KEGG   Ursus arctos (brown bear): 113270772
Entry
113270772         CDS       T05909                                 
Symbol
HADHA
Name
(RefSeq) trifunctional enzyme subunit alpha, mitochondrial isoform X1
  KO
K07515  enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
Organism
uah  Ursus arctos (brown bear)
Pathway
uah00062  Fatty acid elongation
uah00071  Fatty acid degradation
uah00280  Valine, leucine and isoleucine degradation
uah00310  Lysine degradation
uah00380  Tryptophan metabolism
uah00410  beta-Alanine metabolism
uah00640  Propanoate metabolism
uah00650  Butanoate metabolism
uah01100  Metabolic pathways
uah01212  Fatty acid metabolism
Module
uah_M00032  Lysine degradation, lysine => saccharopine => acetoacetyl-CoA
uah_M00085  Fatty acid elongation in mitochondria
uah_M00087  beta-Oxidation
Brite
KEGG Orthology (KO) [BR:uah00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    113270772 (HADHA)
   00650 Butanoate metabolism
    113270772 (HADHA)
  09103 Lipid metabolism
   00062 Fatty acid elongation
    113270772 (HADHA)
   00071 Fatty acid degradation
    113270772 (HADHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    113270772 (HADHA)
   00310 Lysine degradation
    113270772 (HADHA)
   00380 Tryptophan metabolism
    113270772 (HADHA)
  09106 Metabolism of other amino acids
   00410 beta-Alanine metabolism
    113270772 (HADHA)
Enzymes [BR:uah01000]
 1. Oxidoreductases
  1.1  Acting on the CH-OH group of donors
   1.1.1  With NAD+ or NADP+ as acceptor
    1.1.1.211  long-chain-3-hydroxyacyl-CoA dehydrogenase
     113270772 (HADHA)
 4. Lyases
  4.2  Carbon-oxygen lyases
   4.2.1  Hydro-lyases
    4.2.1.17  enoyl-CoA hydratase
     113270772 (HADHA)
SSDB
Motif
Pfam: 3HCDH_N ECH_1 3HCDH ECH_2
Other DBs
NCBI-GeneID: 113270772
NCBI-ProteinID: XP_026376079
LinkDB
Position
Unknown
AA seq 812 aa
MARSQRQLGAGVLVRQYIGHLAGARLRQKSPPHGSPHLSAFHFRPLQLKMVASRAIGSLS
RATASRMLRCPGYICRSFSGTSALRTRTHINYGVKGDVAVVRINSPNSKVNTLNKELQSE
FMEVMNEIWASDQIRSAVLISSKPGCFIAGADINMIASCKTPEEVTKLSQEGQRMFEKLE
KSTKPVVAAISGACLGGGLELAISCQYRIATKDRKTVLGTPEVLLGILPGAGGTQRLPKM
VGVPAAFDMMLTGRNIRADRAKKMGLVDQLVEPLGPGLKPPEERTIEYLEEVAVTFAKGL
SDKKISIKRDKGLVEKLTSYAMSIPFVRQQIYKKVEEKVRKQTKGLYPAPLKIIDVVKTG
IEQGSDAGYLSESQKFAELTMTKESKALIGLYHGQVLCKKNKFGAPQKEAKHLAILGAGL
MGAGIAQVSVDKGLKTILKDATLAGLGRGQQQVFKGLNDKVKKKALTSFERDSIFSNLMG
QLDYQGFEKADMVIEAVFEDLSLKHRVLKEVEAVIPDHCIFASNTSALPINEIAAVSKRP
EKVIGMHYFSPVDKMQLLEIITTEKTSKDTTASAVAVGLKQGKVIIVVKDGPGFYTTRCL
APMMSEVLRILQEGVEPKKLDSLTTSFGFPVGAATLVDEVGVDVAKHVSEDLGKAFGERF
GGGSVELLKQMVSRGFLGRKSGKGFYIYQEGVKSKNVNSDMDGILASLKVPPKSDVSSDE
DIQYRLVTRFVNEAVMCLQEGILATPTEGDIGAVFGLGFPPCLGGPFRFVDLYGAQKIVD
RLRKYEAAYGTQFSPCQLLIDHASSPNKKFFQ
NT seq 2439 nt   +upstreamnt  +downstreamnt
atggcaaggagccagaggcaactcggcgcaggagttttagtcaggcagtacatcggacac
ctagctggggccaggctgaggcagaaaagtcctccgcacggcagcccccatctgagcgct
ttccactttcgtcctcttcaactcaagatggtggcctcccgggcgatcggcagtctcagc
cgcgccactgcctccaggatgctccgctgcccaggttatatttgccgcagcttttcaggg
acctctgctttgcgaaccagaacccatattaactatggagtcaaaggggatgtggctgtt
gttcgaattaactcacccaattcaaaggtaaatacgctaaataaagaactgcagtcagag
ttcatggaagtaatgaatgaaatctgggctagtgatcaaatcagaagtgctgtccttatc
tcatcgaagccaggctgctttattgcaggtgctgacatcaacatgatagcctcttgcaag
acccctgaagaggtaacaaaattgtcacaggaaggacagagaatgtttgagaaactcgag
aagtccacaaagcctgttgtggctgccatcagtggcgcctgcttaggcggaggacttgag
cttgccatttcctgccaatatagaatagcaaccaaagatagaaaaacagtattaggtacc
cctgaagtcttgctgggaatcttgccaggagcaggaggcacacaaagactgcccaaaatg
gtgggtgtgcctgctgcttttgacatgatgttgactggtagaaacattcgtgcagacaga
gcaaagaaaatgggactggttgaccaattggtggaacccctgggaccaggcttaaaacct
ccagaggaacggacaattgaatacttagaagaagttgcagttacttttgccaaaggacta
tccgataagaaaatctctataaagagagataagggattagtagaaaaattgacatcatat
gccatgagtattccatttgtcaggcaacagatttacaaaaaggtggaagaaaaagtacga
aaacagaccaaaggtctttatcctgcacctctgaaaataatcgatgtggtaaagactgga
attgagcaagggagcgatgctggctatctttctgaatctcagaaatttgcagagcttaca
atgaccaaagaatcaaaggccttgataggactttatcatggtcaagtcctgtgtaagaaa
aataaatttggagctccacagaaggaagcaaagcacctcgccattcttggtgcggggctg
atgggagccggcattgcccaggtctctgtggataagggcctgaagaccatacttaaagat
gctaccctagccgggctgggccgaggacagcagcaggtgttcaaaggattgaatgataaa
gtgaagaagaaagctctaacatcatttgaaagggactccattttcagcaacttgatgggg
cagctcgattaccagggttttgaaaaggctgacatggtgattgaagctgtctttgaggac
cttagtcttaagcacagagtgctaaaggaagtagaagcggtgattccggatcactgtatc
tttgccagtaacacatctgctctcccgatcaatgagattgctgctgtcagcaaaagacct
gagaaggtgatcggcatgcactacttctctcctgtggacaagatgcagctgttggagatt
atcacaaccgagaaaacatctaaggacacgaccgcttcggcggtagccgtcgggctcaag
caggggaaggtcatcattgtggttaaggacggacctggcttctacaccaccaggtgtctc
gcacccatgatgtctgaagtcctcagaatcctccaggaaggagttgagcctaagaagctg
gattcccttaccacaagctttggctttcctgtgggtgctgccacgctggtcgatgaagtg
ggtgtggatgtagcaaaacacgtatcagaagatctgggcaaagccttcggggagcggttt
ggaggtggaagcgtagaactgctaaagcagatggtgtccaggggcttcctgggtcgcaag
tctgggaagggcttttacatctaccaggagggtgtgaagagtaagaatgtgaattctgac
atggatggtattttggcaagtctgaaggtgcccccgaagtcggacgtctcctctgacgaa
gacattcagtaccgcctggtgaccagatttgtgaatgaggccgtcatgtgcctgcaggaa
gggatcttggccacacccacagagggggacatcggcgcagtctttgggctcggctttccc
ccgtgtcttggagggcccttccgcttcgtggatctgtatggtgctcagaagatcgtggac
cggctcaggaagtacgaggccgcctatggaacacagttcagcccgtgccagctgctcatt
gaccacgccagcagccctaacaagaagttcttccagtga

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