KEGG   PATHWAY: oor00250
Entry
oor00250                    Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Orcinus orca (killer whale)
Class
Metabolism; Amino acid metabolism
Pathway map
oor00250  Alanine, aspartate and glutamate metabolism
oor00250

Module
oor_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:oor00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Orcinus orca (killer whale) [GN:oor]
Gene
101277576  GOT1; aspartate aminotransferase, cytoplasmic isoform X1 [KO:K14454] [EC:2.6.1.1]
101276910  GOT1L1; putative aspartate aminotransferase, cytoplasmic 2 isoform X1 [KO:K14454] [EC:2.6.1.1]
101287780  GOT2; aspartate aminotransferase, mitochondrial [KO:K14455] [EC:2.6.1.1]
101278148  IL4I1; L-amino-acid oxidase isoform X2 [KO:K03334] [EC:1.4.3.2]
101272245  L-amino-acid oxidase-like isoform X1 [KO:K03334] [EC:1.4.3.2]
101283041  DDO; D-aspartate oxidase isoform X2 [KO:K00272] [EC:1.4.3.1]
101278033  ASRGL1; isoaspartyl peptidase/L-asparaginase isoform X1 [KO:K13051] [EC:3.5.1.1 3.4.19.5]
101283050  ASNS; asparagine synthetase [glutamine-hydrolyzing] [KO:K01953] [EC:6.3.5.4]
101283591  NIT2; omega-amidase NIT2 [KO:K13566] [EC:3.5.1.3]
101287779  GPT2; alanine aminotransferase 2 [KO:K00814] [EC:2.6.1.2]
101275979  GPT; alanine aminotransferase 1 isoform X4 [KO:K00814] [EC:2.6.1.2]
101288519  AGXT; alanine--glyoxylate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
101275910  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
101282312  ASS1; argininosuccinate synthase isoform X2 [KO:K01940] [EC:6.3.4.5]
101271840  ASL; argininosuccinate lyase isoform X1 [KO:K01755] [EC:4.3.2.1]
101289375  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
101272802  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X4 [KO:K01939] [EC:6.3.4.4]
101285115  ADSL; adenylosuccinate lyase isoform X1 [KO:K01756] [EC:4.3.2.2]
101289374  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
101273054  RIMKLB; beta-citrylglutamate synthase B isoform X2 [KO:K18310] [EC:6.3.1.17 6.3.2.41]
101275823  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
101280978  glutamate carboxypeptidase 2 isoform X1 [KO:K14592] [EC:3.4.17.21]
125960271  glutamate carboxypeptidase 2-like [KO:K14592] [EC:3.4.17.21]
101275918  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
101276371  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
101287620  GAD1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
101272599  ABAT; 4-aminobutyrate aminotransferase, mitochondrial isoform X1 [KO:K13524] [EC:2.6.1.19 2.6.1.22]
101288482  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
101282232  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
101281495  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial [KO:K00294] [EC:1.2.1.88]
101288727  GLUL; glutamine synthetase isoform X2 [KO:K01915] [EC:6.3.1.2]
101271999  CAD; CAD protein isoform X1 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
101272028  GLS; glutaminase kidney isoform, mitochondrial isoform X2 [KO:K01425] [EC:3.5.1.2]
101280405  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
101279675  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
101288101  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 [KO:K00820] [EC:2.6.1.16]
101276031  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X2 [KO:K00820] [EC:2.6.1.16]
101288127  PPAT; amidophosphoribosyltransferase [KO:K00764] [EC:2.4.2.14]
101269594  LOW QUALITY PROTEIN: amidophosphoribosyltransferase-like [KO:K00764] [EC:2.4.2.14]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
oor00010  Glycolysis / Gluconeogenesis
oor00020  Citrate cycle (TCA cycle)
oor00220  Arginine biosynthesis
oor00230  Purine metabolism
oor00240  Pyrimidine metabolism
oor00260  Glycine, serine and threonine metabolism
oor00330  Arginine and proline metabolism
oor00340  Histidine metabolism
oor00410  beta-Alanine metabolism
oor00470  D-Amino acid metabolism
oor00480  Glutathione metabolism
oor00520  Amino sugar and nucleotide sugar metabolism
oor00620  Pyruvate metabolism
oor00630  Glyoxylate and dicarboxylate metabolism
oor00650  Butanoate metabolism
oor00760  Nicotinate and nicotinamide metabolism
oor00770  Pantothenate and CoA biosynthesis
oor00860  Porphyrin metabolism
oor00910  Nitrogen metabolism
KO pathway
ko00250   
LinkDB

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