KEGG   PATHWAY: opi00250
Entry
opi00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Ochotona princeps (American pika)
Class
Metabolism; Amino acid metabolism
Pathway map
opi00250  Alanine, aspartate and glutamate metabolism
opi00250

Module
opi_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:opi00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Ochotona princeps (American pika) [GN:opi]
Gene
101516315  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
101516242  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
101534218  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
101530470  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
101528013  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
101518924  DDO; D-aspartate oxidase [KO:K00272] [EC:1.4.3.1]
101522343  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
101517307  ASNS; LOW QUALITY PROTEIN: asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
101519064  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
101535691  GPT2; alanine aminotransferase 2 isoform X1 [KO:K00814] [EC:2.6.1.2]
101534205  GPT; alanine aminotransferase 1 [KO:K00814] [EC:2.6.1.2]
101530322  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
101519119  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X3 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
101524351  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
101522020  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
101519261  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X2 [KO:K01939] [EC:6.3.4.4]
101525324  ADSS2; adenylosuccinate synthetase isozyme 2 isoform X1 [KO:K01939] [EC:6.3.4.4]
101520440  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
101523904  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
101523234  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
101536112  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
101520191  FOLH1B; putative N-acetylated-alpha-linked acidic dipeptidase [KO:K14592] [EC:3.4.17.21]
101533443  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
101533455  GAD1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
101516669  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
101526078  ABAT; 4-aminobutyrate aminotransferase, mitochondrial isoform X1 [KO:K13524] [EC:2.6.1.19 2.6.1.22]
101522893  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
101534051  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
101519298  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
101520151  GLUL; glutamine synthetase [KO:K01915] [EC:6.3.1.2]
101536661  CAD; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
101529820  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
101522810  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
101527604  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
101524601  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 isoform X1 [KO:K00820] [EC:2.6.1.16]
101534777  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 [KO:K00820] [EC:2.6.1.16]
101524729  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
opi00010  Glycolysis / Gluconeogenesis
opi00020  Citrate cycle (TCA cycle)
opi00220  Arginine biosynthesis
opi00230  Purine metabolism
opi00240  Pyrimidine metabolism
opi00260  Glycine, serine and threonine metabolism
opi00330  Arginine and proline metabolism
opi00340  Histidine metabolism
opi00410  beta-Alanine metabolism
opi00470  D-Amino acid metabolism
opi00480  Glutathione metabolism
opi00520  Amino sugar and nucleotide sugar metabolism
opi00620  Pyruvate metabolism
opi00630  Glyoxylate and dicarboxylate metabolism
opi00650  Butanoate metabolism
opi00760  Nicotinate and nicotinamide metabolism
opi00770  Pantothenate and CoA biosynthesis
opi00860  Porphyrin metabolism
opi00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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