KEGG   DISEASE: Bilateral sudden sensorineural hearing loss
Entry
H01705                      Disease                                

Name
Bilateral sudden sensorineural hearing loss
Description
Bilateral sudden sensorineural hearing loss (SNHL) represents a rare disease entity, constituting less than 5 % of all sudden SNHL cases. Unlike unilateral disease, bilateral sudden SNHL appears to be mostly related to serious systemic pathology, and is associated with a more severe degree of hearing loss, poorer prognosis following treatment, and more significant impairment in morbidity and overall quality of life.
Category
Nervous system disease
Brite
Human diseases [BR:br08402]
 Nervous system diseases
  Ear disease
   H01705  Bilateral sudden sensorineural hearing loss
Human diseases in ICD-11 classification [BR:br08403]
 10 Diseases of the ear or mastoid process
  Disorders with hearing impairment
   AB51  Acquired hearing impairment
    H01705  Bilateral sudden sensorineural hearing loss
Gene
ACTG1 [HSA:71] [KO:K05692]
CDH23 [HSA:64072] [KO:K06813]
COCH [HSA:1690] [KO:K23574]
KCNQ4 [HSA:9132] [KO:K04929]
TECTA [HSA:7007] [KO:K18273]
TMPRSS3 [HSA:64699] [KO:K09634]
WFS1 [HSA:7466] [KO:K14020]
Comment
See also H01704 Sudden sensorineural hearing loss, H00604 Deafness, autosomal dominant, and H00605 Deafness, autosomal recessive.
Other DBs
ICD-11: AB51.1
ICD-10: H90.3 H91.2
MeSH: D006312
OMIM: 604717 601386 601369 600101 601543 603629 601072 600965
Reference
  Authors
Sara SA, Teh BM, Friedland P
  Title
Bilateral sudden sensorineural hearing loss: review.
  Journal
J Laryngol Otol 128 Suppl 1:S8-15 (2014)
DOI:10.1017/S002221511300306X
Reference
  Authors
Chen YH, Young YH
  Title
Bilateral simultaneous sudden sensorineural hearing loss.
  Journal
J Neurol Sci 362:139-43 (2016)
DOI:10.1016/j.jns.2016.01.029
Reference
  Authors
Smith RJH, Shearer AE, Hildebrand MS, Van Camp G
  Title
Deafness and Hereditary Hearing Loss Overview
  Journal
GeneReviews (1993)
LinkDB

» Japanese version

DBGET integrated database retrieval system