ORTHOLOGY: K20194
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Entry
K20194 KO
Symbol
HPS4
Name
Hermansky-Pudlak syndrome 4 protein
Disease
H00166
Hermansky-Pudlak syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
04131 Membrane trafficking
K20194 HPS4; Hermansky-Pudlak syndrome 4 protein
Membrane trafficking [BR:
ko04131
]
Endosome - Lysosome transport
Others
BLOC-3 complex
K20194 HPS4; Hermansky-Pudlak syndrome 4 protein
BRITE hierarchy
Other DBs
GO:
0031085
Genes
HSA:
89781
(HPS4)
PTR:
458723
(HPS4)
PPS:
100982998
(HPS4)
GGO:
101139088
(HPS4)
PON:
100173422
(HPS4)
NLE:
100605057
(HPS4)
HMH:
116458919
(HPS4)
MCC:
712549
(HPS4)
MCF:
102136837
(HPS4)
MTHB:
126929498
MNI:
105495716
(HPS4)
CSAB:
103223090
(HPS4)
CATY:
105575655
(HPS4)
PANU:
101007586
(HPS4)
TGE:
112632558
(HPS4)
MLEU:
105536070
(HPS4)
RRO:
104671942
(HPS4)
RBB:
108515887
(HPS4)
TFN:
117096116
(HPS4)
PTEH:
111525387
(HPS4)
CANG:
105506638
(HPS4)
CJC:
100400466
(HPS4)
SBQ:
101028118
(HPS4)
CIMI:
108282216
(HPS4)
CSYR:
103253853
(HPS4)
MMUR:
105866962
(HPS4)
LCAT:
123625786
(HPS4)
PCOQ:
105810226
(HPS4)
OGA:
100940935
(HPS4)
MMU:
192232
(Hps4)
MCAL:
110294520
(Hps4)
MPAH:
110312871
(Hps4)
RNO:
304555
(Hps4)
MCOC:
116068174
(Hps4)
ANU:
117698154
(Hps4)
MUN:
110554330
(Hps4)
CGE:
100774207
(Hps4)
MAUA:
101840838
(Hps4)
PROB:
127215937
(Hps4)
PLEU:
114684309
(Hps4)
MORG:
121446129
(Hps4)
MFOT:
126487970
AAMP:
119825692
(Hps4)
NGI:
103746729
(Hps4)
HGL:
101714464
(Hps4)
CPOC:
100721935
(Hps4)
CCAN:
109693030
(Hps4)
DORD:
105984173
(Hps4)
DSP:
122097922
(Hps4)
PLOP:
125348997
(Hps4)
NCAR:
124991145
MMMA:
107154599
(Hps4)
OCU:
100338186
OPI:
101527325
(HPS4)
TUP:
102477537
(HPS4)
GVR:
103594983
(HPS4)
CFA:
486330
(HPS4)
CLUD:
112676752
(HPS4)
VVP:
112923193
(HPS4)
VLG:
121475684
(HPS4)
NPO:
129507491
(HPS4)
AML:
100475897
(HPS4)
UMR:
103659258
(HPS4)
UAH:
113244990
(HPS4)
UAR:
123788125
(HPS4)
ELK:
111160092
LLV:
125081827
MPUF:
101674761
(HPS4)
MNP:
132023287
(HPS4)
MLK:
131811872
(HPS4)
NVS:
122903304
(HPS4)
ORO:
101384752
(HPS4)
EJU:
114225228
(HPS4)
ZCA:
113912317
(HPS4)
MLX:
118018607
(HPS4)
NSU:
110592428
(HPS4)
LWW:
102738405
(HPS4)
FCA:
101083975
(HPS4)
PYU:
121022689
(HPS4)
PCOO:
112870263
(HPS4)
PBG:
122470442
(HPS4)
PVIV:
125149582
(HPS4)
LRUF:
124518404
PTG:
102956375
(HPS4)
PPAD:
109253520
(HPS4)
PUC:
125913923
AJU:
106982304
HHV:
120227133
(HPS4)
BTA:
615386
(HPS4)
BOM:
102284662
(HPS4)
BIU:
109571407
(HPS4)
BBUB:
102412782
(HPS4)
BBIS:
104980106
(HPS4)
CHX:
102186422
(HPS4)
OAS:
101118387
(HPS4)
BTAX:
128062180
(HPS4)
ODA:
120871215
(HPS4)
CCAD:
122421696
(HPS4)
MBEZ:
129542196
(HPS4)
SSC:
100049674
(HPS4)
CFR:
102523333
(HPS4)
CBAI:
105066037
(HPS4)
CDK:
105099487
(HPS4)
VPC:
102530306
(HPS4)
BACU:
103002927
(HPS4)
BMUS:
118880094
(HPS4)
LVE:
103073964
(HPS4)
OOR:
101270101
(HPS4)
DLE:
111162834
(HPS4)
PCAD:
102984153
(HPS4)
PSIU:
116764892
(HPS4)
NASI:
112397335
(HPS4)
ECB:
100059474
(HPS4)
EPZ:
103550027
(HPS4)
EAI:
106841703
(HPS4)
MYB:
102247556
(HPS4)
MYD:
102764919
(HPS4)
MMYO:
118678193
(HPS4)
MLF:
102416917
(HPS4)
PKL:
118725746
(HPS4)
EFUS:
103286884
(HPS4)
MNA:
107533863
(HPS4)
DRO:
112310704
(HPS4)
SHON:
118991238
(HPS4)
AJM:
119055145
(HPS4)
PDIC:
114509577
(HPS4)
PHAS:
123821624
(HPS4)
MMF:
118640149
(HPS4)
PPAM:
129087499
(HPS4)
HAI:
109394137
(HPS4)
RFQ:
117017543
(HPS4)
PALE:
102880301
(HPS4)
PGIG:
120601931
(HPS4)
PVP:
105301816
(HPS4)
RAY:
107502454
(HPS4)
MJV:
108388718
(HPS4)
TOD:
119244791
(HPS4)
SARA:
101550011
(HPS4)
SETR:
126030574
(HPS4)
LAV:
100666010
(HPS4)
TMU:
101356674
ETF:
101651841
(HPS4)
DNM:
101429942
(HPS4)
MDO:
100011128
(HPS4)
GAS:
123232422
(HPS4)
SHR:
100914359
(HPS4)
AFZ:
127545619
PCW:
110215216
(HPS4)
OAA:
114806195
(HPS4)
GGA:
416907
(HPS4)
PCOC:
116228521
(HPS4)
MGP:
100542291
(HPS4)
CJO:
107321429
(HPS4)
TPAI:
128084671
(HPS4)
LMUT:
125701692
(HPS4)
NMEL:
110406229
(HPS4)
APLA:
119718565
(HPS4)
ACYG:
106031384
(HPS4)
CATA:
118257560
(HPS4)
AFUL:
116496134
(HPS4)
TGU:
100229477
(HPS4)
LSR:
110478141
(HPS4)
SCAN:
103818285
(HPS4)
PMOA:
120509593
(HPS4)
OTC:
121338827
(HPS4)
PRUF:
121364796
(HPS4)
GFR:
102037208
(HPS4)
FAB:
101812651
(HPS4)
OMA:
130259677
(HPS4)
PHI:
102105928
(HPS4)
PMAJ:
107211461
(HPS4)
CCAE:
111936464
(HPS4)
CCW:
104688797
(HPS4)
CBRC:
103616081
(HPS4)
ETL:
114066067
(HPS4)
ZAB:
102064810
(HPS4)
ACHL:
103800952
(HPS4)
SVG:
106852333
(HPS4)
MMEA:
130579635
(HPS4)
HRT:
120760485
(HPS4)
FPG:
101916332
(HPS4)
FCH:
102048427
(HPS4)
CLV:
102096111
(HPS4)
EGZ:
104122583
(HPS4)
NNI:
104015776
(HPS4)
PCRI:
104030084
(HPS4)
PLET:
104626978
(HPS4)
EHS:
104515801
(HPS4)
PCAO:
104043503
(HPS4)
ACUN:
113486279
(HPS4)
TALA:
104360511
(HPS4)
PADL:
103925676
(HPS4)
AFOR:
103901858
(HPS4)
ACHC:
115345755
(HPS4)
HALD:
104317388
(HPS4)
HLE:
104840819
(HPS4)
AGEN:
126041395
GCL:
127022941
CCRI:
104159650
(HPS4)
CSTI:
104556548
(HPS4)
CMAC:
104475702
(HPS4)
MUI:
104536934
(HPS4)
BREG:
104639513
(HPS4)
FGA:
104082517
(HPS4)
GSTE:
104258003
(HPS4)
LDI:
104349550
(HPS4)
MNB:
103774023
(HPS4)
OHA:
104333111
(HPS4)
NNT:
104408337
(HPS4)
SHAB:
115614207
(HPS4)
DPUB:
104308522
(HPS4)
PGUU:
104466931
(HPS4)
ACAR:
104524125
(HPS4)
CPEA:
104388052
(HPS4)
AVIT:
104267413
(HPS4)
CVF:
104290095
(HPS4)
RTD:
128916874
(HPS4)
CUCA:
104058921
(HPS4)
TEO:
104377908
(HPS4)
BRHI:
104499424
(HPS4)
AAM:
106492554
(HPS4)
AROW:
112963352
(HPS4)
NPD:
112945161
(HPS4)
TGT:
104578082
(HPS4)
DNE:
112989027
(HPS4)
SCAM:
104146245
(HPS4)
ASN:
102384820
(HPS4)
AMJ:
102559609
(HPS4)
CPOO:
109312597
(HPS4)
GGN:
109290626
(HPS4)
PSS:
102459842
(HPS4)
CMY:
102946460
(HPS4)
CCAY:
125623160
(HPS4)
DCC:
119843610
(HPS4)
CPIC:
101951247
(HPS4)
TST:
117887884
(HPS4)
CABI:
116818704
(HPS4)
MRV:
120385980
(HPS4)
ASAO:
132780917
(HPS4)
PVT:
110083423
(HPS4)
PBI:
103064292
(HPS4)
PMUR:
107287277
(HPS4)
CTIG:
120316682
(HPS4)
TSR:
106544789
(HPS4)
PGUT:
117672305
(HPS4)
APRI:
131185643
(HPS4)
VKO:
123028713
(HPS4)
PMUA:
114586698
(HPS4)
PRAF:
128403579
(HPS4)
ZVI:
118075634
(HPS4)
GJA:
107118890
(HPS4)
STOW:
125443057
(HPS4)
XLA:
495486
(hps4.L)
XTR:
779927
(hps4)
NPR:
108793633
(HPS4)
RTEM:
120937737
(HPS4)
BBUF:
120988826
(HPS4)
BGAR:
122924367
(HPS4)
MUO:
115480498
(HPS4)
GSH:
117364754
(HPS4)
DRE:
393296
(hps4)
SRX:
107712456
107753110
SANH:
107687970
107703156
SGH:
107550983
107554431
CCAR:
109094767
CAUA:
113093771
113107473
CGIB:
127963412
128018448
PTET:
122350286
(hps4)
LROH:
127169703
(hps4)
PPRM:
120473566
(hps4)
RKG:
130081844
(hps4)
MAMB:
125280066
(hps4)
CIDE:
127517654
MASI:
127424167
TROS:
130568583
(hps4)
TDW:
130439739
(hps4)
MANU:
129414263
(hps4)
IPU:
108264910
IFU:
128607276
(hps4)
PHYP:
113546064
(hps4)
SMEO:
124400228
(hps4)
TFD:
113638859
(hps4)
TVC:
132853229
(hps4)
AMEX:
103027696
(hps4)
CMAO:
118813063
(hps4)
EEE:
113584821
(hps4)
CHAR:
105899092
(hps4)
TRU:
101074151
(hps4)
TFS:
130526323
(hps4)
TNG:
GSTEN00021637G001
LCO:
104936410
(hps4)
NCC:
104950462
(hps4)
TBEN:
117472684
(hps4)
CGOB:
115013020
(hps4)
PGEO:
117452702
(hps4)
GACU:
117543862
(hps4)
EMAC:
134874143
(hps4)
ELY:
117252086
(hps4)
EFO:
125890654
(hps4)
PLEP:
121944561
(hps4)
SLUC:
116050583
(hps4)
ECRA:
117944495
(hps4)
ESP:
116690082
(hps4)
PFLV:
114555934
(hps4)
GAT:
120830650
(hps4)
PPUG:
119225576
(hps4)
AFB:
129101297
(hps4)
CLUM:
117736629
(hps4)
PSWI:
130196562
(hps4)
MSAM:
119892209
(hps4)
SCHU:
122876556
(hps4)
CUD:
121510472
(hps4)
ALAT:
119019607
(hps4)
MZE:
101469669
(hps4)
ONL:
100709428
(hps4)
OAU:
116318857
(hps4)
OLA:
101170522
(hps4)
OML:
112148793
(hps4)
CSAI:
133450916
133451392
XMA:
102220033
(hps4)
XCO:
114154358
(hps4)
XHE:
116729563
(hps4)
PRET:
103469696
(hps4)
PFOR:
103141379
(hps4)
PLAI:
106944634
(hps4)
PMEI:
106907394
(hps4)
GAF:
122828295
(hps4)
PPRL:
129373128
(hps4)
CVG:
107097805
(hps4)
CTUL:
119782419
(hps4)
GMU:
124878069
(hps4)
NFU:
107393583
(hps4)
KMR:
108234906
(hps4)
ALIM:
106522540
(hps4)
NWH:
119414079
(hps4)
AOCE:
111574322
(hps4)
MCEP:
125011969
(hps4)
CSEM:
103396937
103398120
POV:
109633902
(hps4)
SSEN:
122769199
(hps4)
HHIP:
117768201
(hps4)
HSP:
118115474
(hps4)
SMAU:
118313390
(hps4)
LCF:
108878746
SDU:
111231584
(hps4)
SLAL:
111645106
(hps4)
XGL:
120805834
(hps4)
HCQ:
109510883
(hps4)
SSCV:
125993844
SBIA:
133499554
(hps4)
PEE:
133400408
(hps4)
PTAO:
133474629
(hps4)
BPEC:
110163306
(hps4)
MALB:
109954985
(hps4)
BSPL:
114861615
(hps4)
SJO:
128365278
(hps4)
SASA:
100380537
(hps4)
STRU:
115199989
OTW:
112263027
(hps4)
OMY:
110535919
(hps4)
OGO:
124036202
(hps4)
ONE:
115139936
OKI:
109895800
OKE:
118358233
SALP:
111957541
SNH:
120063168
(hps4)
CCLU:
121550208
(hps4)
121584749
ELS:
105014206
(hps4)
SFM:
108921799
(hps4)
PKI:
111858735
(hps4)
AANG:
118206632
(hps4)
PSPA:
121307699
121309236
ARUT:
117427865
LCM:
102362348
(HPS4)
CMK:
103184079
(hps4)
RTP:
109913961
(hps4)
CPLA:
122562551
(hps4)
HOC:
132827047
(hps4)
LERI:
129709202
(hps4)
BFO:
118426604
BBEL:
109466667
SPU:
100893601
APLC:
110976574
SKO:
102807271
DME:
Dmel_CG4966
(HPS4)
DER:
6546781
DSE:
6609652
DSI:
Dsimw501_GD11303
(Dsim_GD11303)
DYA:
Dyak_GE11887
DAN:
6494527
DSR:
110190924
DPO:
4804666
DPE:
6592663
DMN:
108159820
117185782
DWI:
6640951
DGR:
6561191
DMO:
Dmoj_GI20844
DAZ:
108616927
DNV:
115564681
DHE:
111601274
DVI:
6627182
CCAT:
101448490
BOD:
106622507
BDR:
105233007
RZE:
108377491
AOQ:
129245485
TDA:
119677375
119678611
MDE:
101895848
131802923
SCAC:
106086530
LCQ:
111678845
LSQ:
119602998
GFS:
119638251
ECOE:
129949471
CLON:
129606620
HIS:
119655874
AGA:
3291021
ACOZ:
120948333
AARA:
120898779
AMER:
121590966
ASTE:
118508537
AFUN:
125763193
AMOU:
128309970
AALI:
118461390
AAG:
5574380
CQU:
CpipJ_CPIJ018522
CNS:
116350121
BCOO:
119085390
AME:
412265
ACER:
107998067
ALAB:
122712241
ADR:
102679440
AFLR:
100871599
BIM:
100744735
BBIF:
117207270
BVK:
117239652
BVAN:
117165802
BTER:
100646462
BAFF:
126916541
BPYO:
122566081
BPAS:
132905691
FVI:
122528033
CCAL:
108625361
OBB:
114873194
OLG:
117605238
MGEN:
117218133
NMEA:
116433898
CGIG:
122398178
SOC:
105199242
MPHA:
105838818
AEC:
105144281
ACEP:
105619214
PBAR:
105433105
VEM:
105561363
HST:
105183351
DQU:
106748681
CFO:
105251361
FEX:
115242304
115242313
LHU:
105673185
PGC:
109857603
OBO:
113561394
PCF:
106783860
PFUC:
122525964
VPS:
122632863
VCRB:
124428216
VVE:
124953171
NVI:
100116464
CSOL:
105366185
TPRE:
106656455
LHT:
122511429
LBD:
127287256
MDL:
103579620
CGLO:
123264539
FAS:
105270008
DAM:
107040912
AGIF:
122857111
122857112
VCAN:
122414417
CCIN:
107269173
DSM:
124410714
NPT:
124219670
NFB:
124183144
NLO:
107227501
NVG:
124305782
AROA:
105686759
TCA:
658083
DPA:
109539341
SOY:
115877310
AGRG:
126739666
ATD:
109599390
CSET:
123320225
AGB:
108910452
LDC:
111502102
NVL:
108559557
APLN:
108735928
PPYR:
116180308
OTU:
111413404
BMOR:
101743016
BMAN:
114247250
MSEX:
115446566
DPL:
KGM_200862
BANY:
112057897
MJU:
123872403
NIQ:
126773719
VCD:
124534275
MCIX:
123656547
PMAC:
106719293
PPOT:
106108854
PXU:
106119644
PRAP:
110997149
PBX:
123709630
PNAP:
125049176
ZCE:
119838662
CCRC:
123696518
LSIN:
126979144
AAGE:
121732873
HAW:
110382789
HZE:
124637470
TNL:
113491934
SLIU:
111365062
OFU:
114352183
PXY:
105390737
PGW:
126372113
CFEL:
113370591
CCRN:
123297480
API:
100166600
DNX:
107169668
AGS:
114129168
RMD:
113551657
ACOO:
126843832
DVT:
126901221
BTAB:
109039970
CLEC:
106674035
HHAL:
106688690
NLU:
111057824
PHU:
Phum_PHUM369780
FOC:
113215173
TPAL:
117639205
ZNE:
110836134
CSEC:
111862924
BROR:
134530805
IEL:
124158929
FCD:
110859099
PVM:
113812919
PJA:
122251204
PCHN:
125044100
PMOO:
119579415
HAME:
121858416
PCLA:
123774539
PTRU:
123518431
PPOI:
119111589
DSV:
119446621
RSAN:
119389824
RMP:
119176475
PTEP:
107451378
122271956
SDM:
118196500
LGI:
LOTGIDRAFT_231593
PCAN:
112562525
GAE:
121368781
HRF:
124133406
HRJ:
124256549
CRG:
105345695
MYI:
110464062
PMAX:
117333450
MMER:
123533767
OBI:
106882148
OSN:
115213008
LAK:
106157119
106172512
NVE:
5516524
EPA:
110247582
ATEN:
116297747
ADF:
107337463
AMIL:
114960105
PDAM:
113665530
SPIS:
111345190
DGT:
114520346
114538272
HSY:
130624352
AQU:
109583798
» show all
Taxonomy
UniProt
Reference
PMID:
12756248
Authors
Martina JA, Moriyama K, Bonifacino JS
Title
BLOC-3, a protein complex containing the Hermansky-Pudlak syndrome gene products HPS1 and HPS4.
Journal
J Biol Chem 278:29376-84 (2003)
DOI:
10.1074/jbc.M301294200
Sequence
[hsa:
89781
]
LinkDB
All DBs
DBGET
integrated database retrieval system