KEGG   PATHWAY: oaa00250
Entry
oaa00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Ornithorhynchus anatinus (platypus)
Class
Metabolism; Amino acid metabolism
Pathway map
oaa00250  Alanine, aspartate and glutamate metabolism
oaa00250

Module
oaa_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:oaa00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Ornithorhynchus anatinus (platypus) [GN:oaa]
Gene
100076641  GOT1; aspartate aminotransferase, cytoplasmic [KO:K14454] [EC:2.6.1.1]
100090021  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 isoform X2 [KO:K14454] [EC:2.6.1.1]
100075744  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
100079395  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
100092192  DDO; D-aspartate oxidase isoform X1 [KO:K00272] [EC:1.4.3.1]
100089300  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
100078383  asparagine synthetase [glutamine-hydrolyzing] isoform X1 [KO:K01953] [EC:6.3.5.4]
103168209  LOW QUALITY PROTEIN: asparagine synthetase [glutamine-hydrolyzing]-like [KO:K01953] [EC:6.3.5.4]
100089644  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
100089316  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
100681695  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
103164662  alanine aminotransferase 1-like isoform X1 [KO:K00814] [EC:2.6.1.2]
100080454  AGXT; serine--pyruvate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
100078063  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
103168157  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
100091636  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
100083096  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
100091143  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
103170817  ADSL; adenylosuccinate lyase [KO:K01756] [EC:4.3.2.2]
100093218  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
100090307  RIMKLB; beta-citrylglutamate synthase B isoform X1 [KO:K18310] [EC:6.3.1.17 6.3.2.41]
100073839  RIMKLA; N-acetylaspartylglutamate synthase A isoform X1 [KO:K18311] [EC:6.3.2.41 6.3.2.42]
100081512  putative N-acetylated-alpha-linked acidic dipeptidase isoform X1 [KO:K14592] [EC:3.4.17.21]
100077458  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
100075098  GAD2; glutamate decarboxylase 2 isoform X1 [KO:K01580] [EC:4.1.1.15]
100077642  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
100075200  glutamate decarboxylase 1-like isoform X1 [KO:K01580] [EC:4.1.1.15]
100075373  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
114807396  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial [KO:K00139] [EC:1.2.1.24]
100079973  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
100092834  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X2 [KO:K00294] [EC:1.2.1.88]
100081935  GLUL; glutamine synthetase isoform X2 [KO:K01915] [EC:6.3.1.2]
100093029  glutamine synthetase-like [KO:K01915] [EC:6.3.1.2]
100085020  CAD; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
100088607  GLS; glutaminase kidney isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
103169199  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
100077228  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
100073861  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
100073443  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X1 [KO:K00820] [EC:2.6.1.16]
100092533  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
oaa00010  Glycolysis / Gluconeogenesis
oaa00020  Citrate cycle (TCA cycle)
oaa00220  Arginine biosynthesis
oaa00230  Purine metabolism
oaa00240  Pyrimidine metabolism
oaa00260  Glycine, serine and threonine metabolism
oaa00330  Arginine and proline metabolism
oaa00340  Histidine metabolism
oaa00410  beta-Alanine metabolism
oaa00470  D-Amino acid metabolism
oaa00480  Glutathione metabolism
oaa00520  Amino sugar and nucleotide sugar metabolism
oaa00620  Pyruvate metabolism
oaa00630  Glyoxylate and dicarboxylate metabolism
oaa00650  Butanoate metabolism
oaa00760  Nicotinate and nicotinamide metabolism
oaa00770  Pantothenate and CoA biosynthesis
oaa00860  Porphyrin metabolism
oaa00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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