| Entry |
|
|---|
| Name |
Glycine cleavage system, Gly to MTHF
|
|---|
| Definition |
Gly+Lipoyl-H -- GLDC >> AMT -> MTHF+Dihydrolipoyl-H |
|---|
| Expanded |
(C00037+C02051) -- 2731 >> 275 -> (C00143+C02972) |
|---|
| Class |
nt06033 Glycine, serine and arginine metabolism
nt06032 Lipoic acid metabolism
|
|---|
| Type |
Reference
|
|---|
| Pathway |
| hsa00260 | Glycine, serine and threonine metabolism |
|
|---|
| Gene |
| 2731 | GLDC; glycine decarboxylase |
| 275 | AMT; aminomethyltransferase |
|
|---|
| Metabolite |
| C02051 | [H-protein]-lipoyllysine |
| C00143 | 5,10-Methylenetetrahydrofolate |
| C02972 | [H-protein]-dihydrolipoyllysine |
|
|---|
| Reference |
|
|---|
| Authors |
Applegarth DA, Toone JR |
|---|
| Title |
Nonketotic hyperglycinemia (glycine encephalopathy): laboratory diagnosis. |
|---|
| Journal |
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|---|
| LinkDB |
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