KEGG   PATHWAY: aml00250
Entry
aml00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Ailuropoda melanoleuca (giant panda)
Class
Metabolism; Amino acid metabolism
Pathway map
aml00250  Alanine, aspartate and glutamate metabolism
aml00250

Module
aml_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:aml00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Ailuropoda melanoleuca (giant panda) [GN:aml]
Gene
100465209  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
100469239  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
100474677  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
100476680  L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
100465325  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
100473827  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
100468618  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
100483598  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
100471092  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
100471370  GPT; alanine aminotransferase 1 [KO:K00814] [EC:2.6.1.2]
100475183  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
100477831  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
100482092  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
117795006  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
100476336  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
100478474  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
100467024  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
105235509  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
100464561  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
100473320  RIMKLB; beta-citrylglutamate synthase B isoform X1 [KO:K18310] [EC:6.3.1.17 6.3.2.41]
100472546  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
100472805  glutamate carboxypeptidase 2 isoform X2 [KO:K14592] [EC:3.4.17.21]
100483637  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
100463588  GAD1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
100467369  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
100484402  LOW QUALITY PROTEIN: glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
100469592  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
100484592  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
100476541  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
100476799  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X1 [KO:K00294] [EC:1.2.1.88]
100466733  GLUL; glutamine synthetase isoform X2 [KO:K01915] [EC:6.3.1.2]
100465885  CAD; CAD protein isoform X2 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
100473169  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
100473777  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
100466842  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
100478011  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
100469996  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
100482423  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
aml00010  Glycolysis / Gluconeogenesis
aml00020  Citrate cycle (TCA cycle)
aml00220  Arginine biosynthesis
aml00230  Purine metabolism
aml00240  Pyrimidine metabolism
aml00260  Glycine, serine and threonine metabolism
aml00330  Arginine and proline metabolism
aml00340  Histidine metabolism
aml00410  beta-Alanine metabolism
aml00470  D-Amino acid metabolism
aml00480  Glutathione metabolism
aml00520  Amino sugar and nucleotide sugar metabolism
aml00620  Pyruvate metabolism
aml00630  Glyoxylate and dicarboxylate metabolism
aml00650  Butanoate metabolism
aml00760  Nicotinate and nicotinamide metabolism
aml00770  Pantothenate and CoA biosynthesis
aml00860  Porphyrin metabolism
aml00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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