ORTHOLOGY: K01137
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Entry
K01137 KO
Symbol
GNS
Name
N-acetylglucosamine-6-sulfatase [EC:
3.1.6.14
]
Pathway
map00531
Glycosaminoglycan degradation
map01100
Metabolic pathways
map04142
Lysosome
Module
M00078
Heparan sulfate degradation
M00079
Keratan sulfate degradation
Disease
H00130
Mucopolysaccharidosis type III
H00421
Mucopolysaccharidosis
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
K01137 GNS; N-acetylglucosamine-6-sulfatase
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
K01137 GNS; N-acetylglucosamine-6-sulfatase
Enzymes [BR:
ko01000
]
3. Hydrolases
3.1 Acting on ester bonds
3.1.6 Sulfuric-ester hydrolases
3.1.6.14 N-acetylglucosamine-6-sulfatase
K01137 GNS; N-acetylglucosamine-6-sulfatase
BRITE hierarchy
Other DBs
RN:
R07808
R07819
GO:
0008449
Genes
HSA:
2799
(GNS)
PTR:
467054
(GNS)
PPS:
100989065
(GNS)
GGO:
101138415
(GNS)
PON:
100434320
(GNS)
NLE:
100581183
(GNS)
MCC:
717500
(GNS)
MCF:
102145903
(GNS)
MTHB:
126930859
CSAB:
103238645
(GNS)
CATY:
105600535
(GNS)
PANU:
101000540
(GNS)
TGE:
112634079
(GNS)
RRO:
104680826
(GNS)
RBB:
108529983
(GNS)
TFN:
117089812
(GNS)
PTEH:
111551223
(GNS)
CJC:
100400424
(GNS)
SBQ:
101053939
(GNS)
CSYR:
103250679
(GNS)
MMUR:
105880968
(GNS)
LCAT:
123639556
(GNS)
OGA:
100947596
(GNS)
MMU:
75612
(Gns)
MCAL:
110302812
(Gns)
MPAH:
110327096
(Gns)
RNO:
299825
(Gns)
MCOC:
116075787
(Gns)
MUN:
110549055
(Gns)
CGE:
100770659
(Gns)
MAUA:
101836829
(Gns)
PLEU:
114693295
(Gns)
MORG:
121461308
(Gns)
MFOT:
126515652
AAMP:
119803229
(Gns)
NGI:
103730745
(Gns)
HGL:
101710393
(Gns)
CPOC:
100713038
(Gns)
CCAN:
109682634
109689473
(Gns)
DORD:
105989149
(Gns)
DSP:
122124252
(Gns)
NCAR:
124983639
OCU:
100359029
OPI:
101535026
(GNS)
TUP:
102495195
(GNS)
GVR:
103590124
(GNS)
CFA:
474429
(GNS)
CLUD:
112677912
(GNS)
VVP:
112922302
(GNS)
VLG:
121491040
(GNS)
AML:
100484359
(GNS)
UMR:
103656835
(GNS)
UAH:
113256327
(GNS)
UAR:
123787171
(GNS)
ELK:
111142205
LLV:
125106019
MPUF:
101689983
(GNS)
ORO:
101363282
(GNS)
EJU:
114214906
(GNS)
ZCA:
113922113
(GNS)
MLX:
118008620
(GNS)
NSU:
110570582
(GNS)
LWW:
102747357
(GNS)
FCA:
101088174
(GNS)
PYU:
121040816
(GNS)
PBG:
122472936
(GNS)
LRUF:
124500988
PTG:
102960432
(GNS)
PPAD:
109270435
(GNS)
AJU:
106981331
(GNS)
HHV:
120233154
(GNS)
BTA:
512444
(GNS)
BOM:
102278733
(GNS)
BIU:
109559271
(GNS)
BBUB:
102402763
(GNS)
BBIS:
104989795
(GNS)
CHX:
100750233
(GNS)
OAS:
101110316
(GNS)
ODA:
120857690
(GNS)
CCAD:
122427718
(GNS)
SSC:
100623722
(GNS)
CFR:
102514683
(GNS)
CBAI:
105081356
(GNS)
CDK:
105101105
(GNS)
VPC:
102530722
(GNS)
BACU:
103014097
(GNS)
LVE:
103082537
(GNS)
OOR:
101269484
(GNS)
DLE:
111173789
(GNS)
PCAD:
102978507
(GNS)
PSIU:
116760061
(GNS)
ECB:
100034131
(GNS)
EPZ:
103557809
(GNS)
EAI:
106824381
(GNS)
MYB:
102244243
(GNS)
MYD:
102774590
(GNS)
MMYO:
118650169
(GNS)
MLF:
102428922
(GNS)
MNA:
107527081
(GNS)
PKL:
118730759
(GNS)
HAI:
109381692
(GNS)
DRO:
112319053
(GNS)
SHON:
118998726
(GNS)
PDIC:
114513208
(GNS)
PHAS:
123812691
(GNS)
MMF:
118623511
(GNS)
RFQ:
117028463
(GNS)
PALE:
102879622
(GNS)
PGIG:
120605014
(GNS)
PVP:
105302121
(GNS)
RAY:
107508223
(GNS)
MJV:
108397994
(GNS)
TOD:
119247114
(GNS)
SARA:
101543000
(GNS)
LAV:
100666611
(GNS)
TMU:
101351253
ETF:
101638038
(GNS)
DNM:
101424226
(GNS)
GAS:
123249084
(GNS)
SHR:
100925460
(GNS)
116422552
PCW:
110211022
(GNS)
OAA:
100076329
(GNS)
GGA:
417829
(GNS)
PCOC:
116226614
(GNS)
MGP:
100545047
(GNS)
CJO:
107310152
(GNS)
NMEL:
110392753
(GNS)
APLA:
101801092
(GNS)
ACYG:
106047200
(GNS)
AFUL:
116501824
(GNS)
TGU:
100228596
(GNS)
LSR:
110479874
(GNS)
SCAN:
103820401
(GNS)
PMOA:
120499766
(GNS)
OTC:
121339512
(GNS)
PRUF:
121352584
(GNS)
GFR:
102044180
(GNS)
FAB:
101808967
(GNS)
PHI:
102112476
(GNS)
PMAJ:
107204380
(GNS)
CCAE:
111937416
(GNS)
CCW:
104698460
(GNS)
CBRC:
103614803
(GNS)
ETL:
114070115
(GNS)
ZAB:
102061819
(GNS)
ACHL:
103805905
(GNS)
FPG:
101920963
(GNS)
FCH:
102053194
(GNS)
CLV:
102086956
(GNS)
EGZ:
104122208
(GNS)
NNI:
104011053
(GNS)
PLET:
104614442
(GNS)
PCRI:
104028236
(GNS)
PCAO:
104049326
(GNS)
ACUN:
113491215
(GNS)
TALA:
104362158
(GNS)
PADL:
103920047
(GNS)
AFOR:
103900437
(GNS)
ACHC:
115336294
(GNS)
HALD:
104325995
(GNS)
HLE:
104828209
(GNS)
AGEN:
126034371
GCL:
127014356
CCRI:
104169270
(GNS)
CSTI:
104555451
(GNS)
EHS:
104503625
(GNS)
CMAC:
104481187
(GNS)
MUI:
104546051
(GNS)
FGA:
104081974
(GNS)
GSTE:
104257022
(GNS)
LDI:
104345600
(GNS)
MNB:
103773982
(GNS)
OHA:
104326816
(GNS)
NNT:
104403930
(GNS)
DPUB:
104305216
(GNS)
PGUU:
104463832
(GNS)
ACAR:
104518915
(GNS)
CPEA:
104388851
(GNS)
AVIT:
104280318
(GNS)
CVF:
104288959
(GNS)
CUCA:
104061580
(GNS)
TEO:
104374487
(GNS)
BRHI:
104490407
(GNS)
AAM:
106488739
(GNS)
AROW:
112968141
(GNS)
NPD:
112958824
(GNS)
TGT:
104574967
(GNS)
DNE:
112978706
(GNS)
SCAM:
104142059
(GNS)
ASN:
102371974
(GNS)
AMJ:
102561583
(GNS)
CPOO:
109315540
(GNS)
GGN:
109295693
(GNS)
PSS:
102457294
(GNS)
CMY:
102930458
102940101
(GNS)
CPIC:
101939844
101949342
(GNS)
TST:
117877473
(GNS)
CABI:
116821812
(GNS)
116830695
MRV:
120383825
(GNS)
120396633
ACS:
100551899
100554106
(gns)
PVT:
110072145
110075098
(GNS)
SUND:
121931620
(GNS)
121934559
PBI:
103049496
(GNS)
103051498
PMUR:
107287959
107291795
(GNS)
CTIG:
120307409
(GNS)
120318805
120319767
TSR:
106543476
106555618
(GNS)
PGUT:
117655550
(GNS)
117676051
VKO:
123019814
(GNS)
123027101
PMUA:
114602850
114605147
(GNS)
ZVI:
118088022
118090673
(GNS)
GJA:
107107823
107114039
(GNS)
STOW:
125434166
(GNS)
125442150
XLA:
108711078
(gns.L)
379953
(gns.S)
XTR:
100135105
(gns)
NPR:
108801717
(GNS)
RTEM:
120932008
(GNS)
BBUF:
120980306
(GNS)
BGAR:
122928030
(GNS)
DRE:
327635
(gnsb)
566506
(gnsa)
SRX:
107708199
107726052
(gns)
SANH:
107656403
107657752
107658640
107658926
SGH:
107554517
107579236
107579806
107581073
107583955
(gns)
107589010
CCAR:
109062939
109062941
109062988
109071638
109071669
CAUA:
113047860
113048503
113054636
113054691
113064286
113067919
113110341
PPRM:
120476599
(gnsa)
120482716
(gnsb)
MAMB:
125245100
(gnsa)
125262409
(gnsb)
IPU:
108277337
(gnsb)
108279926
(gnsa)
PHYP:
113532260
(gns)
113544942
SMEO:
124393565
(gnsb)
124401767
(gnsa)
TFD:
113638427
(gnsb)
113645947
(gnsa)
AMEX:
103022579
(gns)
103040331
EEE:
113580978
(gns)
113583834
TRU:
101067840
101070232
(gns)
TNG:
GSTEN00023761G001
GSTEN00025357G001
LCO:
104931705
104933096
(gns)
NCC:
104948056
104951394
(gns)
CGOB:
115016478
115028236
(gns)
ELY:
117248948
(gnsa)
117269263
(gnsb)
EFO:
125883100
(gnsa)
125906066
(gnsb)
PLEP:
121959862
(gnsb)
121961267
(gnsa)
SLUC:
116041827
(gnsb)
116060209
(gnsa)
ECRA:
117938903
(gnsa)
117959727
(gnsb)
ESP:
116673386
(gns)
116686180
PFLV:
114550189
(gns)
114571268
GAT:
120815168
(gnsb)
120816983
(gnsa)
PPUG:
119211238
(gnsa)
119226387
(gnsb)
MSAM:
119914271
(gnsb)
119918060
(gnsa)
CUD:
121505214
(gnsa)
121524998
(gnsb)
ALAT:
119030070
(gnsb)
119032187
(gnsa)
MZE:
101468646
(gns)
101474830
ONL:
100691814
(gns)
100701163
OAU:
116314840
(gnsb)
116325487
(gnsa)
OLA:
101164824
101172042
(gns)
OML:
112154851
(gnsa)
112163509
(gnsb)
XMA:
102224851
102233455
(gns)
XCO:
114149340
114161155
(gns)
XHE:
116724080
116737168
(gns)
PRET:
103459377
(gns)
103473209
PFOR:
103140202
(gns)
103151749
PLAI:
106946394
(gns)
106948135
PMEI:
106915156
106926916
(gns)
GAF:
122819289
(gnsb)
122826641
(gnsa)
CVG:
107104702
(gns)
CTUL:
119790906
(gnsb)
119798477
(gnsa)
GMU:
124872861
(gnsb)
124882717
(gnsa)
NFU:
107382500
(gns)
107395870
KMR:
108233312
(gnsa)
108245369
(gnsb)
ALIM:
106524433
(gns)
106526380
NWH:
119425134
(gnsb)
119428271
(gnsa)
AOCE:
111579019
(gns)
MCEP:
124996306
(gnsb)
125000197
(gnsa)
CSEM:
103389648
(gns)
POV:
109626384
109640549
(gns)
SSEN:
122758010
(gnsb)
HHIP:
117757535
(gnsa)
117771909
(gnsb)
HSP:
118101574
(gnsa)
118125462
(gnsb)
LCF:
108895359
(gnsb)
108895933
(gnsa)
SDU:
111224796
(gns)
111239659
SLAL:
111659475
111669098
(gns)
XGL:
120797913
(gnsa)
120806578
(gnsb)
HCQ:
109507189
109532622
(gns)
BPEC:
110161614
(gns)
110166676
MALB:
109952366
109965006
(gns)
BSPL:
114861631
(gnsa)
114866947
(gnsb)
SASA:
100380417
(gns)
STRU:
115159890
115189798
(gns)
OTW:
112220124
(gnsb)
112240493
121844647
OMY:
110511600
110523334
(gnsb)
118942865
OGO:
123989342
(gnsb)
124019611
ONE:
115120065
(gns)
SALP:
111961849
(gns)
SNH:
120025706
(gnsb)
CCLU:
121558509
(gnsa)
121582128
(gnsb)
ELS:
105007344
105007789
(gns)
SFM:
108920982
(gns)
108935811
PKI:
111849756
111851442
111859045
(gns)
AANG:
118206940
118212860
118232018
(gnsa)
LOC:
102685371
102693153
(gns)
PSPA:
121318565
ARUT:
117416020
117419996
PSEX:
120538823
(gnsb)
120539685
(gnsa)
LCM:
102349411
(GNS)
CMK:
103186133
(gnsa)
103187768
RTP:
109933529
(gns)
BFO:
118426612
BBEL:
109470078
CIN:
100187080
SCLV:
120327862
SPU:
588183
APLC:
110989212
AJC:
117108555
SKO:
100369601
DME:
Dmel_CG18278
(CG18278)
Dmel_CG30059
(CG30059)
DER:
6549483
DSI:
Dsimw501_GD25763
(Dsim_GD25763)
DYA:
Dyak_GE13365
DSR:
110191322
DPO:
6898764
DPE:
6590694
DMN:
108159050
DWI:
6637910
DGR:
6565225
DMO:
Dmoj_GI14019
DAZ:
108617790
DNV:
108655520
DHE:
111596960
CCAT:
101449590
BOD:
106620096
RZE:
108366483
MDE:
101889965
SCAC:
106085733
LCQ:
111691039
LSQ:
119602087
HIS:
119654404
AGA:
AgaP_AGAP004721
ACOZ:
120950685
AARA:
120895838
ASTE:
118512415
AAG:
5564874
CQU:
CpipJ_CPIJ000745
CPII:
120419582
CNS:
116348632
BCOO:
119066868
AME:
550869
ACER:
107993470
ALAB:
122715461
BIM:
100747455
BBIF:
117213595
BVK:
117234266
BVAN:
117166176
BTER:
100647617
BPYO:
122568461
CCAL:
108630558
OBB:
114878052
114878893
MGEN:
117218421
NMEA:
116429676
CGIG:
122403484
SOC:
105199010
MPHA:
105829048
AEC:
105147802
ACEP:
105625478
PBAR:
105426645
VEM:
105561695
HST:
105183028
DQU:
106749555
CFO:
105254293
FEX:
115237451
LHU:
105679262
PGC:
109857431
PCF:
106788173
PFUC:
122526315
VPS:
122629838
NVI:
100117101
(Gns)
CSOL:
105364169
TPRE:
106653810
MDL:
103574942
CGLO:
123259239
FAS:
105274205
DAM:
107041315
AGIF:
122860396
LHT:
122499800
CCIN:
107264804
TCA:
662227
DPA:
109546649
SOY:
115881544
ATD:
109599646
CSET:
123319829
AGB:
108908534
108908543
111691362
NVL:
108566233
APLN:
108735831
PPYR:
116160919
OTU:
111421484
111423014
BMOR:
101745680
BMAN:
114246751
MSEX:
115442674
DPL:
KGM_206993
BANY:
112052677
NIQ:
126775544
PMAC:
106714537
PPOT:
106109335
PXU:
106117562
PRAP:
110993226
PBX:
123712893
PNAP:
125060030
ZCE:
119834614
CCRC:
123700235
HAW:
110373657
HZE:
124639572
TNL:
113494214
SLIU:
111360153
OFU:
114358784
PXY:
105384301
CFEL:
113377456
BTAB:
109031196
CLEC:
106664737
HHAL:
106688741
NLU:
111049407
PHU:
Phum_PHUM362030
FOC:
113207058
TPAL:
117651671
ZNE:
110835687
CSEC:
111864097
SGRE:
126336642
126336643
DPX:
DAPPUDRAFT_50373
DMK:
116922310
123472575
DPZ:
124311493
PVM:
113803259
PJA:
122265775
PCHN:
125046094
HAME:
121868439
PCLA:
123764430
PTRU:
123500151
HAZT:
108680029
EAF:
111710072
LSM:
121118785
PPOI:
119096059
119096252
DSV:
119461559
RSAN:
119395936
RMP:
119174271
CSCU:
111623773
PTEP:
107452499
SDM:
118190553
LGI:
LOTGIDRAFT_208806
LOTGIDRAFT_238806
PCAN:
112559084
112559345
BGT:
106054326
GAE:
121381524
HRF:
124116039
124116040
124116042
124117774
124117782
HRJ:
124254025
124254029
124281890
124281891
CRG:
105333379
MYI:
110440675
PMAX:
117336244
MMER:
123537139
OBI:
106870891
OSN:
115213774
LAK:
106157766
106157770
106163980
106166031
NVE:
5521987
EPA:
110249537
ATEN:
116287356
ADF:
107356217
AMIL:
114968864
PDAM:
113678136
SPIS:
111338464
AQU:
100637984
100640152
105312223
QSU:
112000613
VCN:
VOLCADRAFT_104983
(ars1)
MGR:
MGG_07920
MGG_15457
FGR:
FGSG_12251
FPU:
FPSE_08295
FVR:
FVEG_00102
FVEG_11177
FOX:
FOXG_13747
NHE:
NECHADRAFT_42509
NECHADRAFT_45116
NECHADRAFT_95823
TRE:
TRIREDRAFT_61121
TRR:
M419DRAFT_78507
CMT:
CCM_05254
CCM_07457
PLJ:
VFPFJ_02907
VFPFJ_07622
SAPO:
SAPIO_CDS1612
ELA:
UCREL1_10896
UCREL1_6012
UCREL1_711
PFY:
PFICI_00717
PFICI_00803
PFICI_05380
PFICI_06323
PFICI_08657
PFICI_15110
SSL:
SS1G_04337
BFU:
BCIN_01g04510
PSCO:
LY89DRAFT_682887
GLZ:
GLAREA_00160
AOR:
AO090701000355
PCS:
Pc21g23250
TRG:
TRUGW13939_10979
CPW:
CPC735_024540
URE:
UREG_04509
UREG_07890
PTE:
PTT_08067
BZE:
COCCADRAFT_107495
BSC:
COCSADRAFT_168273
BOR:
COCMIDRAFT_108726
AALT:
CC77DRAFT_1042949
CC77DRAFT_202654
ZTR:
MYCGRDRAFT_40096
MYCGRDRAFT_76800
PFJ:
MYCFIDRAFT_65580
MYCFIDRAFT_97143
NPA:
UCRNP2_1611
UCRNP2_5515
UCRNP2_7569
CNB:
CNBC0370
SHS:
STEHIDRAFT_126811
STEHIDRAFT_126817
MRR:
Moror_2117
Moror_7800
PFP:
PFL1_01801
MBR:
MONBRDRAFT_24514
MONBRDRAFT_29207
MONBRDRAFT_29950
MONBRDRAFT_849
SRE:
PTSG_10494
PTSG_11248
PTSG_12796
FCY:
FRACYDRAFT_157083
(GNS1_1)
FRACYDRAFT_247897
(GNS2_1)
AAF:
AURANDRAFT_12528
AURANDRAFT_27956
AURANDRAFT_29931
AURANDRAFT_62077
AURANDRAFT_65638
EHX:
EMIHUDRAFT_100471
EMIHUDRAFT_196221
EMIHUDRAFT_201189
EMIHUDRAFT_215588
EMIHUDRAFT_225471
EMIHUDRAFT_470091
VFI:
VF_A1007
(yidJ)
METU:
GNH96_08405
NIT:
NAL212_0844
NUR:
ATY38_07480
SKR:
BRX40_11950
SPLM:
BXU08_06815
SPHS:
ETR14_01035
ANH:
A6F65_00912
(betC_2)
PORL:
BG023_112788
PSWU:
SY83_17240
NSL:
BOX37_13365
SVL:
Strvi_5923
SRC:
M271_42700
SMAL:
SMALA_0905
SALS:
SLNWT_3919
SAUO:
BV401_08325
SPUN:
BFF78_04275
SSEO:
D0Z67_26900
SCHA:
CP983_10575
NDK:
I601_1074
(betC_2)
I601_2139
(betC_4)
NOY:
EXE57_00415
NOI:
FCL41_00895
FCL41_16560
NDP:
E2C04_01525
NSN:
EXE58_17380
NANO:
G5V58_14490
NMES:
H9L09_20880
NARO:
CFH99_16075
PSIM:
KR76_18900
TCU:
Tcur_0627
ACTW:
F7P10_13845
SRO:
Sros_7372
NOW:
GBF35_30840
GBF35_39565
TBI:
Tbis_1890
FRA:
Francci3_2189
FRE:
Franean1_4926
FSY:
FsymDg_0579
KAL:
KALB_3320
AMS:
AMIS_40290
ACTN:
L083_6331
AFS:
AFR_28430
ATL:
Athai_45150
SNA:
Snas_3902
ABAI:
IMCC26256_11337
RXY:
Rxyl_2114
Rxyl_3110
RRD:
RradSPS_2086
RUB:
GBA63_04165
GBA63_14630
CWO:
Cwoe_1306
CHON:
NIES4102_04040
PBF:
CFX0092_A1548
TRA:
Trad_1260
MSV:
Mesil_1248
MFF:
MFFC18_32330
AHEL:
Q31a_49230
LCRE:
Pla8534_26720
FMR:
Fuma_06709
GMR:
GmarT_23890
GIM:
F1728_02560
F1728_07040
GPN:
Pan110_15320
(betC_2)
SDYN:
Mal52_44170
SUS:
Acid_6855
PFER:
IRI77_11270
ABAC:
LuPra_00356
(betC_2)
GPH:
GEMMAAP_18625
RBAR:
AWN76_006450
LACS:
H4075_16695
MMAB:
HQ865_16160
AGD:
FRZ59_03720
CMR:
Cycma_3755
EST:
DN752_18465
ECHI:
FKX85_11875
SMON:
AWR27_17020
SPIB:
G8759_13535
STAE:
HNV11_22310
RHOZ:
GXP67_12755
RSI:
Runsl_2857
RUN:
DR864_11540
FAE:
FAES_1634
(mdsA)
FIB:
A6C57_18230
ADD:
HUW48_13180
ASWU:
HUW51_13385
FBT:
D770_14500
FBC:
FB2170_09821
CAO:
Celal_2464
CBAL:
M667_00095
M667_09680
CBAT:
M666_00095
M666_09605
» show all
Taxonomy
UniProt
Reference
PMID:
1463457
Authors
Robertson DA, Freeman C, Morris CP, Hopwood JJ
Title
A cDNA clone for human glucosamine-6-sulphatase reveals differences between arylsulphatases and non-arylsulphatases.
Journal
Biochem J 288 ( Pt 2):539-44 (1992)
DOI:
10.1042/bj2880539
Sequence
[hsa:
2799
]
LinkDB
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DBGET
integrated database retrieval system