KEGG   PATHWAY: hsa00250
Entry
hsa00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Homo sapiens (human)
Class
Metabolism; Amino acid metabolism
Pathway map
hsa00250  Alanine, aspartate and glutamate metabolism
hsa00250

Module
hsa_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:hsa00250]
Drug
D07130  Carglumic acid (JAN/USAN/INN)
Other DBs
GO: 0006522 0006531 0006536
Organism
Homo sapiens (human) [GN:hsa]
Gene
2805  GOT1; glutamic-oxaloacetic transaminase 1 [KO:K14454] [EC:2.6.1.1]
137362  GOT1L1; glutamic-oxaloacetic transaminase 1 like 1 [KO:K14454] [EC:2.6.1.1]
2806  GOT2; glutamic-oxaloacetic transaminase 2 [KO:K14455] [EC:2.6.1.1]
259307  IL4I1; interleukin 4 induced 1 [KO:K03334] [EC:1.4.3.2]
8528  DDO; D-aspartate oxidase [KO:K00272] [EC:1.4.3.1]
80150  ASRGL1; asparaginase and isoaspartyl peptidase 1 [KO:K13051] [EC:3.5.1.1 3.4.19.5]
440  ASNS; asparagine synthetase (glutamine-hydrolyzing) [KO:K01953] [EC:6.3.5.4]
56954  NIT2; nitrilase family member 2 [KO:K13566] [EC:3.5.1.3]
84706  GPT2; glutamic--pyruvic transaminase 2 [KO:K00814] [EC:2.6.1.2]
2875  GPT; glutamic--pyruvic transaminase [KO:K00814] [EC:2.6.1.2]
189  AGXT; alanine--glyoxylate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
64902  AGXT2; alanine--glyoxylate aminotransferase 2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
445  ASS1; argininosuccinate synthase 1 [KO:K01940] [EC:6.3.4.5]
435  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
122622  ADSS1; adenylosuccinate synthase 1 [KO:K01939] [EC:6.3.4.4]
159  ADSS2; adenylosuccinate synthase 2 [KO:K01939] [EC:6.3.4.4]
158  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
339983  NAT8L; N-acetyltransferase 8 like [KO:K18309] [EC:2.3.1.17]
57494  RIMKLB; ribosomal modification protein rimK like family member B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
284716  RIMKLA; ribosomal modification protein rimK like family member A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
2346  FOLH1; folate hydrolase 1 [KO:K14592] [EC:3.4.17.21]
443  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
2571  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
2572  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
18  ABAT; 4-aminobutyrate aminotransferase [KO:K13524] [EC:2.6.1.19 2.6.1.22]
7915  ALDH5A1; aldehyde dehydrogenase 5 family member A1 [KO:K00139] [EC:1.2.1.24]
2747  GLUD2; glutamate dehydrogenase 2 [KO:K00261] [EC:1.4.1.3]
2746  GLUD1; glutamate dehydrogenase 1 [KO:K00261] [EC:1.4.1.3]
8659  ALDH4A1; aldehyde dehydrogenase 4 family member A1 [KO:K00294] [EC:1.2.1.88]
2752  GLUL; glutamate-ammonia ligase [KO:K01915] [EC:6.3.1.2]
790  CAD; carbamoyl-phosphate synthetase 2, aspartate transcarbamylase, and dihydroorotase [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
27165  GLS2; glutaminase 2 [KO:K01425] [EC:3.5.1.2]
2744  GLS; glutaminase [KO:K01425] [EC:3.5.1.2]
1373  CPS1; carbamoyl-phosphate synthase 1 [KO:K01948] [EC:6.3.4.16]
9945  GFPT2; glutamine-fructose-6-phosphate transaminase 2 [KO:K00820] [EC:2.6.1.16]
2673  GFPT1; glutamine--fructose-6-phosphate transaminase 1 [KO:K00820] [EC:2.6.1.16]
5471  PPAT; phosphoribosyl pyrophosphate amidotransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
hsa00010  Glycolysis / Gluconeogenesis
hsa00020  Citrate cycle (TCA cycle)
hsa00220  Arginine biosynthesis
hsa00230  Purine metabolism
hsa00240  Pyrimidine metabolism
hsa00260  Glycine, serine and threonine metabolism
hsa00330  Arginine and proline metabolism
hsa00340  Histidine metabolism
hsa00410  beta-Alanine metabolism
hsa00470  D-Amino acid metabolism
hsa00480  Glutathione metabolism
hsa00520  Amino sugar and nucleotide sugar metabolism
hsa00620  Pyruvate metabolism
hsa00630  Glyoxylate and dicarboxylate metabolism
hsa00650  Butanoate metabolism
hsa00760  Nicotinate and nicotinamide metabolism
hsa00770  Pantothenate and CoA biosynthesis
hsa00860  Porphyrin metabolism
hsa00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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