KEGG   PATHWAY: dle00250
Entry
dle00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Delphinapterus leucas (beluga whale)
Class
Metabolism; Amino acid metabolism
Pathway map
dle00250  Alanine, aspartate and glutamate metabolism
dle00250

Module
dle_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:dle00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Delphinapterus leucas (beluga whale) [GN:dle]
Gene
111163454  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
111163477  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
111164589  DDO; D-aspartate oxidase isoform X2 [KO:K00272] [EC:1.4.3.1]
111164816  NAT8L; N-acetylaspartate synthetase isoform X1 [KO:K18309] [EC:2.3.1.17]
111165001  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
111165383  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
111165660  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
111167459  [KO:K00261] [EC:1.4.1.3]
111167881  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 [KO:K00820] [EC:2.6.1.16]
111168563  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
111168761  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
111169268  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
111169430  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
111170975  [KO:K14592] [EC:3.4.17.21]
111171665  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
111171789  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial isoform X1 [KO:K01948] [EC:6.3.4.16]
111172005  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
111172411  GOT1; aspartate aminotransferase, cytoplasmic isoform X1 [KO:K14454] [EC:2.6.1.1]
111172851  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
111173616  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
111173864  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
111174963  CAD; CAD protein [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
111175407  [KO:K03334] [EC:1.4.3.2]
111175673  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
111176010  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X2 [KO:K01939] [EC:6.3.4.4]
111176728  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
111177121  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
111177555  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
111178069  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
111180588  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
111181353  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
111182080  ASL; argininosuccinate lyase isoform X1 [KO:K01755] [EC:4.3.2.1]
111182198  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
111183873  ASRGL1; isoaspartyl peptidase/L-asparaginase isoform X1 [KO:K13051] [EC:3.5.1.1 3.4.19.5]
111185765  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
111186329  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
111187642  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
dle00010  Glycolysis / Gluconeogenesis
dle00020  Citrate cycle (TCA cycle)
dle00220  Arginine biosynthesis
dle00230  Purine metabolism
dle00240  Pyrimidine metabolism
dle00260  Glycine, serine and threonine metabolism
dle00330  Arginine and proline metabolism
dle00340  Histidine metabolism
dle00410  beta-Alanine metabolism
dle00470  D-Amino acid metabolism
dle00480  Glutathione metabolism
dle00520  Amino sugar and nucleotide sugar metabolism
dle00620  Pyruvate metabolism
dle00630  Glyoxylate and dicarboxylate metabolism
dle00650  Butanoate metabolism
dle00760  Nicotinate and nicotinamide metabolism
dle00770  Pantothenate and CoA biosynthesis
dle00860  Porphyrin metabolism
dle00910  Nitrogen metabolism
KO pathway
ko00250   

DBGET integrated database retrieval system