ORTHOLOGY: K17659
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Entry
K17659 KO
Symbol
PTCD3
Name
pentatricopeptide repeat domain-containing protein 3
Disease
H00891
Combined oxidative phosphorylation deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial DNA transcription, translation, and replication factors
Mitochondrial transcription and translation factors
Other mitochondrial DNA transcription and translation factors
K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
BRITE hierarchy
Other DBs
GO:
0043024
Genes
HSA:
55037
(PTCD3)
PTR:
459374
(PTCD3)
PPS:
100973290
(PTCD3)
GGO:
101128771
(PTCD3)
PON:
100172990
(PTCD3)
NLE:
100582730
(PTCD3)
HMH:
116483959
(PTCD3)
MCC:
697081
(PTCD3)
MCF:
101865090
(PTCD3)
MTHB:
126933398
MNI:
105465398
(PTCD3)
CSAB:
103219927
(PTCD3)
CATY:
105587666
(PTCD3)
PANU:
101026374
(PTCD3)
TGE:
112604926
(PTCD3)
MLEU:
105532827
(PTCD3)
RRO:
104677063
(PTCD3)
RBB:
108518116
(PTCD3)
TFN:
117062151
(PTCD3)
PTEH:
111551108
(PTCD3)
CANG:
105527750
(PTCD3)
CJC:
100408328
(PTCD3)
SBQ:
101033248
(PTCD3)
CIMI:
108309997
(PTCD3)
CSYR:
103270049
(PTCD3)
MMUR:
105876611
(PTCD3)
LCAT:
123637138
(PTCD3)
PCOQ:
105810290
(PTCD3)
OGA:
100950863
(PTCD3)
MMU:
69956
(Ptcd3)
MCAL:
110296003
(Ptcd3)
MPAH:
110316412
(Ptcd3)
RNO:
500199
(Ptcd3)
MCOC:
116099067
(Ptcd3)
ANU:
117714923
(Ptcd3)
MUN:
110564153
(Ptcd3)
CGE:
100763681
(Ptcd3)
MAUA:
101844832
(Ptcd3)
PROB:
127235528
(Ptcd3)
PLEU:
114685873
(Ptcd3)
MORG:
121439352
(Ptcd3)
MFOT:
126491038
AAMP:
119807578
(Ptcd3)
NGI:
103737059
(Ptcd3)
HGL:
101697820
(Ptcd3)
CPOC:
100728326
(Ptcd3)
CCAN:
109696131
(Ptcd3)
DORD:
106000214
(Ptcd3)
DSP:
122116890
(Ptcd3)
PLOP:
125356211
(Ptcd3)
NCAR:
124963223
MMMA:
107159737
(Ptcd3)
OCU:
100337958
100345961
OPI:
101525051
(PTCD3)
TUP:
102501268
(PTCD3)
GVR:
103600761
(PTCD3)
CFA:
475765
(PTCD3)
CLUD:
112664335
(PTCD3)
VVP:
112916666
(PTCD3)
VLG:
121490906
(PTCD3)
NPO:
129510922
(PTCD3)
AML:
100470302
(PTCD3)
UMR:
103671462
(PTCD3)
UAH:
113242999
(PTCD3)
UAR:
123799698
(PTCD3)
ELK:
111147987
LLV:
125108279
MPUF:
101680218
(PTCD3)
MNP:
132021384
(PTCD3)
MLK:
131840401
(PTCD3)
NVS:
122915062
(PTCD3)
ORO:
101376989
(PTCD3)
EJU:
114223438
(PTCD3)
ZCA:
113937288
(PTCD3)
MLX:
118007897
(PTCD3)
NSU:
110587295
(PTCD3)
LWW:
102744952
(PTCD3)
FCA:
101087571
(PTCD3)
PYU:
121044497
(PTCD3)
PCOO:
112864255
(PTCD3)
PBG:
122497131
(PTCD3)
PVIV:
125162761
(PTCD3)
LRUF:
124503550
PTG:
102965299
(PTCD3)
PPAD:
109264070
(PTCD3)
PUC:
125937259
AJU:
106978132
HHV:
120245539
(PTCD3)
BTA:
509502
(PTCD3)
BOM:
102267037
(PTCD3)
BIU:
109566159
(PTCD3)
BBUB:
102415100
(PTCD3)
BBIS:
105004574
(PTCD3)
CHX:
102190137
(PTCD3)
OAS:
101105643
(PTCD3)
BTAX:
128055244
(PTCD3)
ODA:
120851489
(PTCD3)
CCAD:
122441754
(PTCD3)
MBEZ:
129539048
(PTCD3)
SSC:
100517886
(PTCD3)
CFR:
102513740
(PTCD3)
CBAI:
105072113
(PTCD3)
CDK:
105104166
(PTCD3)
VPC:
102527999
(PTCD3)
BACU:
103001375
(PTCD3)
BMUS:
118905942
(PTCD3)
LVE:
103074270
(PTCD3)
OOR:
101282726
(PTCD3)
DLE:
111165427
(PTCD3)
PCAD:
102982198
(PTCD3)
PSIU:
116764741
(PTCD3)
NASI:
112398942
(PTCD3)
ECB:
100067047
(PTCD3)
111771969
111771997
EPZ:
103556952
(PTCD3)
EAI:
106838590
(PTCD3)
MYB:
102243543
(PTCD3)
MYD:
102759023
(PTCD3)
MMYO:
118668783
(PTCD3)
MLF:
102441069
(PTCD3)
PKL:
118717624
(PTCD3)
EFUS:
103299083
(PTCD3)
MNA:
107528671
(PTCD3)
DRO:
112303021
(PTCD3)
SHON:
118982196
(PTCD3)
AJM:
119059864
(PTCD3)
PDIC:
114500529
(PTCD3)
PHAS:
123811934
(PTCD3)
MMF:
118630781
(PTCD3)
PPAM:
129073970
(PTCD3)
HAI:
109375923
RFQ:
117032753
(PTCD3)
PALE:
102880606
(PTCD3)
PGIG:
120594391
(PTCD3)
PVP:
105298502
(PTCD3)
RAY:
107506057
(PTCD3)
MJV:
108408697
(PTCD3)
TOD:
119259139
(PTCD3)
SARA:
101549390
(PTCD3)
SETR:
126024175
(PTCD3)
LAV:
100673718
(PTCD3)
TMU:
101343992
ETF:
101650978
(PTCD3)
DNM:
101430417
(PTCD3)
MDO:
100029855
(PTCD3)
GAS:
123236684
(PTCD3)
SHR:
100918514
(PTCD3)
AFZ:
127547457
PCW:
110196319
(PTCD3)
OAA:
100081180
(PTCD3)
GGA:
422911
(PTCD3)
PCOC:
116225713
(PTCD3)
MGP:
100549669
(PTCD3)
CJO:
107313905
(PTCD3)
TPAI:
128079828
(PTCD3)
LMUT:
125692709
(PTCD3)
NMEL:
110398703
(PTCD3)
APLA:
101804718
(PTCD3)
ACYG:
106034054
(PTCD3)
CATA:
118248485
(PTCD3)
AFUL:
116488530
(PTCD3)
TGU:
116808202
(PTCD3)
LSR:
110473302
(PTCD3)
SCAN:
103826111
(PTCD3)
PMOA:
120509401
(PTCD3)
OTC:
121335157
(PTCD3)
GFR:
102040171
(PTCD3)
FAB:
101813348
(PTCD3)
OMA:
130252555
(PTCD3)
PHI:
102113662
(PTCD3)
PMAJ:
107203012
(PTCD3)
CCAE:
111928300
(PTCD3)
CCW:
104690927
(PTCD3)
CBRC:
103611196
(PTCD3)
ETL:
114058526
(PTCD3)
ZAB:
102074897
(PTCD3)
ACHL:
103805243
(PTCD3)
SVG:
106865266
(PTCD3)
MMEA:
130582781
(PTCD3)
HRT:
120752493
(PTCD3)
FPG:
101921775
(PTCD3)
FCH:
102051049
(PTCD3)
CLV:
102085290
(PTCD3)
EGZ:
104135254
(PTCD3)
NNI:
104018567
(PTCD3)
PCRI:
104027045
(PTCD3)
PLET:
104619489
(PTCD3)
EHS:
104516684
(PTCD3)
PCAO:
104051902
(PTCD3)
ACUN:
113479163
(PTCD3)
TALA:
104361911
(PTCD3)
PADL:
103923533
(PTCD3)
AFOR:
103907259
(PTCD3)
ACHC:
115338718
(PTCD3)
HALD:
104323723
(PTCD3)
HLE:
104838133
(PTCD3)
AGEN:
126035674
GCL:
127016179
CCRI:
104159119
CSTI:
104550199
(PTCD3)
CMAC:
104479054
(PTCD3)
MUI:
104543208
(PTCD3)
BREG:
104641710
(PTCD3)
FGA:
104075815
(PTCD3)
GSTE:
104264214
(PTCD3)
LDI:
104349882
(PTCD3)
MNB:
103778036
(PTCD3)
OHA:
104329650
(PTCD3)
NNT:
104413728
(PTCD3)
SHAB:
115610411
(PTCD3)
DPUB:
104304825
(PTCD3)
PGUU:
104458341
(PTCD3)
ACAR:
104523248
(PTCD3)
CPEA:
104391057
(PTCD3)
AVIT:
104270234
CVF:
104284220
(PTCD3)
RTD:
128909990
(PTCD3)
CUCA:
104054947
(PTCD3)
TEO:
104370187
(PTCD3)
BRHI:
104490425
(PTCD3)
AAM:
106488113
(PTCD3)
AROW:
112965563
(PTCD3)
NPD:
112943094
(PTCD3)
TGT:
104566077
(PTCD3)
DNE:
112990800
(PTCD3)
SCAM:
104151420
(PTCD3)
ASN:
102371320
(PTCD3)
AMJ:
102573283
(PTCD3)
CPOO:
109321932
(PTCD3)
GGN:
109303606
(PTCD3)
PSS:
102452683
(PTCD3)
CMY:
102937426
(PTCD3)
CCAY:
125636276
(PTCD3)
DCC:
119854420
(PTCD3)
CPIC:
101942911
(PTCD3)
TST:
117877827
(PTCD3)
CABI:
116819638
(PTCD3)
MRV:
120406060
(PTCD3)
ACS:
100557104
(ptcd3)
ASAO:
132769682
132778408
(PTCD3)
PVT:
110080283
(PTCD3)
SUND:
121935102
(PTCD3)
PBI:
103067878
(PTCD3)
PMUR:
107302398
(PTCD3)
CTIG:
120302632
(PTCD3)
TSR:
106557092
(PTCD3)
PGUT:
117664811
(PTCD3)
APRI:
131198598
(PTCD3)
PTEX:
113447238
(PTCD3)
NSS:
113420078
(PTCD3)
VKO:
123031920
(PTCD3)
PMUA:
114582765
(PTCD3)
PRAF:
128399927
(PTCD3)
ZVI:
118095010
(PTCD3)
GJA:
107106757
(PTCD3)
STOW:
125444684
(PTCD3)
EMC:
129338737
(PTCD3)
XLA:
734981
(ptcd3.L)
XTR:
548397
(ptcd3)
NPR:
108796881
(PTCD3)
RTEM:
120924469
(PTCD3)
BBUF:
120990429
(PTCD3)
BGAR:
122939142
(PTCD3)
MUO:
115461336
(PTCD3)
GSH:
117363718
(PTCD3)
DRE:
553325
(ptcd3)
SRX:
107712298
107722437
(ptcd3)
SANH:
107660436
107667455
SGH:
107550988
107558057
CCAR:
109102536
109102889
CAUA:
113113494
(ptcd3)
CGIB:
127971405
PTET:
122357179
122357857
LROH:
127161721
(ptcd3)
OMC:
131553302
(ptcd3)
PPRM:
120464378
(ptcd3)
RKG:
130102846
(ptcd3)
MAMB:
125259029
(ptcd3)
CIDE:
127494753
MASI:
127418391
TROS:
130564152
(ptcd3)
TDW:
130437941
(ptcd3)
MANU:
129422084
(ptcd3)
IPU:
108268969
IFU:
128611149
(ptcd3)
PHYP:
113542921
(ptcd3)
SMEO:
124385958
(ptcd3)
TFD:
113647725
(ptcd3)
TVC:
132855504
(ptcd3)
AMEX:
107196966
(ptcd3)
CMAO:
118807320
(ptcd3)
EEE:
113576542
(ptcd3)
CHAR:
105903795
(ptcd3)
TRU:
101078881
(ptcd3)
TFS:
130531840
(ptcd3)
TNG:
GSTEN00019178G001
LCO:
104935345
(ptcd3)
TBEN:
117475034
(ptcd3)
CGOB:
115014458
(ptcd3)
PGEO:
117453889
EMAC:
134859813
(ptcd3)
ELY:
117260905
(ptcd3)
EFO:
125894354
(ptcd3)
PLEP:
121947813
(ptcd3)
SLUC:
116036510
(ptcd3)
ECRA:
117951364
(ptcd3)
ESP:
116696666
(ptcd3)
PFLV:
114563163
(ptcd3)
GAT:
120817908
(ptcd3)
PPUG:
119210552
(ptcd3)
AFB:
129090155
(ptcd3)
CLUM:
117737191
(ptcd3)
PSWI:
130209922
(ptcd3)
MSAM:
119888485
(ptcd3)
SCHU:
122880794
(ptcd3)
CUD:
121516393
(ptcd3)
ALAT:
119007069
(ptcd3)
MZE:
101486156
(ptcd3)
ONL:
100704541
(ptcd3)
OAU:
116333962
(ptcd3)
OLA:
101157067
(ptcd3)
OML:
112153289
(ptcd3)
CSAI:
133447691
(ptcd3)
XMA:
102223406
(ptcd3)
XCO:
114138891
(ptcd3)
XHE:
116714718
(ptcd3)
PRET:
103471011
(ptcd3)
PFOR:
103151716
(ptcd3)
PLAI:
106940581
(ptcd3)
PMEI:
106903285
(ptcd3)
GAF:
122836794
(ptcd3)
PPRL:
129362958
(ptcd3)
CVG:
107094159
(ptcd3)
CTUL:
119794101
(ptcd3)
GMU:
124860545
(ptcd3)
NFU:
107391069
(ptcd3)
KMR:
108240008
(ptcd3)
ALIM:
106511385
106533013
(ptcd3)
NWH:
119408568
(ptcd3)
AOCE:
111580993
(ptcd3)
MCEP:
125008676
(ptcd3)
CSEM:
103391486
(ptcd3)
POV:
109625973
(ptcd3)
SSEN:
122778860
(ptcd3)
HHIP:
117768946
(ptcd3)
HSP:
118112655
(ptcd3)
SMAU:
118319212
(ptcd3)
LCF:
108879121
SDU:
111226552
(ptcd3)
SLAL:
111667590
(ptcd3)
XGL:
120785329
(ptcd3)
HCQ:
109515778
(ptcd3)
SSCV:
125990877
SBIA:
133508668
(ptcd3)
PEE:
133407607
(ptcd3)
PTAO:
133484391
(ptcd3)
BPEC:
110156348
(ptcd3)
MALB:
109957519
(ptcd3)
BSPL:
114864611
(ptcd3)
SJO:
128362977
(ptcd3)
SASA:
106611965
(ptcd3)
STRU:
115205508
(ptcd3)
OTW:
112256002
(ptcd3)
OMY:
110504736
(ptcd3)
OGO:
124011336
(ptcd3)
ONE:
115129271
(ptcd3)
OKI:
109905010
(ptcd3)
OKE:
118363310
(ptcd3)
SALP:
111967308
(ptcd3)
SNH:
120062483
(ptcd3)
CCLU:
121586698
(ptcd3)
ELS:
105026820
(ptcd3)
SFM:
108920070
(ptcd3)
PKI:
111837671
(ptcd3)
AANG:
118231042
(ptcd3)
LOC:
102683857
(ptcd3)
PSPA:
121325719
(ptcd3)
ARUT:
117420974
(ptcd3)
PSEX:
120527878
(ptcd3)
LCM:
102360549
(PTCD3)
CMK:
103181478
(ptcd3)
RTP:
109918014
(ptcd3)
CPLA:
122557746
(ptcd3)
HOC:
132817982
(ptcd3)
LERI:
129705816
(ptcd3)
PMRN:
116951447
(PTCD3)
LRJ:
133340844
(PTCD3)
BFO:
118414298
BBEL:
109475481
CIN:
100179249
SPU:
594213
LPIC:
129272531
APLC:
110973850
SKO:
100372578
DME:
Dmel_CG4679
(CG4679)
DER:
6549358
DSE:
6608971
DSI:
Dsimw501_GD25775
(Dsim_GD25775)
DYA:
Dyak_GE13378
DAN:
6494062
DSR:
110178418
DPO:
6898770
DPE:
6590643
DMN:
108160442
117193397
DWI:
6650640
DGR:
6559090
DMO:
Dmoj_GI19450
DAZ:
108617201
DNV:
108655084
DHE:
111593893
DVI:
6625759
CCAT:
101450807
BOD:
106625700
BDR:
105233505
RZE:
108377062
AOQ:
129245629
TDA:
119686484
119686485
MDE:
101897392
SCAC:
106083739
LCQ:
111677217
GFS:
119641596
ECOE:
129952934
CLON:
129611016
HIS:
119661650
AGA:
1279178
ACOZ:
120957400
AARA:
120902993
AMER:
121597115
ASTE:
118509956
AFUN:
125761354
AMOU:
128302379
AALI:
118468601
AAG:
5572772
AALB:
109409185
115265574
CQU:
CpipJ_CPIJ019121
CPII:
120419018
CNS:
116345212
BCOO:
119073326
AME:
113218580
ACER:
108000981
ALAB:
122712969
ADR:
102671246
AFLR:
100868567
BIM:
100743216
BBIF:
117209771
BVK:
117230383
BVAN:
117165696
BTER:
100647674
BAFF:
126924529
BPYO:
122575456
BPAS:
132911730
FVI:
122536264
CCAL:
108630667
OBB:
114875124
OLG:
117603802
MGEN:
117219648
NMEA:
116431445
CGIG:
122394834
SOC:
105193815
MPHA:
105836665
AEC:
105148182
ACEP:
105624334
PBAR:
105433520
VEM:
105563883
HST:
105184836
DQU:
106749711
CFO:
105254527
FEX:
115240557
LHU:
105672587
PGC:
109859452
OBO:
105281778
PCF:
106787386
PFUC:
122513218
VPS:
122637090
VCRB:
124431221
VVE:
124957169
NVI:
100121935
CSOL:
105361993
TPRE:
106651447
LBD:
127285520
MDL:
103579688
CGLO:
123264795
FAS:
105272778
DAM:
107048891
AGIF:
122850250
VCAN:
122405901
CCIN:
107266304
DSM:
124413589
NPT:
124222216
NFB:
124184856
NLO:
107227223
NVG:
124307093
AROA:
105693340
TCA:
663577
DPA:
109541338
SOY:
115879293
AGRG:
126742620
ATD:
109596657
CSET:
123309243
AGB:
108910361
LDC:
111506536
NVL:
108564340
APLN:
108740995
PPYR:
116164393
OTU:
111416935
BMOR:
101744266
BMAN:
114248811
MSEX:
115443966
DPL:
KGM_205658
BANY:
112045979
MJU:
123866540
NIQ:
126781766
VCD:
124544341
MCIX:
123670070
PMAC:
106713513
PPOT:
106100447
PXU:
106123264
PRAP:
110995079
PBX:
123711660
PNAP:
125057872
ZCE:
119833519
CCRC:
123691713
LSIN:
126970449
AAGE:
121728549
HAW:
110371833
HZE:
124632471
TNL:
113508484
SLIU:
111358591
OFU:
114355243
PXY:
105398006
PGW:
126366390
CFEL:
113366808
113366813
CCRN:
123300052
API:
100159904
DNX:
107164220
AGS:
114127187
RMD:
113553359
113553405
ACOO:
126833450
DVT:
126908334
BTAB:
109041398
CLEC:
106669144
HHAL:
106683665
NLU:
111059886
HVI:
124353151
MQU:
128983631
PHU:
Phum_PHUM226550
FOC:
113210731
TPAL:
117640955
ZNE:
110837091
CSEC:
111875703
SGRE:
126347560
BROR:
134530363
IEL:
124155739
FCD:
110843115
DPX:
DAPPUDRAFT_221711
DMK:
116921914
DPZ:
124336944
PVM:
113814806
PJA:
122262186
PCHN:
125043818
PMOO:
119585781
HAME:
121868463
PCLA:
123754007
CQD:
128700594
PTRU:
123506597
ESN:
126987445
MNZ:
135206526
HAZT:
108680939
EAF:
111694975
LSM:
121128156
PPOI:
119099372
DSV:
119461423
RMP:
119174369
VDE:
111246201
VJA:
111270501
TUT:
107360831
DPTE:
113796292
DFR:
124492882
CSCU:
111641670
ABRU:
129981864
UDV:
129222521
SDM:
118200288
LPOL:
106463433
PMEO:
129599992
CEL:
CELE_Y110A7A.19
(let-630)
CBR:
CBG_23745
CRQ:
GCK72_000359
NAI:
NECAME_17071
BMY:
BM_BM7285
(Bma-let-630)
LOA:
LOAG_09745
TSP:
Tsp_05092
HRO:
HELRODRAFT_194044
LGI:
LOTGIDRAFT_232120
PVUL:
126815714
PCAN:
112555621
BGT:
106054606
GAE:
121382973
HRF:
124123697
HRJ:
124262219
CRG:
105347178
CVN:
111136260
CANU:
128179277
OED:
125658707
MYI:
110452538
PMAX:
117339295
MMER:
123546302
RPHI:
132714139
DPOL:
127840953
127842842
OBI:
106868930
OSN:
115219485
LAK:
106150469
106180701
SMM:
Smp_033770
NVE:
5508367
EPA:
110237996
ATEN:
116302042
ADF:
107327353
AMIL:
114960256
PDAM:
113667492
SPIS:
111320641
DGT:
114526046
HMG:
100210577
HSY:
130662391
130662739
AQU:
100635261
» show all
Taxonomy
UniProt
Reference
PMID:
19427859
Authors
Davies SM, Rackham O, Shearwood AM, Hamilton KL, Narsai R, Whelan J, Filipovska A
Title
Pentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translation.
Journal
FEBS Lett 583:1853-8 (2009)
DOI:
10.1016/j.febslet.2009.04.048
Sequence
[hsa:
55037
]
LinkDB
All DBs
DBGET
integrated database retrieval system