KEGG   Ornithorhynchus anatinus (platypus): 100077524
Entry
100077524         CDS       T01045                                 
Symbol
HADHA
Name
(RefSeq) trifunctional enzyme subunit alpha, mitochondrial isoform X1
  KO
K07515  enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
Organism
oaa  Ornithorhynchus anatinus (platypus)
Pathway
oaa00062  Fatty acid elongation
oaa00071  Fatty acid degradation
oaa00280  Valine, leucine and isoleucine degradation
oaa00310  Lysine degradation
oaa00380  Tryptophan metabolism
oaa00410  beta-Alanine metabolism
oaa00640  Propanoate metabolism
oaa00650  Butanoate metabolism
oaa01100  Metabolic pathways
oaa01212  Fatty acid metabolism
Module
oaa_M00032  Lysine degradation, lysine => saccharopine => acetoacetyl-CoA
oaa_M00085  Fatty acid elongation in mitochondria
oaa_M00087  beta-Oxidation
Brite
KEGG Orthology (KO) [BR:oaa00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100077524 (HADHA)
   00650 Butanoate metabolism
    100077524 (HADHA)
  09103 Lipid metabolism
   00062 Fatty acid elongation
    100077524 (HADHA)
   00071 Fatty acid degradation
    100077524 (HADHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100077524 (HADHA)
   00310 Lysine degradation
    100077524 (HADHA)
   00380 Tryptophan metabolism
    100077524 (HADHA)
  09106 Metabolism of other amino acids
   00410 beta-Alanine metabolism
    100077524 (HADHA)
Enzymes [BR:oaa01000]
 1. Oxidoreductases
  1.1  Acting on the CH-OH group of donors
   1.1.1  With NAD+ or NADP+ as acceptor
    1.1.1.211  long-chain-3-hydroxyacyl-CoA dehydrogenase
     100077524 (HADHA)
 4. Lyases
  4.2  Carbon-oxygen lyases
   4.2.1  Hydro-lyases
    4.2.1.17  enoyl-CoA hydratase
     100077524 (HADHA)
SSDB
Motif
Pfam: 3HCDH_N ECH_1 3HCDH ECH_2
Other DBs
NCBI-GeneID: 100077524
NCBI-ProteinID: XP_001508292
Ensembl: ENSOANG00000015830
UniProt: F7EMK0
LinkDB
Position
9:41188221..41212643
AA seq 763 aa
MVAARAIGSLSRLTVNGRSRFPGYVSRNFTQSSTLLSRTHINYAVKGDVAVVRINSPNSK
VNTLNKELKLEFMQVMNEIWASEAIRSAVLISAKPGCFIAGADLNMLADCKSPQEVTQLS
QEGQQMLEKLEKSPKPIVAAISGSCLGGGLELAIACQYRIATKDKKTVLGVPEVLLGILP
GAGGTQRLPKMVGVPAAFDMMLTGRNIRADRAKKMGLVDQLVEPLGPGLKAPEERTIEYL
EEVAVTFAKDLADKKVSAKKNKSLVEKVTSYAMTIPFVRQQIYKTVEEKVRKQTKGLYPA
PLKIIDVVKTGLEEGNDAGYLSESQKFGELIMTNESKALVGLYHGQVLCKKNKFGAPQKD
VKHLAILGAGLMGAGIAQVSVDKGLKTILKDTTLTGLGRGQQQVFKGLNDKVKKKNLTSF
ERDSIFSTLTGQLDYQGFEKADMVIEAVFEDLNIKHKVLKEVEAVIPAHCVFASNTSALP
INEIAAVSKRPEKVIGMHYFSPVDKMQLLEIITTEKTSKDTTASAVAVGLKQGKVIIVVK
DGPGFYTTRCLAPMMSEVVRALQEGVEPKKLDSLTTSFGFPVGAATLVDEVGVDVAGHVS
EELGKAFGERLGGGSPELLKLMVNKGFLGRKAGKGFYIYQEGVKNRSLNSGMDEILTQLR
VSARPEVSTDEDIQYRLVTRFVNEAAMCLQEGILATPAEGDIGAVFGLGFPPCLGGPFRF
TDLYGARKLVDRLKKYEDVYGKQFTPCQLLVDHANNPDKKFYQ
NT seq 2292 nt   +upstreamnt  +downstreamnt
atggtggccgcgcgggccatcggcagcctcagccgcctcaccgtcaacggccggagccgc
ttcccaggttatgtctcccgaaactttactcagtcttccactttactatccagaacccat
attaactatgccgtcaaaggggatgtggccgtggtccgaatcaactccccaaattcaaag
gtaaacactctgaacaaagagttgaagttggagttcatgcaagtaatgaatgagatttgg
gccagtgaagccatcagaagtgcagtcctcatttcagcaaagccaggctgctttattgct
ggtgctgatctcaacatgctagcagattgtaagagtcctcaggaagtgacacaactatct
caagaaggacagcaaatgctggagaagcttgaaaagtccccgaagcctattgtagctgcc
atcagtggatcctgcttgggaggaggactggagcttgccatcgcctgccagtacagaata
gcaacaaaagacaaaaagactgtattgggtgttcctgaagtgctactggggatattgcca
ggggcgggaggcacacagaggctcccaaagatggtgggtgtccccgctgcctttgacatg
atgcttactggtagaaacattcgtgctgacagagcaaagaagatgggacttgttgaccaa
ttggtggagcctctgggaccaggtttgaaagctccagaagaaaggacaattgaatacctt
gaagaagtagccgttacttttgctaaagacctagctgataaaaaggtttctgccaagaag
aacaagagtctggtggagaaggtgacatcctacgccatgacaattccatttgtcaggcaa
cagatctacaaaacagtggaagaaaaagttagaaagcagaccaaagggctgtatcctgct
cccctgaagatcattgatgttgttaagactggacttgaagaggggaatgatgctgggtat
ctgtcggaatcccagaaatttggtgaacttataatgaccaatgaatccaaggctttggtt
ggactctaccatggtcaagttctgtgcaagaaaaataagtttggggcccctcagaaggat
gtcaagcatctggctattcttggagcagggctcatgggagctggcattgctcaagtctca
gtggataaggggttgaagaccattctcaaagacaccacattaacaggcttgggcagagga
cagcagcaagtcttcaaagggttaaatgacaaagtgaagaagaagaatctgacgtcattt
gaaagggactccatcttcagcaccctaacggggcagctcgattaccagggatttgagaag
gcagacatggtgattgaagctgtctttgaggacctcaacattaagcacaaagtgctgaag
gaggtggaagctgtaattcctgctcactgtgtctttgccagtaacacatctgctctccca
atcaatgaaattgctgccgtcagcaaaaggcctgaaaaggttattggcatgcactacttc
tctccagtggacaagatgcagttactagagatcatcacgacagaaaaaacctccaaagac
acaactgcctctgctgtagcagttggcctcaaacagggcaaagtcatcattgtggtcaag
gatgggccgggcttttacaccaccaggtgcctcgcccccatgatgtctgaagttgtccgg
gctctgcaggaaggcgttgagcctaagaaattggattccttgaccaccagctttggcttt
cctgtgggtgctgccaccctggtggatgaagttggtgtggatgtggccggacacgtctca
gaggagctgggcaaagcctttggggagcggttaggcggtggaagcccagaactgctgaag
ctcatggtgaataaaggcttcctgggtcgcaaagctgggaaaggtttttatatctaccag
gagggcgtcaagaaccgaagtttgaattctggcatggatgagattctgacccagttgagg
gtctcggcccgacctgaggtctccactgatgaagacattcaatatcgactggtgacgcgg
ttcgtcaatgaggcagccatgtgcctacaggaggggatcctggccacgcccgcggaggga
gacatcggggcagtgttcgggctcggcttcccgccttgtctcggaggtcccttccgtttc
acagacctgtacggtgcccggaagcttgtggatcgactcaagaagtatgaggatgtgtat
gggaaacagttcaccccatgtcagctgctggtagaccacgctaacaacccagacaagaag
ttttatcagtga

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