KEGG   PATHWAY: uar00250
Entry
uar00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Ursus americanus (American black bear)
Class
Metabolism; Amino acid metabolism
Pathway map
uar00250  Alanine, aspartate and glutamate metabolism
uar00250

Module
uar_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:uar00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Ursus americanus (American black bear) [GN:uar]
Gene
123780351  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
123783619  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
123798468  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
123793625  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
123776239  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
123792950  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
123789836  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
123789251  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
123784111  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
123779336  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
123776583  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
123791242  AGXT; serine--pyruvate aminotransferase isoform X1 [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
123785468  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
123775610  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
123784704  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
123791407  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
123778655  ADSS1; adenylosuccinate synthetase isozyme 1 [KO:K01939] [EC:6.3.4.4]
123780717  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
123777861  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
123781552  RIMKLB; beta-citrylglutamate synthase B isoform X1 [KO:K18310] [EC:6.3.1.17 6.3.2.41]
123793822  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
123803814  glutamate carboxypeptidase 2 isoform X1 [KO:K14592] [EC:3.4.17.21]
123776937  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
123787432  glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
123780849  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
123778151  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
123783654  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
123794260  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
123783072  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
123782190  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
123801396  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
123799913  CAD; LOW QUALITY PROTEIN: CAD protein [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
123787244  GLS2; glutaminase liver isoform, mitochondrial [KO:K01425] [EC:3.5.1.2]
123798146  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
123798268  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
123786018  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
123790497  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
123803984  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
uar00010  Glycolysis / Gluconeogenesis
uar00020  Citrate cycle (TCA cycle)
uar00220  Arginine biosynthesis
uar00230  Purine metabolism
uar00240  Pyrimidine metabolism
uar00260  Glycine, serine and threonine metabolism
uar00330  Arginine and proline metabolism
uar00340  Histidine metabolism
uar00410  beta-Alanine metabolism
uar00470  D-Amino acid metabolism
uar00480  Glutathione metabolism
uar00520  Amino sugar and nucleotide sugar metabolism
uar00620  Pyruvate metabolism
uar00630  Glyoxylate and dicarboxylate metabolism
uar00650  Butanoate metabolism
uar00760  Nicotinate and nicotinamide metabolism
uar00770  Pantothenate and CoA biosynthesis
uar00860  Porphyrin metabolism
uar00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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