KEGG   MODULE: M00862
Entry
M00862            Pathway   Module                                 
Name
beta-Oxidation, peroxisome, tri/dihydroxycholestanoyl-CoA => choloyl/chenodeoxycholoyl-CoA
Definition
K10214 K12405 K08764
Diagram
M00862  beta-Oxidation, peroxisome, tri/dihydroxycholestanoyl-CoA => choloyl/chenodeoxycholoyl-CoA
M00862

Class
Pathway modules; Lipid metabolism; Sterol biosynthesis
Pathway
map00120  Primary bile acid biosynthesis
map01100  Metabolic pathways
Orthology
K10214  
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoyl-CoA 24-hydroxylase [EC:1.17.99.3] [RN:R08735 R08740]
K12405  
(3R)-3-hydroxyacyl-CoA dehydrogenase / 3a,7a,12a-trihydroxy-5b-cholest-24-enoyl-CoA hydratase [EC:1.1.1.- 4.2.1.107] [RN:R04813 R04812 R04809 R04810]
K08764  
sterol carrier protein 2 [EC:2.3.1.176] [RN:R03719 R04811]
Complete
hsa  Homo sapiens (human)
ptr  Pan troglodytes (chimpanzee)
pps  Pan paniscus (bonobo)
ggo  Gorilla gorilla gorilla (western lowland gorilla)
pon  Pongo abelii (Sumatran orangutan)
ppyg  Pongo pygmaeus (Bornean orangutan)
nle  Nomascus leucogenys (northern white-cheeked gibbon)
hmh  Hylobates moloch (silvery gibbon)
ssyn  Symphalangus syndactylus (siamang)
mcc  Macaca mulatta (rhesus monkey)
mcf  Macaca fascicularis (crab-eating macaque)
mthb  Macaca thibetana thibetana (Pere David's macaque)
mni  Macaca nemestrina (pig-tailed macaque)
csab  Chlorocebus sabaeus (green monkey)
caty  Cercocebus atys (sooty mangabey)
panu  Papio anubis (olive baboon)
tge  Theropithecus gelada (gelada)
mleu  Mandrillus leucophaeus (drill)
rro  Rhinopithecus roxellana (golden snub-nosed monkey)
rbb  Rhinopithecus bieti (black snub-nosed monkey)
tfn  Trachypithecus francoisi (Francois's langur)
pteh  Piliocolobus tephrosceles (Ugandan red Colobus)
cang  Colobus angolensis palliatus (Angola colobus)
cjc  Callithrix jacchus (white-tufted-ear marmoset)
sbq  Saimiri boliviensis boliviensis (Bolivian squirrel monkey)
cimi  Cebus imitator (Panamanian white-faced capuchin)
anan  Aotus nancymaae (Ma's night monkey)
csyr  Carlito syrichta (Philippine tarsier)
mmur  Microcebus murinus (gray mouse lemur)
lcat  Lemur catta (Ring-tailed lemur)
eruf  Eulemur rufifrons (Bennett's brown lemur)
pcoq  Propithecus coquereli (Coquerel's sifaka)
oga  Otolemur garnettii (small-eared galago)
mmu  Mus musculus (house mouse)
mcal  Mus caroli (Ryukyu mouse)
mpah  Mus pahari (shrew mouse)
rno  Rattus norvegicus (rat)
mcoc  Mastomys coucha (southern multimammate mouse)
anu  Arvicanthis niloticus (African grass rat)
asyl  Apodemus sylvaticus (European woodmouse)
mun  Meriones unguiculatus (Mongolian gerbil)
cge  Cricetulus griseus (Chinese hamster)
maua  Mesocricetus auratus (golden hamster)
prob  Phodopus roborovskii (desert hamster)
pleu  Peromyscus leucopus (white-footed mouse)
pmav  Peromyscus maniculatus bairdii (prairie deer mouse)
morg  Microtus oregoni (creeping vole)
mfot  Alexandromys fortis (reed vole)
aamp  Arvicola amphibius (Eurasian water vole)
cnl  Chionomys nivalis (European snow vole)
ngi  Nannospalax galili (Upper Galilee mountains blind mole rat)
hgl  Heterocephalus glaber (naked mole-rat)
cpoc  Cavia porcellus (domestic guinea pig)
ccan  Castor canadensis (American beaver)
dord  Dipodomys ordii (Ord's kangaroo rat)
dsp  Dipodomys spectabilis (banner-tailed kangaroo rat)
dmer  Dipodomys merriami (Merriam's kangaroo rat)
plop  Perognathus longimembris pacificus (Pacific pocket mouse)
ncar  Sciurus carolinensis (gray squirrel)
mmma  Marmota marmota marmota (Alpine marmot)
iti  Ictidomys tridecemlineatus (thirteen-lined ground squirrel)
ocu  Oryctolagus cuniculus (rabbit)
opi  Ochotona princeps (American pika)
ocz  Ochotona curzoniae (black-lipped pika)
tup  Tupaia chinensis (Chinese tree shrew)
gvr  Galeopterus variegatus (Sunda flying lemur)
cfa  Canis lupus familiaris (dog)
clud  Canis lupus dingo (dingo)
vvp  Vulpes vulpes (red fox)
vlg  Vulpes lagopus (Arctic fox)
npo  Nyctereutes procyonoides (raccoon dog)
aml  Ailuropoda melanoleuca (giant panda)
umr  Ursus maritimus (polar bear)
uah  Ursus arctos (brown bear)
uar  Ursus americanus (American black bear)
elk  Enhydra lutris kenyoni (northern sea otter)
llv  Lutra lutra (Eurasian river otter)
mpuf  Mustela putorius furo (domestic ferret)
mnp  Mustela nigripes (black-footed ferret)
mlk  Mustela lutreola (European mink)
nvs  Neogale vison (American mink)
oro  Odobenus rosmarus divergens (Pacific walrus)
eju  Eumetopias jubatus (Steller sea lion)
zca  Zalophus californianus (California sea lion)
mlx  Mirounga leonina (Southern elephant seal)
mano  Mirounga angustirostris (Northern elephant seal)
nsu  Neomonachus schauinslandi (Hawaiian monk seal)
lww  Leptonychotes weddellii (Weddell seal)
fca  Felis catus (domestic cat)
pyu  Herpailurus yagouaroundi (jaguarundi)
pcoo  Puma concolor (puma)
pbg  Prionailurus bengalensis (leopard cat)
pviv  Prionailurus viverrinus (fishing cat)
lruf  Lynx rufus (bobcat)
lgf  Leopardus geoffroyi (Geoffroy's cat)
aju  Acinonyx jubatus (cheetah)
ptg  Panthera tigris altaica (Amur tiger)
ppad  Panthera pardus (leopard)
puc  Panthera uncia (snow leopard)
plez  Panthera leo (lion)
hhv  Hyaena hyaena (striped hyena)
ccru  Crocuta crocuta (spotted hyena)
bta  Bos taurus (cow)
bom  Bos mutus (wild yak)
bbub  Bubalus bubalis (water buffalo)
bke  Bubalus kerabau (carabao)
bbis  Bison bison bison (American bison)
chx  Capra hircus (goat)
oas  Ovis aries (sheep)
btax  Budorcas taxicolor (takin)
csum  Capricornis sumatraensis (Sumatran serow)
oda  Oryx dammah (scimitar-horned oryx)
ccad  Cervus canadensis (wapiti)
mree  Muntiacus reevesi (Reeves' muntjac)
ovr  Odocoileus virginianus (white-tailed deer)
mbez  Moschus berezovskii (Chinese forest musk deer)
ssc  Sus scrofa (pig)
cfr  Camelus ferus (Wild Bactrian camel)
cbai  Camelus bactrianus (Bactrian camel)
cdk  Camelus dromedarius (Arabian camel)
vpc  Vicugna pacos (alpaca)
bmus  Balaenoptera musculus (blue whale)
lve  Lipotes vexillifer (Yangtze River dolphin)
oor  Orcinus orca (killer whale)
lalb  Lagenorhynchus albirostris (white-beaked dolphin)
gmf  Globicephala melas (long-finned pilot whale)
ddp  Delphinus delphis (saddleback dolphin)
dle  Delphinapterus leucas (beluga whale)
pcad  Physeter macrocephalus (sperm whale)
psiu  Phocoena sinus (vaquita)
pphc  Phocoena phocoena (harbor porpoise)
nasi  Neophocaena asiaeorientalis asiaeorientalis (Yangtze finless porpoise)
ecb  Equus caballus (horse)
epz  Equus przewalskii (Przewalski's horse)
eai  Equus asinus (ass)
myb  Myotis brandtii (Brandt's bat)
myd  Myotis davidii (David's myotis)
mmyo  Myotis myotis (greater mouse-eared bat)
mlf  Myotis lucifugus (little brown bat)
mdt  Myotis daubentonii (Daubenton's bat)
myum  Myotis yumanensis (Yuma myotis)
pkl  Pipistrellus kuhlii (Kuhl's pipistrelle)
efus  Eptesicus fuscus (big brown bat)
mna  Miniopterus natalensis (Natal long-fingered bat)
dro  Desmodus rotundus (common vampire bat)
shon  Sturnira hondurensis
ajm  Artibeus jamaicensis (Jamaican fruit-eating bat)
pdic  Phyllostomus discolor (pale spear-nosed bat)
phas  Phyllostomus hastatus (greater spear-nosed bat)
mmf  Molossus molossus (Pallas's mastiff bat)
ppam  Pteronotus mesoamericanus (Parnell's mustached bat)
rfq  Rhinolophus ferrumequinum (greater horseshoe bat)
pale  Pteropus alecto (black flying fox)
pgig  Pteropus vampyrus (Indian flying fox)
pvp  Pteropus vampyrus (large flying fox)
ray  Rousettus aegyptiacus (Egyptian rousette)
tod  Talpa occidentalis (Iberian mole)
sara  Sorex araneus (European shrew)
sfum  Sorex fumeus (smoky shrew)
setr  Suncus etruscus (white-toothed pygmy shrew)
lav  Loxodonta africana (African savanna elephant)
tmu  Trichechus manatus latirostris (Florida manatee)
etf  Echinops telfairi (small Madagascar hedgehog)
dnm  Dasypus novemcinctus (nine-banded armadillo)
mdo  Monodelphis domestica (gray short-tailed opossum)
gas  Gracilinanus agilis (agile gracile opossum)
shr  Sarcophilus harrisii (Tasmanian devil)
pcw  Phascolarctos cinereus (koala)
tvp  Trichosurus vulpecula (common brushtail)
pbrv  Petaurus breviceps papuanus (sugar glider)
mlao  Macrotis lagotis (bilby)
oaa  Ornithorhynchus anatinus (platypus)
tacu  Tachyglossus aculeatus (Australian echidna)
gga  Gallus gallus (chicken)
pcoc  Phasianus colchicus (Ring-necked pheasant)
cjo  Coturnix japonica (Japanese quail)
tpai  Tympanuchus pallidicinctus (lesser prairie-chicken)
lmut  Lagopus muta (rock ptarmigan)
nmel  Numida meleagris (helmeted guineafowl)
apla  Anas platyrhynchos (mallard)
aacu  Anas acuta (northern pintail)
acyg  Anser cygnoides (swan goose)
cata  Cygnus atratus (black swan)
aful  Aythya fuligula (tufted duck)
tgu  Taeniopygia guttata (zebra finch)
lsr  Lonchura striata (white-rumped munia)
scan  Serinus canaria (common canary)
pmoa  Passer montanus (Eurasian tree sparrow)
otc  Onychostruthus taczanowskii (white-rumped snowfinch)
pruf  Pyrgilauda ruficollis (rufous-necked snowfinch)
atrc  Agelaius tricolor (tricolored blackbird)
gfr  Geospiza fortis (medium ground-finch)
fab  Ficedula albicollis (collared flycatcher)
oma  Oenanthe melanoleuca (Eastern black-eared wheatear)
phi  Pseudopodoces humilis (Tibetan ground-tit)
pmaj  Parus major (Great Tit)
ccae  Cyanistes caeruleus (blue tit)
ccw  Corvus cornix (hooded crow)
cbrc  Corvus brachyrhynchos (American crow)
acoe  Aphelocoma coerulescens (scrub jay)
etl  Empidonax traillii (willow flycatcher)
zab  Zonotrichia albicollis (white-throated sparrow)
zle  Zonotrichia leucophrys gambelii (white-crowned sparrow)
achl  Acanthisitta chloris (rifleman)
svg  Sturnus vulgaris (common starling)
mmea  Malurus melanocephalus (red-backed fairy wren)
hrt  Hirundo rustica (Barn swallow)
sati  Sylvia atricapilla (blackcap)
cfai  Chamaea fasciata (wrentit)
ccic  Cinclus cinclus (white-throated dipper)
fpg  Falco peregrinus (peregrine falcon)
fch  Falco cherrug (Saker falcon)
nnt  Nestor notabilis (Kea)
shab  Strigops habroptila (Kakapo)
acun  Athene cunicularia (burrowing owl)
sura  Strix uralensis (Ural owl)
tala  Tyto alba (Barn owl)
achc  Aquila chrysaetos chrysaetos (golden eagle)
hald  Haliaeetus albicilla (white-tailed eagle)
hle  Haliaeetus leucocephalus (bald eagle)
agen  Astur gentilis (Northern goshawk)
hhar  Harpia harpyja (harpy eagle)
bbut  Buteo buteo (common buzzard)
gcl  Gymnogyps californianus (California condor)
dpub  Dryobates pubescens (Downy woodpecker)
ppus  Pogoniulus pusillus (red-fronted tinkerbird)
brhi  Buceros rhinoceros silvestris (rhinoceros hornbill)
egz  Egretta garzetta (little egret)
parx  Phalacrocorax aristotelis (European shag)
padl  Pygoscelis adeliae (Adelie penguin)
afor  Aptenodytes forsteri (emperor penguin)
fga  Fulmarus glacialis (Northern fulmar)
cbor  Calonectris borealis (Cory's shearwater)
cboy  Ciconia boyciana (Oriental stork)
mame  Mycteria americana (wood stork)
clv  Columba livia (rock pigeon)
cnic  Caloenas nicobarica (Nicobar pigeon)
mui  Mesitornis unicolor (brown roatelo)
cmac  Chlamydotis macqueenii (Macqueen's bustard)
cuca  Cuculus canorus (common cuckoo)
breg  Balearica regulorum gibbericeps (East African grey crowned-crane)
game  Grus americana (Whooping crane)
oha  Opisthocomus hoazin (hoatzin)
cpea  Chaetura pelagica (chimney swift)
cvf  Charadrius vociferus (killdeer)
rtd  Rissa tridactyla (black-legged kittiwake)
crid  Chroicocephalus ridibundus (black-headed gull)
lmic  Larus michahellis (yellow-legged gull)
narq  Numenius arquata (Eurasian curlew)
arow  Apteryx rowi (Okarito brown kiwi)
npd  Nothoprocta perdicaria (Chilean tinamou)
tgt  Tinamus guttatus (white-throated tinamou)
dne  Dromaius novaehollandiae (emu)
scam  Struthio camelus australis (South African ostrich)
amj  Alligator mississippiensis (American alligator)
ggn  Gavialis gangeticus (Gharial)
pss  Pelodiscus sinensis (Chinese soft-shelled turtle)
ciz  Carettochelys insculpta (pitted-shelled turtle)
cmy  Chelonia mydas (green sea turtle)
ccay  Caretta caretta (Loggerhead turtle)
lkp  Lepidochelys kempii (Atlantic ridley)
nds  Natator depressus (flatback sea turtle)
dcc  Dermochelys coriacea (leatherback sea turtle)
cpic  Chrysemys picta (western painted turtle)
tst  Trachemys scripta elegans (red-eared slider)
cabi  Chelonoidis abingdonii (Abingdon island giant tortoise)
mrv  Mauremys reevesii (Reeves's turtle)
acs  Anolis carolinensis (green anole)
asao  Anolis sagrei ordinatus (Brown anole)
pvt  Pogona vitticeps (central bearded dragon)
sund  Sceloporus undulatus (fence lizard)
pbi  Python bivittatus (Burmese python)
pmur  Protobothrops mucrosquamatus (Taiwan habu)
ctig  Crotalus tigris (Tiger rattlesnake)
tsr  Thamnophis sirtalis (common garter snake)
pgut  Pantherophis guttatus (corn snake)
pcae  Pituophis catenifer annectens (San Diego gophersnake)
apri  Ahaetulla prasina (Asian vine snake)
ptex  Pseudonaja textilis (eastern brown snake)
nss  Notechis scutatus (mainland tiger snake)
vko  Varanus komodoensis (Komodo dragon)
pmua  Podarcis muralis (common wall lizard)
praf  Podarcis raffonei (Aeolian wall lizard)
zvi  Zootoca vivipara (common lizard)
hcg  Hemicordylus capensis (graceful crag lizard)
gja  Gekko japonicus (Schlegel's Japanese gecko)
stow  Sphaerodactylus townsendi (Townsend's least gecko)
emc  Eublepharis macularius (Leopard gecko)
xla  Xenopus laevis (African clawed frog)
xtr  Xenopus tropicalis (tropical clawed frog)
npr  Nanorana parkeri (Xizang Plateau frog)
rtem  Rana temporaria (common frog)
acat  Aquarana catesbeiana (American bullfrog)
pads  Pyxicephalus adspersus (African bullfrog)
bbuf  Bufo bufo (common toad)
bgar  Bufo gargarizans (Asiatic toad)
dtc  Dendrobates tinctorius (dyeing poison frog)
pwl  Pleurodeles waltl (Iberian ribbed newt)
muo  Microcaecilia unicolor
gsh  Geotrypetes seraphini (Gaboon caecilian)
lcm  Latimeria chalumnae (coelacanth)
cmk  Callorhinchus milii (elephant shark)
rtp  Rhincodon typus (whale shark)
cpla  Chiloscyllium plagiosum (whitespotted bambooshark)
cpun  Chiloscyllium punctatum (brownbanded bambooshark)
hoc  Hemiscyllium ocellatum (epaulette shark)
scau  Scyliorhinus canicula (smaller spotted catshark)
leri  Leucoraja erinaceus (little skate)
haka  Hemitrygon akajei (red stingray)
cin  Ciona intestinalis (yellow sea squirt)
sclv  Styela clava (leathery sea squirt)
clep  Clavelina lepadiformis (light-bulb sea squirt)
ajj  Apostichopus japonicus (Japanese sea cucumber)
lsax  Littorina saxatilis
 » show all
Reaction
Compound
C17343  (25S)-3alpha,7alpha,12alpha-Trihydroxy-5beta-cholestan-26-oyl-CoA
C05460  (24E)-3alpha,7alpha,12alpha-Trihydroxy-5beta-cholest-24-enoyl-CoA
C15614  (24R,25R)-3alpha,7alpha,12alpha,24-Tetrahydroxy-5beta-cholestanoyl-CoA
C05467  3alpha,7alpha,12alpha-Trihydroxy-5beta-24-oxocholestanoyl-CoA
C01794  Choloyl-CoA
C17346  (25S)-3alpha,7alpha-Dihydroxy-5beta-cholestanoyl-CoA
C05447  (24E)-3alpha,7alpha-Dihydroxy-5beta-cholest-24-enoyl-CoA
C05448  (24R,25R)-3alpha,7alpha,24-Trihydroxy-5beta-cholestanoyl-CoA
C05449  3alpha,7alpha-Dihydroxy-5beta-24-oxocholestanoyl-CoA
C05337  Chenodeoxycholoyl-CoA
RModule
RM018  Beta oxidation in acyl-CoA degradation
Reference
  Authors
Waterham HR, Ferdinandusse S, Wanders RJ
  Title
Human disorders of peroxisome metabolism and biogenesis.
  Journal
Biochim Biophys Acta 1863:922-33 (2016)
DOI:10.1016/j.bbamcr.2015.11.015
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