KEGG   PATHWAY: dpe00280
Entry
dpe00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Drosophila persimilis
Class
Metabolism; Amino acid metabolism
Pathway map
dpe00280  Valine, leucine and isoleucine degradation
dpe00280

Module
dpe_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:dpe00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Drosophila persimilis [GN:dpe]
Gene
6600072  branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
6591427  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
6597984  2-oxoisovalerate dehydrogenase subunit beta, mitochondrial [KO:K00167] [EC:1.2.4.4]
6600400  lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
6598891  dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
6594625  short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
6591392  short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
6595907  probable medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
6602478  isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
6595810  short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
6589537  trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
6592438  probable enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
6599292  3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
6589709  3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
6590371  trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
6594815  3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X2 [KO:K05605] [EC:3.1.2.4]
6591227  probable 3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K23146] [EC:1.1.1.31 1.1.1.59]
6598146  probable methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
6593373  aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
6593374  aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
6588193  aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
6602384  putative aldehyde dehydrogenase family 7 member A1 homolog [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
6588871  uncharacterized protein LOC6588871 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
6597648  acyl-CoA synthetase family member 3, mitochondrial [KO:K18660] [EC:6.2.1.76 6.2.1.-]
6589366  acyl-CoA synthetase family member 3, mitochondrial [KO:K18660] [EC:6.2.1.76 6.2.1.-]
6603329  4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
6603439  alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
6587506  methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial [KO:K01968] [EC:6.4.1.4]
6590276  probable methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
6590800  methylglutaconyl-CoA hydratase, mitochondrial [KO:K05607] [EC:4.2.1.18]
6593418  hydroxymethylglutaryl-CoA lyase, mitochondrial [KO:K01640] [EC:4.1.3.4]
6599089  succinyl-CoA:3-ketoacid-coenzyme A transferase, mitochondrial [KO:K01027] [EC:2.8.3.5]
6597613  acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
6601016  uncharacterized protein LOC6601016 [KO:K00626] [EC:2.3.1.9]
6590096  hydroxymethylglutaryl-CoA synthase 1 [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
dpe00020  Citrate cycle (TCA cycle)
dpe00240  Pyrimidine metabolism
dpe00290  Valine, leucine and isoleucine biosynthesis
dpe00640  Propanoate metabolism
dpe00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

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