KEGG   PATHWAY: xma00250
Entry
xma00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Xiphophorus maculatus (southern platyfish)
Class
Metabolism; Amino acid metabolism
Pathway map
xma00250  Alanine, aspartate and glutamate metabolism
xma00250

Module
xma_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:xma00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Xiphophorus maculatus (southern platyfish) [GN:xma]
Gene
102216447  [KO:K00814] [EC:2.6.1.2]
102216968  asl; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
102217588  agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
102217687  [KO:K01915] [EC:6.3.1.2]
102217885  glud1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
102218509  [KO:K03334] [EC:1.4.3.2]
102218635  [KO:K18310] [EC:6.3.1.17 6.3.2.41]
102218672  [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
102220855  [KO:K00814] [EC:2.6.1.2]
102221709  [KO:K01915] [EC:6.3.1.2]
102221824  [KO:K01425] [EC:3.5.1.2]
102222033  abat; 4-aminobutyrate aminotransferase, mitochondrial isoform X1 [KO:K13524] [EC:2.6.1.19 2.6.1.22]
102222509  [KO:K01425] [EC:3.5.1.2]
102222791  gad2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
102223675  [KO:K01425] [EC:3.5.1.2]
102224357  adsl; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
102224683  cad; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
102225213  [KO:K01425] [EC:3.5.1.2]
102225475  [KO:K13051] [EC:3.5.1.1 3.4.19.5]
102225683  aldh5a1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
102225872  ddo; D-aspartate oxidase [KO:K00272] [EC:1.4.3.1]
102226170  gpt; alanine aminotransferase 1 [KO:K00814] [EC:2.6.1.2]
102226227  gad1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
102226323  [KO:K01939] [EC:6.3.4.4]
102227198  agxt; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
102227603  [KO:K00814] [EC:2.6.1.2]
102227815  [KO:K03334] [EC:1.4.3.2]
102228075  [KO:K03334] [EC:1.4.3.2]
102228200  got1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
102228336  got2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
102228360  aspa; aspartoacylase [KO:K01437] [EC:3.5.1.15]
102229547  [KO:K00814] [EC:2.6.1.2]
102230331  [KO:K00814] [EC:2.6.1.2]
102230667  nat8l; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
102231045  [KO:K14454] [EC:2.6.1.1]
102231329  [KO:K00820] [EC:2.6.1.16]
102232024  cps1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
102232819  nit2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
102233507  [KO:K01580] [EC:4.1.1.15]
102233597  asns; asparagine synthetase [glutamine-hydrolyzing] isoform X1 [KO:K01953] [EC:6.3.5.4]
102233922  ass1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
102234057  ppat; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
102234110  [KO:K01939] [EC:6.3.4.4]
102234399  [KO:K01915] [EC:6.3.1.2]
102235867  [KO:K00261] [EC:1.4.1.3]
102236833  [KO:K01939] [EC:6.3.4.4]
102236958  aldh4a1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X1 [KO:K00294] [EC:1.2.1.88]
102236979  [KO:K00820] [EC:2.6.1.16]
102237752  [KO:K13051] [EC:3.5.1.1 3.4.19.5]
106700049  [KO:K03334] [EC:1.4.3.2]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
xma00010  Glycolysis / Gluconeogenesis
xma00020  Citrate cycle (TCA cycle)
xma00220  Arginine biosynthesis
xma00230  Purine metabolism
xma00240  Pyrimidine metabolism
xma00260  Glycine, serine and threonine metabolism
xma00330  Arginine and proline metabolism
xma00340  Histidine metabolism
xma00410  beta-Alanine metabolism
xma00470  D-Amino acid metabolism
xma00480  Glutathione metabolism
xma00520  Amino sugar and nucleotide sugar metabolism
xma00620  Pyruvate metabolism
xma00630  Glyoxylate and dicarboxylate metabolism
xma00650  Butanoate metabolism
xma00760  Nicotinate and nicotinamide metabolism
xma00770  Pantothenate and CoA biosynthesis
xma00860  Porphyrin metabolism
xma00910  Nitrogen metabolism
KO pathway
ko00250   

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