KEGG   PATHWAY: cpla00280
Entry
cpla00280                   Pathway                                
Name
Valine, leucine and isoleucine degradation - Chiloscyllium plagiosum (whitespotted bambooshark)
Class
Metabolism; Amino acid metabolism
Pathway map
cpla00280  Valine, leucine and isoleucine degradation
cpla00280

Module
cpla_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:cpla00280]
cpla_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:cpla00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Chiloscyllium plagiosum (whitespotted bambooshark) [GN:cpla]
Gene
122561578  bcat1; branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
122542074  bcat2; branched-chain-amino-acid aminotransferase, mitochondrial [KO:K00826] [EC:2.6.1.42]
122542845  bckdha; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
122548384  bckdhb; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1 [KO:K00167] [EC:1.2.4.4]
122554527  dbt; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial isoform X1 [KO:K09699] [EC:2.3.1.168]
122563780  dldh; dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
122562770  acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K00248] [EC:1.3.8.1]
122554689  acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
122553828  ivd; isovaleryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K00253] [EC:1.3.8.4]
122561166  acadsb; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K09478] [EC:1.3.8.5]
122540762  acad8; isobutyryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K11538] [EC:1.3.99.-]
122540281  hadhaa; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a [KO:K07515] [EC:4.2.1.17 1.1.1.211]
122541833  echs1; LOW QUALITY PROTEIN: enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
122539468  hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
122542360  hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X1 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
122550164  acaa1; 3-ketoacyl-CoA thiolase, peroxisomal [KO:K07513] [EC:2.3.1.16]
122564480  acaa2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
122540288  hadhb; trifunctional enzyme subunit beta, mitochondrial isoform X1 [KO:K07509] [EC:2.3.1.16]
122550493  pcca; propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3]
122555798  pccb; propionyl-CoA carboxylase beta chain, mitochondrial [KO:K01966] [EC:6.4.1.3 2.1.3.15]
122562990  mcee; methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
122548688  mmut; methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
122551248  hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial [KO:K05605] [EC:3.1.2.4]
122550227  3-hydroxyisobutyrate dehydrogenase, mitochondrial-like [KO:K00020] [EC:1.1.1.31]
122548285  methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial-like [KO:K00140] [EC:1.2.1.18 1.2.1.27]
122562400  aldehyde dehydrogenase, mitochondrial-like [KO:K00128] [EC:1.2.1.3]
122563925  aldehyde dehydrogenase family 3 member A2-like [KO:K00128] [EC:1.2.1.3]
122563929  aldehyde dehydrogenase, dimeric NADP-preferring-like [KO:K00128] [EC:1.2.1.3]
122542182  aldh16a1; aldehyde dehydrogenase family 16 member A1 isoform X1 [KO:K00128] [EC:1.2.1.3]
122560822  aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
122554585  4-trimethylaminobutyraldehyde dehydrogenase-like [KO:K00149] [EC:1.2.1.47 1.2.1.3]
122551442  aldehyde oxidase 2-like [KO:K00157] [EC:1.2.3.1]
122558181  acsf3; malonate--CoA ligase ACSF3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
122560679  abat; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
122555995  mccc1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1 [KO:K01968] [EC:6.4.1.4]
122554404  si:ch211-198n5.11; methylcrotonoyl-coenzyme A carboxylase 2 isoform X1 [KO:K01969] [EC:6.4.1.4]
122558910  mccc2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
122561848  auh; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
122563693  hmgcl; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1 [KO:K01640] [EC:4.1.3.4]
122542040  hmgcll1; 3-hydroxy-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1 [KO:K01640] [EC:4.1.3.4]
122565524  succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial-like [KO:K01027] [EC:2.8.3.5]
122562705  aacs; acetoacetyl-CoA synthetase isoform X1 [KO:K01907] [EC:6.2.1.16]
122550709  acat1; acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
122552932  acat2; acetyl-CoA acetyltransferase, cytosolic isoform X1 [KO:K00626] [EC:2.3.1.9]
122557064  hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1 [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
cpla00020  Citrate cycle (TCA cycle)
cpla00240  Pyrimidine metabolism
cpla00290  Valine, leucine and isoleucine biosynthesis
cpla00640  Propanoate metabolism
cpla00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

DBGET integrated database retrieval system