ORTHOLOGY: K10532
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Entry
K10532 KO
Symbol
HGSNAT
Name
heparan-alpha-glucosaminide N-acetyltransferase [EC:
2.3.1.78
]
Pathway
map00531
Glycosaminoglycan degradation
map01100
Metabolic pathways
map04142
Lysosome
Module
M00078
Heparan sulfate degradation
Reaction
R07815
acetyl-CoA:heparan-alpha-D-glucosaminide N-acetyltransferase
Disease
H00130
Mucopolysaccharidosis type III
H00421
Mucopolysaccharidosis
H00527
Retinitis pigmentosa
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
K10532 HGSNAT; heparan-alpha-glucosaminide N-acetyltransferase
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
K10532 HGSNAT; heparan-alpha-glucosaminide N-acetyltransferase
Enzymes [BR:
ko01000
]
2. Transferases
2.3 Acyltransferases
2.3.1 Transferring groups other than aminoacyl groups
2.3.1.78 heparan-alpha-glucosaminide N-acetyltransferase
K10532 HGSNAT; heparan-alpha-glucosaminide N-acetyltransferase
BRITE hierarchy
Other DBs
GO:
0015019
Genes
HSA:
138050
(HGSNAT)
PTR:
464155
(HGSNAT)
PPS:
100984595
(HGSNAT)
GGO:
101149295
(HGSNAT)
PON:
100447325
(HGSNAT)
PPYG:
129043139
(HGSNAT)
NLE:
100606132
(HGSNAT)
HMH:
116462136
(HGSNAT)
SSYN:
129491566
(HGSNAT)
MCC:
720331
(HGSNAT)
MCF:
102129964
(HGSNAT)
MTHB:
126960753
MNI:
105476620
CSAB:
103215704
(HGSNAT)
CATY:
105595740
(HGSNAT)
PANU:
101025303
(HGSNAT)
TGE:
112630442
(HGSNAT)
MLEU:
105554541
(HGSNAT)
RRO:
104668313
(HGSNAT)
RBB:
108534354
(HGSNAT)
TFN:
117095880
(HGSNAT)
PTEH:
111544083
(HGSNAT)
CANG:
105522559
(HGSNAT)
CJC:
100403479
(HGSNAT)
SBQ:
101052325
(HGSNAT)
CIMI:
108316202
(HGSNAT)
ANAN:
105733487
(HGSNAT)
MMUR:
105878130
(HGSNAT)
LCAT:
123626593
(HGSNAT)
PCOQ:
105819694
(HGSNAT)
OGA:
100950122
(HGSNAT)
MMU:
52120
(Hgsnat)
MCAL:
110300501
(Hgsnat)
MPAH:
110336556
(Hgsnat)
RNO:
361165
(Hgsnat)
MCOC:
116069071
(Hgsnat)
ANU:
117721645
(Hgsnat)
ASYL:
127668603
(Hgsnat)
MUN:
110566307
(Hgsnat)
CGE:
100752593
(Hgsnat)
MAUA:
101840158
(Hgsnat)
PROB:
127220364
(Hgsnat)
PLEU:
114681347
(Hgsnat)
MORG:
121462391
(Hgsnat)
MFOT:
126504436
AAMP:
119811743
(Hgsnat)
HGL:
101698026
(Hgsnat)
CPOC:
100734837
(Hgsnat)
CCAN:
109690641
109690642
DORD:
105993410
(Hgsnat)
DSP:
122107659
(Hgsnat)
DMER:
138823120
(Hgsnat)
PLOP:
125339265
(Hgsnat)
NCAR:
124982625
MMMA:
107160921
(Hgsnat)
ITI:
101961359
(Hgsnat)
OCU:
100355407
OPI:
101524261
(HGSNAT)
OCZ:
121165541
(HGSNAT)
TUP:
102478224
(HGSNAT)
GVR:
103586944
(HGSNAT)
CFA:
482833
(HGSNAT)
CLUD:
112658741
(HGSNAT)
VVP:
112916321
(HGSNAT)
VLG:
121489025
(HGSNAT)
NPO:
129515876
(HGSNAT)
AML:
100466980
(HGSNAT)
UMR:
103677041
(HGSNAT)
UAH:
113245550
(HGSNAT)
UAR:
123780301
(HGSNAT)
ELK:
111144416
LLV:
125092816
MPUF:
101692240
(HGSNAT)
MNP:
132006342
(HGSNAT)
MLK:
131820375
(HGSNAT)
NVS:
122890370
(HGSNAT)
ORO:
101370676
(HGSNAT)
EJU:
114224811
(HGSNAT)
ZCA:
113924792
(HGSNAT)
MLX:
118009905
(HGSNAT)
NSU:
110573144
(HGSNAT)
LWW:
102741284
(HGSNAT)
FCA:
101101049
(HGSNAT)
PYU:
121010257
(HGSNAT)
PCOO:
112858934
(HGSNAT)
PBG:
122472808
(HGSNAT)
PVIV:
125164937
(HGSNAT)
LRUF:
124520563
LGF:
123588149
(HGSNAT)
AJU:
106978258
PTG:
102958238
(HGSNAT)
PPAD:
109262246
(HGSNAT)
PUC:
125923840
PLEZ:
122217564
(HGSNAT)
HHV:
120234019
(HGSNAT)
BTA:
511607
(HGSNAT)
BOM:
102272015
(HGSNAT)
BIU:
109553469
(HGSNAT)
BBUB:
102405713
(HGSNAT)
BBIS:
104993234
(HGSNAT)
CHX:
102179068
(HGSNAT)
OAS:
101102037
(HGSNAT)
BTAX:
128068212
(HGSNAT)
CSUM:
138078022
(HGSNAT)
ODA:
120865863
(HGSNAT)
CCAD:
122432246
(HGSNAT)
MREE:
136176566
(HGSNAT)
OVR:
110135571
(HGSNAT)
MBEZ:
129549444
(HGSNAT)
SSC:
100517562
(HGSNAT)
CFR:
102515446
(HGSNAT)
CBAI:
105071102
(HGSNAT)
CDK:
105094298
(HGSNAT)
VPC:
102532227
(HGSNAT)
BACU:
103014371
(HGSNAT)
BMUS:
118887835
(HGSNAT)
LVE:
103085420
(HGSNAT)
OOR:
101269692
(HGSNAT)
LALB:
132512608
(HGSNAT)
GMF:
115841051
(HGSNAT)
DDP:
132417528
(HGSNAT)
DLE:
111173566
(HGSNAT)
PCAD:
102976976
(HGSNAT)
PSIU:
116746730
(HGSNAT)
PPHC:
136141802
(HGSNAT)
NASI:
112413159
(HGSNAT)
ECB:
100053359
(HGSNAT)
EPZ:
103540950
(HGSNAT)
EAI:
106828971
(HGSNAT)
MYB:
102255817
(HGSNAT)
MYD:
102753313
(HGSNAT)
MMYO:
118651151
(HGSNAT)
MLF:
102424014
(HGSNAT)
MDT:
132228587
(HGSNAT)
MYUM:
139006040
(HGSNAT)
PKL:
118729220
(HGSNAT)
EFUS:
103288295
(HGSNAT)
MNA:
107523903
(HGSNAT)
DRO:
112321437
(HGSNAT)
SHON:
118993040
(HGSNAT)
AJM:
119060883
(HGSNAT)
PDIC:
114508545
(HGSNAT)
PHAS:
123807618
(HGSNAT)
MMF:
118622338
(HGSNAT)
PPAM:
129064778
(HGSNAT)
HAI:
109386280
(HGSNAT)
RFQ:
117021402
(HGSNAT)
PALE:
102898024
(HGSNAT)
PGIG:
120595663
(HGSNAT)
PVP:
105301026
(HGSNAT)
RAY:
107501324
(HGSNAT)
MJV:
108408370
(HGSNAT)
TOD:
119258231
(HGSNAT)
SARA:
101539323
(HGSNAT)
SFUM:
130026139
(HGSNAT)
SETR:
126006418
(HGSNAT)
LAV:
100668824
(HGSNAT)
TMU:
101344649
ETF:
101658900
(HGSNAT)
DNM:
101443079
(HGSNAT)
MDO:
100015953
100033053
(HGSNAT)
GAS:
123234328
123236973
(HGSNAT)
SHR:
100926947
100930224
(HGSNAT)
AFZ:
127548288
127551861
PCW:
110196372
(HGSNAT)
TVP:
118828694
118841701
(HGSNAT)
PBRV:
138146447
138152071
(HGSNAT)
MLAO:
141504213
(HGSNAT)
OAA:
100086649
(HGSNAT)
100681967
TACU:
119925261
119928815
(HGSNAT)
GGA:
422490
(HGSNAT)
PCOC:
116238084
(HGSNAT)
MGP:
100540377
(HGSNAT)
CJO:
107313211
(HGSNAT)
LMUT:
125692136
(HGSNAT)
NMEL:
110397659
(HGSNAT)
APLA:
101798941
(HGSNAT)
ACYG:
106035184
(HGSNAT)
CATA:
118246611
(HGSNAT)
AFUL:
116488631
(HGSNAT)
TGU:
100228309
(HGSNAT)
LSR:
110471714
(HGSNAT)
SCAN:
103826250
(HGSNAT)
PMOA:
120502695
(HGSNAT)
OTC:
121331450
(HGSNAT)
PRUF:
121360189
(HGSNAT)
ATRC:
139592201
(HGSNAT)
GFR:
102033589
(HGSNAT)
FAB:
101811325
(HGSNAT)
OMA:
130252746
(HGSNAT)
PHI:
102113040
(HGSNAT)
PMAJ:
107203298
(HGSNAT)
CCAE:
111927792
(HGSNAT)
CCW:
104697135
(HGSNAT)
CBRC:
103617403
(HGSNAT)
ACOE:
138109638
(HGSNAT)
ETL:
114062175
(HGSNAT)
ZAB:
102063652
(HGSNAT)
ZLE:
135446743
(HGSNAT)
ACHL:
103800596
(HGSNAT)
SVG:
106854410
(HGSNAT)
MMEA:
130576243
(HGSNAT)
HRT:
120752632
(HGSNAT)
SATI:
136360496
(HGSNAT)
CCIC:
134044517
(HGSNAT)
FPG:
101916028
(HGSNAT)
FCH:
102048397
(HGSNAT)
CCRI:
104155717
(HGSNAT)
NNT:
104404949
(HGSNAT)
SHAB:
115610316
(HGSNAT)
ACUN:
113479860
(HGSNAT)
TALA:
104357322
(HGSNAT)
ACHC:
115339478
(HGSNAT)
HALD:
104314658
(HGSNAT)
HLE:
104843358
(HGSNAT)
AGEN:
126044970
HHAR:
128135441
(HGSNAT)
GCL:
127015624
CSTI:
104556678
(HGSNAT)
LDI:
104354120
(HGSNAT)
MNB:
103778195
(HGSNAT)
DPUB:
104304153
(HGSNAT)
PPUS:
135178052
(HGSNAT)
AVIT:
104280464
(HGSNAT)
BRHI:
104500460
(HGSNAT)
EGZ:
104135512
(HGSNAT)
NNI:
104021308
(HGSNAT)
PCRI:
104027626
(HGSNAT)
PCAO:
104053267
(HGSNAT)
PADL:
103925425
(HGSNAT)
AFOR:
103894296
(HGSNAT)
FGA:
104076952
(HGSNAT)
GSTE:
104254804
(HGSNAT)
CBOY:
140652475
(HGSNAT)
CLV:
102088426
(HGSNAT)
CNIC:
135988780
(HGSNAT)
MUI:
104545518
(HGSNAT)
PGUU:
104465384
(HGSNAT)
PLET:
104622638
(HGSNAT)
CMAC:
104486202
(HGSNAT)
CUCA:
104064694
(HGSNAT)
TEO:
104370413
(HGSNAT)
BREG:
104634254
(HGSNAT)
OHA:
104329206
(HGSNAT)
ACAR:
104527410
(HGSNAT)
CPEA:
104398866
(HGSNAT)
CVF:
104283004
(HGSNAT)
RTD:
128910104
(HGSNAT)
CRID:
134516764
(HGSNAT)
LMIC:
141744067
(HGSNAT)
AAM:
106484356
(HGSNAT)
AROW:
112972165
(HGSNAT)
NPD:
112953454
(HGSNAT)
TGT:
104564851
(HGSNAT)
DNE:
112993258
(HGSNAT)
SCAM:
104152107
(HGSNAT)
ASN:
102367842
102380180
(HGSNAT)
AMJ:
102558169
(BMS1)
102567230
(HGSNAT)
CPOO:
109309427
(HGSNAT)
109324298
GGN:
109287345
109301228
(HGSNAT)
PSS:
102446451
(HGSNAT)
CMY:
102929508
(HGSNAT)
CCAY:
125635902
(HGSNAT)
DCC:
119854447
(HGSNAT)
CPIC:
101949968
(HGSNAT)
TST:
117877943
(HGSNAT)
CABI:
116834476
(HGSNAT)
MRV:
120406731
(HGSNAT)
ACS:
100567269
(hgsnat)
103279643
ASAO:
132770189
132778439
(HGSNAT)
PVT:
110083669
110086321
(HGSNAT)
SUND:
121925876
121932987
(HGSNAT)
PBI:
103067626
(HGSNAT)
PMUR:
107302378
(HGSNAT)
CTIG:
120302787
(HGSNAT)
TSR:
106550264
(HGSNAT)
PGUT:
117664776
(HGSNAT)
APRI:
131196943
(HGSNAT)
PTEX:
113447279
(HGSNAT)
VKO:
123031847
(HGSNAT)
PMUA:
114581520
(HGSNAT)
114597092
PRAF:
128400673
(HGSNAT)
128413775
ZVI:
118095208
(HGSNAT)
118096362
HCG:
128328732
(HGSNAT)
128352324
GJA:
107107429
(HGSNAT)
STOW:
125437821
125440713
(HGSNAT)
EMC:
129332906
129337464
(HGSNAT)
XLA:
108695792
108712227
(hgsnat.L)
XTR:
100485725
(hgsnat)
100496969
NPR:
108786592
108804914
(HGSNAT)
RTEM:
120910441
120914568
(HGSNAT)
ACAT:
141106724
141107402
(HGSNAT)
BBUF:
120989664
(HGSNAT)
121004622
BGAR:
122942431
122945817
DTC:
141047864
(HGSNAT)
141088638
PWL:
138260231
(HGSNAT)
138300602
MUO:
115458896
115463783
(HGSNAT)
115471277
GSH:
117346072
(HGSNAT)
DRE:
100329505
(hgsnat)
565246
SRX:
107726935
107742491
(hgsnat)
107750043
SANH:
107655416
107656620
107666356
107702325
SGH:
107559314
107562920
107565475
107601802
CCAR:
109061693
109068429
109090745
(si:dkey-192p21.6)
CAUA:
113044152
(hgsnat)
113057486
113106107
CGIB:
127949352
127970045
127970747
(si:dkey-192p21.6)
PTET:
122343495
(hgsnat)
122356929
(si:dkey-192p21.6)
LROH:
127167795
(hgsnat)
127175375
(si:dkey-192p21.6)
GRF:
141325326
141336492
(hgsnat)
OMC:
131538598
(hgsnat)
131552327
(si:dkey-192p21.6)
PPRM:
120481193
(hgsnat)
RKG:
130071410
(hgsnat)
MAMB:
125272530
(hgsnat)
125276930
(si:dkey-192p21.6)
CIDE:
127515353
127524402
(si:dkey-192p21.6)
CERY:
137020568
(si:dkey-192p21.6)
137032211
(hgsnat)
MASI:
127411705
(si:dkey-192p21.6)
127444124
127445282
TROS:
130553671
(hgsnat)
130559029
(si:dkey-192p21.6)
TDW:
130431360
(si:dkey-192p21.6)
130439468
(hgsnat)
MANU:
129415679
129444810
(hgsnat)
PDAB:
135735862
(hgsnat)
135787022
IPU:
108260558
108263840
(si:dkey-192p21.6)
IFU:
128605776
(si:dkey-192p21.6)
PHYP:
113525575
(hgsnat)
113539706
SMEO:
124381159
(hgsnat)
124399983
(si:dkey-192p21.6)
TFD:
113636316
(si:dkey-192p21.6)
113649174
(hgsnat)
TVC:
132842030
(hgsnat)
132847386
(si:dkey-192p21.6)
CGAR:
128508344
(hgsnat)
128528497
(si:dkey-192p21.6)
NGRA:
132883332
132888698
(si:dkey-192p21.6)
TRN:
134327108
(hgsnat)
AMEX:
103035691
(hgsnat)
103038051
(si:dkey-192p21.6)
CMAO:
118810503
(si:dkey-192p21.6)
118817023
(hgsnat)
EEE:
113585225
113591477
(hgsnat)
CHAR:
105890900
(si:dkey-192p21.6)
105908502
(hgsnat)
SPIL:
134064395
(si:dkey-192p21.6)
134064821
(hgsnat)
ASAD:
121685320
(si:dkey-192p21.6)
121711269
(hgsnat)
TRU:
101077979
101078824
105418605
TFS:
130527306
(hgsnat)
130534088
(si:dkey-192p21.6)
TNG:
GSTEN00009084G001
LCO:
104921898
104930930
(hgsnat)
NCC:
104951383
(hgsnat)
104952735
TBEN:
117481695
(hgsnat)
117499567
(si:dkey-192p21.6)
CGOB:
115015167
(hgsnat)
115020240
PGEO:
117445581
(hgsnat)
117459917
GACU:
117537928
(hgsnat)
117552323
(si:dkey-192p21.6)
EMAC:
134858914
(si:dkey-192p21.6)
134864308
(hgsnat)
ELY:
117248020
(si:dkey-192p21.6)
117255894
(hgsnat)
EFO:
125886622
(hgsnat)
125903142
(si:dkey-192p21.6)
PLEP:
121941895
(hgsnat)
121955009
(si:dkey-192p21.6)
SLUC:
116039391
(si:dkey-192p21.6)
116040421
(hgsnat)
ECRA:
117957131
(hgsnat)
117960080
(si:dkey-192p21.6)
ESP:
116683578
116695137
(hgsnat)
PFLV:
114569503
(hgsnat)
114572400
GAT:
120820239
(si:dkey-192p21.6)
120825258
(hgsnat)
PPUG:
119214670
(si:dkey-192p21.6)
119218089
(hgsnat)
AFB:
129092772
(si:dkey-192p21.6)
129096223
(hgsnat)
CLUM:
117729859
(hgsnat)
117744332
(si:dkey-192p21.6)
PSWI:
130189804
(hgsnat)
130207208
(si:dkey-192p21.6)
CANA:
137780177
(si:dkey-192p21.6)
137794852
(hgsnat)
CVE:
137884390
(si:dkey-192p21.6)
137885241
(hgsnat)
MSAM:
119899121
(hgsnat)
119917614
(si:dkey-192p21.6)
SCHU:
122873191
(hgsnat)
122884855
(si:dkey-192p21.6)
CUD:
121507987
(hgsnat)
121511339
(si:dkey-192p21.6)
SPUL:
138588197
138594679
(hgsnat)
LMIX:
132975993
(si:dkey-192p21.6)
132992102
(hgsnat)
ALAT:
119020893
(hgsnat)
119033747
(si:dkey-192p21.6)
ASTR:
137599732
(hgsnat)
137603362
(si:dkey-192p21.6)
MZE:
101474778
101485947
(hgsnat)
ONL:
100702339
100708281
(hgsnat)
OAU:
116318786
(si:dkey-192p21.6)
116325993
(hgsnat)
OLA:
101155794
101166687
(hgsnat)
OML:
112157172
(hgsnat)
112161842
(si:dkey-192p21.6)
CSAI:
133424158
(hgsnat)
133464074
(si:dkey-192p21.6)
XMA:
102219750
102237227
XCO:
114137570
114144330
XHE:
116712640
116720330
PRET:
103469275
(hgsnat)
103477188
PFOR:
103137789
103148274
PLAI:
106941119
106952698
PMEI:
106909852
106916247
GAF:
122830110
(hgsnat)
122842269
(si:dkey-192p21.6)
PPRL:
129352640
(si:dkey-192p21.6)
CVG:
107088428
107099485
CTUL:
119782900
(si:dkey-192p21.6)
119786778
(hgsnat)
GMU:
124858781
(si:dkey-192p21.6)
124868876
(hgsnat)
NFU:
107372418
(hgsnat)
107375363
KMR:
108240660
(si:dkey-192p21.6)
108241548
(hgsnat)
ALIM:
106515196
106525611
NWH:
119421944
(si:dkey-192p21.6)
119430802
(hgsnat)
AOCE:
111573116
(si:dkey-192p21.6)
111574877
(hgsnat)
EJA:
138195594
138209676
(hgsnat)
BFRE:
138616013
138620320
(hgsnat)
MCEP:
125003799
(hgsnat)
125018406
CSEM:
103383737
(hgsnat)
103387461
POV:
109636795
109637803
(hgsnat)
SSEN:
122770866
(hgsnat)
122781398
(si:dkey-192p21.6)
SSOE:
131466451
(hgsnat)
131473547
(si:dkey-192p21.6)
HHIP:
117762556
(hgsnat)
117775327
(si:dkey-192p21.6)
HSP:
118117906
(hgsnat)
118119139
(si:dkey-192p21.6)
PPLT:
128436849
(hgsnat)
128453792
(si:dkey-192p21.6)
SMAU:
118283522
(si:dkey-192p21.6)
118312342
(hgsnat)
LCF:
108886253
(si:dkey-192p21.6)
108896428
SDU:
111220771
111231551
(hgsnat)
SLAL:
111664520
(hgsnat)
111669430
XGL:
120796814
(si:dkey-192p21.6)
120799977
(hgsnat)
HCQ:
109511354
(hgsnat)
109523168
SSCV:
125968536
(hgsnat)
125978424
(si:dkey-192p21.6)
SBIA:
133506748
(hgsnat)
PEE:
133403783
(hgsnat)
133410104
(si:dkey-192p21.6)
PTAO:
133477056
(hgsnat)
133485355
(si:dkey-192p21.6)
BPEC:
110162343
110172620
(hgsnat)
ENY:
140351642
140377691
(hgsnat)
MALB:
109958392
109958414
BSPL:
114848233
(hgsnat)
114870727
(si:dkey-192p21.6)
SJO:
128372418
(si:dkey-192p21.6)
128379626
(hgsnat)
SSCO:
133991518
(si:dkey-192p21.6)
134000219
(hgsnat)
TTY:
137173520
(hgsnat)
GMH:
115539827
(hgsnat)
115560136
SASA:
106576822
106590768
(hgsnat)
STRU:
115187357
115187381
(hgsnat)
115194001
OTW:
112252803
(si:dkey-192p21.6)
112256992
OMY:
110514029
(hgsnat)
110515920
110532528
(si:dkey-192p21.6)
OGO:
124018032
124018041
124018042
124029691
124041438
(si:dkey-192p21.6)
ONE:
115127606
(hgsnat)
115135307
OKI:
109884362
109884364
109889772
OKE:
118369506
(si:dkey-192p21.6)
118379753
127923793
OMM:
135507154
(hgsnat)
135510835
(si:dkey-192p21.6)
OCLA:
139374634
139394628
139405161
139409456
SALP:
111952083
112077206
SNH:
120017385
(si:dkey-192p21.6)
120051719
120052312
SFON:
129836108
(si:dkey-192p21.6)
129842059
129842061
CCLU:
121553517
(si:dkey-192p21.6)
121562675
(hgsnat)
ELS:
105007438
114830693
OEP:
134022899
(si:dkey-192p21.6)
134033233
(hgsnat)
SFM:
108925690
(hgsnat)
108932733
PKI:
111848991
111853138
(hgsnat)
AANG:
118217947
(si:dkey-192p21.6)
118227356
(hgsnat)
AROT:
135245255
(si:dkey-192p21.6)
135254438
(hgsnat)
CCOG:
133118569
(si:dkey-192p21.6)
133130740
(hgsnat)
LOC:
102682901
(hgsnat)
102697613
PSPA:
121319496
(hgsnat)
ARUT:
117421022
(hgsnat)
PSEX:
120527549
(hgsnat)
LCM:
102358104
102364435
CMK:
103180601
(hgsnat)
RTP:
109935287
(hgsnat)
CPLA:
122539253
(hgsnat)
HOC:
132833357
(hgsnat)
SCAU:
119956214
(si:dkey-192p21.6)
119963474
(hgsnat)
LERI:
129701218
129712936
(si:dkey-192p21.6)
HAKA:
140714445
140726328
(hgsnat)
PMRN:
116956958
(HGSNAT)
LRJ:
133359669
(HGSNAT)
BFO:
118408382
118410737
118423594
BBEL:
109466833
109477266
CIN:
100185618
SCLV:
120331184
SPU:
584064
590342
752871
LPIC:
129276578
129281973
129282019
LVG:
121427291
121427674
121431667
121432248
AJJ:
139968773
APLC:
110987515
ARUN:
117303857
AAMU:
139953167
AFIL:
140159115
140159640
AJC:
117103606
117103616
SKO:
102806658
PFLL:
139118401
139122446
DME:
Dmel_CG6903
(Hgsnat)
DER:
6551198
DSE:
6612452
DSI:
Dsimw501_GD16714
(Dsim_GD16714)
DYA:
Dyak_GE16376
DAN:
6503060
DSR:
110180614
DPO:
4814666
DPE:
6599099
DMN:
108161578
DWI:
6648367
DGR:
6565076
DMO:
Dmoj_GI16326
DAZ:
108618640
DNV:
108656299
DHE:
111605156
DVI:
6634788
(Hgsnat)
CCAT:
101452968
BOD:
106614424
BDR:
105228814
RZE:
108374929
108376701
AOQ:
129239032
ALUD:
128857794
TDA:
119666757
119670085
119670441
MDE:
101898084
131807138
SCAC:
106080878
LCQ:
111684197
LSQ:
119600703
CVJ:
135958129
(Hgsnat)
GFS:
119637628
ECOE:
129948597
CLON:
129611714
HIS:
119661595
AGA:
1276430
ACOZ:
120950507
AARA:
120896592
AMER:
121592597
ASTE:
118513172
AMAP:
126563600
AFUN:
125767730
AMOU:
128305575
AMRS:
128715977
AALI:
118466752
AAG:
5567477
AALB:
109410268
109411089
ASUA:
134211598
CQU:
CpipJ_CPIJ000061
CPII:
120431060
CBRI:
134834408
CNS:
116343879
BCOO:
119066567
119066702
119073027
LLL:
129788402
129788403
PPAP:
129807423
129807424
AME:
413119
551314
ACER:
108000398
108003351
ALAB:
122711653
122714656
ADR:
102675880
102678417
AFLR:
100867903
100872232
BIM:
100740677
100748696
BBIF:
117211120
117211127
BVK:
117237990
117238503
BVAN:
117160307
117160317
BHUN:
126875312
126875442
BTER:
100648231
100652298
BAFF:
126926422
126926544
BPYO:
122577232
122577287
BPAS:
132915423
132915468
132915552
FVI:
122530843
122533767
CCAL:
108625036
108632541
OBB:
114877140
114879285
OLG:
117605649
117609258
MGEN:
117223951
117227497
NMEA:
116423945
116424377
CGIG:
122395635
122395831
SOC:
105198606
105202153
MPHA:
105832689
105837694
AEC:
105143444
105143478
ACEP:
105617438
105617659
ACOC:
108685586
108685717
MZT:
108725392
108730111
CCOA:
108772562
108772595
PBAR:
105425954
105433786
VEM:
105559074
105559274
COBS:
139105956
139106431
TLN:
139811563
139812255
HST:
105181483
105186152
DQU:
106742509
106749252
CFO:
105252337
105252366
FEX:
115233513
115237085
PMEC:
138933404
138933777
LHU:
105669209
105674256
PGC:
109852282
109855753
OBO:
105274689
105277303
PCF:
106785743
106789896
PFUC:
122517113
122519608
VPS:
122628564
122630625
VCRB:
124424512
124424983
VVE:
124948245
124950531
NVI:
100113968
100119588
CSOL:
105362568
105365077
TPRE:
106650608
106657013
LHT:
122503523
122506589
LBD:
127286343
127286557
MDL:
103570907
103573925
CGLO:
123263122
123268698
CTYP:
141525365
141530344
FAS:
105262726
105266922
DAM:
107036949
107047776
AGIF:
122849647
122856029
CINS:
118065286
118072884
VCAN:
122410287
122411648
CCIN:
107265228
107273128
DSM:
124411745
124416714
NPT:
124217564
124220532
NFB:
124183695
124185985
NLO:
107217936
107221169
NVG:
124304382
124305426
AROA:
105684723
105690407
TCA:
655343
663306
TMOL:
138123578
138128232
(Hgsnat)
DPA:
109534473
109539358
ESIM:
136411869
(Hgsnat)
136415508
EFOR:
136344484
136349435
(Hgsnat)
SOY:
115878974
115883771
AGRG:
126739424
126740015
ATD:
109594231
109596254
CSET:
123309343
123309347
123311996
HAXR:
123672826
123672827
AGB:
108916210
108916571
LDC:
111514502
DVV:
114324836
114349364
NVL:
108563069
108567540
APLN:
108744298
112906598
PPYR:
116180339
116180842
OTU:
111425870
111426029
BMOR:
101742059
101742351
BMAN:
114241768
114247854
MSEX:
115442167
115450328
DPL:
KGM_210294
BANY:
112050245
112053619
MJU:
123865292
123866421
NIQ:
126777054
126781834
VCD:
124540073
124544289
MCIX:
123665693
123669925
PMAC:
106715697
106718677
PPOT:
106102818
106103379
PXU:
106113429
106128620
BPHI:
137925417
137928835
(Hgsnat)
PRAP:
110994491
110996781
PBX:
123707631
123711209
PNAP:
125050239
125059123
ZCE:
119833663
119836899
CCRC:
123692132
123701661
LSIN:
126969751
126976959
AAGE:
121728977
121730090
HAW:
110377402
110380743
HZE:
124632219
124641334
TNL:
113494320
113507582
SLIU:
111350979
111358472
OFU:
114350678
114358763
ONU:
135073352
135082600
ATRA:
106135848
106138388
106139228
GMW:
113511050
113523482
PXY:
105381008
105391139
105394688
PGW:
126366238
126375673
126376863
126376864
LGLY:
125228688
125236034
125237699
CSTB:
134741307
134747031
134751108
CFUM:
141435552
141441564
141441737
(Hgsnat)
CFEL:
113363561
113381407
113381482
CCRN:
123295811
123298183
API:
100159605
DNX:
107170094
AGS:
114125225
RMD:
113554428
ACOO:
126838113
DVT:
126900257
BTAB:
109029940
109029963
DCI:
103507565
103513098
CLEC:
106663961
106664032
HHAL:
106685197
(Hgsnat)
106687606
NLU:
111061962
111063781
HVI:
124354012
124354385
124355737
124356306
124359243
124364658
MQU:
128983554
129001464
129005033
PHU:
Phum_PHUM127270
Phum_PHUM535950
FOC:
113205877
113213986
TPAL:
117647234
117650597
ZNE:
110828853
110837448
CSEC:
111861261
111873685
PAME:
138710739
(Hgsnat)
138710831
SGRE:
126284570
126334812
BROR:
134528063
134539516
IEL:
124160085
124160099
HAMR:
139689288
(Hgsnat)
139689310
FCD:
110851771
110852738
110852791
DPX:
DAPPUDRAFT_129175
DAPPUDRAFT_309035
DMK:
116916393
116932716
DPZ:
124340622
124350582
AFRA:
136034673
PVM:
113800127
(Hgsnat)
113811195
PJA:
122259620
122263826
PCHN:
125031023
125038778
PMOO:
119580698
119598168
HAME:
121860830
121866480
PCLA:
123754446
(Hgsnat)
123758635
CQD:
128686859
(Hgsnat)
128697234
PTRU:
123510567
123513616
ESN:
126982260
126999366
MNZ:
135214913
135215180
MRJ:
136826547
(Hgsnat)
136851812
PORN:
139752199
(Hgsnat)
139756382
HAZT:
108676362
108680040
EAF:
111697040
111709167
LSM:
121115662
121119858
TCF:
131881650
131885659
PPOI:
119089289
119113584
119113852
ISC:
8024755
DSV:
119437725
RSAN:
119392259
RMP:
119160788
GOE:
100900363
TUT:
107364433
DPTE:
113798298
DFR:
124490699
CSCU:
111619585
CVS:
136968059
(Hgsnat)
PTEP:
107452184
ABRU:
129988031
UDV:
129229331
129229645
SDM:
118196928
LPOL:
106463010
106472013
106473335
PMEO:
129593813
HRO:
HELRODRAFT_167380
HELRODRAFT_191057
LGI:
LOTGIDRAFT_135049
LOTGIDRAFT_211131
PVUL:
126811700
126832271
PCAN:
112563038
112563539
LSAX:
138958379
138958380
138981459
BGT:
106054603
106063823
GAE:
121379047
121382074
HRF:
124115624
124132561
HRJ:
124274165
124279564
HASI:
137255712
137284868
HCRA:
139464210
139469806
CRG:
105341999
105346373
CANU:
128163234
128164682
CVN:
111110879
OED:
125665710
125668434
MYI:
110448038
110448229
PMAX:
117334466
117343870
AIRR:
138314568
138323339
MCAF:
127707712
127709544
127731180
MMER:
123531661
123564591
123564772
RPHI:
132720955
132730466
132736766
DPOL:
127855926
127856117
127856120
127868561
127868922
MAEA:
128219246
128222895
128229648
128245600
OBI:
106879750
106883086
OSN:
115211878
LJP:
135477553
135479356
LAK:
106150667
106157997
106170895
LLON:
135494698
NVE:
5519326
5519327
EPA:
110251396
110251399
ATEN:
116288208
116305528
ADF:
107334072
107334078
AMIL:
114946788
114946814
MCAZ:
138023298
138023311
MFOO:
137993323
137993325
PDAM:
113676139
113676144
SPIS:
111332767
111332777
DGT:
114527601
XEN:
124456884
HMG:
100199128
101236405
HSY:
130647398
130647846
RES:
135689422
TAD:
TRIADDRAFT_54611
TRIADDRAFT_59909
AQU:
100639521
MBR:
MONBRDRAFT_30330
SRE:
PTSG_05197
DDI:
DDB_G0286315
DPP:
DICPUDRAFT_49381
DFA:
DFA_08785
ACAN:
ACA1_028160
SPAR:
SPRG_06722
SPRG_10180
» show all
Taxonomy
UniProt
Reference
PMID:
16960811
Authors
Fan X, Zhang H, Zhang S, Bagshaw RD, Tropak MB, Callahan JW, Mahuran DJ
Title
Identification of the gene encoding the enzyme deficient in mucopolysaccharidosis IIIC (Sanfilippo disease type C).
Journal
Am J Hum Genet 79:738-44 (2006)
DOI:
10.1086/508068
Sequence
[hsa:
138050
]
LinkDB
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DBGET
integrated database retrieval system