Mus caroli (Ryukyu mouse): 110298425
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Entry
110298425 CDS
T05910
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
mcal
Mus caroli (Ryukyu mouse)
Pathway
mcal00280
Valine, leucine and isoleucine degradation
mcal00640
Propanoate metabolism
mcal00785
Lipoic acid metabolism
mcal01100
Metabolic pathways
mcal01210
2-Oxocarboxylic acid metabolism
Module
mcal_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mcal00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
110298425 (Bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
110298425 (Bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
110298425 (Bckdha)
Enzymes [BR:
mcal01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
110298425 (Bckdha)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
110298425
NCBI-ProteinID:
XP_021023326
Ensembl:
MGP_CAROLIEiJ_G0029375
UniProt:
A0A6P5Q3P2
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Position
7:complement(24842933..24872885)
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AA seq
446 aa
AA seq
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MAIVMSAAKIWRPSRGLGQAARLLLGRSGVRGLARSHPSRQQQQQFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPIYRVMDRQGQIINASEDPHLPQEEVLKFYRSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALERTDLVFGQYREAGVLMYRDYPLELFMSQCY
GNVNDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRIVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRQYLLNQGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPNPSLLFSDVYQEMPAQ
LRRQQESLARHLQTYGEHYPLDHFDK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcgatagtgatgtctgcggccaagatctggaggccgagccgtggcttgggccaggct
gcccgcctcctgttggggcgatctggagttcgtggtttggctagatcccaccccagcagg
cagcagcaacagcagttcccatccctggacgacaagccccagttcccaggggcctctgca
gagtttgtagacaagcttgagttcatccagcccaatgtcatctctggcatccccatctac
cgtgtcatggaccgccagggccagatcatcaatgccagtgaagatccccacctgccccag
gaggaggtgctgaagttctaccggagcatgacgctgctcaacaccatggaccgcattctc
tatgagtcccagcggcagggccggatctccttctacatgaccaactatggcgaggagggg
acacatgtgggcagtgctgctgccttggagcgcacagacctggtgtttggccagtaccgg
gaggcaggtgtgctcatgtaccgggactacccgctggagctgttcatgtcccagtgctac
ggcaacgtgaatgatccaggcaagggacgccagatgccagttcactacggctgcaaggaa
cgacacttcgtcaccatttcctctccactggccacgcagatccctcaggcggtaggggca
gcctatgctgccaagcgggccaatgccaaccggattgtgatctgttattttggtgagggg
gcagccagtgaaggggatgcccacgccggtttcaatttcgctgccaccctggagtgtccc
atcatcttcttctgccggaacaatggctatgccatctccacaccaacctctgagcagtac
cgtggggatggcatagccgctcggggccctgggtatggcatcatgtcaatccgtgtggac
ggcaacgatgtgtttgctgtgtacaacgccactaaggaggcccgacgtcgggctgtggct
gagaaccagcccttcctcattgaggccatgacctacaggattggccaccacagcaccagt
gacgacagctcggcgtaccgttcggtggacgaggtcaattactgggacaagcaggaccac
ccaatctcgaggctgaggcagtacctgctgaaccagggttggtgggatgaggaacaggag
aaggcctggcggaagcagtcacgaaagaaggtcatggaagcctttgagcaggctgagcgg
aagctaaagccgaacccaagcctcctcttctccgatgtgtaccaggagatgcccgcccag
ctccgcaggcagcaggagtcgctggcacggcacctgcagacttacggggagcactacccc
ctggaccactttgacaagtga
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