KEGG   PATHWAY: hhv00250
Entry
hhv00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Hyaena hyaena (striped hyena)
Class
Metabolism; Amino acid metabolism
Pathway map
hhv00250  Alanine, aspartate and glutamate metabolism
hhv00250

Module
hhv_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:hhv00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Hyaena hyaena (striped hyena) [GN:hhv]
Gene
120224806  aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
120238682  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 isoform X1 [KO:K14454] [EC:2.6.1.1]
120232160  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
120240706  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
120236036  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
120226027  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
120226501  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
120234411  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
120245095  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
120238176  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
120246578  GPT; alanine aminotransferase 1 [KO:K00814] [EC:2.6.1.2]
120229494  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
120242473  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
120230118  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
120235678  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
120235271  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
120247768  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
120234084  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
120231840  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
120222721  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
120236090  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
120246246  FOLH1B; putative N-acetylated-alpha-linked acidic dipeptidase isoform X1 [KO:K14592] [EC:3.4.17.21]
120224768  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
120222594  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
120222620  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
120230791  glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
120223570  glutamate decarboxylase 2-like [KO:K01580] [EC:4.1.1.15]
120239832  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
120219836  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
120225422  LOW QUALITY PROTEIN: glutamate dehydrogenase 1, mitochondrial-like [KO:K00261] [EC:1.4.1.3]
120232794  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
120229815  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
120243229  GLUL; glutamine synthetase [KO:K01915] [EC:6.3.1.2]
120235931  CAD; CAD protein [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
120233449  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
120219931  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
120243755  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
120219777  LOW QUALITY PROTEIN: glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2-like [KO:K00820] [EC:2.6.1.16]
120236631  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 [KO:K00820] [EC:2.6.1.16]
120245696  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
120243045  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
hhv00010  Glycolysis / Gluconeogenesis
hhv00020  Citrate cycle (TCA cycle)
hhv00220  Arginine biosynthesis
hhv00230  Purine metabolism
hhv00240  Pyrimidine metabolism
hhv00260  Glycine, serine and threonine metabolism
hhv00330  Arginine and proline metabolism
hhv00340  Histidine metabolism
hhv00410  beta-Alanine metabolism
hhv00470  D-Amino acid metabolism
hhv00480  Glutathione metabolism
hhv00520  Amino sugar and nucleotide sugar metabolism
hhv00620  Pyruvate metabolism
hhv00630  Glyoxylate and dicarboxylate metabolism
hhv00650  Butanoate metabolism
hhv00760  Nicotinate and nicotinamide metabolism
hhv00770  Pantothenate and CoA biosynthesis
hhv00860  Porphyrin metabolism
hhv00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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