ORTHOLOGY: K01132
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Entry
K01132 KO
Symbol
GALNS
Name
N-acetylgalactosamine-6-sulfatase [EC:
3.1.6.4
]
Pathway
map00531
Glycosaminoglycan degradation
map01100
Metabolic pathways
map04142
Lysosome
Module
M00077
Chondroitin sulfate degradation
M00079
Keratan sulfate degradation
Reaction
R07806
N-acetyl-D-galactosamine 6-sulfate 6-sulfohydrolase
Disease
H00123
Mucopolysaccharidosis type IV
H00421
Mucopolysaccharidosis
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
K01132 GALNS; N-acetylgalactosamine-6-sulfatase
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
K01132 GALNS; N-acetylgalactosamine-6-sulfatase
Enzymes [BR:
ko01000
]
3. Hydrolases
3.1 Acting on ester bonds
3.1.6 Sulfuric-ester hydrolases
3.1.6.4 N-acetylgalactosamine-6-sulfatase
K01132 GALNS; N-acetylgalactosamine-6-sulfatase
BRITE hierarchy
Other DBs
GO:
0043890
Genes
HSA:
2588
(GALNS)
PTR:
736362
(GALNS)
GGO:
101147331
(GALNS)
PON:
100457027
(GALNS)
NLE:
100602504
(GALNS)
HMH:
116470703
(GALNS)
MCC:
697850
(GALNS)
MCF:
102118579
(GALNS)
MTHB:
126944297
MNI:
105488842
(GALNS)
CSAB:
103233460
(GALNS)
CATY:
105588730
(GALNS)
PANU:
101009427
(GALNS)
TGE:
112613969
(GALNS)
MLEU:
105533415
(GALNS)
RRO:
104655978
(GALNS)
115895245
115896020
RBB:
108519980
(GALNS)
TFN:
117088216
(GALNS)
PTEH:
111553847
(GALNS)
CANG:
105501931
(GALNS)
CJC:
100389028
(GALNS)
SBQ:
101046061
(GALNS)
CIMI:
108292811
(GALNS)
CSYR:
103277361
(GALNS)
MMUR:
105855880
(GALNS)
LCAT:
123625385
(GALNS)
PCOQ:
105821060
(GALNS)
OGA:
100959495
(GALNS)
MMU:
50917
(Galns)
MCAL:
110300029
(Galns)
MPAH:
110337430
(Galns)
RNO:
292073
(Galns)
MCOC:
116070337
(Galns)
ANU:
117722919
(Galns)
MUN:
110545224
(Galns)
CGE:
100753973
(Galns)
MAUA:
101843866
(Galns)
PROB:
127234651
(Galns)
PLEU:
114700977
(Galns)
MORG:
121446991
(Galns)
MFOT:
126515499
AAMP:
119801966
(Galns)
NGI:
103740004
(Galns)
HGL:
101712119
(Galns)
CPOC:
100732880
(Galns)
CCAN:
109692745
(Galns)
DORD:
105983007
(Galns)
DSP:
122127911
(Galns)
PLOP:
125358083
(Galns)
NCAR:
124966494
MMMA:
107150819
(Galns)
OPI:
101533979
(GALNS)
TUP:
102495455
(GALNS)
GVR:
103585012
(GALNS)
CFA:
489661
(GALNS)
CLUD:
112646823
(GALNS)
VVP:
112924627
(GALNS)
VLG:
121500285
(GALNS)
NPO:
129497042
(GALNS)
AML:
100479531
(GALNS)
UMR:
103673849
(GALNS)
UAH:
113252143
(GALNS)
UAR:
123776601
(GALNS)
ELK:
111152803
LLV:
125088735
MPUF:
101693199
(GALNS)
MNP:
132005422
(GALNS)
MLK:
131817433
(GALNS)
NVS:
122911134
(GALNS)
ORO:
101366420
(GALNS)
EJU:
114199244
(GALNS)
ZCA:
113935705
(GALNS)
MLX:
118023463
(GALNS)
NSU:
110591472
(GALNS)
LWW:
102727198
(GALNS)
102728108
FCA:
101099168
(GALNS)
PYU:
121009927
(GALNS)
PCOO:
112857533
(GALNS)
PBG:
122494604
(GALNS)
PVIV:
125158761
(GALNS)
LRUF:
124511580
PTG:
102972741
(GALNS)
PPAD:
109245536
(GALNS)
PUC:
125916546
AJU:
106973500
HHV:
120228057
(GALNS)
BTA:
515809
(GALNS)
BOM:
102269249
(GALNS)
BIU:
109572729
(GALNS)
BBUB:
102408891
(GALNS)
BBIS:
104991469
(GALNS)
CHX:
102190539
(GALNS)
OAS:
101107214
(GALNS)
BTAX:
128063323
(GALNS)
ODA:
120872955
(GALNS)
CCAD:
122420353
(GALNS)
MBEZ:
129547169
(GALNS)
SSC:
397000
(GALNS)
CFR:
102509603
CBAI:
105079439
(GALNS)
CDK:
105104689
VPC:
102538945
(GALNS)
BACU:
103007439
(GALNS)
BMUS:
118884707
(GALNS)
LVE:
103068680
(GALNS)
OOR:
101273563
(GALNS)
DLE:
111179391
(GALNS)
PCAD:
102995899
PSIU:
116743506
(GALNS)
NASI:
112393359
(GALNS)
ECB:
100051284
(GALNS)
EPZ:
103541880
(GALNS)
EAI:
106828247
(GALNS)
MYB:
102243422
(GALNS)
MYD:
102759580
(GALNS)
MMYO:
118674319
(GALNS)
MLF:
102428724
(GALNS)
PKL:
118720682
(GALNS)
EFUS:
103284456
(GALNS)
MNA:
107543502
(GALNS)
DRO:
112300688
(GALNS)
SHON:
118982962
(GALNS)
AJM:
119047031
(GALNS)
PDIC:
114488241
(GALNS)
PHAS:
123805898
(GALNS)
MMF:
118639488
(GALNS)
PPAM:
129083148
(GALNS)
RFQ:
117034469
(GALNS)
PALE:
102887232
(GALNS)
PGIG:
120622885
(GALNS)
PVP:
105299912
(GALNS)
RAY:
107502355
(GALNS)
MJV:
108385617
(GALNS)
TOD:
119248859
(GALNS)
SARA:
101538760
(GALNS)
SETR:
126027304
(GALNS)
LAV:
100666004
(GALNS)
TMU:
101357559
ETF:
101656997
(GALNS)
DNM:
101425086
(GALNS)
MDO:
100026247
(GALNS)
GAS:
123236766
(GALNS)
SHR:
100933785
(GALNS)
AFZ:
127547785
PCW:
110210301
(GALNS)
OAA:
100089863
(GALNS)
PCOC:
116243926
(GALNS)
MGP:
100543323
(GALNS)
CJO:
107319490
(GALNS)
TPAI:
128082263
(GALNS)
LMUT:
125699344
(GALNS)
NMEL:
110404190
(GALNS)
APLA:
101792596
(GALNS)
ACYG:
106046507
(GALNS)
CATA:
118257825
(GALNS)
AFUL:
116493952
(GALNS)
TGU:
100222785
(GALNS)
LSR:
110468778
(GALNS)
SCAN:
103816759
(GALNS)
PMOA:
120496245
(GALNS)
OTC:
121333791
(GALNS)
PRUF:
121362139
(GALNS)
GFR:
102043643
(GALNS)
FAB:
101811724
(GALNS)
OMA:
130257929
(GALNS)
PHI:
102101123
(GALNS)
PMAJ:
107209820
(GALNS)
CCAE:
111934402
(GALNS)
CCW:
104691852
(GALNS)
CBRC:
103620531
(GALNS)
ETL:
114060570
(GALNS)
ZAB:
102061073
(GALNS)
102069306
ZLE:
135452950
(GALNS)
ACHL:
103801189
(GALNS)
SVG:
106852073
(GALNS)
MMEA:
130585964
(GALNS)
HRT:
120757714
(GALNS)
FPG:
101915149
(GALNS)
FCH:
102047887
(GALNS)
CLV:
102096794
(GALNS)
EGZ:
104127040
(GALNS)
NNI:
104023569
(GALNS)
PCRI:
104028377
(GALNS)
PLET:
104625077
(GALNS)
EHS:
104514048
(GALNS)
PCAO:
104050843
(GALNS)
ACUN:
113484623
(GALNS)
TALA:
104363110
(GALNS)
PADL:
103919464
(GALNS)
AFOR:
103893827
(GALNS)
ACHC:
115345352
(GALNS)
HALD:
104322368
(GALNS)
HLE:
104839339
(GALNS)
AGEN:
126041141
GCL:
127021315
CCRI:
104163967
(GALNS)
CSTI:
104557832
(GALNS)
CMAC:
104472925
(GALNS)
MUI:
104538532
(GALNS)
BREG:
104636034
(GALNS)
FGA:
104069072
(GALNS)
GSTE:
104263598
(GALNS)
LDI:
104351583
(GALNS)
MNB:
103776695
(GALNS)
OHA:
104329136
(GALNS)
NNT:
104409341
(GALNS)
SHAB:
115619566
(GALNS)
DPUB:
104303833
(GALNS)
PGUU:
104458036
(GALNS)
ACAR:
104517665
(GALNS)
CPEA:
104398323
(GALNS)
AVIT:
104273135
(GALNS)
CVF:
104290871
(GALNS)
RTD:
128908466
(GALNS)
CUCA:
104061255
(GALNS)
TEO:
104377077
BRHI:
104493548
(GALNS)
AAM:
106491425
(GALNS)
AROW:
112978484
(GALNS)
NPD:
112949943
(GALNS)
TGT:
104577576
DNE:
112989077
(GALNS)
SCAM:
104145362
(GALNS)
ASN:
102384115
(GALNS)
AMJ:
102560299
(GALNS)
CPOO:
109310712
(GALNS)
GGN:
109289387
(GALNS)
PSS:
102445221
(GALNS)
CMY:
102937794
(GALNS)
CCAY:
125645388
(GALNS)
DCC:
119841115
(GALNS)
CPIC:
101934226
(GALNS)
TST:
117886379
(GALNS)
CABI:
116815680
(GALNS)
MRV:
120384171
(GALNS)
ACS:
100556157
(galns)
ASAO:
132783058
(GALNS)
PVT:
110076238
(GALNS)
SUND:
121914957
(GALNS)
PBI:
103067280
(GALNS)
PMUR:
107283519
(GALNS)
CTIG:
120302469
(GALNS)
TSR:
106552196
(GALNS)
PGUT:
117671022
(GALNS)
APRI:
131184122
(GALNS)
PTEX:
113448913
(GALNS)
NSS:
113427286
(GALNS)
VKO:
123022275
(GALNS)
PMUA:
114602133
(GALNS)
PRAF:
128419373
(GALNS)
ZVI:
118086417
(GALNS)
HCG:
128334401
(GALNS)
GJA:
107115627
(GALNS)
STOW:
125443448
(GALNS)
EMC:
129344217
(GALNS)
XLA:
495239
(galns.L)
XTR:
100485376
(galns)
NPR:
108787709
(GALNS)
RTEM:
120917919
(GALNS)
BBUF:
120980190
(GALNS)
BGAR:
122920554
(GALNS)
MUO:
115470949
(GALNS)
115470950
GSH:
117359132
(GALNS)
DRE:
791159
(galns)
SRX:
107728036
107730157
(galns)
SANH:
107663041
107685869
SGH:
107561424
CCAR:
109052187
109072047
CAUA:
113106343
(galns)
CGIB:
127962658
PTET:
122349543
(galns)
LROH:
127168451
(galns)
OMC:
131544947
(galns)
PPRM:
120492607
(galns)
RKG:
130070420
(galns)
MAMB:
125265846
(galns)
CIDE:
127516461
MASI:
127447379
TROS:
130558994
(galns)
TDW:
130427992
(galns)
MANU:
129452592
(galns)
IPU:
108259597
IFU:
128602800
(galns)
PHYP:
113546742
(galns)
SMEO:
124380157
(galns)
TFD:
113634223
(galns)
TVC:
132838565
(galns)
TRN:
134303909
(galns)
AMEX:
103034478
(galns)
CMAO:
118817604
(galns)
EEE:
113575705
(galns)
CHAR:
105892912
(galns)
TRU:
101062701
(galns)
TFS:
130521832
(galns)
TNG:
GSTEN00017886G001
LCO:
104922746
NCC:
104947090
(galns)
TBEN:
117471744
(galns)
CGOB:
115005461
(galns)
PGEO:
117466696
(galns)
GACU:
117547444
(galns)
EMAC:
134863047
(galns)
ELY:
117256764
(galns)
EFO:
125902169
(galns)
PLEP:
121948104
(galns)
SLUC:
116034032
(galns)
ECRA:
117950807
(galns)
ESP:
116696521
(galns)
PFLV:
114552310
(galns)
GAT:
120807952
(galns)
PPUG:
119198284
(galns)
AFB:
129104840
(galns)
CLUM:
117725926
(galns)
PSWI:
130193076
(galns)
MSAM:
119889945
(galns)
SCHU:
122880626
(galns)
CUD:
121507649
(galns)
ALAT:
119018165
(galns)
MZE:
101471725
(galns)
ONL:
100694056
(galns)
OAU:
116324295
(galns)
OLA:
101171730
(galns)
OML:
112160349
(galns)
CSAI:
133461121
(galns)
XMA:
102237545
(galns)
XCO:
114142561
(galns)
XHE:
116718196
(galns)
PRET:
103462372
(galns)
PFOR:
103139344
(galns)
PLAI:
106947220
(galns)
PMEI:
106928083
(galns)
GAF:
122822484
(galns)
PPRL:
129369659
(galns)
CVG:
107090762
(galns)
CTUL:
119782664
(galns)
GMU:
124866905
(galns)
NFU:
107381170
(galns)
KMR:
108229109
(galns)
ALIM:
106513999
106535460
(galns)
NWH:
119428716
(galns)
AOCE:
111588401
(galns)
MCEP:
125005486
(galns)
CSEM:
103378683
(galns)
POV:
109624779
(galns)
SSEN:
122772677
(galns)
HHIP:
117759144
(galns)
HSP:
118106961
(galns)
PPLT:
128443953
(galns)
SMAU:
118302364
(galns)
LCF:
108887657
SDU:
111238375
(galns)
SLAL:
111668284
(galns)
XGL:
120788744
(galns)
HCQ:
109519694
(galns)
SSCV:
125967321
SBIA:
133498299
(galns)
PEE:
133399053
(galns)
PTAO:
133472694
(galns)
BPEC:
110172948
(galns)
MALB:
109966269
(galns)
BSPL:
114852174
(galns)
SJO:
128357231
(galns)
SASA:
106587262
(galns)
STRU:
115167380
(galns)
OTW:
112249114
OMY:
110506416
110526298
OGO:
124033834
(galns)
ONE:
115112157
(galns)
OKI:
109886553
(galns)
OKE:
118358704
(galns)
SALP:
111969099
SNH:
120025054
120046281
(galns)
CCLU:
121548309
(galns)
ELS:
105017049
(galns)
SFM:
108934575
(galns)
PKI:
111832952
(galns)
AANG:
118227539
(galns)
LOC:
102682809
(galns)
PSPA:
121325621
(galns)
ARUT:
117425033
PSEX:
120535428
(galns)
LCM:
102351372
(GALNS)
CMK:
103188083
(galns)
RTP:
109927191
(galns)
CPLA:
122558182
(galns)
HOC:
132824049
(galns)
LERI:
129715073
(galns)
PMRN:
116944099
(GALNS)
LRJ:
133350812
(GALNS)
BFO:
118417061
BBEL:
109487383
CIN:
100177085
SCLV:
120337476
SPU:
579130
588014
LPIC:
129254082
APLC:
110988485
AJC:
117123524
SKO:
100369185
RZE:
108377917
PVM:
113810897
PJA:
122250835
122265722
PCHN:
125024895
PMOO:
119595418
HAME:
121873258
PCLA:
123769173
CQD:
128690115
128690116
PTRU:
123507765
ESN:
126998113
MNZ:
135214409
HAZT:
108669890
EAF:
111703859
TCF:
131885716
PPOI:
119105862
119105964
DSV:
119436208
119436209
RSAN:
119407081
119407091
RMP:
119177296
119177297
TUT:
107369286
DPTE:
113792048
DFR:
124500144
CSCU:
111634997
PTEP:
107451534
ABRU:
129984049
UDV:
129223889
SDM:
118203759
LPOL:
106468150
HRO:
HELRODRAFT_95956
LGI:
LOTGIDRAFT_159001
PVUL:
126814591
PCAN:
112576502
BGT:
106058711
GAE:
121388395
HRF:
124112853
HRJ:
124266348
CRG:
105348100
CVN:
111134369
111134371
CANU:
128188777
OED:
125651774
MYI:
110464777
110467289
PMAX:
117327359
117337667
MCAF:
127703049
MMER:
123548759
RPHI:
132758283
132758538
DPOL:
127844465
127846125
OBI:
106880025
OSN:
115215877
LAK:
106161119
106180844
ADF:
107327708
AMIL:
114954146
PDAM:
113665844
SPIS:
111325693
DGT:
114516978
114542597
HSY:
130614798
AQU:
100637906
FPOA:
FPOAC1_009868
FVN:
FVRRES_10522
FMU:
J7337_011392
PMES:
FX988_03340
SPHP:
LH20_14895
SMAZ:
LH19_12295
STER:
AOA14_10930
SGI:
SGRAN_1170
SPHX:
E5675_14210
SPAP:
H3Z74_11860
SMIC:
SmB9_09240
PIR:
VN12_16015
(atsA_21)
RUL:
UC8_51720
(atsA_48)
AAGG:
ETAA8_41730
(atsA_43)
PND:
Pla175_22360
(atsA_36)
PBS:
Plabr_2973
GPN:
Pan110_45830
(atsA_48)
MRI:
Mal4_02690
(atsA_4)
Mal4_26260
(atsA_36)
PFER:
IRI77_14315
MCOS:
GM418_24990
CHK:
D4L85_03380
FNK:
E1750_03490
» show all
Taxonomy
UniProt
Reference
PMID:
1755850
Authors
Tomatsu S, Fukuda S, Masue M, Sukegawa K, Fukao T, Yamagishi A, Hori T, Iwata H, Ogawa T, Nakashima Y, et al.
Title
Morquio disease: isolation, characterization and expression of full-length cDNA for human N-acetylgalactosamine-6-sulfate sulfatase.
Journal
Biochem Biophys Res Commun 181:677-83 (1991)
DOI:
10.1016/0006-291x(91)91244-7
Sequence
[hsa:
2588
]
LinkDB
All DBs
DBGET
integrated database retrieval system