ORTHOLOGY: K19054
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Entry
K19054 KO
Symbol
FXN
Name
frataxin [EC:
1.16.3.1
]
Pathway
map00860
Porphyrin metabolism
Reaction
R00078
Fe(II):oxygen oxidoreductase
Disease
H00067
Friedreich ataxia
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09108 Metabolism of cofactors and vitamins
00860 Porphyrin metabolism
K19054 FXN; frataxin
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K19054 FXN; frataxin
Enzymes [BR:
ko01000
]
1. Oxidoreductases
1.16 Oxidizing metal ions
1.16.3 With oxygen as acceptor
1.16.3.1 ferroxidase
K19054 FXN; frataxin
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial quality control factors
Regulator of mitochondrial biogenesis
Proteins involved in Fe-S cluster biogenesis
K19054 FXN; frataxin
BRITE hierarchy
Other DBs
COG:
COG1965
GO:
0004322
TC:
9.B.21.1
Genes
HSA:
2395
(FXN)
PTR:
107976773
737660
(FXN)
PPS:
100981926
(FXN)
134728565
GGO:
101151837
(FXN)
PON:
100433909
(FXN)
103891535
PPYG:
129044041
(FXN)
129044412
NLE:
100595202
(FXN)
115834064
HMH:
116458960
(FXN)
SSYN:
129490468
(FXN)
MCC:
699469
(FXN)
MCF:
102120656
(FXN)
MTHB:
126937649
MNI:
105483761
105491777
(FXN)
CSAB:
103219550
(FXN)
CATY:
105584150
(FXN)
PANU:
101026641
(FXN)
TGE:
112608225
(FXN)
MLEU:
105532092
(FXN)
RRO:
104662060
(FXN)
RBB:
108530269
(FXN)
TFN:
117098497
(FXN)
PTEH:
111543334
(FXN)
CANG:
105516625
(FXN)
CJC:
100390674
(FXN)
SBQ:
101028037
101032553
(FXN)
CIMI:
108314515
(FXN)
ANAN:
105718566
(FXN)
CSYR:
103257959
MMUR:
105856583
(FXN)
LCAT:
123645885
(FXN)
PCOQ:
105808040
(FXN)
OGA:
100963253
(FXN)
MMU:
14297
(Fxn)
MCAL:
110285725
(Fxn)
MPAH:
110332125
(Fxn)
RNO:
499335
(Fxn)
MCOC:
116103676
(Fxn)
ANU:
117716184
(Fxn)
ASYL:
127688945
(Fxn)
MUN:
110555635
(Fxn)
CGE:
100755339
(Fxn)
MAUA:
101830018
(Fxn)
PROB:
127233601
(Fxn)
PLEU:
114710022
(Fxn)
MORG:
121454403
(Fxn)
MFOT:
126497082
126511467
AAMP:
119805530
(Fxn)
NGI:
103749403
(Fxn)
HGL:
101724952
(Fxn)
CPOC:
100729273
(Fxn)
CCAN:
109696410
(Fxn)
DORD:
105987206
(Fxn)
DSP:
122124685
(Fxn)
PLOP:
125340947
(Fxn)
NCAR:
124964607
MMMA:
107144436
107148260
(Fxn)
ITI:
101972352
120890581
OCU:
103348216
OPI:
101527826
(FXN)
TUP:
102481422
(FXN)
CFA:
609051
(FXN)
CLUD:
112644753
(FXN)
VVP:
112922122
(FXN)
VLG:
121482549
(FXN)
NPO:
129500845
(FXN)
AML:
100464806
(FXN)
UMR:
103663245
(FXN)
UAH:
113270198
(FXN)
UAR:
123776485
(FXN)
123799513
ELK:
111153642
LLV:
125082901
MPUF:
101691289
(FXN)
MNP:
132024835
(FXN)
MLK:
131812392
(FXN)
NVS:
122917719
(FXN)
ORO:
101371865
(FXN)
EJU:
114219805
(FXN)
ZCA:
113935006
(FXN)
NSU:
110584367
(FXN)
LWW:
102738646
102749145
(FXN)
FCA:
101085159
(FXN)
PYU:
121013662
(FXN)
PBG:
122474783
(FXN)
PVIV:
125150844
(FXN)
LRUF:
124528273
LGF:
123593486
(FXN)
AJU:
106968176
PTG:
102957864
(FXN)
PPAD:
109275435
(FXN)
PUC:
125924760
PLEZ:
122204448
(FXN)
HHV:
120243410
(FXN)
BTA:
505694
(FXN)
BOM:
102280982
(FXN)
BIU:
109562939
(FXN)
BBUB:
102399412
(FXN)
BBIS:
105003474
(FXN)
CHX:
102179765
(FXN)
OAS:
101107413
(FXN)
BTAX:
128052352
(FXN)
CSUM:
138081287
(FXN)
ODA:
120870359
(FXN)
CCAD:
122451864
122453227
(FXN)
MREE:
136148599
(FXN)
OVR:
110149478
(FXN)
MBEZ:
129557635
(FXN)
SSC:
110255665
(FXN)
CFR:
102514206
(FXN)
CBAI:
105079196
(FXN)
CDK:
105105930
(FXN)
VPC:
102540335
(FXN)
BACU:
103000378
(FXN)
BMUS:
118889076
118897170
(FXN)
LVE:
103072643
103084919
(FXN)
OOR:
101278823
(FXN)
101286121
LALB:
132506056
132523603
(FXN)
DLE:
111174622
(FXN)
PCAD:
102994809
(FXN)
PSIU:
116740746
116755642
(FXN)
NASI:
112392503
(FXN)
112407442
ECB:
100056887
(FXN)
EPZ:
103558797
(FXN)
EAI:
106834404
(FXN)
MYB:
102242757
(FXN)
MYD:
102754259
(FXN)
MMYO:
118667481
(FXN)
MLF:
102425181
(FXN)
MDT:
132211971
(FXN)
MYUM:
139021210
(FXN)
PKL:
118716513
(FXN)
EFUS:
103286664
(FXN)
MNA:
107541865
(FXN)
DRO:
112299974
(FXN)
SHON:
118997834
(FXN)
AJM:
119058424
(FXN)
PDIC:
114501777
(FXN)
PHAS:
123819872
(FXN)
MMF:
118630194
(FXN)
PPAM:
129078277
(FXN)
RFQ:
117032411
(FXN)
PALE:
102887609
(FXN)
PVP:
105307131
(FXN)
RAY:
107505405
(FXN)
TOD:
119231040
(FXN)
SFUM:
130016256
(FXN)
SETR:
126004556
(FXN)
LAV:
100665301
(FXN)
TMU:
101347335
ETF:
101653601
(FXN)
101655535
DNM:
101438250
(FXN)
MDO:
100021784
(FXN)
GAS:
123233214
(FXN)
SHR:
100925413
(FXN)
AFZ:
127538215
PCW:
110218873
(FXN)
TVP:
118830615
(FXN)
PBRV:
138160298
(FXN)
OAA:
120638170
(FXN)
TACU:
119947803
(FXN)
GGA:
427244
(FXN)
PCOC:
116238857
(FXN)
MGP:
104915055
(FXN)
CJO:
107306174
(FXN)
TPAI:
128089358
(FXN)
LMUT:
125686991
(FXN)
NMEL:
110390257
(FXN)
APLA:
101800676
(FXN)
ACYG:
106044140
(FXN)
CATA:
118253768
(FXN)
AFUL:
116500728
(FXN)
TGU:
100218768
(FXN)
LSR:
110470692
(FXN)
SCAN:
103819440
(FXN)
PMOA:
120511932
(FXN)
OTC:
121333059
(FXN)
PRUF:
121363341
(FXN)
ATRC:
139588997
(FXN)
GFR:
102032266
(FXN)
FAB:
101807729
(FXN)
PHI:
102104392
(FXN)
PMAJ:
107216230
(FXN)
CCAE:
111940734
(FXN)
CCW:
104685214
(FXN)
CBRC:
103613131
(FXN)
ACOE:
138103774
(FXN)
ETL:
114056562
(FXN)
ZAB:
102074299
(FXN)
ZLE:
135460070
(FXN)
ACHL:
103802469
(FXN)
MMEA:
130573259
(FXN)
HRT:
131378468
(FXN)
SATI:
136373987
(FXN)
CCIC:
134056544
(FXN)
FPG:
101915868
(FXN)
FCH:
102059419
(FXN)
CCRI:
104155527
(FXN)
NNT:
104404064
(FXN)
SHAB:
115619634
(FXN)
ACUN:
113490127
(FXN)
TALA:
104367025
(FXN)
ACHC:
115336479
(FXN)
HALD:
104312639
(FXN)
HLE:
104832418
(FXN)
AGEN:
126036097
HHAR:
128136300
(FXN)
GCL:
127027841
CSTI:
104551208
(FXN)
LDI:
104341447
(FXN)
MNB:
103775388
(FXN)
DPUB:
104305731
(FXN)
PPUS:
135173460
(FXN)
AVIT:
104268958
(FXN)
BRHI:
104488553
(FXN)
EGZ:
104123825
(FXN)
NNI:
104008677
(FXN)
PCRI:
104024987
(FXN)
PCAO:
104039948
(FXN)
PADL:
103920367
(FXN)
AFOR:
103903966
(FXN)
FGA:
104079327
(FXN)
GSTE:
104251418
(FXN)
CBOY:
140650530
(FXN)
CLV:
102093958
(FXN)
MUI:
104534333
(FXN)
PGUU:
104458733
(FXN)
PLET:
104616950
(FXN)
CMAC:
104474240
(FXN)
CUCA:
104063171
(FXN)
TEO:
104375817
(FXN)
BREG:
104630817
(FXN)
OHA:
104338991
(FXN)
CPEA:
104398382
(FXN)
CVF:
104288844
(FXN)
RTD:
128902535
(FXN)
CRID:
134508792
(FXN)
AAM:
106484413
(FXN)
AROW:
112969823
(FXN)
NPD:
112944401
(FXN)
TGT:
104578789
(FXN)
DNE:
112981836
(FXN)
SCAM:
104142237
(FXN)
AMJ:
102570616
(FXN)
CPOO:
109323531
(FXN)
GGN:
109297609
(FXN)
PSS:
102454196
(FXN)
CMY:
102938275
(FXN)
CCAY:
125637364
(FXN)
DCC:
119856133
(FXN)
CPIC:
101933337
(FXN)
TST:
117878833
(FXN)
CABI:
116837454
(FXN)
MRV:
120407591
(FXN)
ACS:
100564369
(fxn)
ASAO:
132767369
(FXN)
PVT:
110085451
(FXN)
110088843
SUND:
121920622
(FXN)
PBI:
103050170
(FXN)
PMUR:
107294421
(FXN)
CTIG:
120314366
(FXN)
TSR:
106537989
(FXN)
PGUT:
117661465
(FXN)
APRI:
131192627
(FXN)
PTEX:
113438425
(FXN)
NSS:
113417221
(FXN)
VKO:
123031542
(FXN)
PMUA:
114606407
(FXN)
ZVI:
118076973
(FXN)
HCG:
128346653
(FXN)
GJA:
107105853
(FXN)
STOW:
125437275
(FXN)
EMC:
129334718
(FXN)
XLA:
108714196
(fxn.L)
XTR:
100497789
(fxn)
NPR:
108786367
(FXN)
RTEM:
120943548
(FXN)
BBUF:
120991520
(FXN)
BGAR:
122932677
(FXN)
PWL:
138287821
(FXN)
MUO:
115463387
(FXN)
GSH:
117350547
(FXN)
DRE:
556389
(fxn)
SRX:
107725327
(fxn)
SANH:
107664976
107674317
SGH:
107566812
107598972
CCAR:
109069647
122134126
CAUA:
113071758
113106972
113107155
CGIB:
127962925
128018915
PTET:
122349980
(fxn)
LROH:
127169173
(fxn)
OMC:
131545746
(fxn)
PPRM:
120474611
(fxn)
RKG:
130091694
(fxn)
MAMB:
125280110
(fxn)
CIDE:
127518014
CERY:
137026252
(fxn)
MASI:
127414707
127423939
TROS:
130568123
(fxn)
TDW:
130407019
(fxn)
MANU:
129415042
(fxn)
PDAB:
135729983
(fxn)
IPU:
108265194
108265371
IFU:
128608106
128608280
PHYP:
113535331
(fxn)
SMEO:
124400529
(fxn)
TFD:
113634318
(fxn)
TVC:
132854058
(fxn)
CGAR:
128529795
(fxn)
NGRA:
132893318
(fxn)
TRN:
134317767
(fxn)
AMEX:
107197449
(fxn)
CMAO:
118813841
(fxn)
EEE:
113580070
(fxn)
CHAR:
105901145
(fxn)
SPIL:
134089065
(fxn)
TRU:
101078193
(fxn)
TFS:
130525563
(fxn)
TNG:
GSTEN00007212G001
LCO:
104937870
(fxn)
TBEN:
117472821
(fxn)
CGOB:
115013952
(fxn)
PGEO:
117452676
(fxn)
GACU:
117534994
(fxn)
EMAC:
134873128
(fxn)
ELY:
117252011
(fxn)
EFO:
125890973
(fxn)
PLEP:
121944630
(fxn)
ECRA:
117945266
(fxn)
PFLV:
114555728
(fxn)
PPUG:
119225531
(fxn)
AFB:
129101529
(fxn)
CLUM:
117737006
(fxn)
PSWI:
130196523
(fxn)
CANA:
137799455
(fxn)
CVE:
137867554
(fxn)
MSAM:
119882048
119891652
SCHU:
122876894
(fxn)
CUD:
121510161
(fxn)
SPUL:
138610232
(fxn)
LMIX:
132973848
(fxn)
ALAT:
119019423
(fxn)
ASTR:
137592467
(fxn)
MZE:
101472359
106676935
(fxn)
ONL:
100698805
(fxn)
OAU:
116316680
(fxn)
OLA:
101173603
(fxn)
OML:
112136406
(fxn)
CSAI:
133450785
(fxn)
XMA:
102231271
(fxn)
XCO:
114154106
(fxn)
XHE:
116729478
(fxn)
PRET:
103470680
(fxn)
PFOR:
103155667
(fxn)
PLAI:
106940182
(fxn)
GAF:
122828241
(fxn)
PPRL:
129355317
129355384
CVG:
107093681
(fxn)
CTUL:
119795595
(fxn)
GMU:
124877216
(fxn)
KMR:
108250817
(fxn)
ALIM:
106531756
(fxn)
NWH:
119413595
(fxn)
AOCE:
111579326
(fxn)
EJA:
138198477
(fxn)
BFRE:
138614586
(fxn)
MCEP:
125012260
(fxn)
CSEM:
103397368
(fxn)
POV:
109640149
(fxn)
SSEN:
122762084
(fxn)
SSOE:
131464539
(fxn)
HHIP:
117767892
(fxn)
HSP:
118115437
(fxn)
PPLT:
128438107
(fxn)
SMAU:
118314147
(fxn)
LCF:
108878543
SDU:
111229393
(fxn)
SLAL:
111647997
(fxn)
XGL:
120805772
(fxn)
HCQ:
109510533
(fxn)
SBIA:
133499224
(fxn)
PEE:
133400478
(fxn)
PTAO:
133475456
(fxn)
BPEC:
110172504
(fxn)
ENY:
140347497
(fxn)
MALB:
109959746
(fxn)
BSPL:
114846431
(fxn)
SJO:
128365275
(fxn)
SSCO:
133979460
(fxn)
GMH:
115545797
(fxn)
SASA:
100194686
106570805
STRU:
115200535
(fxn)
OTW:
112263904
(fxn)
OMY:
110536404
(fxn)
OGO:
124035296
(fxn)
ONE:
115115546
(fxn)
OKI:
109896206
(fxn)
OKE:
118358578
(fxn)
OMM:
135513770
(fxn)
OCLA:
139389814
SALP:
111974382
112071248
SNH:
120063477
(fxn)
CCLU:
121530715
ELS:
105014078
(fxn)
OEP:
134015297
(fxn)
SFM:
108938951
(fxn)
PKI:
111839354
(fxn)
AANG:
118237446
(fxn)
AROT:
135233398
(fxn)
CCOG:
133139931
(fxn)
LOC:
102686726
(fxn)
PSPA:
121314885
(fxn)
ARUT:
117408732
117411684
PSEX:
120527395
(fxn)
LCM:
102354435
(FXN)
CMK:
103178108
(fxn)
RTP:
109926659
(fxn)
CPLA:
122563243
(fxn)
HOC:
132828865
(fxn)
LERI:
129695517
(fxn)
PMRN:
116955012
(FXN)
LRJ:
133357028
(FXN)
BFO:
118410396
BBEL:
109482403
SCLV:
120332237
SPU:
594679
LPIC:
129262340
AJJ:
139978766
APLC:
110988710
ARUN:
117295384
AAMU:
139942078
AFIL:
140152955
AJC:
117104657
SKO:
100376006
PFLL:
139122131
DME:
Dmel_CG8971
(fh)
DER:
6549891
DSE:
6619771
DSI:
Dsimw501_GD16083
(Dsim_GD16083)
DYA:
Dyak_GE17413
(Dyak_fh)
DAN:
6501892
DPO:
4815334
DPE:
6599957
DMN:
108160293
DWI:
6648483
DGR:
6565384
DMO:
Dmoj_GI15054
DAZ:
108619039
DNV:
108656086
DHE:
111603154
DVI:
6636037
CCAT:
101457549
BOD:
106627002
BDR:
105225554
RZE:
108353987
AOQ:
129237381
ALUD:
128856964
TDA:
119669894
MDE:
101890248
SCAC:
106088641
LCQ:
111682368
LSQ:
119604152
CVJ:
135959103
(fh)
GFS:
119637383
ECOE:
129947634
CLON:
129615999
HIS:
119658231
AGA:
1272401
ACOZ:
120956602
AARA:
120906680
AMER:
121590697
ASTE:
118504681
AMAP:
126559121
AFUN:
125771164
AMOU:
128307454
AMRS:
128719067
AALI:
118466569
ACOS:
131259785
131269154
AAG:
5576595
AALB:
109416551
ASUA:
134205847
CQU:
CpipJ_CPIJ014024
CpipJ_CPIJ014025
CPII:
120428508
120430550
CBRI:
134833181
CNS:
116342010
BCOO:
119068631
119068948
LLL:
129788793
PPAP:
129807911
AME:
552635
ACER:
107999075
ALAB:
122720064
ADR:
102674826
AFLR:
100870072
BIM:
100748679
BBIF:
117204073
BVK:
117235684
BVAN:
117159516
BHUN:
126868005
BTER:
100642799
BAFF:
126914533
BPYO:
122567206
BPAS:
132909577
FVI:
122533745
CCAL:
108633045
OBB:
114876743
OLG:
117601774
MGEN:
117220502
NMEA:
116427821
CGIG:
122404596
SOC:
105194758
MPHA:
105838244
AEC:
105151794
ACEP:
105627760
PBAR:
105425138
VEM:
105569379
COBS:
139101470
(Fh)
TLN:
139810631
(Fh)
HST:
109503755
DQU:
106741315
CFO:
105253011
FEX:
115244895
PMEC:
138932265
(Fh)
LHU:
105673991
(fh)
PGC:
109854040
OBO:
105281188
PCF:
106791866
PFUC:
122522364
VPS:
122636475
VCRB:
124432300
VVE:
124956589
CSOL:
105361159
TPRE:
106653904
LHT:
122502136
MDL:
103576647
CGLO:
123262885
123275166
FAS:
105268127
DAM:
107045816
AGIF:
122853753
CINS:
118068926
VCAN:
122409946
CCIN:
107264996
DSM:
124405641
NPT:
124223333
(fh)
NFB:
124185630
NLO:
107222751
NVG:
124308710
AROA:
105688633
TCA:
658405
TMOL:
138136580
(fh)
DPA:
109543441
ESIM:
136411569
(fh)
SOY:
115879714
AGRG:
126736076
CSET:
123307200
HAXR:
123688650
AGB:
108914544
LDC:
111508006
DVV:
114337175
NVL:
108557126
PPYR:
116182064
OTU:
111417027
BMOR:
134199322
BMAN:
114253275
MSEX:
115449100
DPL:
KGM_209818
BANY:
112050629
MJU:
123867813
VCD:
124532493
MCIX:
123655028
PMAC:
106720241
PPOT:
106108360
PXU:
106121189
BPHI:
137931739
(fh)
PRAP:
111004167
PBX:
123710739
PNAP:
125053180
ZCE:
119840504
CCRC:
123693468
LSIN:
126967130
AAGE:
121727142
HAW:
110379195
HZE:
124631643
TNL:
113500566
SLIU:
111355771
OFU:
114364033
ONU:
135074249
ATRA:
106130374
GMW:
128201861
PXY:
105386790
PGW:
126369721
LGLY:
125242615
CSTB:
134743787
CFEL:
113375074
113377229
CCRN:
123305747
API:
100571875
DNX:
107162495
AGS:
114131426
RMD:
113549089
DVT:
126896475
BTAB:
109042588
DCI:
103508303
103508307
CLEC:
106661212
NLU:
111055420
120355613
MQU:
128984297
PHU:
Phum_PHUM414880
FOC:
113216100
TPAL:
117651777
ZNE:
110831472
CSEC:
111871050
SGRE:
126356679
IEL:
124160465
HAMR:
139686791
(fh)
FCD:
110842515
DPX:
DAPPUDRAFT_333409
DMK:
116919880
DPZ:
124343472
AFRA:
136034813
PVM:
113803990
(fh)
PJA:
122249404
PCHN:
125036681
PMOO:
119592273
HAME:
121879891
PCLA:
123762069
(fh)
CQD:
128695410
(fh)
PTRU:
123512077
ESN:
126996752
MNZ:
135195513
HAZT:
108666819
EAF:
111712054
LSM:
121123921
(fh)
TCF:
131889708
PPOI:
119098848
DSV:
119442856
RSAN:
119388116
RMP:
119187007
VDE:
111247876
TUT:
107360744
DPTE:
113790037
DFR:
124494171
CSCU:
111613971
CVS:
136979764
(fh)
ABRU:
129969603
SDM:
118182046
PMEO:
129584893
CEL:
CELE_F59G1.7
(frh-1)
CBR:
CBG_02538
(Cbr-frh-1)
CRQ:
GCK72_006151
NAI:
NECAME_15871
BMY:
BM_BM4611
(Bma-frh-1)
LOA:
LOAG_11762
HRO:
HELRODRAFT_63973
LGI:
LOTGIDRAFT_126633
PCAN:
112553543
LSAX:
138978984
BGT:
106051192
GAE:
121377651
HRF:
124150138
HRJ:
124287715
HASI:
137277151
HCRA:
139461064
CRG:
105332219
CANU:
128178066
CVN:
111128562
111130805
OED:
125652605
MYI:
110447232
PMAX:
117335130
AIRR:
138332977
MCAF:
127735251
MMER:
123566403
RPHI:
132729088
132736515
DPOL:
127876869
MAEA:
128228665
OBI:
106877921
OSN:
115215113
LJP:
135473917
LAK:
106163079
106164829
SMM:
Smp_137190
OVI:
T265_07662
EGL:
EGR_07948
NVE:
5507635
EPA:
110243169
ATEN:
116294635
ADF:
107344117
AMIL:
114954072
MCAZ:
138049981
MFOO:
137992004
PDAM:
113672575
SPIS:
111324823
DGT:
114522614
XEN:
124446997
HMG:
100211504
HSY:
130630663
RES:
135687288
TAD:
TRIADDRAFT_23043
AQU:
100632700
100632940
ATH:
AT4G03240
(FH)
ALY:
9310941
CRB:
17882468
CSAT:
104707764
104715034
104737482
104738250
104783636
EUS:
EUTSA_v10028999mg
BRP:
103846758
103858710
BNA:
106386184
106431493
106443795
BOE:
106315452
106334514
RSZ:
108828266
108835517
108845948
THJ:
104806805
CPAP:
110821173
CIT:
102624465
CIC:
CICLE_v10016814mg
PVY:
116124229
MINC:
123196272
123222756
TCC:
18608575
GRA:
105794928
GHI:
107886816
107909316
107934849
GAB:
108474646
HSYR:
120171526
120172682
120178132
120197008
DZI:
111283144
EGR:
104424829
RARG:
115750917
GMX:
100811801
100815916
GSJ:
114399066
114405724
PVU:
137813782
VRA:
106753999
106764299
VAR:
108329534
VUN:
114191500
VUM:
124826166
CCAJ:
109802202
APRC:
113863189
MTR:
112422695
11419302
11428991
TPRA:
123893215
CAM:
101504575
PSAT:
127126573
VVO:
131612350
ADU:
107465063
AIP:
107604754
AHF:
112710640
112754727
LANG:
109341418
109357790
PCIN:
129311560
QSA:
O6P43_000640
O6P43_028737
FVE:
101298868
AANS:
126800711
RCN:
112183978
PPER:
18782465
PMUM:
103329488
PAVI:
110770178
PDUL:
117622068
MDM:
103425927
MSYL:
126612485
126634170
PXB:
103933489
103941867
103944488
PCOX:
137708658
137740805
ZJU:
107416895
MNT:
21405046
CSAV:
115716089
CSV:
101210597
CMO:
103490464
BHJ:
120087759
MCHA:
111011350
CMAX:
111469879
CMOS:
111451278
CPEP:
111795393
RCU:
8269381
MEAN:
126673555
HBR:
110653963
110667038
MESC:
110607091
POP:
7494452
PEU:
105142530
PALZ:
118028188
PNZ:
133669420
JRE:
108991988
109020003
CILL:
122303872
CAVE:
132168188
132180764
AGLU:
133860940
QSU:
112012391
QLO:
115954620
TWL:
119999662
120007009
VVI:
100252899
VRI:
117926023
117926653
SLY:
101265146
SPEN:
107024574
SOT:
102599759
SSTN:
125876645
SDUL:
129891739
CANN:
107876758
LBB:
132617881
NTA:
107759791
107795592
NSY:
104236630
NTO:
104102180
NAU:
109221440
INI:
109187866
ITR:
115995736
116008644
SIND:
105162653
OEU:
111374116
111380648
111385561
EGT:
105963846
SSPL:
121756226
121757859
121783919
121785696
SMIL:
130999340
131012618
SHIS:
125212301
APAN:
127240745
HAN:
110923051
ECAD:
122579823
LSV:
111890103
CCAV:
112527872
DCR:
108211521
108225167
CSIN:
114261795
114269206
RVL:
131323100
AEW:
130761413
130791063
DLT:
127792114
BVG:
104887578
104892089
SOE:
110795217
CQI:
110692767
110721098
110732718
ATRI:
130801206
MOF:
131149474
NNU:
104594628
MING:
122094385
TSS:
122639389
122658170
PSOM:
113353048
113357745
OSA:
4327058
OBR:
102722906
OGL:
127774127
BDI:
100824478
ATS:
109771096
TDC:
119269223
119277215
TAES:
123062261
123071018
123079391
TUA:
125543158
LPER:
127344049
LRD:
124689075
SBI:
8054718
8064041
ZMA:
100279847
100284365
MFLO:
136472699
136472806
136482886
136501872
136501873
SITA:
101765293
SVS:
117854853
PVIR:
120674323
120708289
PHAI:
112896012
PAUA:
133908891
133922110
PDA:
103706570
103723975
EGU:
105046968
105049654
MUS:
104000447
135610669
ZOF:
121976313
DCT:
110092510
PEQ:
110032319
AOF:
109822382
MSIN:
131248080
ACAK:
137941336
NCOL:
116250613
ATR:
18426399
CJF:
131030358
SMO:
SELMODRAFT_103203
SELMODRAFT_126074
PPP:
112286219
CRE:
CHLRE_12g538350v5
VCN:
VOLCADRAFT_117689
(ftx1)
CSL:
COCSUDRAFT_19698
CVR:
CHLNCDRAFT_20883
APRO:
F751_1790
OLU:
OSTLU_30187
OTA:
OT_ostta02g01420
BPG:
Bathy08g03350
MIS:
MICPUN_107399
(FRA)
MPP:
MICPUCDRAFT_9181
CME:
CYME_CMK051C
SCE:
YDL120W
(YFH1)
SEUB:
DI49_0951
SPAO:
SPAR_D01180
AGO:
AGOS_AGR387C
ERC:
Ecym_3347
KLA:
KLLA0_E08845g
KMX:
KLMA_80109
(YFH1)
LTH:
KLTH0G10978g
VPO:
Kpol_1043p33
ZRO:
ZYRO0A02464g
CGR:
2891639
(YFH1)
NCS:
NCAS_0B06120
(NCAS0B06120)
NCAS_0G03670
(NCAS0G03670)
NDI:
NDAI_0B03410
(NDAI0B03410)
NDAI_0G00790
(NDAI0G00790)
TPF:
TPHA_0C03530
(TPHA0C03530)
TBL:
TBLA_0B07150
(TBLA0B07150)
TGB:
HG536_0A02370
TDL:
TDEL_0G02390
(TDEL0G02390)
KAF:
KAFR_0A06890
(KAFR0A06890)
KNG:
KNAG_0A05470
(KNAG0A05470)
ZMK:
HG535_0D01800
SLUD:
SCDLUD_002729
DHA:
DEHA2C10604g
PIC:
PICST_63502
(FRD1)
PGU:
PGUG_03715
SPAA:
SPAPADRAFT_58839
LEL:
PVL30_004367
(YFH1)
LBG:
92210446
(LODBEIA_P52500)
CAL:
CAALFM_C404340CA
(YFH1)
CTP:
CTRG_03932
COT:
CORT_0E04470
CDU:
CD36_44010
CTEN:
90982157
(YFH1)
CLU:
CLUG_05631
CLUS:
A9F13_05g03333
CAUR:
CJI96_0005217
ASAU:
88173191
(PUMCH_002126)
PPA:
PAS_chr1-4_0025
PKZ:
C5L36_0A04650
BNN:
FOA43_004004
BBRX:
BRETT_002948
OPA:
HPODL_03451
NCR:
NCU09754
NTE:
NEUTE1DRAFT117198
(NEUTE1DRAFT_117198)
SMP:
10808731
(SMAC4_08169)
PAN:
PODANSg6878
PBEL:
QC761_310280
PPSD:
QC762_310280
PPSP:
QC763_310280
PPSA:
QC764_310280
TTT:
THITE_109555
MTM:
MYCTH_2312932
CTHR:
CTHT_0015430
RTHE:
98128293
(VTJ83DRAFT_6889)
MGR:
MGG_02435
PPEI:
PpBr36_07016
PGRI:
PgNI_05577
TMN:
UCRPA7_7504
SSCK:
SPSK_00332
FGR:
FGSG_06006
FPU:
FPSE_02965
FPOA:
FPOAC1_008971
FVN:
FVRRES_09589
FVR:
FVEG_04636
FOX:
FOXG_07712
NHE:
NECHADRAFT_78848
FFC:
NCS54_00536200
FKR:
NCS57_00574400
FMU:
J7337_006675
TRE:
TRIREDRAFT_33197
TRR:
M419DRAFT_25182
TATV:
25778129
(TrAtP1_004108)
TASP:
36611503
(TrAFT101_003585)
MAW:
19247967
(J3458_005099)
MAJ:
MAA_02532
MBRN:
26241973
(FRTXN)
PCHM:
VFPPC_00958
CMT:
CCM_00224
AMUS:
LMH87_000462
PLJ:
90643341
(PLICBS_008544)
PTKZ:
JDV02_006087
VAL:
VDBG_05732
VDA:
VDAG_07667
CFJ:
CFIO01_05018
CLUP:
CLUP02_01700
CHIG:
CH63R_10538
CDET:
87943648
(CDEST_07145)
SAPO:
SAPIO_CDS0930
ELA:
UCREL1_9955
PFY:
PFICI_09254
SSL:
SS1G_10732
BFU:
BCIN_04g05230
(Bcyfh1)
MBE:
MBM_02617
PSCO:
LY89DRAFT_687611
GLZ:
GLAREA_03552
ANI:
ANIA_01986
AFM:
AFUA_4G10510
ACT:
ACLA_049710
NFI:
NFIA_105560
AOR:
AO090003001160
ANG:
An04g06160
AFV:
AFLA_000507
ALUC:
AKAW2_51581A
(FRR4)
ACHE:
ACHE_10785S
(FRR4)
APUU:
APUU_21069S
(FRR4)
PCS:
N7525_005512
PDP:
PDIP_32860
POU:
POX_d06029
TMF:
EYB26_005254
TRG:
TRUGW13939_02752
CIM:
CIMG_01457
CPW:
9691229
(FRR4)
URE:
UREG_05138
ABE:
ARB_03745
TVE:
TRV_05003
PBL:
PAAG_02608
PBN:
PADG_01626
AJE:
HCAG_06107
BGH:
BDBG_02323
PNO:
SNOG_15577
PTE:
PTT_05976
PTRR:
6343547
(PtrM4_111790)
BZE:
COCCADRAFT_2791
BSC:
COCSADRAFT_32092
BOR:
COCMIDRAFT_82129
AALT:
CC77DRAFT_954775
ADAC:
96089309
(ACET3X_008987)
ARAB:
EKO05_0006166
ZTR:
MYCGRDRAFT_41229
PFJ:
MYCFIDRAFT_101814
FFU:
CLAFUR5_01246
CBET:
CB0940_00935
BCOM:
BAUCODRAFT_47876
NPA:
UCRNP2_5905
TML:
GSTUM_00000153001
SPO:
2539143
(fxn1)
SOM:
SOMG_04302
(fxn1)
CNE:
CNL06050
CNB:
CNBI0780
CNG:
CNAG_05011
CGI:
CGB_D0690C
CDEU:
CNBG_4670
CDEP:
91086876
(L203_102665)
KMG:
30163376
(I203_102578)
KNE:
92182368
(IAR55_005110)
TMS:
TREMEDRAFT_28077
TASA:
A1Q1_04736
CCAC:
CcaHIS019_0202330
(YFH1)
TVS:
TRAVEDRAFT_159598
DSQ:
DICSQDRAFT_75270
PCO:
PHACADRAFT_82303
SHS:
STEHIDRAFT_107190
HIR:
HETIRDRAFT_457050
PSQ:
PUNSTDRAFT_59718
ADL:
AURDEDRAFT_49862
FME:
FOMMEDRAFT_121504
GTR:
GLOTRDRAFT_32459
LBC:
LACBIDRAFT_228512
CCI:
CC1G_08622
ABP:
AGABI1DRAFT32410
(AGABI1DRAFT_32410)
ABV:
AGABI2DRAFT61965
(AGABI2DRAFT_61965)
PCUB:
JR316_0001218
MRR:
Moror_181
MORE:
E1B28_001301
SCM:
SCHCO_02490619
(SCHCODRAFT_02490619)
CPUT:
CONPUDRAFT_114898
SLA:
SERLADRAFT_414631
WSE:
WALSEDRAFT_49219
WIC:
J056_001908
UMA:
UMAG_04428
PFP:
PFL1_05750
SGRA:
EX895_002388
MRT:
MRET_2446
PGR:
PGTG_11242
PSTR:
Pst134EA_024196
MLR:
MELLADRAFT_93828
ECU:
ECU01_1310
EIN:
Eint_011240
EHE:
EHEL_011220
ERO:
EROM_011140
VNX:
VNE69_02252
MBR:
MONBRDRAFT_28012
SRE:
PTSG_05027
DDI:
DDB_G0293246
(fxn)
DPP:
DICPUDRAFT_11345
DFA:
DFA_05886
(fxn)
ACAN:
ACA1_219430
BBIG:
BBBOND_0400660
CPV:
cgd5_4320
CHO:
Chro.50410
TGO:
TGME49_262810
TET:
TTHERM_00989460
PTM:
GSPATT00024939001
GSPATT00026713001
PTI:
PHATRDRAFT_14927
FCY:
FRACYDRAFT_177808
TPS:
THAPSDRAFT_32741
AAF:
AURANDRAFT_38974
AURANDRAFT_55119
PIF:
PITG_01287
PSOJ:
PHYSODRAFT_354548
SPAR:
SPRG_00493
TBR:
Tb927.3.1000
TBG:
TbgDal_III690
TCR:
511865.19
LMA:
LMJF_25_1050
LIF:
LINJ_25_1090
LDO:
LDBPK_251090
LMI:
LMXM_25_1050
LMAT:
92515292
(LSCM1_05309)
LBZ:
LBRM_25_0940
LPAN:
LPMP_251080
LOI:
92360373
(LSCM4_04455)
LEIS:
94179760
(GH5_04319)
LENR:
94172411
(CUR178_05207)
LEIN:
94188169
(JIQ42_04511)
PHET:
94290665
(JKF63_04606)
NGR:
NAEGRDRAFT_63017
TVA:
TVAG_2v0528410
TVAG_2v0570800
EHX:
EMIHUDRAFT_209055
EMIHUDRAFT_355136
EMIHUDRAFT_366087
GTT:
GUITHDRAFT_146273
» show all
Taxonomy
UniProt
Reference
PMID:
15641778
Authors
O'Neill HA, Gakh O, Park S, Cui J, Mooney SM, Sampson M, Ferreira GC, Isaya G
Title
Assembly of human frataxin is a mechanism for detoxifying redox-active iron.
Journal
Biochemistry 44:537-45 (2005)
DOI:
10.1021/bi048459j
Sequence
[hsa:
2395
]
Reference
PMID:
12732649
Authors
Park S, Gakh O, O'Neill HA, Mangravita A, Nichol H, Ferreira GC, Isaya G
Title
Yeast frataxin sequentially chaperones and stores iron by coupling protein assembly with iron oxidation.
Journal
J Biol Chem 278:31340-51 (2003)
DOI:
10.1074/jbc.M303158200
Sequence
[sce:
YDL120W
]
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