ORTHOLOGY: K19401
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Entry
K19401 KO
Symbol
BBS10
Name
Bardet-Biedl syndrome 10 protein
Disease
H00418
Bardet-Biedl syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09183 Protein families: signaling and cellular processes
03037 Cilium and associated proteins
K19401 BBS10; Bardet-Biedl syndrome 10 protein
Cilium and associated proteins [BR:
ko03037
]
Primary cilia and associated proteins
BBS-CCT complex
K19401 BBS10; Bardet-Biedl syndrome 10 protein
BRITE hierarchy
Genes
HSA:
79738
(BBS10)
PTR:
452084
(BBS10)
PPS:
100968695
(BBS10)
GGO:
101128419
(BBS10)
PON:
100173034
(BBS10)
PPYG:
129009795
(BBS10)
NLE:
100594778
(BBS10)
HMH:
116479034
(BBS10)
SSYN:
129460924
(BBS10)
MCC:
693270
(BBS10)
MCF:
102140638
(BBS10)
MTHB:
126930932
MNI:
105473330
(BBS10)
CSAB:
103238757
(BBS10)
CATY:
105581058
(BBS10)
PANU:
101012880
(BBS10)
TGE:
112634211
(BBS10)
MLEU:
105540684
(BBS10)
RRO:
104661834
(BBS10)
RBB:
108529954
(BBS10)
TFN:
117089709
(BBS10)
PTEH:
111546039
(BBS10)
CANG:
105502720
(BBS10)
CJC:
100409524
(BBS10)
SBQ:
101038442
(BBS10)
CIMI:
108305856
(BBS10)
ANAN:
105709524
(BBS10)
CSYR:
103262164
(BBS10)
MMUR:
105863377
(BBS10)
LCAT:
123639497
(BBS10)
PCOQ:
105813602
(BBS10)
OGA:
100959600
(BBS10)
MMU:
71769
(Bbs10)
MCAL:
110303567
(Bbs10)
MPAH:
110326995
(Bbs10)
RNO:
500832
(Bbs10)
MCOC:
116076254
(Bbs10)
ANU:
117696167
(Bbs10)
ASYL:
127670430
(Bbs10)
127670431
127670432
MUN:
110564831
(Bbs10)
CGE:
100763026
(Bbs10)
MAUA:
101841696
(Bbs10)
PROB:
127237978
(Bbs10)
PLEU:
114695646
(Bbs10)
MORG:
121461491
(Bbs10)
MFOT:
126497439
AAMP:
119803525
(Bbs10)
NGI:
103749105
(Bbs10)
HGL:
101708171
(Bbs10)
CPOC:
100714699
(Bbs10)
CCAN:
109691155
(Bbs10)
DORD:
105990651
(Bbs10)
DSP:
122124365
(Bbs10)
PLOP:
125361044
(Bbs10)
NCAR:
124983092
MMMA:
107140040
(Bbs10)
ITI:
101973738
(Bbs10)
OCU:
100347226
OPI:
101527636
(BBS10)
TUP:
102467685
(BBS10)
GVR:
103594235
(BBS10)
CFA:
100688777
CLUD:
112654485
(BBS10)
VVP:
112914868
(BBS10)
VLG:
121481603
(BBS10)
NPO:
129520900
(BBS10)
AML:
100484188
(BBS10)
UMR:
103656906
(BBS10)
UAH:
130541800
(BBS10)
UAR:
123801217
(BBS10)
ELK:
111142143
LLV:
125107595
MPUF:
101692515
(BBS10)
MNP:
132019402
(BBS10)
MLK:
131839194
(BBS10)
NVS:
122891203
(BBS10)
ORO:
101386596
(BBS10)
EJU:
114210961
(BBS10)
ZCA:
113921379
(BBS10)
MLX:
118008543
(BBS10)
NSU:
110570526
(BBS10)
LWW:
102733979
(BBS10)
FCA:
101083862
(BBS10)
PYU:
121040060
(BBS10)
PCOO:
112863288
(BBS10)
PBG:
122473664
(BBS10)
PVIV:
125171234
(BBS10)
LRUF:
124502510
LGF:
123591877
(BBS10)
AJU:
106967393
PTG:
102955146
(BBS10)
PPAD:
109270538
(BBS10)
PUC:
125920294
PLEZ:
122224848
(BBS10)
HHV:
120243694
(BBS10)
BTA:
538638
(BBS10)
BOM:
102267327
(BBS10)
BIU:
109558882
(BBS10)
BBUB:
102401987
(BBS10)
BBIS:
104984216
(BBS10)
CHX:
102181188
(BBS10)
OAS:
101122679
(BBS10)
BTAX:
128048579
(BBS10)
CSUM:
138079341
(BBS10)
ODA:
120857945
(BBS10)
CCAD:
122427645
(BBS10)
MREE:
136167005
(BBS10)
OVR:
139029597
(BBS10)
MBEZ:
129536778
(BBS10)
SSC:
100737698
(BBS10)
CFR:
102510488
(BBS10)
CBAI:
105072034
(BBS10)
CDK:
105095982
(BBS10)
VPC:
102537095
(BBS10)
BACU:
103002631
(BBS10)
BMUS:
118901561
(BBS10)
LVE:
103083641
(BBS10)
OOR:
101276435
(BBS10)
LALB:
132528825
(BBS10)
DLE:
111167257
(BBS10)
PCAD:
102990166
(BBS10)
PSIU:
116761279
(BBS10)
NASI:
112393968
(BBS10)
ECB:
100058970
(BBS10)
EPZ:
103551988
(BBS10)
EAI:
106831453
(BBS10)
MYB:
102246730
(BBS10)
MYD:
102773424
(BBS10)
MMYO:
118651844
(BBS10)
MLF:
102425923
(BBS10)
MDT:
132227960
(BBS10)
MYUM:
139005359
(BBS10)
PKL:
118729225
(BBS10)
EFUS:
103288097
(BBS10)
MNA:
107526869
(BBS10)
DRO:
112322165
(BBS10)
SHON:
118989326
(BBS10)
AJM:
119038503
(BBS10)
PDIC:
114489853
(BBS10)
PHAS:
123812861
(BBS10)
MMF:
118624072
(BBS10)
PPAM:
129076067
(BBS10)
HAI:
109388496
(BBS10)
RFQ:
117028236
(BBS10)
PALE:
102895709
(BBS10)
PGIG:
120583361
(BBS10)
PVP:
105301751
(BBS10)
RAY:
107507164
(BBS10)
MJV:
108403243
(BBS10)
TOD:
119247486
(BBS10)
SARA:
101547834
(BBS10)
SFUM:
130026457
(BBS10)
SETR:
126022470
(BBS10)
LAV:
100674020
(BBS10)
TMU:
101344660
ETF:
101649154
(BBS10)
DNM:
101436819
(BBS10)
MDO:
100018323
(BBS10)
GAS:
123249470
(BBS10)
SHR:
100923708
(BBS10)
AFZ:
127564633
PCW:
110195933
(BBS10)
TVP:
118849790
(BBS10)
PBRV:
138166387
(BBS10)
OAA:
114816384
(BBS10)
TACU:
119936596
(BBS10)
GGA:
417865
(BBS10)
PCOC:
116226737
(BBS10)
MGP:
104910233
(BBS10)
CJO:
107310854
(BBS10)
TPAI:
128073428
(BBS10)
LMUT:
125694670
(BBS10)
NMEL:
110392851
(BBS10)
APLA:
101790161
(BBS10)
ACYG:
106045336
(BBS10)
CATA:
118246684
(BBS10)
AFUL:
116501905
(BBS10)
TGU:
100221822
(BBS10)
LSR:
110469437
(BBS10)
SCAN:
108961593
(BBS10)
PMOA:
120499751
(BBS10)
OTC:
121339442
(BBS10)
PRUF:
121352581
(BBS10)
ATRC:
139588262
(BBS10)
GFR:
102035330
(BBS10)
FAB:
101819800
(BBS10)
OMA:
130262630
(BBS10)
PHI:
102102991
(BBS10)
PMAJ:
107204178
(BBS10)
CCAE:
111937622
(BBS10)
CCW:
104698477
(BBS10)
CBRC:
103614905
(BBS10)
ACOE:
138101547
(BBS10)
ETL:
114058929
(BBS10)
ZAB:
102064447
(BBS10)
ZLE:
135442306
(BBS10)
ACHL:
103810488
(BBS10)
SVG:
106862752
(BBS10)
MMEA:
130580507
(BBS10)
HRT:
120752076
(BBS10)
SATI:
136361353
(BBS10)
CCIC:
134043777
(BBS10)
FPG:
101917229
(BBS10)
FCH:
102054403
(BBS10)
CCRI:
104156665
(BBS10)
NNT:
104405785
(BBS10)
SHAB:
115605651
(BBS10)
ACUN:
113489340
(BBS10)
TALA:
104358354
(BBS10)
ACHC:
115336213
(BBS10)
HALD:
104319883
(BBS10)
HLE:
104828331
(BBS10)
AGEN:
126034380
HHAR:
128135398
(BBS10)
GCL:
127020154
CSTI:
104551734
(BBS10)
LDI:
104344940
(BBS10)
MNB:
103777090
(BBS10)
DPUB:
104299988
(BBS10)
PPUS:
135187490
(BBS10)
AVIT:
104281384
(BBS10)
BRHI:
104488872
(BBS10)
EGZ:
104132964
(BBS10)
NNI:
104011032
(BBS10)
PCRI:
104034267
(BBS10)
PCAO:
104053279
(BBS10)
PADL:
103920027
(BBS10)
AFOR:
103898639
(BBS10)
FGA:
104083851
(BBS10)
GSTE:
104263424
(BBS10)
CBOY:
140652755
(BBS10)
CLV:
102093094
(BBS10)
MUI:
104536432
(BBS10)
PGUU:
104466984
(BBS10)
PLET:
104617668
(BBS10)
EHS:
104517217
(BBS10)
CMAC:
104478086
(BBS10)
CUCA:
104061143
(BBS10)
TEO:
104382967
(BBS10)
BREG:
104630698
(BBS10)
OHA:
104326790
(BBS10)
ACAR:
104532468
(BBS10)
CPEA:
104393562
(BBS10)
CVF:
104292099
(BBS10)
RTD:
128904099
(BBS10)
CRID:
134510072
(BBS10)
AAM:
106488164
(BBS10)
AROW:
112970177
(BBS10)
NPD:
112946652
(BBS10)
DNE:
112983305
(BBS10)
SCAM:
104140700
(BBS10)
ASN:
102376638
(BBS10)
AMJ:
102564517
(BBS10)
CPOO:
109315475
(BBS10)
GGN:
109295745
(BBS10)
PSS:
102462354
(BBS10)
CMY:
102937557
(BBS10)
CCAY:
125630156
(BBS10)
DCC:
119859130
(BBS10)
CPIC:
101939885
(BBS10)
TST:
117878016
(BBS10)
CABI:
116826767
(BBS10)
MRV:
120395702
120395987
ACS:
100559127
(bbs10)
ASAO:
132775106
132775107
PVT:
110080533
(BBS10)
SUND:
121929843
(BBS10)
PBI:
103062936
(BBS10)
PMUR:
107295854
(BBS10)
CTIG:
120315464
(BBS10)
TSR:
106538279
(BBS10)
PGUT:
117668407
(BBS10)
APRI:
131195129
(BBS10)
PTEX:
113438308
(BBS10)
NSS:
113419629
(BBS10)
VKO:
123033702
(BBS10)
PMUA:
114600259
114600260
PRAF:
128417085
(BBS10)
ZVI:
118089922
(BBS10)
HCG:
128323104
(BBS10)
GJA:
107118938
(BBS10)
STOW:
125439012
(BBS10)
EMC:
129333577
(BBS10)
XLA:
734282
(bbs10.L)
XTR:
100145168
(bbs10)
NPR:
108800666
(BBS10)
RTEM:
120931953
(BBS10)
BBUF:
120980812
(BBS10)
BGAR:
122925775
(BBS10)
PWL:
138288207
(BBS10)
MUO:
115477386
(BBS10)
GSH:
117363271
(BBS10)
DRE:
100034535
(bbs10)
SRX:
107733261
107736428
SANH:
107662861
SGH:
107601001
CCAR:
109108881
CAUA:
113079279
113100331
CGIB:
127933919
PTET:
122322965
(bbs10)
LROH:
127181242
(bbs10)
OMC:
131524654
(bbs10)
PPRM:
120464786
(bbs10)
RKG:
130071292
(bbs10)
MAMB:
125254633
(bbs10)
CIDE:
127500145
CERY:
137022738
(bbs10)
MASI:
127416729
TROS:
130562824
(bbs10)
TDW:
130435285
(bbs10)
MANU:
129419533
(bbs10)
PDAB:
135773800
(bbs10)
IPU:
108264161
IFU:
128606361
(bbs10)
PHYP:
113526674
(bbs10)
SMEO:
124395974
(bbs10)
TFD:
113649669
(bbs10)
TVC:
132851764
(bbs10)
CGAR:
128528123
(bbs10)
NGRA:
132887661
(bbs10)
TRN:
134323094
(bbs10)
AMEX:
103030963
(bbs10)
CMAO:
118818321
(bbs10)
EEE:
113580503
(bbs10)
CHAR:
105892376
(bbs10)
SPIL:
134093550
(bbs10)
TRU:
101065662
(bbs10)
TFS:
130536595
(bbs10)
TNG:
GSTEN00035588G001
LCO:
109141848
(bbs10)
NCC:
104957241
(bbs10)
TBEN:
117491828
(bbs10)
CGOB:
115009311
(bbs10)
PGEO:
117448074
(bbs10)
GACU:
117557707
(bbs10)
EMAC:
134882055
(bbs10)
ELY:
117262085
(bbs10)
EFO:
125887453
(bbs10)
PLEP:
121949664
(bbs10)
SLUC:
116045625
(bbs10)
ECRA:
117948870
(bbs10)
ESP:
116694017
(bbs10)
PFLV:
114560478
(bbs10)
GAT:
120809007
(bbs10)
PPUG:
119195445
(bbs10)
AFB:
129108829
(bbs10)
CLUM:
117732696
(bbs10)
PSWI:
130195417
(bbs10)
CANA:
137803598
(bbs10)
CVE:
137881496
(bbs10)
MSAM:
119893268
(bbs10)
SCHU:
122875485
(bbs10)
CUD:
121515693
(bbs10)
SPUL:
138613416
(bbs10)
LMIX:
132972437
(bbs10)
ASTR:
137593921
(bbs10)
MZE:
101482324
(bbs10)
ONL:
102083141
(bbs10)
OAU:
116313526
(bbs10)
OLA:
101162598
(bbs10)
OML:
112151692
(bbs10)
CSAI:
133444277
(bbs10)
XMA:
102222095
(bbs10)
XCO:
114135175
(bbs10)
PRET:
103466663
(bbs10)
PFOR:
103133802
(bbs10)
PLAI:
106956227
(bbs10)
PMEI:
106915460
(bbs10)
GAF:
122835509
(bbs10)
PPRL:
129361591
(bbs10)
CVG:
107102391
(bbs10)
CTUL:
119772372
(bbs10)
GMU:
124883066
(bbs10)
NFU:
107388833
(bbs10)
KMR:
108230116
(bbs10)
ALIM:
106514307
(bbs10)
NWH:
119415710
(bbs10)
EJA:
138206124
(bbs10)
BFRE:
138628205
(bbs10)
MCEP:
125015151
(bbs10)
CSEM:
103380061
(bbs10)
POV:
109624330
(bbs10)
SSEN:
122775882
(bbs10)
SSOE:
131470405
(bbs10)
HHIP:
117763315
(bbs10)
HSP:
118109684
(bbs10)
PPLT:
128444358
(bbs10)
SMAU:
118315607
(bbs10)
LCF:
108875157
SDU:
111228526
(bbs10)
SLAL:
111653368
(bbs10)
XGL:
120793074
(bbs10)
HCQ:
109528084
(bbs10)
SSCV:
125971076
(bbs10)
SBIA:
133502769
(bbs10)
PEE:
133403343
(bbs10)
PTAO:
133478300
(bbs10)
BPEC:
110169186
(bbs10)
ENY:
140348634
(bbs10)
MALB:
109967646
(bbs10)
BSPL:
114857804
(bbs10)
SJO:
128359015
(bbs10)
SSCO:
133982189
(bbs10)
GMH:
115550382
(bbs10)
SASA:
106576085
(bbs10)
STRU:
115180048
(bbs10)
OTW:
112217164
(bbs10)
OGO:
123995504
(bbs10)
ONE:
115106102
(bbs10)
OKE:
118365941
(bbs10)
OMM:
135514803
(bbs10)
OCLA:
139393022
SALP:
111950358
111951255
SNH:
120032023
(bbs10)
CCLU:
121543664
123482247
ELS:
105025670
(bbs10)
OEP:
134021153
(bbs10)
SFM:
108942232
(bbs10)
PKI:
111843385
(bbs10)
AANG:
118218914
118218915
118218917
118218923
118218926
118218927
118218928
118218929
118219196
118219202
118219208
AROT:
135245724
135246020
135246027
CCOG:
133113917
(bbs10)
LOC:
102696386
(bbs10)
PSPA:
121319045
121320276
ARUT:
117419611
(bbs10)
PSEX:
120534360
(bbs10)
LCM:
102349965
(BBS10)
CPLA:
122547886
(bbs10)
LERI:
129693693
(bbs10)
PMRN:
116956056
(BBS10)
LRJ:
133357912
(BBS10)
BFO:
118418468
SPU:
115917934
LPIC:
129271887
129276776
AJJ:
139965784
APLC:
110981319
ARUN:
117289458
AAMU:
139934660
AFIL:
140136355
AJC:
117123493
SKO:
100377996
PFLL:
139117578
ZNE:
110830015
IEL:
124163271
PJA:
122249299
122253205
PCHN:
125043609
PMOO:
119575702
PCLA:
123746831
CQD:
128699207
PTRU:
123520759
ESN:
126981727
MNZ:
135213620
MRJ:
136825518
PORN:
139764785
HAZT:
125179260
CSCU:
111618979
CVS:
136990284
SDM:
118199716
LGI:
LOTGIDRAFT_169741
PVUL:
126816132
PCAN:
112577420
GAE:
121388934
HRF:
124113032
HRJ:
124260377
HASI:
137258197
HCRA:
139448501
CRG:
105341621
CANU:
128188701
CVN:
111136494
OED:
125663988
MYI:
110443422
PMAX:
117338193
AIRR:
138315188
MCAF:
127701295
MMER:
123549720
RPHI:
132743101
DPOL:
127843810
MAEA:
128202958
OBI:
106874925
OSN:
115222979
LJP:
135465671
LAK:
106160450
106169740
LLON:
135482486
NVE:
5518059
EPA:
110236676
ATEN:
116305574
ADF:
107335887
AMIL:
114955455
122958826
MCAZ:
138022432
MFOO:
137994386
PDAM:
113673946
SPIS:
111329577
DGT:
114517103
XEN:
124436520
HMG:
105844356
HSY:
130656851
RES:
135690500
» show all
Taxonomy
UniProt
Reference
PMID:
19190184
Authors
Marion V, Stoetzel C, Schlicht D, Messaddeq N, Koch M, Flori E, Danse JM, Mandel JL, Dollfus H
Title
Transient ciliogenesis involving Bardet-Biedl syndrome proteins is a fundamental characteristic of adipogenic differentiation.
Journal
Proc Natl Acad Sci U S A 106:1820-5 (2009)
DOI:
10.1073/pnas.0812518106
Sequence
[hsa:
79738
]
Reference
PMID:
20080638
Authors
Seo S, Baye LM, Schulz NP, Beck JS, Zhang Q, Slusarski DC, Sheffield VC
Title
BBS6, BBS10, and BBS12 form a complex with CCT/TRiC family chaperonins and mediate BBSome assembly.
Journal
Proc Natl Acad Sci U S A 107:1488-93 (2010)
DOI:
10.1073/pnas.0910268107
Sequence
[hsa:
79738
]
LinkDB
All DBs
DBGET
integrated database retrieval system