KEGG   PATHWAY: hsa00500
Entry
hsa00500                    Pathway                                
Name
Starch and sucrose metabolism - Homo sapiens (human)
Class
Metabolism; Carbohydrate metabolism
Pathway map
hsa00500  Starch and sucrose metabolism
hsa00500

Module
hsa_M00854  Glycogen biosynthesis, glucose-1P => glycogen/starch [PATH:hsa00500]
hsa_M00855  Glycogen degradation, glycogen => glucose-6P [PATH:hsa00500]
Network
nt06017  Glycogen metabolism
  Element
N00713  Glycogen biosynthesis
N00718  Glycogen degradation
N00720  Glycogen degradation (amylase)
Drug
D00216  Acarbose (JAN/USAN/INN)
D00625  Miglitol (JP19/USAN/INN)
D01665  Voglibose (JP19/USAN/INN)
D03207  Alglucosidase alfa (USAN/INN)
D03342  Camiglibose (USAN)
D04537  Ingliforib (USAN/INN)
D05782  Sacrosidase (USAN)
D09605  Duvoglustat (USAN/INN)
D09606  Duvoglustat hydrochloride (USAN)
D11744  Avalglucosidase alfa (USAN/INN)
D11798  Cipaglucosidase alfa (USAN)
D11828  Clervonafusp alfa (USAN/INN)
Other DBs
GO: 0005982 0005985
Organism
Homo sapiens (human) [GN:hsa]
Gene
11181  TREH; trehalase isoform 1 precursor [KO:K01194] [EC:3.2.1.28]
178  AGL; glycogen debranching enzyme isoform 1 [KO:K01196] [EC:2.4.1.25 3.2.1.33]
2538  G6PC1; glucose-6-phosphatase catalytic subunit 1 isoform 1 [KO:K01084] [EC:3.1.3.9]
2548  GAA; lysosomal alpha-glucosidase preproprotein [KO:K12316] [EC:3.2.1.20]
2595  GANC; neutral alpha-glucosidase C isoform 1 [KO:K12317] [EC:3.2.1.20]
2632  GBE1; 1,4-alpha-glucan-branching enzyme [KO:K00700] [EC:2.4.1.18]
2645  GCK; hexokinase-4 isoform 1 [KO:K12407] [EC:2.7.1.2]
276  AMY1A; alpha-amylase 1A precursor [KO:K01176] [EC:3.2.1.1]
277  AMY1B; alpha-amylase 1B precursor [KO:K01176] [EC:3.2.1.1]
278  AMY1C; alpha-amylase 1C precursor [KO:K01176] [EC:3.2.1.1]
279  AMY2A; pancreatic alpha-amylase precursor [KO:K01176] [EC:3.2.1.1]
280  AMY2B; alpha-amylase 2B precursor [KO:K01176] [EC:3.2.1.1]
2821  GPI; glucose-6-phosphate isomerase isoform 2 [KO:K01810] [EC:5.3.1.9]
283209  PGM2L1; glucose 1,6-bisphosphate synthase [KO:K11809] [EC:2.7.1.106]
2992  GYG1; glycogenin-1 isoform 1 [KO:K00750] [EC:2.4.1.186]
2997  GYS1; glycogen [starch] synthase, muscle isoform 1 [KO:K00693] [EC:2.4.1.11]
2998  GYS2; glycogen [starch] synthase, liver [KO:K00693] [EC:2.4.1.11]
3098  HK1; hexokinase-1 isoform HKI [KO:K00844] [EC:2.7.1.1]
3099  HK2; hexokinase-2 isoform 1 [KO:K00844] [EC:2.7.1.1]
3101  HK3; hexokinase-3 [KO:K00844] [EC:2.7.1.1]
5167  ENPP1; ectonucleotide pyrophosphatase/phosphodiesterase family member 1 [KO:K01513] [EC:3.1.4.1 3.6.1.9]
5169  ENPP3; ectonucleotide pyrophosphatase/phosphodiesterase family member 3 [KO:K01513] [EC:3.1.4.1 3.6.1.9]
5236  PGM1; phosphoglucomutase-1 isoform 1 [KO:K01835] [EC:5.4.2.2]
55276  PGM2; phosphopentomutase [KO:K15779] [EC:5.4.2.2 5.4.2.7]
57733  GBA3; cytosolic beta-glucosidase isoform a [KO:K05350] [EC:3.2.1.21]
57818  G6PC2; glucose-6-phosphatase 2 isoform 1 [KO:K01084] [EC:3.1.3.9]
5834  PYGB; glycogen phosphorylase, brain form [KO:K00688] [EC:2.4.1.1]
5836  PYGL; glycogen phosphorylase, liver form isoform 1 [KO:K00688] [EC:2.4.1.1]
5837  PYGM; glycogen phosphorylase, muscle form isoform 1 [KO:K00688] [EC:2.4.1.1]
6476  SI; sucrase-isomaltase, intestinal [KO:K01203] [EC:3.2.1.48 3.2.1.10]
7360  UGP2; UTP--glucose-1-phosphate uridylyltransferase isoform a [KO:K00963] [EC:2.7.7.9]
80201  HKDC1; hexokinase HKDC1 [KO:K00844] [EC:2.7.1.1]
8908  GYG2; glycogenin-2 isoform b [KO:K00750] [EC:2.4.1.186]
8972  MGAM; maltase-glucoamylase isoform 1 [KO:K12047] [EC:3.2.1.20 3.2.1.3]
92579  G6PC3; glucose-6-phosphatase 3 isoform 1 [KO:K01084] [EC:3.1.3.9]
93432  MGAM2; probable maltase-glucoamylase 2 [KO:K12047] [EC:3.2.1.20 3.2.1.3]
Compound
C00029  UDP-glucose
C00031  D-Glucose
C00085  D-Fructose 6-phosphate
C00089  Sucrose
C00092  D-Glucose 6-phosphate
C00095  D-Fructose
C00103  D-Glucose 1-phosphate
C00185  Cellobiose
C00208  Maltose
C00252  Isomaltose
C00369  Starch
C00372  Dextran
C00394  GDP-glucose
C00498  ADP-glucose
C00501  CDP-glucose
C00663  beta-D-Glucose 1-phosphate
C00689  alpha,alpha'-Trehalose 6-phosphate
C00718  Amylose
C00721  Dextrin
C00760  Cellulose
C00963  beta-D-Glucoside
C00965  1,3-beta-D-Glucan
C00973  Cyclomaltodextrin
C01083  alpha,alpha-Trehalose
C01231  alpha-D-Glucose 1,6-bisphosphate
C01725  Levanbiose
C01898  Cellodextrin
C01935  Maltodextrin
C02591  Sucrose 6'-phosphate
C02995  Maltose 6'-phosphate
C03323  (2,1-beta-D-Fructosyl)n
C04534  6-Phospho-beta-D-glucosyl-(1,4)-D-glucose
C05731  3-Ketosucrose
C06215  Levan
C06400  1-alpha-D-[(1->4)-alpha-D-Glucosyl](n-1)-alpha-D-glucopyranoside
C16688  Sucrose 6-phosphate
C20237  alpha-Maltose 1-phosphate
Related
pathway
hsa00010  Glycolysis / Gluconeogenesis
hsa00520  Amino sugar and nucleotide sugar metabolism
KO pathway
ko00500   

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