KEGG   PATHWAY: mlk00250
Entry
mlk00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Mustela lutreola (European mink)
Class
Metabolism; Amino acid metabolism
Pathway map
mlk00250  Alanine, aspartate and glutamate metabolism
mlk00250

Module
mlk_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:mlk00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Mustela lutreola (European mink) [GN:mlk]
Gene
131820473  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 isoform X1 [KO:K14454] [EC:2.6.1.1]
131828562  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
131818234  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
131809419  L-amino-acid oxidase-like isoform X1 [KO:K03334] [EC:1.4.3.2]
131818022  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
131833511  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
131813877  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
131829419  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
131825198  NIT2; omega-amidase NIT2 isoform X1 [KO:K13566] [EC:3.5.1.3]
131818012  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
131826323  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
131827257  AGXT; alanine--glyoxylate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
131831648  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
131812699  ASS1; argininosuccinate synthase isoform X1 [KO:K01940] [EC:6.3.4.5]
131819661  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
131837050  ADSS1; adenylosuccinate synthetase isozyme 1 [KO:K01939] [EC:6.3.4.4]
131814440  ADSS2; adenylosuccinate synthetase isozyme 2 isoform X1 [KO:K01939] [EC:6.3.4.4]
131839508  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
131827032  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
131839093  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
131809477  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
131839422  FOLH1; glutamate carboxypeptidase 2 isoform X1 [KO:K14592] [EC:3.4.17.21]
131815711  ASPA; aspartoacylase isoform X1 [KO:K01437] [EC:3.5.1.15]
131838143  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
131811276  LOW QUALITY PROTEIN: glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
131827109  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
131819678  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
131834817  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
131828736  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
131809489  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
131814422  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
131825500  glutamine synthetase [KO:K01915] [EC:6.3.1.2]
131840626  CAD; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
131838588  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
131827657  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
131827499  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
131840247  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
131832666  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
131823837  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
mlk00010  Glycolysis / Gluconeogenesis
mlk00020  Citrate cycle (TCA cycle)
mlk00220  Arginine biosynthesis
mlk00230  Purine metabolism
mlk00240  Pyrimidine metabolism
mlk00260  Glycine, serine and threonine metabolism
mlk00330  Arginine and proline metabolism
mlk00340  Histidine metabolism
mlk00410  beta-Alanine metabolism
mlk00470  D-Amino acid metabolism
mlk00480  Glutathione metabolism
mlk00520  Amino sugar and nucleotide sugar metabolism
mlk00620  Pyruvate metabolism
mlk00630  Glyoxylate and dicarboxylate metabolism
mlk00650  Butanoate metabolism
mlk00760  Nicotinate and nicotinamide metabolism
mlk00770  Pantothenate and CoA biosynthesis
mlk00860  Porphyrin metabolism
mlk00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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