KEGG    Network variation - Molybdenum cofactor biosynthesis
[ Network menu | Network entry | Help ]
ENTRYnt06025
NameMolybdenum cofactor biosynthesis
CategoryPathway view; Cofactor/vitamin metabolism
Pathwayhsa00790 Folate biosynthesis
hsa00230 Purine metabolism
Modulehsa_M00880 Molybdenum cofactor biosynthesis, GTP => molybdenum cofactor
DiseaseH00192 Xanthinuria
H02311 Molybdenum cofactor deficiency
Display drug-target relation   disease type
N00888    HypoxanthineXDHUrate
    Xanthinuria, type I   XDH*
N00890    GTPMOCS1cPMPMOCS2GPHNMocoMOCOSMoco(sulfide)
   D1
 |
    MOCODA   MOCS1*
    MOCODB       MOCS2*
    MOCODC         GPHN*
    Xanthinuria, type II             MOCOS*

Disease nameDisease category
Xanthinuria, type IH00192XanthinuriaInherited metabolic disorder
MOCODAH02311Molybdenum cofactor deficiencyInherited metabolic disorder
MOCODBH02311Molybdenum cofactor deficiencyInherited metabolic disorder
MOCODCH02311Molybdenum cofactor deficiencyInherited metabolic disorder
Xanthinuria, type IIH00192XanthinuriaInherited metabolic disorder


Drug name
D1D11780Fosdenopterin hydrobromide (USAN)