KEGG   PATHWAY: umr00250
Entry
umr00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Ursus maritimus (polar bear)
Class
Metabolism; Amino acid metabolism
Pathway map
umr00250  Alanine, aspartate and glutamate metabolism
umr00250

Module
umr_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:umr00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Ursus maritimus (polar bear) [GN:umr]
Gene
103675855  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
103659119  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 [KO:K14454] [EC:2.6.1.1]
103673742  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
103657267  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
103670918  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
103677001  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
103678181  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
103658756  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
103673279  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
103673815  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
103656687  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
103662813  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
103664720  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
103670262  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
103670183  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
103668952  ADSS2; adenylosuccinate synthetase isozyme 2 isoform X2 [KO:K01939] [EC:6.3.4.4]
103676912  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
103676365  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
103676989  NAT8L; LOW QUALITY PROTEIN: N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
103669163  RIMKLB; beta-citrylglutamate synthase B [KO:K18310] [EC:6.3.1.17 6.3.2.41]
103670923  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
103675371  FOLH1B; putative N-acetylated-alpha-linked acidic dipeptidase isoform X1 [KO:K14592] [EC:3.4.17.21]
103667137  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
103676246  glutamate decarboxylase 1-like [KO:K01580] [EC:4.1.1.15]
103659552  GAD1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
103680146  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
103668578  ABAT; 4-aminobutyrate aminotransferase, mitochondrial isoform X1 [KO:K13524] [EC:2.6.1.19 2.6.1.22]
103665177  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
103668049  GLUD1; glutamate dehydrogenase 1, mitochondrial isoform X1 [KO:K00261] [EC:1.4.1.3]
103666818  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
103672426  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
103671649  CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
103656269  GLS2; glutaminase liver isoform, mitochondrial [KO:K01425] [EC:3.5.1.2]
103659932  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
103659822  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
103679991  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 isoform X1 [KO:K00820] [EC:2.6.1.16]
103671806  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 [KO:K00820] [EC:2.6.1.16]
103672749  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
umr00010  Glycolysis / Gluconeogenesis
umr00020  Citrate cycle (TCA cycle)
umr00220  Arginine biosynthesis
umr00230  Purine metabolism
umr00240  Pyrimidine metabolism
umr00260  Glycine, serine and threonine metabolism
umr00330  Arginine and proline metabolism
umr00340  Histidine metabolism
umr00410  beta-Alanine metabolism
umr00470  D-Amino acid metabolism
umr00480  Glutathione metabolism
umr00520  Amino sugar and nucleotide sugar metabolism
umr00620  Pyruvate metabolism
umr00630  Glyoxylate and dicarboxylate metabolism
umr00650  Butanoate metabolism
umr00760  Nicotinate and nicotinamide metabolism
umr00770  Pantothenate and CoA biosynthesis
umr00860  Porphyrin metabolism
umr00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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