 | | NETWORK: N00856 | |
| Entry |
|
| Name |
|
| Definition |
2-MB-CoA -- (ACADS,ACADSB,ACADM) >> (ECHS1,HADHA) >> (HSD17B10,HADH) >> (ACAA1/2,HADHB) -> Propanoyl-CoA |
| Expanded |
C15980 -- (35,36,34) >> (1892,3030) >> (3028,3033) >> (30,10449,3032) -> C00100 |
| Class |
nt06024 Valine, leucine and isoleucine degradation
|
| Type |
Reference
|
| Pathway |
| hsa00280 | Valine, leucine and isoleucine degradation |
|
| Gene |
| 35 | ACADS; acyl-CoA dehydrogenase short chain |
| 36 | ACADSB; acyl-CoA dehydrogenase short/branched chain |
| 34 | ACADM; acyl-CoA dehydrogenase medium chain |
| 1892 | ECHS1; enoyl-CoA hydratase, short chain 1 |
| 3030 | HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha |
| 3028 | HSD17B10; hydroxysteroid 17-beta dehydrogenase 10 |
| 3033 | HADH; hydroxyacyl-CoA dehydrogenase |
| 30 | ACAA1; acetyl-CoA acyltransferase 1 |
| 10449 | ACAA2; acetyl-CoA acyltransferase 2 |
| 3032 | HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta |
|
| Metabolite |
| C15980 | (S)-2-Methylbutanoyl-CoA |
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| LinkDB |
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