KEGG   PATHWAY: mlx00250
Entry
mlx00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Mirounga leonina (Southern elephant seal)
Class
Metabolism; Amino acid metabolism
Pathway map
mlx00250  Alanine, aspartate and glutamate metabolism
mlx00250

Module
mlx_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:mlx00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Mirounga leonina (Southern elephant seal) [GN:mlx]
Gene
118024778  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
118009968  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
118023718  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
118019531  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
117998280  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
118001596  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
118015933  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
118020795  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
118017373  NIT2; omega-amidase NIT2 isoform X1 [KO:K13566] [EC:3.5.1.3]
118015331  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
118023823  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
118011710  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
118006359  alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
118006488  alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
118017584  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
117999535  ASL; argininosuccinate lyase isoform X1 [KO:K01755] [EC:4.3.2.1]
118002047  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
118014559  ADSS2; adenylosuccinate synthetase isozyme 2 isoform X1 [KO:K01939] [EC:6.3.4.4]
117998650  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
118010179  NAT8L; LOW QUALITY PROTEIN: N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
118025692  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
118019547  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
118013456  FOLH1B; putative N-acetylated-alpha-linked acidic dipeptidase [KO:K14592] [EC:3.4.17.21]
118025177  ASPA; aspartoacylase isoform X1 [KO:K01437] [EC:3.5.1.15]
118004722  LOW QUALITY PROTEIN: glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
118011811  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
118026564  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
118021813  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
118027227  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
118022691  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
118019944  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
118014356  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
118007689  CAD; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
118008704  GLS2; glutaminase liver isoform, mitochondrial [KO:K01425] [EC:3.5.1.2]
118012207  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
118012083  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
118008021  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
118026505  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
118010505  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
mlx00010  Glycolysis / Gluconeogenesis
mlx00020  Citrate cycle (TCA cycle)
mlx00220  Arginine biosynthesis
mlx00230  Purine metabolism
mlx00240  Pyrimidine metabolism
mlx00260  Glycine, serine and threonine metabolism
mlx00330  Arginine and proline metabolism
mlx00340  Histidine metabolism
mlx00410  beta-Alanine metabolism
mlx00470  D-Amino acid metabolism
mlx00480  Glutathione metabolism
mlx00520  Amino sugar and nucleotide sugar metabolism
mlx00620  Pyruvate metabolism
mlx00630  Glyoxylate and dicarboxylate metabolism
mlx00650  Butanoate metabolism
mlx00760  Nicotinate and nicotinamide metabolism
mlx00770  Pantothenate and CoA biosynthesis
mlx00860  Porphyrin metabolism
mlx00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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