 | | MODULE: clv_M00861 | |
| Entry |
clv_M00861 Pathway Module
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| Name |
beta-Oxidation, peroxisome, VLCFA
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| Definition |
K00232 K12405 (K07513,K08764)
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| Diagram |
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| Class |
Pathway modules; Lipid metabolism; Fatty acid metabolism
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| Pathway |
| clv01040 | Biosynthesis of unsaturated fatty acids |
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| Organism |
Columba livia (rock pigeon) [GN: clv]
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| Gene |
| 102090446 | ACOX3; peroxisomal acyl-coenzyme A oxidase 3 isoform X1 [KO:K00232] |
| 102091425 | ACOX1; LOW QUALITY PROTEIN: peroxisomal acyl-coenzyme A oxidase 1 [KO:K00232] |
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| Reaction |
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| Compound |
| C16168 | (6Z,9Z,12Z,15Z,18Z,21Z)-Tetracosahexaenoyl-CoA |
| C16374 | (2E,6Z,9Z,12Z,15Z,18Z,21Z)-Tetracosaheptaenoyl-CoA |
| C16375 | (3R,6Z,9Z,12Z,15Z,18Z,21Z)-3-Hydroxytetracosahexaenoyl-CoA |
| C16376 | (6Z,9Z,12Z,15Z,18Z,21Z)-3-Oxotetracosahexaenoyl-CoA |
| C16169 | (4Z,7Z,10Z,13Z,16Z,19Z)-Docosahexaenoyl-CoA |
| C16172 | (6Z,9Z,12Z,15Z,18Z)-Tetracosapentaenoyl-CoA |
| C16387 | (2E,6Z,9Z,12Z,15Z,18Z)-Tetracosahexaenoyl-CoA |
| C16388 | (3R,6Z,9Z,12Z,15Z,18Z)-3-Hydroxytetracosapentaenoyl-CoA |
| C16389 | (6Z,9Z,12Z,15Z,18Z)-3-Oxotetracosapentaenoyl-CoA |
| C16173 | (4Z,7Z,10Z,13Z,16Z)-Docosapentaenoyl-CoA |
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| RModule |
| RM018 | Beta oxidation in acyl-CoA degradation |
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| Reference |
|
| Authors |
Ferdinandusse S, Denis S, Mooijer PA, Zhang Z, Reddy JK, Spector AA, Wanders RJ |
| Title |
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid. |
| Journal |
J Lipid Res 42:1987-95 (2001) |
| Reference |
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| Authors |
Waterham HR, Ferdinandusse S, Wanders RJ |
| Title |
Human disorders of peroxisome metabolism and biogenesis. |
| Journal |
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| KO module |
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| LinkDB |
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