KEGG   PATHWAY: etf00250
Entry
etf00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Echinops telfairi (small Madagascar hedgehog)
Class
Metabolism; Amino acid metabolism
Pathway map
etf00250  Alanine, aspartate and glutamate metabolism
etf00250

Module
etf_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:etf00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Echinops telfairi (small Madagascar hedgehog) [GN:etf]
Gene
101645666  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
101641395  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
123522011  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
101660188  L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
101663616  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
101662116  DDO; D-aspartate oxidase [KO:K00272] [EC:1.4.3.1]
101662070  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
101652606  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
101664333  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
101639357  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
101643182  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
101663497  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
101663774  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
101660926  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
101639417  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
101656444  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
101640029  adenylosuccinate synthetase isozyme 2-like [KO:K01939] [EC:6.3.4.4]
101642416  ADSS1; adenylosuccinate synthetase isozyme 1 [KO:K01939] [EC:6.3.4.4]
101644647  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
101643562  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
101645920  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
101661935  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
101664149  glutamate carboxypeptidase 2 [KO:K14592] [EC:3.4.17.21]
101648226  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
101639636  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
101653629  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
101643406  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
101648602  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
101652855  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
101659860  glutamate dehydrogenase 1, mitochondrial-like [KO:K00261] [EC:1.4.1.3]
101653557  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X1 [KO:K00294] [EC:1.2.1.88]
105978980  GLUL; LOW QUALITY PROTEIN: glutamine synthetase [KO:K01915] [EC:6.3.1.2]
101650987  CAD; CAD protein isoform X5 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
101656356  GLS; glutaminase kidney isoform, mitochondrial [KO:K01425] [EC:3.5.1.2]
101660654  GLS2; glutaminase liver isoform, mitochondrial [KO:K01425] [EC:3.5.1.2]
101651869  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
101659644  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 [KO:K00820] [EC:2.6.1.16]
101653282  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
101647743  PPAT; amidophosphoribosyltransferase isoform X1 [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
etf00010  Glycolysis / Gluconeogenesis
etf00020  Citrate cycle (TCA cycle)
etf00220  Arginine biosynthesis
etf00230  Purine metabolism
etf00240  Pyrimidine metabolism
etf00260  Glycine, serine and threonine metabolism
etf00330  Arginine and proline metabolism
etf00340  Histidine metabolism
etf00410  beta-Alanine metabolism
etf00470  D-Amino acid metabolism
etf00480  Glutathione metabolism
etf00520  Amino sugar and nucleotide sugar metabolism
etf00620  Pyruvate metabolism
etf00630  Glyoxylate and dicarboxylate metabolism
etf00650  Butanoate metabolism
etf00760  Nicotinate and nicotinamide metabolism
etf00770  Pantothenate and CoA biosynthesis
etf00860  Porphyrin metabolism
etf00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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