KEGG   Mus caroli (Ryukyu mouse): 110298425
Entry
110298425         CDS       T05910                                 
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mcal  Mus caroli (Ryukyu mouse)
Pathway
mcal00280  Valine, leucine and isoleucine degradation
mcal00640  Propanoate metabolism
mcal00785  Lipoic acid metabolism
mcal01100  Metabolic pathways
mcal01210  2-Oxocarboxylic acid metabolism
Module
mcal_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mcal00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    110298425 (Bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    110298425 (Bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    110298425 (Bckdha)
Enzymes [BR:mcal01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     110298425 (Bckdha)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 110298425
NCBI-ProteinID: XP_021023326
Ensembl: MGP_CAROLIEiJ_G0029375
UniProt: A0A6P5Q3P2
LinkDB
Position
7:complement(24842933..24872885)
AA seq 446 aa
MAIVMSAAKIWRPSRGLGQAARLLLGRSGVRGLARSHPSRQQQQQFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPIYRVMDRQGQIINASEDPHLPQEEVLKFYRSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALERTDLVFGQYREAGVLMYRDYPLELFMSQCY
GNVNDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRIVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRQYLLNQGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPNPSLLFSDVYQEMPAQ
LRRQQESLARHLQTYGEHYPLDHFDK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcgatagtgatgtctgcggccaagatctggaggccgagccgtggcttgggccaggct
gcccgcctcctgttggggcgatctggagttcgtggtttggctagatcccaccccagcagg
cagcagcaacagcagttcccatccctggacgacaagccccagttcccaggggcctctgca
gagtttgtagacaagcttgagttcatccagcccaatgtcatctctggcatccccatctac
cgtgtcatggaccgccagggccagatcatcaatgccagtgaagatccccacctgccccag
gaggaggtgctgaagttctaccggagcatgacgctgctcaacaccatggaccgcattctc
tatgagtcccagcggcagggccggatctccttctacatgaccaactatggcgaggagggg
acacatgtgggcagtgctgctgccttggagcgcacagacctggtgtttggccagtaccgg
gaggcaggtgtgctcatgtaccgggactacccgctggagctgttcatgtcccagtgctac
ggcaacgtgaatgatccaggcaagggacgccagatgccagttcactacggctgcaaggaa
cgacacttcgtcaccatttcctctccactggccacgcagatccctcaggcggtaggggca
gcctatgctgccaagcgggccaatgccaaccggattgtgatctgttattttggtgagggg
gcagccagtgaaggggatgcccacgccggtttcaatttcgctgccaccctggagtgtccc
atcatcttcttctgccggaacaatggctatgccatctccacaccaacctctgagcagtac
cgtggggatggcatagccgctcggggccctgggtatggcatcatgtcaatccgtgtggac
ggcaacgatgtgtttgctgtgtacaacgccactaaggaggcccgacgtcgggctgtggct
gagaaccagcccttcctcattgaggccatgacctacaggattggccaccacagcaccagt
gacgacagctcggcgtaccgttcggtggacgaggtcaattactgggacaagcaggaccac
ccaatctcgaggctgaggcagtacctgctgaaccagggttggtgggatgaggaacaggag
aaggcctggcggaagcagtcacgaaagaaggtcatggaagcctttgagcaggctgagcgg
aagctaaagccgaacccaagcctcctcttctccgatgtgtaccaggagatgcccgcccag
ctccgcaggcagcaggagtcgctggcacggcacctgcagacttacggggagcactacccc
ctggaccactttgacaagtga

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