KEGG   MODULE: clv_M00861
Entry
clv_M00861        Pathway   Module                                 
Name
beta-Oxidation, peroxisome, VLCFA
Definition
K00232 K12405 (K07513,K08764)
Diagram
clv_M00861  beta-Oxidation, peroxisome, VLCFA
clv_M00861

Class
Pathway modules; Lipid metabolism; Fatty acid metabolism
Pathway
clv01040  Biosynthesis of unsaturated fatty acids
clv01212  Fatty acid metabolism
clv01100  Metabolic pathways
Organism
Columba livia (rock pigeon) [GN:clv]
Gene
102087499  SCP2; non-specific lipid-transfer protein [KO:K08764]
102088336  ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal [KO:K07513]
102090446  ACOX3; peroxisomal acyl-coenzyme A oxidase 3 isoform X1 [KO:K00232]
102091425  ACOX1; LOW QUALITY PROTEIN: peroxisomal acyl-coenzyme A oxidase 1 [KO:K00232]
102095771  HSD17B4; peroxisomal multifunctional enzyme type 2 [KO:K12405]
Reaction
Compound
C16168  (6Z,9Z,12Z,15Z,18Z,21Z)-Tetracosahexaenoyl-CoA
C16374  (2E,6Z,9Z,12Z,15Z,18Z,21Z)-Tetracosaheptaenoyl-CoA
C16375  (3R,6Z,9Z,12Z,15Z,18Z,21Z)-3-Hydroxytetracosahexaenoyl-CoA
C16376  (6Z,9Z,12Z,15Z,18Z,21Z)-3-Oxotetracosahexaenoyl-CoA
C16169  (4Z,7Z,10Z,13Z,16Z,19Z)-Docosahexaenoyl-CoA
C16172  (6Z,9Z,12Z,15Z,18Z)-Tetracosapentaenoyl-CoA
C16387  (2E,6Z,9Z,12Z,15Z,18Z)-Tetracosahexaenoyl-CoA
C16388  (3R,6Z,9Z,12Z,15Z,18Z)-3-Hydroxytetracosapentaenoyl-CoA
C16389  (6Z,9Z,12Z,15Z,18Z)-3-Oxotetracosapentaenoyl-CoA
C16173  (4Z,7Z,10Z,13Z,16Z)-Docosapentaenoyl-CoA
RModule
RM018  Beta oxidation in acyl-CoA degradation
Reference
  Authors
Ferdinandusse S, Denis S, Mooijer PA, Zhang Z, Reddy JK, Spector AA, Wanders RJ
  Title
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid.
  Journal
J Lipid Res 42:1987-95 (2001)
Reference
  Authors
Waterham HR, Ferdinandusse S, Wanders RJ
  Title
Human disorders of peroxisome metabolism and biogenesis.
  Journal
Biochim Biophys Acta 1863:922-33 (2016)
DOI:10.1016/j.bbamcr.2015.11.015
KO module
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