_100669)
30211374
(I302_107289)
30211378
(I302_107285)
30211380
(I302_107283)
30213331
(I302_104996)
KPIN:
30169196
(I206_100501)
30172263
(I206_105197)
30172270
(I206_105190)
30172271
(I206_105189)
KSH:
87953031
(IL334_000900)
87954071
(IL334_001940)
87954072
(IL334_001941)
87956324
(IL334_004193)
KER:
91098867
(V865_000063)
91098870
(V865_000066)
91098884
(V865_000080)
91104825
(V865_006024)
91106133
(V865_007332)
KSN:
43588557
(CI109_102422)
KEP:
91091594
(L201_000922)
91092688
(L201_002016)
91092696
(L201_002024)
91095548
(L201_004878)
91095966
(L201_005296)
91095971
(L201_005301)
TMS:
TREMEDRAFT_27280
TREMEDRAFT_39838
TREMEDRAFT_62261
TREMEDRAFT_73837
TASA:
A1Q1_01633
CCAC:
CcaHIS019_0403290
(BCS1)
PPL:
POSPLDRAFT_24229
TVS:
TRAVEDRAFT_160965
TRAVEDRAFT_167458
TRAVEDRAFT_168153
TRAVEDRAFT_27987
TRAVEDRAFT_47707
DSQ:
DICSQDRAFT_123961
DICSQDRAFT_132726
DICSQDRAFT_139690
DICSQDRAFT_140557
DICSQDRAFT_69964
PCO:
PHACADRAFT_143806
PHACADRAFT_258919
PHACADRAFT_263985
SHS:
STEHIDRAFT_118952
STEHIDRAFT_157096
STEHIDRAFT_51737
STEHIDRAFT_57885
STEHIDRAFT_62902
STEHIDRAFT_64826
STEHIDRAFT_87633
HIR:
HETIRDRAFT_109007
HETIRDRAFT_155952
HETIRDRAFT_172230
HETIRDRAFT_58075
HETIRDRAFT_60257
HETIRDRAFT_63656
PSQ:
PUNSTDRAFT_104854
PUNSTDRAFT_106413
PUNSTDRAFT_127854
PUNSTDRAFT_50243
PUNSTDRAFT_75035
PUNSTDRAFT_86846
ADL:
AURDEDRAFT_112830
AURDEDRAFT_113059
AURDEDRAFT_145769
AURDEDRAFT_182372
AURDEDRAFT_77515
AURDEDRAFT_84193
AURDEDRAFT_90038
FME:
FOMMEDRAFT_112889
FOMMEDRAFT_18207
FOMMEDRAFT_22463
FOMMEDRAFT_86815
GTR:
GLOTRDRAFT_110317
GLOTRDRAFT_126816
GLOTRDRAFT_129183
GLOTRDRAFT_39873
GLOTRDRAFT_48634
GLOTRDRAFT_48749
GLOTRDRAFT_74861
GLOTRDRAFT_74864
RSX:
RhiXN_04678
RhiXN_04726
RhiXN_06627
RhiXN_09617
RhiXN_10051
LBC:
LACBIDRAFT_187928
LACBIDRAFT_244188
LACBIDRAFT_291958
LACBIDRAFT_318752
LACBIDRAFT_396180
CCI:
CC1G_00820
CC1G_00842
CC1G_01181
CC1G_01608
CC1G_02392
CC1G_04010
CC1G_09806
CC1G_11035
CC1G_11036
ABP:
AGABI1DRAFT108111
(AGABI1DRAFT_108111)
AGABI1DRAFT108687
(AGABI1DRAFT_108687)
AGABI1DRAFT116485
(AGABI1DRAFT_116485)
AGABI1DRAFT34350
(AGABI1DRAFT_34350)
AGABI1DRAFT36444
(AGABI1DRAFT_36444)
AGABI1DRAFT62968
(AGABI1DRAFT_62968)
ABV:
AGABI2DRAFT180594
(AGABI2DRAFT_180594)
AGABI2DRAFT180828
(AGABI2DRAFT_180828)
AGABI2DRAFT196029
(AGABI2DRAFT_196029)
AGABI2DRAFT210088
(AGABI2DRAFT_210088)
AGABI2DRAFT63145
(AGABI2DRAFT_63145)
AGABI2DRAFT70517
(AGABI2DRAFT_70517)
PCUB:
JR316_0001652
JR316_0003164
JR316_0007845
JR316_0007937
JR316_0010552
MPR:
MPER_04883
MPER_12612
MPER_15830
MRR:
Moror_10129
Moror_1040
Moror_14311
Moror_16541
Moror_2622
Moror_5007
MORE:
E1B28_000029
E1B28_002070
E1B28_008974
E1B28_011207
E1B28_011416
E1B28_011830
SCM:
SCHCO_01186842
(SCHCODRAFT_01186842)
SCHCO_02481375
(SCHCODRAFT_02481375)
SCHCO_02620364
(SCHCODRAFT_02620364)
SCHCO_02634784
(SCHCODRAFT_02634784)
SCHCO_02691288
(SCHCODRAFT_02691288)
CPUT:
CONPUDRAFT_112319
CONPUDRAFT_140136
CONPUDRAFT_148000
CONPUDRAFT_166050
CONPUDRAFT_169497
CONPUDRAFT_169502
CONPUDRAFT_81184
CONPUDRAFT_85412
CONPUDRAFT_97799
SLA:
SERLADRAFT_364293
SERLADRAFT_448902
SERLADRAFT_473328
WSE:
WALSEDRAFT_38133
WALSEDRAFT_59685
WIC:
J056_004291
UMA:
UMAG_04201
PFP:
PFL1_04409
PFL1_06072
SGRA:
EX895_001653
MGL:
MGL_3700
MRT:
MRET_1645
MSYM:
MSY001_0040
PGR:
PGTG_19037
PTRC:
PtA15_8A430
PSTR:
Pst134EA_015828
MLR:
MELLADRAFT_65472
RIE:
OCT59_019745
SRE:
PTSG_09789
DDI:
DDB_G0286765
DDB_G0289135
(bcs1lA)
DDB_G0291910
(bcs1lB)
DPP:
DICPUDRAFT_28373
DICPUDRAFT_31265
DICPUDRAFT_49377
DFA:
DFA_01976
(bcs1lB)
DFA_03149
DFA_03225
(bcs1lA)
ACAN:
ACA1_040870
ACA1_107600
ACA1_140770
ACA1_175540
ACA1_246080
ACA1_289200
ACA1_291670
ACA1_291780
PFA:
PF3D7_0603200
PFD:
PFDG_00238
PFH:
PFHG_01199
PREI:
PRSY57_0601800
PGAB:
PGSY75_0603200
PLAG:
39740648
(PADL01_0601300)
PYO:
PY17X_0103600
PCB:
PCHAS_0102700
PBE:
PBANKA_0102000
PVV:
PVVCY_0100340
PKN:
PKNH_1147500
PVX:
PVX_113325
PCY:
PCYB_115320
PMAL:
PMUG01_11059600
PBRS:
92372019
(MKS88_003932)
PREL:
PRELSG_1145100
PCOT:
PCOAH_00036880
BMIC:
BMR1_02g00285
TGO:
TGME49_243490
BBES:
BESB_046690
AAF:
AURANDRAFT_30024
AURANDRAFT_5693
AURANDRAFT_5728
AURANDRAFT_62882
TBR:
Tb927.8.3580
TBG:
TbgDal_VIII3290
TCR:
505945.50
509553.20
LMA:
LMJF_34_1330
LIF:
LINJ_34_1440
LDO:
LDBPK_341440
LMI:
LMXM_33_1330
LMAT:
92512292
(LSCM1_02194)
LBZ:
LBRM_20_1360
LPAN:
LPMP_201420
LOI:
92356903
(LSCM4_00901)
LEIS:
94177440
(GH5_01887)
LENR:
94168743
(CUR178_01463)
LEIN:
94185224
(JIQ42_01484)
PHET:
94287867
(JKF63_01744)
NGR:
NAEGRDRAFT_2052
NAEGRDRAFT_3835
NAEGRDRAFT_59933
NAEGRDRAFT_70080
NAEGRDRAFT_70508
NAEGRDRAFT_72457
EHX:
EMIHUDRAFT_104465
EMIHUDRAFT_212353
EMIHUDRAFT_369425
EMIHUDRAFT_41925
EMIHUDRAFT_66523
EMIHUDRAFT_68829
EMIHUDRAFT_74848
EMIHUDRAFT_77639
EMIHUDRAFT_96085
GTT:
GUITHDRAFT_111783
GUITHDRAFT_153155
GUITHDRAFT_74509
GUITHDRAFT_86537
OTD:
J1M35_08860
HPSE:
HPF_17785
(yjoB)
SMIO:
CATMQ487_48460
MBRY:
B1812_13615
MPAR:
F7D14_14285
MECI:
RVU70_00310
MALU:
KU6B_51550
LRS:
PX52LOC_05939
PBOR:
BSF38_05768
(yjoB)
AGV:
OJF2_38590
(yjoB)
ABA:
Acid345_2241
CMP:
Cha6605_4543
DGO:
DGo_CA2897
DSW:
QR90_16245
DFC:
DFI_01405
DEIN:
DAAJ005_02450
DGA:
DEGR_30160
DTAE:
LAJ19_12070
DEID:
HLB42_16595
» show all
Taxonomy
UniProt
Reference
PMID:
19162478
Authors
Blazquez A, Gil-Borlado MC, Moran M, Verdu A, Cazorla-Calleja MR, Martin MA, Arenas J, Ugalde C
Title
Infantile mitochondrial encephalomyopathy with unusual phenotype caused by a novel BCS1L mutation in an isolated complex III-deficient patient.
Journal
Neuromuscul Disord 19:143-6 (2009)
DOI:
10.1016/j.nmd.2008.11.016
Sequence
[hsa:
617
]
Reference
PMID:
18628306
Authors
Tamai S, Iida H, Yokota S, Sayano T, Kiguchiya S, Ishihara N, Hayashi J, Mihara K, Oka T
Title
Characterization of the mitochondrial protein LETM1, which maintains the mitochondrial tubular shapes and interacts with the AAA-ATPase BCS1L.
Journal
J Cell Sci 121:2588-600 (2008)
DOI:
10.1242/jcs.026625
Sequence
[hsa:
617
]
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DBGET
integrated database retrieval system