ORTHOLOGY: K05626
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Entry
K05626 KO
Symbol
DRPLA
Name
atrophin-1 (dentatorubral-pallidoluysian atrophy protein)
Disease
H00060
Dentatorubropallidoluysian atrophy (DRPLA)
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09190 Not Included in Pathway or Brite
09193 Unclassified: signaling and cellular processes
99995 Signaling proteins
K05626 DRPLA; atrophin-1 (dentatorubral-pallidoluysian atrophy protein)
BRITE hierarchy
Genes
HSA:
1822
(ATN1)
PTR:
451803
(ATN1)
PPS:
100994844
(ATN1)
GGO:
109029059
(ATN1)
PON:
100448818
(ATN1)
NLE:
100599977
(ATN1)
HMH:
116472604
(ATN1)
MCC:
722114
(ATN1)
MCF:
102132888
(ATN1)
MTHB:
126930428
MNI:
105484213
(ATN1)
CSAB:
103218489
(ATN1)
CATY:
105583044
(ATN1)
PANU:
101000537
(ATN1)
TGE:
112635579
(ATN1)
MLEU:
105541819
(ATN1)
RRO:
104680087
(ATN1)
RBB:
108542022
(ATN1)
TFN:
117090603
(ATN1)
PTEH:
111555914
(ATN1)
CANG:
105519107
(ATN1)
CJC:
100409521
(ATN1)
SBQ:
101033589
(ATN1)
CIMI:
108294987
(ATN1)
MMUR:
105868992
(ATN1)
LCAT:
123640093
(ATN1)
PCOQ:
105805038
(ATN1)
OGA:
100948851
(ATN1)
MMU:
13498
(Atn1)
MCAL:
110296416
(Atn1)
MPAH:
110316180
(Atn1)
RNO:
29515
(Atn1)
MCOC:
116099570
(Atn1)
ANU:
117714767
(Atn1)
MUN:
110548580
(Atn1)
CGE:
100767627
(Atn1)
MAUA:
101844714
(Atn1)
PROB:
127213038
(Atn1)
PLEU:
114708784
(Atn1)
MORG:
121434794
(Atn1)
MFOT:
126514834
AAMP:
119807646
(Atn1)
NGI:
103727494
(Atn1)
HGL:
101723354
(Atn1)
CPOC:
100733654
(Atn1)
CCAN:
109682812
(Atn1)
DSP:
122101948
(Atn1)
NCAR:
124983059
MMMA:
107154933
(Atn1)
OCU:
100349239
OPI:
101517352
(ATN1)
TUP:
102488708
(ATN1)
GVR:
103586400
(ATN1)
CFA:
611607
(ATN1)
CLUD:
112675366
(ATN1)
VVP:
112917326
(ATN1)
VLG:
121479997
(ATN1)
NPO:
129503478
(ATN1)
AML:
100474046
(ATN1)
UMR:
103656222
(ATN1)
UAH:
113257949
(ATN1)
UAR:
123781555
(ATN1)
ELK:
111159799
LLV:
125106085
MPUF:
101678310
(ATN1)
MNP:
132019903
(ATN1)
MLK:
131838461
(ATN1)
NVS:
122892660
(ATN1)
ORO:
101374271
(ATN1)
EJU:
114222535
(ATN1)
ZCA:
113921840
(ATN1)
MLX:
118025719
(ATN1)
NSU:
110581056
(ATN1)
LWW:
102735092
(ATN1)
FCA:
101093617
(ATN1)
PYU:
121021912
(ATN1)
PBG:
122472387
(ATN1)
PVIV:
125170379
(ATN1)
LRUF:
124501430
PTG:
102955053
(ATN1)
PPAD:
109276097
(ATN1)
PUC:
125918212
125918218
AJU:
106965439
HHV:
120220430
(ATN1)
BTA:
513125
(ATN1)
BOM:
102288144
(ATN1)
BIU:
109558912
(ATN1)
BBUB:
102389691
(ATN1)
BBIS:
104992332
(ATN1)
CHX:
102187302
(ATN1)
OAS:
101108302
(ATN1)
BTAX:
128047423
(ATN1)
ODA:
120858744
(ATN1)
CCAD:
122423268
(ATN1)
MBEZ:
129536437
(ATN1)
SSC:
100153709
(ATN1)
CFR:
102515605
(ATN1)
CBAI:
105071205
(ATN1)
CDK:
105098195
(ATN1)
VPC:
102532627
(ATN1)
BACU:
103006159
(ATN1)
BMUS:
118901758
(ATN1)
LVE:
103087983
(ATN1)
OOR:
101288757
(ATN1)
DLE:
111176701
(ATN1)
PCAD:
102985049
(ATN1)
PSIU:
116760534
(ATN1)
NASI:
112391699
(ATN1)
ECB:
100060226
(ATN1)
EPZ:
103547025
(ATN1)
EAI:
106847313
(ATN1)
MYB:
102257828
(ATN1)
MYD:
102754400
(ATN1)
MMYO:
118649838
(ATN1)
PKL:
118720253
118730174
(ATN1)
EFUS:
103289034
(ATN1)
MNA:
107544061
(ATN1)
DRO:
112321721
(ATN1)
SHON:
119002401
(ATN1)
AJM:
119065686
(ATN1)
PDIC:
114513334
(ATN1)
PHAS:
123810563
(ATN1)
MMF:
118624349
(ATN1)
PPAM:
129085051
(ATN1)
129085058
HAI:
109373663
(ATN1)
RFQ:
117028001
(ATN1)
PALE:
102895411
(ATN1)
PGIG:
120611672
(ATN1)
PVP:
105295944
(ATN1)
RAY:
107519827
(ATN1)
MJV:
108384834
(ATN1)
TOD:
119247765
(ATN1)
SARA:
101546293
(ATN1)
SETR:
126006510
(ATN1)
LAV:
100676703
(ATN1)
TMU:
101357414
ETF:
101639976
(ATN1)
DNM:
101440463
(ATN1)
MDO:
100033075
(ATN1)
GAS:
123248544
(ATN1)
AFZ:
127539229
PCW:
110213781
(ATN1)
OAA:
103169606
(ATN1)
GGA:
427946
(ATN1)
PCOC:
116239991
(ATN1)
MGP:
100548938
104913104
CJO:
107318623
(ATN1)
TPAI:
128089877
(ATN1)
LMUT:
125685186
(ATN1)
NMEL:
110398296
(ATN1)
APLA:
101795518
(ATN1)
ACYG:
106047825
(ATN1)
CATA:
118247631
(ATN1)
AFUL:
116498796
(ATN1)
TGU:
100229755
(ATN1)
LSR:
110480839
(ATN1)
SCAN:
103812465
(ATN1)
PMOA:
120506453
(ATN1)
OTC:
121339340
(ATN1)
PRUF:
121351689
(ATN1)
GFR:
102040712
(ATN1)
FAB:
101813001
(ATN1)
OMA:
130253991
(ATN1)
PHI:
102110702
(ATN1)
PMAJ:
107211589
(ATN1)
CCAE:
111945169
(ATN1)
CCW:
104687226
(ATN1)
CBRC:
103614066
(ATN1)
ETL:
114058139
(ATN1)
ZAB:
102063014
(ATN1)
SVG:
106857892
(ATN1)
MMEA:
130574781
(ATN1)
HRT:
120749107
(ATN1)
FPG:
101914391
(ATN1)
FCH:
102055471
(ATN1)
CLV:
102085150
(ATN1)
EGZ:
104126603
(ATN1)
NNI:
104009743
(ATN1)
ACUN:
113479393
(ATN1)
TALA:
116962317
(ATN1)
PADL:
103921920
(ATN1)
AFOR:
103905504
(ATN1)
ACHC:
115343910
(ATN1)
HLE:
104831777
(ATN1)
AGEN:
126049041
GCL:
127021638
SHAB:
115601656
(ATN1)
DPUB:
104299506
(ATN1)
CPEA:
104389853
(ATN1)
RTD:
128904216
(ATN1)
CUCA:
104064396
(ATN1)
AAM:
106497248
(ATN1)
AROW:
112973022
(ATN1)
NPD:
112960146
(ATN1)
TGT:
104565676
(ATN1)
DNE:
112991065
(ATN1)
SCAM:
104150752
(ATN1)
ASN:
102375019
(ATN1)
AMJ:
102569960
(ATN1)
CPOO:
109319379
(ATN1)
GGN:
109304427
(ATN1)
PSS:
102450875
(ATN1)
CMY:
102932251
(ATN1)
CCAY:
125622620
(ATN1)
DCC:
119849859
(ATN1)
CPIC:
101940262
(ATN1)
TST:
117885672
(ATN1)
CABI:
116821046
(ATN1)
MRV:
120372519
(ATN1)
ACS:
100567809
(atn1)
ASAO:
132767529
(ATN1)
PVT:
110084629
(ATN1)
SUND:
121922414
(ATN1)
PBI:
103067127
(ATN1)
PMUR:
107285776
(ATN1)
CTIG:
120306106
(ATN1)
TSR:
106552514
(ATN1)
PGUT:
117661825
(ATN1)
APRI:
131190847
(ATN1)
PTEX:
113444559
(ATN1)
NSS:
113424527
(ATN1)
VKO:
123033216
(ATN1)
PMUA:
114587354
(ATN1)
PRAF:
128405252
(ATN1)
ZVI:
118097465
(ATN1)
HCG:
128342811
(ATN1)
GJA:
107116795
(ATN1)
STOW:
125436160
(ATN1)
EMC:
129345324
(ATN1)
XLA:
108696045
(atn1.L)
108697336
(atn1.S)
XTR:
100486351
(atn1)
NPR:
108784408
(ATN1)
RTEM:
120946622
(ATN1)
BBUF:
121004037
(ATN1)
BGAR:
122941598
(ATN1)
MUO:
115456949
(ATN1)
GSH:
117350141
(ATN1)
LCM:
102351834
(ATN1)
DPX:
DAPPUDRAFT_308596
» show all
Taxonomy
UniProt
Reference
PMID:
10085113
Authors
Ellerby LM, Andrusiak RL, Wellington CL, Hackam AS, Propp SS, Wood JD, Sharp AH, Margolis RL, Ross CA, Salvesen GS, Hayden MR, Bredesen DE
Title
Cleavage of atrophin-1 at caspase site aspartic acid 109 modulates cytotoxicity.
Journal
J Biol Chem 274:8730-6 (1999)
DOI:
10.1074/jbc.274.13.8730
Sequence
[hsa:
1822
]
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