KEGG   Homo sapiens (human): 1757
Entry
1757              CDS       T01001                                 
Symbol
SARDH, BPR-2, DMGDHL1, SAR, SARD, SDH
Name
(RefSeq) sarcosine dehydrogenase
  KO
K00314  sarcosine dehydrogenase [EC:1.5.8.3]
Organism
hsa  Homo sapiens (human)
Pathway
hsa00260  Glycine, serine and threonine metabolism
hsa00670  One carbon pool by folate
hsa01100  Metabolic pathways
Module
hsa_M00974  Betaine metabolism, animals, betaine => glycine
Network
nt06033  Glycine, serine and arginine metabolism
nt06038  Folate metabolism
  Element
N01789  Betaine metabolism
N01868  Demethylation of sarcosine
Disease
H02657  Sarcosinemia
Brite
KEGG Orthology (KO) [BR:hsa00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00260 Glycine, serine and threonine metabolism
    1757 (SARDH)
  09108 Metabolism of cofactors and vitamins
   00670 One carbon pool by folate
    1757 (SARDH)
Enzymes [BR:hsa01000]
 1. Oxidoreductases
  1.5  Acting on the CH-NH group of donors
   1.5.8  With a flavin or flavoprotein as acceptor
    1.5.8.3  sarcosine dehydrogenase
     1757 (SARDH)
SSDB
Motif
Pfam: DAO GCV_T FAO_M GCV_T_C Pyr_redox_2 PrpF
Other DBs
NCBI-GeneID: 1757
NCBI-ProteinID: NP_001128179
OMIM: 604455
HGNC: 10536
Ensembl: ENSG00000123453
UniProt: Q9UL12 A8K596
LinkDB
Position
9:complement(133659418..133739955)
AA seq 918 aa
MASLSRALRVAAAHPRQSPTRGMGPCNLSSAAGPTAEKSVPYQRTLKEGQGTSVVAQGPS
RPLPSTANVVVIGGGSLGCQTLYHLAKLGMSGAVLLERERLTSGTTWHTAGLLWQLRPSD
VEVELLAHTRRVVSRELEEETGLHTGWIQNGGLFIASNRQRLDEYKRLMSLGKAYGVESH
VLSPAETKTLYPLMNVDDLYGTLYVPHDGTMDPAGTCTTLARAASARGAQVIENCPVTGI
RVWTDDFGVRRVAGVETQHGSIQTPCVVNCAGVWASAVGRMAGVKVPLVAMHHAYVVTER
IEGIQNMPNVRDHDASVYLRLQGDALSVGGYEANPIFWEEVSDKFAFGLFDLDWEVFTQH
IEGAINRVPVLEKTGIKSTVCGPESFTPDHKPLMGEAPELRGFFLGCGFNSAGMMLGGGC
GQELAHWIIHGRPEKDMHGYDIRRFHHSLTDHPRWIRERSHESYAKNYSVVFPHDEPLAG
RNMRRDPLHEELLGQGCVFQERHGWERPGWFHPRGPAPVLEYDYYGAYGSRAHEDYAYRR
LLADEYTFAFPPHHDTIKKECLACRGAAAVFDMSYFGKFYLVGLDARKAADWLFSADVSR
PPGSTVYTCMLNHRGGTESDLTVSRLAPSHQASPLAPAFEGDGYYLAMGGAVAQHNWSHI
TTVLQDQKSQCQLIDSSEDLGMISIQGPASRAILQEVLDADLSNEAFPFSTHKLLRAAGH
LVRAMRLSFVGELGWELHIPKASCVPVYRAVMAAGAKHGLINAGYRAIDSLSIEKGYRHW
HADLRPDDSPLEAGLAFTCKLKSPVPFLGREALEQQRAAGLRRRLVCFTMEDKVPMFGLE
AIWRNGQVVGHVRRADFGFAIDKTIAYGYIHDPSGGPVSLDFVKSGDYALERMGVTYGAQ
AHLKSPFDPNNKRVKGIY
NT seq 2757 nt   +upstreamnt  +downstreamnt
atggcctcactgagccgagccctacgtgtggctgctgcccaccctcgccagagccctacc
cggggcatggggccatgcaacctgtccagcgcagctggccccacagccgagaagagtgtg
ccatatcagcggaccctgaaggagggacagggcacctcggtggtggcccaaggcccaagc
cggcccctgcccagcacggccaacgtggtggtcattggtggaggcagcttgggctgccag
accctgtaccacctggccaagctgggcatgagtggggcggtgctgctggagcgggagcgg
ctgacctccgggaccacctggcacacggcaggcctgctgtggcagctgcggcccagtgac
gtggaggtggagcttctggcccacactcggcgggtggtgagccgggagctggaggaggag
acgggactacacacgggctggatccagaatgggggcctcttcatcgcgtccaaccggcag
cgcctggacgagtacaagaggctcatgtcgctgggcaaggcgtatggtgtggaatcccat
gtgctgagcccggcagagaccaagactctgtacccgctgatgaatgtggacgacctctac
gggaccctgtatgtgccgcacgacggtaccatggaccccgctggcacctgtaccaccctc
gccagggcagcttctgcccgaggagcacaggtcattgagaactgcccagtgaccggcatt
cgtgtgtggacggatgattttggggtgcggcgggtcgcgggtgtggagactcagcatggt
tccatccagacaccctgcgtggtcaactgtgcaggagtgtgggcaagtgctgtgggccgg
atggctggagtcaaggtcccgctggtggccatgcaccatgcctatgtcgtcaccgagcgc
atcgaggggattcagaacatgcccaatgtccgtgatcatgatgcctctgtctacctccgc
ctccaaggggatgccttgtctgtgggtggctatgaggccaaccccatcttttgggaggag
gtgtcagacaagtttgccttcggcctctttgacctggactgggaggtgttcacccagcac
attgaaggcgccatcaacagggtccccgtgctggagaagacaggaatcaagtccacggtc
tgcggccctgaatccttcacgcccgaccacaagcccctgatgggggaggcacctgagctc
cgagggttcttcctgggctgtggcttcaacagcgcaggaatgatgctgggtggtggctgt
gggcaggagctggcccactggatcatccatgggcgcccggagaaggacatgcatggctat
gacatcaggcgcttccatcactcgctcacggaccacccccgctggatccgagagcgaagc
catgagtcctacgccaagaactactccgtcgtcttcccccacgatgagccgctggccggg
cgcaacatgaggagagacccgctgcacgaggaactccttggacaaggctgcgtgttccag
gagcggcatggctgggagcgaccgggatggtttcatccccgaggcccagctccggtcctc
gagtacgactactacggggcttacgggagccgcgcgcacgaggactacgcctaccgcagg
ctgctggcagacgagtacaccttcgccttcccgccccaccacgacacgatcaagaaggag
tgcctggcctgcagaggggccgccgctgtgtttgacatgtcctacttcgggaagttctac
ctggtggggctggatgcaaggaaggctgccgactggctcttctccgcagatgtcagccga
cccccaggctccaccgtgtacacgtgcatgctcaaccaccgtgggggcaccgagagtgac
ctgactgtcagccgcctggcacccagccaccaggcctccccgctggcccccgcctttgaa
ggggacggttactacctggccatgggcggggccgtggcccagcacaactggtcccacatc
accaccgtgctgcaggaccagaagtcccagtgccagctcatcgacagctccgaggacctg
ggtatgatcagtatccagggcccagccagccgagccattttgcaggaggtgctggacgca
gacctgagcaacgaggccttcccgttctccacccacaagctactgagagccgcagggcac
ctggtccgagccatgcggctgtcctttgtgggggagctgggctgggagctgcacattcca
aaggcgtcctgcgtgcctgtgtaccgggctgtgatggccgcgggtgccaagcacggcctc
atcaacgcagggtaccgcgccatcgactccctgagcattgagaaaggctaccggcactgg
cacgcggacctgcggccagacgacagccccctggaggcaggcctggccttcacctgcaag
ctcaagtcgccggtgcccttcctggggagggaggccctggagcagcagcgggccgcaggc
ctccgccggcgcctggtgtgcttcaccatggaggacaaagtacccatgtttggcctggag
gccatctggaggaacggccaagtggtgggccatgtccggagggctgactttgggttcgcc
atcgacaagaccatcgcctacggttacatccatgaccccagcggtgggccggtctcgctg
gactttgtgaagagcggggactatgccctggagagaatgggggtgacctatggtgcccag
gctcacctgaagtcgcccttcgaccccaacaacaagagggtgaagggaatctactga

KEGG   Homo sapiens (human): 51268
Entry
51268             CDS       T01001                                 
Symbol
PIPOX, LPIPOX
Name
(RefSeq) pipecolic acid and sarcosine oxidase
  KO
K00306  sarcosine oxidase / L-pipecolate oxidase [EC:1.5.3.1 1.5.3.7]
Organism
hsa  Homo sapiens (human)
Pathway
hsa00260  Glycine, serine and threonine metabolism
hsa00310  Lysine degradation
hsa01100  Metabolic pathways
hsa04146  Peroxisome
Module
hsa_M00974  Betaine metabolism, animals, betaine => glycine
Network
nt06033  Glycine, serine and arginine metabolism
  Element
N01789  Betaine metabolism
Brite
KEGG Orthology (KO) [BR:hsa00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00260 Glycine, serine and threonine metabolism
    51268 (PIPOX)
   00310 Lysine degradation
    51268 (PIPOX)
 09140 Cellular Processes
  09141 Transport and catabolism
   04146 Peroxisome
    51268 (PIPOX)
Enzymes [BR:hsa01000]
 1. Oxidoreductases
  1.5  Acting on the CH-NH group of donors
   1.5.3  With oxygen as acceptor
    1.5.3.1  sarcosine oxidase (formaldehyde-forming)
     51268 (PIPOX)
    1.5.3.7  L-pipecolate oxidase
     51268 (PIPOX)
SSDB
Motif
Pfam: DAO NAD_binding_8 HI0933_like Pyr_redox_2 GIDA FAD_binding_2 ApbA Thi4
Other DBs
NCBI-GeneID: 51268
NCBI-ProteinID: NP_057602
OMIM: 616713
HGNC: 17804
Ensembl: ENSG00000179761
UniProt: Q9P0Z9
LinkDB
Position
17:29043141..29057216
AA seq 390 aa
MAAQKDLWDAIVIGAGIQGCFTAYHLAKHRKRILLLEQFFLPHSRGSSHGQSRIIRKAYL
EDFYTRMMHECYQIWAQLEHEAGTQLHRQTGLLLLGMKENQELKTIQANLSRQRVEHQCL
SSEELKQRFPNIRLPRGEVGLLDNSGGVIYAYKALRALQDAIRQLGGIVRDGEKVVEINP
GLLVTVKTTSRSYQAKSLVITAGPWTNQLLRPLGIEMPLQTLRINVCYWREMVPGSYGVS
QAFPCFLWLGLCPHHIYGLPTGEYPGLMKVSYHHGNHADPEERDCPTARTDIGDVQILSS
FVRDHLPDLKPEPAVIESCMYTNTPDEQFILDRHPKYDNIVIGAGFSGHGFKLAPVVGKI
LYELSMKLTPSYDLAPFRISRFPSLGKAHL
NT seq 1173 nt   +upstreamnt  +downstreamnt
atggcggctcagaaagatctctgggacgccattgtgattggggcggggatccagggctgc
ttcactgcataccacctggccaaacacaggaagaggatcctcctgctggagcagttcttt
ctaccacactcccgaggaagctcccatggacaaagccggataatccgaaaggcgtacctg
gaagacttttacacccggatgatgcatgagtgctatcagatatgggcccagctggagcac
gaggctggaacccaattgcacaggcagactggattactgctgctgggaatgaaagagaat
caagaattaaagacaatccaggccaatctgtcgaggcagagggtagaacaccagtgtctt
tcatctgaggaactgaagcaacgtttcccaaatattcggttgcccaggggagaagtgggg
ctcttggacaattccggaggagttatctatgcatataaggccctcagagccctgcaggat
gcaattcgacagctaggaggcatagtgcgtgacggagagaaggtggtggagataaaccca
gggctactggtcacggtgaaaaccacctccaggagctaccaagctaagagcttggtcatc
acagcaggtccttggaccaaccagctcctccgtcccctgggcattgagatgcctctccag
accctgcggatcaacgtgtgttactggcgagagatggttcctgggagctatggtgtgtcc
caggcctttccgtgcttcctgtggctgggcttgtgtccccaccacatctacggactgccc
acaggagagtacccagggctgatgaaggtcagctatcaccacggcaaccacgcagaccct
gaggagcgggactgccccacagcacgcacagacatcggagacgtccagatcctgagcagc
tttgtcagagatcacttacctgatctgaagcccgagcctgctgtcattgagagctgcatg
tacacgaatacccctgatgagcagttcattctcgatcgccacccaaagtatgacaacatt
gtcattggtgctggattctctgggcacgggttcaagctggcccctgtggtggggaagatc
ctgtatgaattaagcatgaaattaacaccatcttatgacttggcaccttttcgaatcagc
cgtttcccaagcctgggcaaagcccacctttga

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