KEGG   PATHWAY: mmma00250
Entry
mmma00250                   Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Marmota marmota marmota (Alpine marmot)
Class
Metabolism; Amino acid metabolism
Pathway map
mmma00250  Alanine, aspartate and glutamate metabolism
mmma00250

Module
mmma_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:mmma00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Marmota marmota marmota (Alpine marmot) [GN:mmma]
Gene
107149784  Got1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
107155338  Got1l1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
107144811  Got2; aspartate aminotransferase, mitochondrial isoform X1 [KO:K14455] [EC:2.6.1.1]
107159797  aspartate aminotransferase, mitochondrial-like [KO:K14455] [EC:2.6.1.1]
107151225  Il4i1; L-amino-acid oxidase isoform X3 [KO:K03334] [EC:1.4.3.2]
107141477  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
107159769  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
107154499  Ddo; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
107135909  Asrgl1; isoaspartyl peptidase/L-asparaginase isoform X1 [KO:K13051] [EC:3.5.1.1 3.4.19.5]
107144463  Asns; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
107136365  Nit2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
107143036  alanine aminotransferase 1 isoform X6 [KO:K00814] [EC:2.6.1.2]
107144896  Gpt2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
107138863  Agxt; alanine--glyoxylate aminotransferase isoform X1 [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
107151125  Agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
107152001  Ass1; argininosuccinate synthase isoform X1 [KO:K01940] [EC:6.3.4.5]
107147008  Asl; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
107144930  Adss1; adenylosuccinate synthetase isozyme 1 [KO:K01939] [EC:6.3.4.4]
107140470  Adss2; adenylosuccinate synthetase isozyme 2 isoform X2 [KO:K01939] [EC:6.3.4.4]
107155860  Adsl; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
107145128  LOW QUALITY PROTEIN: adenylosuccinate lyase-like [KO:K01756] [EC:4.3.2.2]
107138892  Nat8l; N-acetylaspartate synthetase isoform X2 [KO:K18309] [EC:2.3.1.17]
107159921  Rimklb; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
107141636  Rimkla; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
107135437  LOW QUALITY PROTEIN: glutamate carboxypeptidase 2 [KO:K14592] [EC:3.4.17.21]
107159402  Aspa; aspartoacylase isoform X1 [KO:K01437] [EC:3.5.1.15]
107155184  aspartoacylase-like isoform X1 [KO:K01437] [EC:3.5.1.15]
107136916  Gad1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
107150323  Gad2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
107146635  Abat; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
107149296  Aldh5a1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
107154450  Glud1; glutamate dehydrogenase 1, mitochondrial isoform X1 [KO:K00261] [EC:1.4.1.3]
107142190  Aldh4a1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X4 [KO:K00294] [EC:1.2.1.88]
107147322  Glul; glutamine synthetase [KO:K01915] [EC:6.3.1.2]
107137422  Cad; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
107140161  Gls2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
107138351  Gls; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
107138386  Cps1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
107159799  Gfpt2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
107136979  Gfpt1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
mmma00010  Glycolysis / Gluconeogenesis
mmma00020  Citrate cycle (TCA cycle)
mmma00220  Arginine biosynthesis
mmma00230  Purine metabolism
mmma00240  Pyrimidine metabolism
mmma00260  Glycine, serine and threonine metabolism
mmma00330  Arginine and proline metabolism
mmma00340  Histidine metabolism
mmma00410  beta-Alanine metabolism
mmma00470  D-Amino acid metabolism
mmma00480  Glutathione metabolism
mmma00520  Amino sugar and nucleotide sugar metabolism
mmma00620  Pyruvate metabolism
mmma00630  Glyoxylate and dicarboxylate metabolism
mmma00650  Butanoate metabolism
mmma00760  Nicotinate and nicotinamide metabolism
mmma00770  Pantothenate and CoA biosynthesis
mmma00860  Porphyrin metabolism
mmma00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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